{"id":"https://openalex.org/W7225333583","doi":"https://doi.org/10.1111/cup.70233","title":"Histiocytoid Sweet Syndrome: A Distinct Entity Within the Spectrum of Myeloid Dermatoses","display_name":"Histiocytoid Sweet Syndrome: A Distinct Entity Within the Spectrum of Myeloid Dermatoses","publication_year":2026,"publication_date":"2026-11-05","ids":{"openalex":"https://openalex.org/W7225333583","doi":"https://doi.org/10.1111/cup.70233","pmid":"https://pubmed.ncbi.nlm.nih.gov/42984447"},"language":"en","primary_location":{"id":"doi:10.1111/cup.70233","doi":"https://doi.org/10.1111/cup.70233","is_oa":true,"landing_page_url":"https://doi.org/10.1111/cup.70233","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1111/cup.70233","source":{"id":"https://openalex.org/S92442678","display_name":"Journal of Cutaneous Pathology","issn_l":"0303-6987","issn":["0303-6987","1600-0560"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-1","medline","norway-1","poland-70","russia-white-list-3"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Cutaneous Pathology","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"bronze","oa_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1111/cup.70233","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5139784518","display_name":"Ava Scott","orcid":"https://orcid.org/0009-0003-7655-2186","observed_orcids":["https://orcid.org/0009-0003-7655-2186"]},"institutions":[{"id":"https://openalex.org/I47838141","display_name":"Saint Louis University","ror":"https://ror.org/01p7jjy08","country_code":"US","type":"education","lineage":["https://openalex.org/I47838141"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Ava Scott","raw_affiliation_strings":["Saint Louis University School of Medicine  St. Louis Missouri USA"],"raw_orcid":"https://orcid.org/0009-0003-7655-2186","affiliations":[{"raw_affiliation_string":"Saint Louis University School of Medicine  St. Louis Missouri USA","institution_ids":["https://openalex.org/I47838141"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5112650338","display_name":"Emily H. Smith","orcid":"https://orcid.org/0000-0002-8993-439X","observed_orcids":["https://orcid.org/0000-0002-8993-439X"]},"institutions":[{"id":"https://openalex.org/I2802034949","display_name":"Saint Louis University Hospital","ror":"https://ror.org/01v49sd11","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I2801580383","https://openalex.org/I2802034949"]},{"id":"https://openalex.org/I47838141","display_name":"Saint Louis University","ror":"https://ror.org/01p7jjy08","country_code":"US","type":"education","lineage":["https://openalex.org/I47838141"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"Emily Smith","raw_affiliation_strings":["Department of Dermatology SSM Health/Saint Louis University  St. Louis Missouri USA"],"raw_orcid":"https://orcid.org/0000-0002-8993-439X","affiliations":[{"raw_affiliation_string":"Department of Dermatology SSM Health/Saint Louis University  St. Louis Missouri USA","institution_ids":["https://openalex.org/I2802034949","https://openalex.org/I47838141"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":["https://openalex.org/A5112650338"],"corresponding_institution_ids":["https://openalex.org/I2802034949","https://openalex.org/I47838141"],"apc_list":{"value":3570,"currency":"USD","value_usd":3570},"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12328","display_name":"Autoimmune and Inflammatory Disorders","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12328","display_name":"Autoimmune and Inflammatory Disorders","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11909","display_name":"Histiocytic Disorders and Treatments","score":0.00019999999494757503,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12600","display_name":"Eosinophilic Disorders and Syndromes","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/histiocytoid-sweet-syndrome","display_name":"histiocytoid Sweet syndrome","score":0.9950000047683716},{"id":"https://openalex.org/keywords/sweet-syndrome","display_name":"Sweet syndrome","score":0.953000009059906},{"id":"https://openalex.org/keywords/immature-myeloid-cells","display_name":"immature myeloid cells","score":0.8759999871253967},{"id":"https://openalex.org/keywords/myeloperoxidase","display_name":"myeloperoxidase","score":0.9739999771118164},{"id":"https://openalex.org/keywords/lysozyme","display_name":"lysozyme","score":0.902999997138977},{"id":"https://openalex.org/keywords/cd15","display_name":"CD15","score":0.9869999885559082},{"id":"https://openalex.org/keywords/cd13","display_name":"CD13","score":0.9990000128746033},{"id":"https://openalex.org/keywords/relapse","display_name":"relapse","score":0.8690000176429749},{"id":"https://openalex.org/keywords/clinicopathological-features","display_name":"clinicopathological features","score":0.8970000147819519},{"id":"https://openalex.org/keywords/immunophenotype","display_name":"immunophenotype","score":0.9710000157356262},{"id":"https://openalex.org/keywords/treatment","display_name":"treatment","score":0.7179999947547913}],"concepts":[{"id":"https://openalex.org/C2779282312","wikidata":"https://www.wikidata.org/wiki/Q1956561","display_name":"Myeloid","level":2,"score":0.8011999726295471},{"id":"https://openalex.org/C2994430510","wikidata":"https://www.wikidata.org/wiki/Q3270846","display_name":"Myeloid