{"id":"https://openalex.org/W93341040","doi":null,"title":"[An adult case of Williams-Campbell syndrome associated with pulmonary hypertension and a severe decrease in ventilatory response].","display_name":"[An adult case of Williams-Campbell syndrome associated with pulmonary hypertension and a severe decrease in ventilatory response].","publication_year":1997,"publication_date":"1997-11-01","ids":{"openalex":"https://openalex.org/W93341040","mag":"93341040","pmid":"https://pubmed.ncbi.nlm.nih.gov/9493457"},"language":"ja","primary_location":{"id":"pmid:9493457","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/9493457","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Nihon Kyobu Shikkan Gakkai zasshi","raw_type":"Case Reports"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":null,"display_name":"S Amano","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210131904","display_name":"Numazu City Hospital","ror":"https://ror.org/03btaj690","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210131904"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"S Amano","raw_affiliation_strings":["Department of Medicine, Numazu-city Hospital, Shizuoka, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Medicine, Numazu-city Hospital, Shizuoka, Japan","institution_ids":["https://openalex.org/I4210131904"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5102921300","display_name":"Yuki Yoshida","orcid":"https://orcid.org/0000-0002-7857-0842","observed_orcids":["https://orcid.org/0000-0002-7857-0842"]},"institutions":[{"id":"https://openalex.org/I4210131904","display_name":"Numazu City Hospital","ror":"https://ror.org/03btaj690","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210131904"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"Y Yoshida","raw_affiliation_strings":["Department of Medicine, Numazu-city Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Medicine, Numazu-city Hospital","institution_ids":["https://openalex.org/I4210131904"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5068411111","display_name":"Hiroaki Shimizu","orcid":"https://orcid.org/0000-0002-8550-4181","observed_orcids":["https://orcid.org/0000-0002-8550-4181"]},"institutions":[{"id":"https://openalex.org/I4210131904","display_name":"Numazu City Hospital","ror":"https://ror.org/03btaj690","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210131904"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"H Shimizu","raw_affiliation_strings":["Department of Medicine, Numazu-city Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Medicine, Numazu-city Hospital","institution_ids":["https://openalex.org/I4210131904"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5025274406","display_name":"T Takeda","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210131904","display_name":"Numazu City Hospital","ror":"https://ror.org/03btaj690","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210131904"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"T Takeda","raw_affiliation_strings":["Department of Respiratory Surgery, Numazu-city Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Respiratory Surgery, Numazu-city Hospital","institution_ids":["https://openalex.org/I4210131904"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5009431062","display_name":"Norikazu Urabe","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210131904","display_name":"Numazu City Hospital","ror":"https://ror.org/03btaj690","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210131904"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"N Urabe","raw_affiliation_strings":["Department of Respiratory Surgery, Numazu-city Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Respiratory Surgery, Numazu-city Hospital","institution_ids":["https://openalex.org/I4210131904"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5076378478","display_name":"Akira Mizoo","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I159385669","display_name":"Chiba University","ror":"https://ror.org/01hjzeq58","country_code":"JP","type":"education","lineage":["https://openalex.org/I159385669"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"A Mizoo","raw_affiliation_strings":["Department of Chest Medicine, Chiba University School of Medicine"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Chest Medicine, Chiba University School of Medicine","institution_ids":["https://openalex.org/I159385669"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5036834366","display_name":"Hiroshi