{"id":"https://openalex.org/W7225776128","doi":"https://doi.org/10.1111/bjh.70939","title":"Clinical phenotypes, autoimmunity and outcomes in Rosai\u2013Dorfman disease: An international multicentre cohort study","display_name":"Clinical phenotypes, autoimmunity and outcomes in Rosai\u2013Dorfman disease: An international multicentre cohort study","publication_year":2026,"publication_date":"2026-11-11","ids":{"openalex":"https://openalex.org/W7225776128","doi":"https://doi.org/10.1111/bjh.70939"},"language":"en","primary_location":{"id":"doi:10.1111/bjh.70939","doi":"https://doi.org/10.1111/bjh.70939","is_oa":false,"landing_page_url":"https://doi.org/10.1111/bjh.70939","pdf_url":null,"source":{"id":"https://openalex.org/S153015021","display_name":"British Journal of Haematology","issn_l":"0007-1048","issn":["0007-1048","1365-2141"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-1","medline","norway-1","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"British Journal of Haematology","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5008986795","display_name":"Mitali Sen","orcid":"https://orcid.org/0000-0002-0510-5958","observed_orcids":["https://orcid.org/0000-0002-0510-5958"]},"institutions":[{"id":"https://openalex.org/I32389192","display_name":"University of Alabama at Birmingham","ror":"https://ror.org/008s83205","country_code":"US","type":"education","lineage":["https://openalex.org/I32389192"]},{"id":"https://openalex.org/I4390039250","display_name":"UAB Medicine","ror":"https://ror.org/036554539","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I4390039250"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Mitali Sen","raw_affiliation_strings":["Division of Clinical Immunology and Rheumatology University of Alabama at Birmingham  Birmingham Alabama USA"],"raw_orcid":"https://orcid.org/0000-0002-0510-5958","affiliations":[{"raw_affiliation_string":"Division of Clinical Immunology and Rheumatology University of Alabama at Birmingham  Birmingham Alabama USA","institution_ids":["https://openalex.org/I32389192","https://openalex.org/I4390039250"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5002128895","display_name":"Gordon J. Ruan","orcid":"https://orcid.org/0000-0002-6969-9169","observed_orcids":["https://orcid.org/0000-0002-6969-9169"]},"institutions":[{"id":"https://openalex.org/I4210100549","display_name":"Frauenshuh Cancer Center","ror":"https://ror.org/00yd0be35","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I4210100549"]},{"id":"https://openalex.org/I52792670","display_name":"HealthPartners","ror":"https://ror.org/03s9ada67","country_code":"US","type":"nonprofit","lineage":["https://openalex.org/I52792670"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Gordon J. Ruan","raw_affiliation_strings":["HealthPartners Frauenshuh Cancer Center  St Louis Park Minnesota USA"],"raw_orcid":"https://orcid.org/0000-0002-6969-9169","affiliations":[{"raw_affiliation_string":"HealthPartners Frauenshuh Cancer Center  St Louis Park Minnesota USA","institution_ids":["https://openalex.org/I4210100549","https://openalex.org/I52792670"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5088950360","display_name":"Samuel Benjamin Reynolds","orcid":"https://orcid.org/0000-0002-8652-183X","observed_orcids":["https://orcid.org/0000-0002-8652-183X"]},"institutions":[{"id":"https://openalex.org/I3019308854","display_name":"Moffitt Cancer Center","ror":"https://ror.org/01xf75524","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I3019308854"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Samuel B. Reynolds","raw_affiliation_strings":["Division of Hematology and Oncology Moffitt Cancer Center  Tampa Florida USA"],"raw_orcid":"https://orcid.org/0000-0002-8652-183X","affiliations":[{"raw_affiliation_string":"Division of Hematology and Oncology Moffitt Cancer Center  Tampa Florida USA","institution_ids":["https://openalex.org/I3019308854"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5113162514","display_name":"Haadi Ali","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I27837315","display_name":"University of Michigan","ror":"https://ror.org/00jmfr291","country_code":"US","type":"education","lineage":["https://openalex.org/I27837315"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Haadi