cells","level":3,"score":0.6708999872207642},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.6620000004768372},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.526199996471405},{"id":"https://openalex.org/C2908805171","wikidata":"https://www.wikidata.org/wiki/Q1514476","display_name":"Sweet Syndrome","level":2,"score":0.5194000005722046},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.5159000158309937},{"id":"https://openalex.org/C549673821","wikidata":"https://www.wikidata.org/wiki/Q683455","display_name":"Anatomical pathology","level":3,"score":0.3709000051021576},{"id":"https://openalex.org/C2993296363","wikidata":"https://www.wikidata.org/wiki/Q11688946","display_name":"Myeloid leukaemia","level":2,"score":0.35370001196861267},{"id":"https://openalex.org/C3020442560","wikidata":"https://www.wikidata.org/wiki/Q4971815","display_name":"Broad spectrum","level":2,"score":0.3449000120162964},{"id":"https://openalex.org/C86803240","wikidata":"https://www.wikidata.org/wiki/Q420","display_name":"Biology","level":0,"score":0.33489999175071716},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.29330000281333923},{"id":"https://openalex.org/C3018156656","wikidata":"https://www.wikidata.org/wiki/Q5376560","display_name":"Disease entity","level":3,"score":0.2921999990940094},{"id":"https://openalex.org/C2776817793","wikidata":"https://www.wikidata.org/wiki/Q6553369","display_name":"Lineage (genetic)","level":3,"score":0.2824999988079071},{"id":"https://openalex.org/C204232928","wikidata":"https://www.wikidata.org/wiki/Q899285","display_name":"Immunohistochemistry","level":2,"score":0.27639999985694885}],"mesh":[],"locations_count":2,"locations":[{"id":"doi:10.1111/cup.70233","doi":"https://doi.org/10.1111/cup.70233","is_oa":true,"landing_page_url":"https://doi.org/10.1111/cup.70233","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1111/cup.70233","source":{"id":"https://openalex.org/S92442678","display_name":"Journal of Cutaneous Pathology","issn_l":"0303-6987","issn":["0303-6987","1600-0560"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-1","medline","norway-1","poland-70","russia-white-list-3"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Cutaneous Pathology","raw_type":"journal-article"},{"id":"pmid:42984447","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/42984447","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of cutaneous pathology","raw_type":"Journal Article"}],"best_oa_location":{"id":"doi:10.1111/cup.70233","doi":"https://doi.org/10.1111/cup.70233","is_oa":true,"landing_page_url":"https://doi.org/10.1111/cup.70233","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1111/cup.70233","source":{"id":"https://openalex.org/S92442678","display_name":"Journal of Cutaneous Pathology","issn_l":"0303-6987","issn":["0303-6987","1600-0560"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-1","medline","norway-1","poland-70","russia-white-list-3"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Cutaneous Pathology","raw_type":"journal-article"},"sustainable_development_goals":[{"score":0.9537000060081482,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7225333583.pdf","grobid_xml":"https://content.openalex.org/works/W7225333583.grobid-xml"},"referenced_works_count":20,"referenced_works":["https://openalex.org/W744463625","https://openalex.org/W2033315333","https://openalex.org/W2049320874","https://openalex.org/W2083760792","https://openalex.org/W2109446357","https://openalex.org/W2217381307","https://openalex.org/W2346571134","https://openalex.org/W2601779515","https://openalex.org/W2766119955","https://openalex.org/W2784986333","https://openalex.org/W3094531119","https://openalex.org/W4212815560","https://openalex.org/W4229440546","https://openalex.org/W4310952020","https://openalex.org/W4386602994","https://openalex.org/W4389938182","https://openalex.org/W4390611561","https://openalex.org/W4393385960","https://openalex.org/W4400592541","https://openalex.org/W4405643857"],"related_works":["https://openalex.org/W2601779515","https://openalex.org/W2049320874","https://openalex.org/W1527420074","https://openalex.org/W2217381307","https://openalex.org/W2346571134","https://openalex.org/W4386602994","https://openalex.org/W3008530668","https://openalex.org/W2093078005","https://openalex.org/W4415533641","https://openalex.org/W2154419327"],"abstract_inverted_index":{"Histiocytoid":[0],"Sweet":[1,8,52],"syndrome":[2,9],"(H-SS)":[3],"is":[4],"a":[5,12],"variant":[6],"of":[7,15,68,78],"characterized":[10],"by":[11],"dermal":[13],"infiltrate":[14],"immature":[16],"myeloid":[17,29,79],"cells":[18,27],"with":[19,41,50],"histiocytoid":[20],"morphology":[21],"rather":[22],"than":[23],"mature":[24],"neutrophils.":[25],"These":[26],"express":[28],"markers":[30],"including":[31],"myeloperoxidase,":[32],"lysozyme,":[33],"CD15,":[34],"and":[35,44,66,70],"CD13.":[36],"H-SS":[37],"has":[38],"been":[39],"associated":[40],"hematologic":[42],"malignancies":[43],"demonstrates":[45],"higher":[46],"relapse":[47],"rates":[48],"compared":[49],"classic":[51],"syndrome.":[53],"This":[54],"review":[55],"synthesizes":[56],"current":[57],"evidence":[58],"on":[59],"the":[60,75],"clinicopathologic":[61],"features,":[62],"immunophenotype,":[63],"disease":[64],"associations,":[65],"treatment":[67],"H-SS,":[69],"examines":[71],"its":[72],"position":[73],"within":[74],"broader":[76],"spectrum":[77],"cutaneous":[80],"infiltrates.":[81]},"counts_by_year":[],"updated_date":"2026-11-07T11:25:07.637180","created_date":"2026-11-06T00:00:00"}