Kimura","orcid":"https://orcid.org/0009-0001-1010-2540","observed_orcids":["https://orcid.org/0009-0001-1010-2540"]},"institutions":[{"id":"https://openalex.org/I159385669","display_name":"Chiba University","ror":"https://ror.org/01hjzeq58","country_code":"JP","type":"education","lineage":["https://openalex.org/I159385669"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"H Kimura","raw_affiliation_strings":["Department of Chest Medicine, Chiba University School of Medicine"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Chest Medicine, Chiba University School of Medicine","institution_ids":["https://openalex.org/I159385669"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5111488357","display_name":"T Kuriyama","orcid":"https://orcid.org/0000-0001-9391-3930","observed_orcids":["https://orcid.org/0000-0001-9391-3930"]},"institutions":[{"id":"https://openalex.org/I159385669","display_name":"Chiba University","ror":"https://ror.org/01hjzeq58","country_code":"JP","type":"education","lineage":["https://openalex.org/I159385669"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"T Kuriyama","raw_affiliation_strings":["Department of Chest Medicine, Chiba University School of Medicine"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Chest Medicine, Chiba University School of Medicine","institution_ids":["https://openalex.org/I159385669"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":9,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":95},"biblio":{"volume":"35","issue":"11","first_page":"1265","last_page":"70"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10665","display_name":"Cystic Fibrosis Research Advances","score":0.9394999742507935,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10665","display_name":"Cystic Fibrosis Research Advances","score":0.9394999742507935,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11260","display_name":"Tracheal and airway disorders","score":0.03440000116825104,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T13759","display_name":"Medical Imaging and Pathology Studies","score":0.0031999999191612005,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/williams-campbell-syndrome","display_name":"Williams-Campbell syndrome","score":0.9990000128746033},{"id":"https://openalex.org/keywords/bronchiectasis","display_name":"bronchiectasis","score":0.8339999914169312},{"id":"https://openalex.org/keywords/pulmonary-hypertension","display_name":"pulmonary hypertension","score":0.9279999732971191},{"id":"https://openalex.org/keywords/ventilatory-response","display_name":"ventilatory response","score":0.7720000147819519},{"id":"https://openalex.org/keywords/hypercapnic-respiratory-failure","display_name":"hypercapnic respiratory failure","score":0.925000011920929},{"id":"https://openalex.org/keywords/bronchography","display_name":"bronchography","score":0.597000002861023},{"id":"https://openalex.org/keywords/cystic-bronchiectasis","display_name":"cystic bronchiectasis","score":0.7009999752044678}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9552749395370483},{"id":"https://openalex.org/C2779379686","wikidata":"https://www.wikidata.org/wiki/Q32778","display_name":"Bronchiectasis","level":3,"score":0.7538508176803589},{"id":"https://openalex.org/C2780930700","wikidata":"https://www.wikidata.org/wiki/Q1128595","display_name":"Pulmonary hypertension","level":2,"score":0.664629340171814},{"id":"https://openalex.org/C7836513","wikidata":"https://www.wikidata.org/wiki/Q1641506","display_name":"Hypoxia (environmental)","level":3,"score":0.5761945247650146},{"id":"https://openalex.org/C164705383","wikidata":"https://www.wikidata.org/wiki/Q10379","display_name":"Cardiology","level":1,"score":0.5506935119628906},{"id":"https://openalex.org/C75603125","wikidata":"https://www.wikidata.org/wiki/Q1877462","display_name":"Pulmonary function testing","level":2,"score":0.5028371214866638},{"id":"https://openalex.org/C2776164194","wikidata":"https://www.wikidata.org/wiki/Q2501440","display_name":"Expiration","level":3,"score":0.46421387791633606},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.4276656210422516},{"id":"https://openalex.org/C534529494","wikidata":"https://www.wikidata.org/wiki/Q7891","display_name":"Respiratory