Ali","raw_affiliation_strings":["Division of Hematology and Oncology University of Michigan  Ann Arbor Michigan USA"],"raw_orcid":"https://orcid.org/0009-0001-1723-6736","affiliations":[{"raw_affiliation_string":"Division of Hematology and Oncology University of Michigan  Ann Arbor Michigan USA","institution_ids":["https://openalex.org/I27837315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148637859","display_name":"Xi Yang","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I27837315","display_name":"University of Michigan","ror":"https://ror.org/00jmfr291","country_code":"US","type":"education","lineage":["https://openalex.org/I27837315"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Xi Yang","raw_affiliation_strings":["Division of Hematology and Oncology University of Michigan  Ann Arbor Michigan USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Hematology and Oncology University of Michigan  Ann Arbor Michigan USA","institution_ids":["https://openalex.org/I27837315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5058645403","display_name":"Diana M. Morlote","orcid":"https://orcid.org/0000-0001-9226-8001","observed_orcids":["https://orcid.org/0000-0001-9226-8001"]},"institutions":[{"id":"https://openalex.org/I32389192","display_name":"University of Alabama at Birmingham","ror":"https://ror.org/008s83205","country_code":"US","type":"education","lineage":["https://openalex.org/I32389192"]},{"id":"https://openalex.org/I4390039250","display_name":"UAB Medicine","ror":"https://ror.org/036554539","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I4390039250"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Diana Morlote","raw_affiliation_strings":["Department of Pathology University of Alabama at Birmingham  Birmingham Alabama USA"],"raw_orcid":"https://orcid.org/0000-0001-9226-8001","affiliations":[{"raw_affiliation_string":"Department of Pathology University of Alabama at Birmingham  Birmingham Alabama USA","institution_ids":["https://openalex.org/I32389192","https://openalex.org/I4390039250"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5090092577","display_name":"Aishwarya Ravindran","orcid":"https://orcid.org/0000-0003-4503-440X","observed_orcids":["https://orcid.org/0000-0003-4503-440X"]},"institutions":[{"id":"https://openalex.org/I1330342723","display_name":"Mayo Clinic","ror":"https://ror.org/02qp3tb03","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Aishwarya Ravindran","raw_affiliation_strings":["Department of Laboratory Medicine and Pathology Mayo Clinic  Rochester Minnesota USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Laboratory Medicine and Pathology Mayo Clinic  Rochester Minnesota USA","institution_ids":["https://openalex.org/I1330342723"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5040342262","display_name":"Lauren Kelly Shea","orcid":"https://orcid.org/0000-0002-3584-9296","observed_orcids":["https://orcid.org/0000-0002-3584-9296"]},"institutions":[{"id":"https://openalex.org/I32389192","display_name":"University of Alabama at Birmingham","ror":"https://ror.org/008s83205","country_code":"US","type":"education","lineage":["https://openalex.org/I32389192"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Lauren Shea","raw_affiliation_strings":["Division of Hematology and Oncology University of Alabama at Birmingham  Birmingham Alabama USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Hematology and Oncology University of Alabama at Birmingham  Birmingham Alabama USA","institution_ids":["https://openalex.org/I32389192"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5013000204","display_name":"Matthew J. Koster","orcid":"https://orcid.org/0000-0002-2895-6755","observed_orcids":["https://orcid.org/0000-0002-2895-6755"]},"institutions":[{"id":"https://openalex.org/I1330342723","display_name":"Mayo Clinic","ror":"https://ror.org/02qp3tb03","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Matthew J. Koster","raw_affiliation_strings":["Division of Rheumatology Mayo Clinic  Rochester Minnesota USA"],"raw_orcid":"https://orcid.org/0000-0002-2895-6755","affiliations":[{"raw_affiliation_string":"Division