{"id":"https://openalex.org/W7225830737","doi":"https://doi.org/10.5281/zenodo.24135433","title":"Bilateral Orbital Involvement with Severe Visual Impairment and Anterior Staphyloma in a 13-year-old boy with Acute Myeloid Leukaemia: A Case Report","display_name":"Bilateral Orbital Involvement with Severe Visual Impairment and Anterior Staphyloma in a 13-year-old boy with Acute Myeloid Leukaemia: A Case Report","publication_year":2026,"publication_date":"2026-11-11","ids":{"openalex":"https://openalex.org/W7225830737","doi":"https://doi.org/10.5281/zenodo.24135433"},"language":"en","primary_location":{"id":"doi:10.5281/zenodo.24135433","doi":"https://doi.org/10.5281/zenodo.24135433","is_oa":true,"landing_page_url":"https://doi.org/10.5281/zenodo.24135433","pdf_url":null,"source":{"id":"https://openalex.org/S4306400562","display_name":"Zenodo (CERN European Organization for Nuclear Research)","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I67311998","host_organization_name":"European Organization for Nuclear Research","host_organization_lineage":["https://openalex.org/I67311998"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":null,"is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":"JournalArticle"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["datacite"],"open_access":{"is_oa":true,"oa_status":"green","oa_url":"https://doi.org/10.5281/zenodo.24135433","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5115579434","display_name":"Haziel Rynjah","orcid":"https://orcid.org/0009-0004-8249-7010","observed_orcids":["https://orcid.org/0009-0004-8249-7010"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Haziel Rynjah","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5158991691","display_name":"Rojita Athokpam","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Rojita Athokpam","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5140167952","display_name":"Wapang T. Jamir","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Wapang T Jamir","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":0,"institutions_distinct_count":0,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11328","display_name":"Ocular Oncology and Treatments","score":0.9829000234603882,"subfield":{"id":"https://openalex.org/subfields/2731","display_name":"Ophthalmology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11328","display_name":"Ocular Oncology and Treatments","score":0.9829000234603882,"subfield":{"id":"https://openalex.org/subfields/2731","display_name":"Ophthalmology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10309","display_name":"Acute Myeloid Leukemia Research","score":0.00430000014603138,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12599","display_name":"Retinal and Optic Conditions","score":0.002400000113993883,"subfield":{"id":"https://openalex.org/subfields/2731","display_name":"Ophthalmology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9373999834060669},{"id":"https://openalex.org/C2781302119","wikidata":"https://www.wikidata.org/wiki/Q48228","display_name":"Eyelid","level":2,"score":0.490200012922287},{"id":"https://openalex.org/C2779399171","wikidata":"https://www.wikidata.org/wiki/Q1483951","display_name":"Malignancy","level":2,"score":0.4634000062942505},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.45179998874664307},{"id":"https://openalex.org/C2778729363","wikidata":"https://www.wikidata.org/wiki/Q11688946","display_name":"Myeloid leukemia","level":2,"score":0.4059000015258789},{"id":"https://openalex.org/C509974204","wikidata":"https://www.wikidata.org/wiki/Q180507","display_name":"Radiation therapy","level":2,"score":0.4009999930858612},{"id":"https://openalex.org/C527108885","wikidata":"https://www.wikidata.org/wiki/Q835153","display_name":"Physical examination","level":2,"score":0.3833000063896179},{"id":"https://openalex.org/C206179267","wikidata":"https://www.wikidata.org/wiki/Q188952","display_name":"Medical history","level":2,"score":0.31859999895095825},{"id":"https://openalex.org/C2776694085","wikidata":"https://www.wikidata.org/wiki/Q974135","display_name":"Chemotherapy","level":2,"score":0.3070000112056732},{"id":"https://openalex.org/C2778257484","wikidata":"https://www.wikidata.org/wiki/Q555066","display_name":"Visual acuity","level":2,"score":0.29409998655319214},{"id":"https://openalex.org/C2779282312","wikidata":"https://www.wikidata.org/wiki/Q1956561","display_name":"Myeloid","level":2,"score":0.29339998960494995},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.27549999952316284},{"id":"https://openalex.org/C2776391266","wikidata":"https://www.wikidata.org/wiki/Q9612","display_name":"Fundus (uterus)","level":2,"score":0.2678000032901764},{"id":"https://openalex.org/C2775908122","wikidata":"https://www.wikidata.org/wiki/Q3070621","display_name":"External beam radiotherapy","level":4,"score":0.265500009059906},{"id":"https://openalex.org/C143409427","wikidata":"https://www.wikidata.org/wiki/Q161238","display_name":"Magnetic resonance imaging","level":2,"score":0.26499998569488525},{"id":"https://openalex.org/C2776148792","wikidata":"https://www.wikidata.org/wiki/Q3041498","display_name":"Eye disease","level":2,"score":0.26440000534057617},{"id":"https://openalex.org/C196644772","wikidata":"https://www.wikidata.org/wiki/Q3884964","display_name":"Orbit (dynamics)","level":2,"score":0.2615000009536743},{"id":"https://openalex.org/C126838900","wikidata":"https://www.wikidata.org/wiki/Q77604","display_name":"Radiology","level":1,"score":0.2574999928474426},{"id":"https://openalex.org/C2778461978","wikidata":"https://www.wikidata.org/wiki/Q29496","display_name":"Leukemia","level":2,"score":0.2522999942302704},{"id":"https://openalex.org/C2778938557","wikidata":"https://www.wikidata.org/wiki/Q1439392","display_name":"Anterior