system","level":2,"score":0.41374871134757996},{"id":"https://openalex.org/C2777714996","wikidata":"https://www.wikidata.org/wiki/Q7886","display_name":"Lung","level":2,"score":0.3382088541984558},{"id":"https://openalex.org/C540031477","wikidata":"https://www.wikidata.org/wiki/Q629","display_name":"Oxygen","level":2,"score":0.0592191219329834},{"id":"https://openalex.org/C185592680","wikidata":"https://www.wikidata.org/wiki/Q2329","display_name":"Chemistry","level":0,"score":0.0},{"id":"https://openalex.org/C178790620","wikidata":"https://www.wikidata.org/wiki/Q11351","display_name":"Organic chemistry","level":1,"score":0.0}],"mesh":[{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000860","descriptor_name":"Hypoxia","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D001982","descriptor_name":"Bronchial Diseases","qualifier_ui":"Q000151","qualifier_name":"congenital","is_major_topic":false},{"descriptor_ui":"D001987","descriptor_name":"Bronchiectasis","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D001987","descriptor_name":"Bronchiectasis","qualifier_ui":"Q000151","qualifier_name":"congenital","is_major_topic":false},{"descriptor_ui":"D002357","descriptor_name":"Cartilage Diseases","qualifier_ui":"Q000151","qualifier_name":"congenital","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006935","descriptor_name":"Hypercapnia","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D006976","descriptor_name":"Hypertension, Pulmonary","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":true},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D012131","descriptor_name":"Respiratory Insufficiency","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":true},{"descriptor_ui":"D013577","descriptor_name":"Syndrome","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"pmid:9493457","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/9493457","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Nihon Kyobu Shikkan Gakkai zasshi","raw_type":"Case Reports"},{"id":"mag:93341040","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/9493457","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":"PubMed","raw_type":null}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":0.98580002784729}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":8,"referenced_works":["https://openalex.org/W1765340466","https://openalex.org/W1950707731","https://openalex.org/W1980186845","https://openalex.org/W1992968518","https://openalex.org/W2082439565","https://openalex.org/W2087497300","https://openalex.org/W2111051358","https://openalex.org/W2112816675"],"related_works":["https://openalex.org/W2975427295","https://openalex.org/W2410808653","https://openalex.org/W3096444524","https://openalex.org/W2535168303","https://openalex.org/W2277107016","https://openalex.org/W2016606894","https://openalex.org/W2465514222","https://openalex.org/W4413125074","https://openalex.org/W4400143412","https://openalex.org/W1488050658"],"abstract_inverted_index":{"Williams-Campbell":[0,80],"syndrome":[1],"is":[2,17],"a":[3,10,30,33],"unique":[4],"form":[5],"of":[6,79],"bronchiectasis":[7],"caused":[8],"by":[9],"congenital":[11],"defect":[12],"in":[13,19,51,55],"bronchial":[14],"cartilage,":[15],"and":[16,32,74,98,101,104],"rare":[18],"Japan.":[20],"A":[21],"34-year-old":[22],"man":[23],"was":[24,115],"admitted":[25],"to":[26,95],"our":[27],"hospital":[28],"with":[29,70],"fever,":[31],"productive":[34],"cough.":[35],"Arterial":[36],"blood":[37],"gas":[38],"analysis":[39],"revealed":[40,63],"severe":[41,83],"type":[42],"II-respiratory":[43],"failure.":[44],"Many":[45],"thin-walled":[46],"cystic":[47,68],"shadows":[48],"(5-60":[49],"mm":[50],"diameter)":[52],"were":[53,106],"present":[54],"the":[56,110],"entire":[57],"lung":[58],"field.":[59],"Pulmonary":[60],"function":[61],"tests":[62],"obstructive":[64],"impairment.":[65],"Bronchograms":[66],"demonstrated":[67],"bronchiectasis,":[69],"ballooning":[71],"on":[72,76],"inspiration":[73],"collapse":[75],"expiration,":[77],"characteristic":[78],"syndrome.":[81],"Despite":[82],"hypoxia,":[84],"he":[85],"did":[86],"not":[87],"suffer":[88],"from":[89],"dyspnea.":[90],"We":[91],"examined":[92],"ventilatory":[93],"response":[94],"hypercapnea":[96],"(HCVR)":[97],"hypoxia":[99],"(HVR),":[100],"both":[102],"HCVR":[103],"HVR":[105],"abnormal.":[107],"In":[108],"addition,":[109],"mean":[111],"pulmonary":[112,119],"artery":[113],"pressure":[114],"26":[116],"mmHg,":[117],"indicating":[118],"hypertension.":[120]},"counts_by_year":[{"year":2024,"cited_by_count":1},{"year":2022,"cited_by_count":1},{"year":2020,"cited_by_count":1},{"year":2014,"cited_by_count":2},{"year":2012,"cited_by_count":2}],"updated_date":"2026-11-02T09:45:03.842371","created_date":"2016-06-24T00:00:00"}