of Rheumatology Mayo Clinic  Rochester Minnesota USA","institution_ids":["https://openalex.org/I1330342723"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5010727520","display_name":"Jithma P. Abeykoon","orcid":"https://orcid.org/0000-0003-3939-6252","observed_orcids":["https://orcid.org/0000-0003-3939-6252"]},"institutions":[{"id":"https://openalex.org/I1330342723","display_name":"Mayo Clinic","ror":"https://ror.org/02qp3tb03","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723"]},{"id":"https://openalex.org/I4390039279","display_name":"Mayo Clinic Comprehensive Cancer Center (Minnesota)","ror":"https://ror.org/012wxv498","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723","https://openalex.org/I4390039279"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Jithma P. Abeykoon","raw_affiliation_strings":["Division of Hematology and Oncology Mayo Clinic  Rochester Minnesota USA"],"raw_orcid":"https://orcid.org/0000-0003-3939-6252","affiliations":[{"raw_affiliation_string":"Division of Hematology and Oncology Mayo Clinic  Rochester Minnesota USA","institution_ids":["https://openalex.org/I1330342723","https://openalex.org/I4390039279"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5103135411","display_name":"Hind Salama","orcid":"https://orcid.org/0000-0001-9698-0813","observed_orcids":["https://orcid.org/0000-0001-9698-0813"]},"institutions":[{"id":"https://openalex.org/I185203018","display_name":"King Saud bin Abdulaziz University for Health Sciences","ror":"https://ror.org/0149jvn88","country_code":"SA","type":"education","lineage":["https://openalex.org/I185203018"]},{"id":"https://openalex.org/I2802517405","display_name":"King Abdulaziz Medical City","ror":"https://ror.org/009djsq06","country_code":"SA","type":"healthcare","lineage":["https://openalex.org/I2802517405"]}],"countries":["SA"],"is_corresponding":false,"raw_author_name":"Hind Salama","raw_affiliation_strings":["Department of Oncology King Abdulaziz Medical City, King Saud bin Abdulaziz University  Riyadh Saudi Arabia"],"raw_orcid":"https://orcid.org/0000-0001-9698-0813","affiliations":[{"raw_affiliation_string":"Department of Oncology King Abdulaziz Medical City, King Saud bin Abdulaziz University  Riyadh Saudi Arabia","institution_ids":["https://openalex.org/I185203018","https://openalex.org/I2802517405"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5074426418","display_name":"Xinxin Cao","orcid":"https://orcid.org/0000-0001-7807-9714","observed_orcids":["https://orcid.org/0000-0001-7807-9714"]},"institutions":[{"id":"https://openalex.org/I2801228662","display_name":"Peking Union Medical College Hospital","ror":"https://ror.org/04jztag35","country_code":"CN","type":"healthcare","lineage":["https://openalex.org/I2801228662"]}],"countries":["CN"],"is_corresponding":false,"raw_author_name":"Xin\u2010Xin Cao","raw_affiliation_strings":["Department of Hematology Peking Union Medical College Hospital  Beijing China"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology Peking Union Medical College Hospital  Beijing China","institution_ids":["https://openalex.org/I2801228662"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5112334806","display_name":"Asra Z. Ahmed","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I27837315","display_name":"University of Michigan","ror":"https://ror.org/00jmfr291","country_code":"US","type":"education","lineage":["https://openalex.org/I27837315"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Asra Z. Ahmed","raw_affiliation_strings":["Division of Hematology and Oncology University of Michigan  Ann Arbor Michigan USA"],"raw_orcid":"https://orcid.org/0009-0002-9805-2636","affiliations":[{"raw_affiliation_string":"Division of Hematology and Oncology University of Michigan  Ann Arbor Michigan USA","institution_ids":["https://openalex.org/I27837315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5029802364","display_name":"Ronald S. Go","orcid":"https://orcid.org/0000-0002-8284-3495","observed_orcids":["https://orcid.org/0000-0002-8284-3495"]},"institutions":[{"id":"https://openalex.org/I1330342723","display_name":"Mayo Clinic","ror":"https://ror.org/02qp3tb03","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723"]},{"id":"https://openalex.org/I4390039279","display_name":"Mayo