cranial fossa","level":3,"score":0.25049999356269836}],"mesh":[],"locations_count":2,"locations":[{"id":"doi:10.5281/zenodo.24135433","doi":"https://doi.org/10.5281/zenodo.24135433","is_oa":true,"landing_page_url":"https://doi.org/10.5281/zenodo.24135433","pdf_url":null,"source":{"id":"https://openalex.org/S4306400562","display_name":"Zenodo (CERN European Organization for Nuclear Research)","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I67311998","host_organization_name":"European Organization for Nuclear Research","host_organization_lineage":["https://openalex.org/I67311998"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":null,"is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":"JournalArticle"},{"id":"doi:10.5281/zenodo.24135434","doi":"https://doi.org/10.5281/zenodo.24135434","is_oa":true,"landing_page_url":"https://doi.org/10.5281/zenodo.24135434","pdf_url":null,"source":{"id":"https://openalex.org/S4306400562","display_name":"Zenodo (CERN European Organization for Nuclear Research)","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I67311998","host_organization_name":"European Organization for Nuclear Research","host_organization_lineage":["https://openalex.org/I67311998"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":null,"is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":"JournalArticle"}],"best_oa_location":{"id":"doi:10.5281/zenodo.24135433","doi":"https://doi.org/10.5281/zenodo.24135433","is_oa":true,"landing_page_url":"https://doi.org/10.5281/zenodo.24135433","pdf_url":null,"source":{"id":"https://openalex.org/S4306400562","display_name":"Zenodo (CERN European Organization for Nuclear Research)","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I67311998","host_organization_name":"European Organization for Nuclear Research","host_organization_lineage":["https://openalex.org/I67311998"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":null,"is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":"JournalArticle"},"sustainable_development_goals":[],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":[],"abstract_inverted_index":{"Background:":[0],"Acute":[1],"myeloid":[2,45,218],"leukaemia":[3,46],"(AML)":[4],"is":[5,23],"a":[6,40],"haematological":[7],"malignancy":[8],"that":[9],"can":[10],"involve":[11],"extramedullary":[12],"tissues,":[13],"including":[14,164],"the":[15,53,134,187,201,208],"orbit":[16],"and":[17,70,73,111,139,156,168,177,194,225,239,248],"ocular":[18,109,179,237],"structures.":[19],"Orbital":[20],"leukemic":[21,116,144,234],"infiltration":[22],"an":[24],"uncommon":[25],"but":[26],"potentially":[27],"vision-threatening":[28],"manifestation,":[29],"particularly":[30],"in":[31,55,92,149,184,200,214],"paediatric":[32],"patients.":[33],"Case":[34],"Presentation:":[35],"A":[36,171],"13-year-old":[37],"male":[38],"with":[39,48,151,216,221],"known":[41],"history":[42],"of":[43,52,68,115,210,231],"acute":[44,217],"presented":[47],"gradually":[49],"progressive":[50],"swelling":[51,224],"eyelids":[54],"both":[56,93],"eyes":[57],"over":[58],"eight":[59],"months.":[60],"The":[61,158],"patient":[62,159],"had":[63],"previously":[64],"received":[65],"four":[66],"doses":[67],"chemotherapy":[69],"radiation":[71],"therapy":[72],"was":[74,123,146,175,182],"undergoing":[75],"oral":[76],"metronomic":[77],"treatment.":[78],"Ophthalmological":[79],"examination":[80,97],"revealed":[81,105],"severely":[82],"reduced":[83],"visual":[84,119,128,173,195,227],"acuity,":[85],"limited":[86],"to":[87,126,186],"hand":[88],"movement":[89],"perception":[90],"(HM+)":[91],"eyes.":[94],"Anterior":[95],"segment":[96],"documented":[98,199],"bilateral":[99,142],"localized":[100,152],"anterior":[101,153],"staphyloma.":[102,154],"B-scan":[103],"ultrasonography":[104],"vitreous":[106],"echoes,":[107],"structural":[108],"changes,":[110],"orbital":[112,143,233],"findings":[113],"suggestive":[114],"infiltration.":[117],"Flash":[118],"evoked":[120],"potential":[121],"testing":[122],"also":[124],"performed":[125],"assess":[127],"pathway":[129],"function.":[130],"Diagnosis:":[131],"Based":[132],"on":[133],"clinical":[135,246],"history,":[136],"ophthalmological":[137,162],"examination,":[138],"ultrasonographic":[140],"findings,":[141],"involvement":[145],"clinically":[147],"assessed":[148],"association":[150],"Management":[155],"Outcome:":[157],"underwent":[160],"multidisciplinary":[161,241],"evaluation,":[163],"recommendations":[165],"for":[166,245],"oculoplastic":[167],"corneal":[169],"consultations.":[170],"guarded":[172],"prognosis":[174],"explained,":[176],"further":[178],"surgical":[180],"intervention":[181],"considered":[183],"relation":[185],"patient's":[188],"systemic":[189],"condition.":[190],"Subsequent":[191],"treatment":[192,249],"response":[193],"outcome":[196],"were":[197],"not":[198],"available":[202],"records.":[203],"Conclusion:":[204],"This":[205],"case":[206],"highlights":[207],"importance":[209],"comprehensive":[211],"ophthalmic":[212],"evaluation":[213],"children":[215],"leukemia":[219],"presenting":[220],"persistent":[222],"eyelid":[223],"severe":[226],"impairment.":[228],"Early":[229],"recognition":[230],"suspected":[232],"infiltration,":[235],"appropriate":[236],"imaging,":[238],"coordinated":[240],"management":[242],"are":[243],"essential":[244],"assessment":[247],"planning.":[250]},"counts_by_year":[],"updated_date":"2026-11-12T12:28:57.059296","created_date":"2026-11-12T00:00:00"}