Clinic Comprehensive Cancer Center (Minnesota)","ror":"https://ror.org/012wxv498","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723","https://openalex.org/I4390039279"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Ronald S. Go","raw_affiliation_strings":["Division of Hematology and Oncology Mayo Clinic  Rochester Minnesota USA"],"raw_orcid":"https://orcid.org/0000-0002-8284-3495","affiliations":[{"raw_affiliation_string":"Division of Hematology and Oncology Mayo Clinic  Rochester Minnesota USA","institution_ids":["https://openalex.org/I1330342723","https://openalex.org/I4390039279"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5056210769","display_name":"Gaurav Goyal","orcid":"https://orcid.org/0000-0001-6148-5177","observed_orcids":["https://orcid.org/0000-0001-6148-5177"]},"institutions":[{"id":"https://openalex.org/I32389192","display_name":"University of Alabama at Birmingham","ror":"https://ror.org/008s83205","country_code":"US","type":"education","lineage":["https://openalex.org/I32389192"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Gaurav Goyal","raw_affiliation_strings":["Division of Hematology and Oncology University of Alabama at Birmingham  Birmingham Alabama USA"],"raw_orcid":"https://orcid.org/0000-0001-6148-5177","affiliations":[{"raw_affiliation_string":"Division of Hematology and Oncology University of Alabama at Birmingham  Birmingham Alabama USA","institution_ids":["https://openalex.org/I32389192"]}]}],"institutions":[],"countries_distinct_count":3,"institutions_distinct_count":11,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":{"value":5190,"currency":"USD","value_usd":5190},"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11909","display_name":"Histiocytic Disorders and Treatments","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11909","display_name":"Histiocytic Disorders and Treatments","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10980","display_name":"Vascular Malformations and Hemangiomas","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8953999876976013},{"id":"https://openalex.org/C2780130043","wikidata":"https://www.wikidata.org/wiki/Q192360","display_name":"Autoimmunity","level":3,"score":0.5719000101089478},{"id":"https://openalex.org/C163764329","wikidata":"https://www.wikidata.org/wiki/Q785022","display_name":"Autoantibody","level":3,"score":0.5715000033378601},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.5559999942779541},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.5152999758720398},{"id":"https://openalex.org/C45189115","wikidata":"https://www.wikidata.org/wiki/Q502159","display_name":"Serology","level":3,"score":0.48089998960494995},{"id":"https://openalex.org/C2778256501","wikidata":"https://www.wikidata.org/wiki/Q223911","display_name":"Sarcoma","level":2,"score":0.4465000033378601},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.4366999864578247},{"id":"https://openalex.org/C72563966","wikidata":"https://www.wikidata.org/wiki/Q1303415","display_name":"Cohort","level":2,"score":0.43529999256134033},{"id":"https://openalex.org/C167135981","wikidata":"https://www.wikidata.org/wiki/Q2146302","display_name":"Retrospective cohort study","level":2,"score":0.4350000023841858},{"id":"https://openalex.org/C201903717","wikidata":"https://www.wikidata.org/wiki/Q1778788","display_name":"Cohort study","level":2,"score":0.4115000069141388},{"id":"https://openalex.org/C2779075594","wikidata":"https://www.wikidata.org/wiki/Q8084905","display_name":"Autoimmune disease","level":3,"score":0.38199999928474426},{"id":"https://openalex.org/C2780648854","wikidata":"https://www.wikidata.org/wiki/Q2745824","display_name":"Immunopathology","level":2,"score":0.34389999508857727},{"id":"https://openalex.org/C121608353","wikidata":"https://www.wikidata.org/wiki/Q12078","display_name":"Cancer","level":2,"score":0.32989999651908875},{"id":"https://openalex.org/C8891405","wikidata":"https://www.wikidata.org/wiki/Q1059","display_name":"Immune system","level":2,"score":0.30480000376701355},{"id":"https://openalex.org/C143998085","wikidata":"https://www.wikidata.org/wiki/Q162555","display_name":"Oncology","level":1,"score":0.28110000491142273},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.262800008058548},{"id":"https://openalex.org/C2780140570","wikidata":"https://www.wikidata.org/wiki/Q3545481","display_name":"Surgical oncology","level":2,"score":0.2581999897956848}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.1111/bjh.70939","doi":"https://doi.org/10.1111/bjh.70939","is_oa":false,"landing_page_url":"https://doi.org/10.1111/bjh.70939","pdf_url":null,"source":{"id":"https://openalex.org/S153015021","display_name":"British Journal of Haematology","issn_l":"0007-1048","issn":["0007-1048","1365-2141"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-1","medline","norway-1","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"British Journal of Haematology","raw_type":"journal-article"}],"best_oa_location":null,"sustainable_development_goals":[],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":10,"referenced_works":["https://openalex.org/W2027921255","https://openalex.org/W2730295253","https://openalex.org/W2802582740","https://openalex.org/W2934777769","https://openalex.org/W2938722712","https://openalex.org/W3213913971","https://openalex.org/W4302306958","https://openalex.org/W4307434382","https://openalex.org/W4405318361","https://openalex.org/W4410152526"],"related_works":[],"abstract_inverted_index":{"Summary":[0],"Rosai\u2013Dorfman":[1],"disease":[2,50,113,119,160,163,206],"(RDD)":[3],"is":[4],"a":[5,22,177],"rare":[6],"histiocytic":[7],"neoplasm":[8],"with":[9,16,29,88,111,134,147,166,198],"diverse":[10],"clinical":[11,18,227],"behaviour":[12],"and":[13,45,64,130,170,192,208,220],"immune":[14],"abnormalities":[15,222],"unknown":[17],"significance.":[19],"We":[20],"performed":[21],"retrospective":[23],"cohort":[24],"study":[25],"of":[26,180,215],"162":[27],"patients":[28,54,125,132,146],"RDD":[30,216],"from":[31],"2003":[32],"to":[33],"2025":[34],"at":[35,139],"five":[36],"international":[37],"referral":[38],"centres.":[39],"Median":[40],"age":[41],"was":[42,69,121,164,189],"48":[43],"years":[44],"64.8%":[46],"were":[47,76,109,195],"female.":[48],"Multisystem":[49],"occurred":[51,152],"in":[52,123,153,226],"87":[53],"(53.7%),":[55],"commonly":[56,87],"involving":[57],"skin/subcutaneous":[58],"tissue":[59],"(49.4%),":[60],"lymph":[61],"nodes":[62],"(39.5%)":[63],"bones":[65],"(34%).":[66],"Molecular":[67],"testing":[68],"available":[70,135],"for":[71],"102":[72],"patients;":[73],"40":[74],"(39.2%)":[75],"mitogen\u2010activated":[77,99],"protein":[78,100],"kinase/rat":[79],"sarcoma":[80,91],"virus":[81],"oncogene":[82,93],"homolog":[83,94],"signaling":[84],"pathway":[85],"(MAPK/RAS)\u2010altered,":[86],"kirsten":[89],"rat":[90],"viral":[92],"(":[95,103,114],"KRAS":[96],")":[97,105],"or":[98,200],"kinase":[101],"1":[102],"MAP2K/MEK":[104],"alterations.":[106],"MAPK/RAS":[107],"alterations":[108],"associated":[110,165,197],"multisystem":[112,174],"p":[115],"=":[116],"0.0034).":[117],"Autoimmune":[118],"(AID)":[120],"documented":[122],"29":[124],"(17.9%),":[126],"usually":[127],"preceding":[128],"RDD,":[129],"45/95":[131],"(47.4%)":[133],"autoantibody":[136,193],"status":[137,210],"had":[138],"least":[140],"one":[141],"positive":[142],"autoantibody.":[143],"Among":[144],"153":[145],"response":[148,151,199],"data,":[149],"objective":[150],"94":[154],"(61.4%).":[155],"Response":[156],"distribution":[157],"differed":[158],"by":[159],"extent;":[161],"single\u2010system":[162],"more":[167],"complete":[168],"responses":[169],"less":[171],"progression":[172],"than":[173],"disease.":[175],"At":[176],"median":[178],"follow\u2010up":[179],"2.49":[181],"years,":[182],"eight":[183],"deaths":[184],"occurred;":[185],"5\u2010year":[186],"overall":[187,201],"survival":[188],"93.4%.":[190],"AID":[191],"positivity":[194],"not":[196],"survival.":[202],"These":[203],"findings":[204],"support":[205],"extent":[207],"molecular":[209],"as":[211],"clinically":[212],"relevant":[213],"dimensions":[214],"assessment,":[217],"while":[218],"autoimmune":[219],"serological":[221],"should":[223],"be":[224],"interpreted":[225],"context.":[228]},"counts_by_year":[],"updated_date":"2026-11-12T12:28:57.059296","created_date":"2026-11-12T00:00:00"}
