{"id":"https://openalex.org/W7224875767","doi":"https://doi.org/10.4103/ijd.ijd_908_24","title":"Widespread Bilateral Systematized Blaschko Linear Porokeratotic Eccrine and Hair Follicle Nevus; A Report of Rare Case","display_name":"Widespread Bilateral Systematized Blaschko Linear Porokeratotic Eccrine and Hair Follicle Nevus; A Report of Rare Case","publication_year":2026,"publication_date":"2026-10-30","ids":{"openalex":"https://openalex.org/W7224875767","doi":"https://doi.org/10.4103/ijd.ijd_908_24"},"language":"en","primary_location":{"id":"doi:10.4103/ijd.ijd_908_24","doi":"https://doi.org/10.4103/ijd.ijd_908_24","is_oa":true,"landing_page_url":"https://doi.org/10.4103/ijd.ijd_908_24","pdf_url":null,"source":{"id":"https://openalex.org/S40624954","display_name":"Indian Journal of Dermatology","issn_l":"0019-5154","issn":["0019-5154","1998-3611"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-b","doyens","norway-1","poland-40","russia-white-list-3"],"host_organization":"https://openalex.org/P4310320448","host_organization_name":"Medknow","host_organization_lineage":["https://openalex.org/P4310320448","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Medknow","Wolters Kluwer"],"type":"journal"},"license":"cc-by-nc-sa","license_id":"https://openalex.org/licenses/cc-by-nc-sa","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Indian Journal of Dermatology","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","doaj"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://doi.org/10.4103/ijd.ijd_908_24","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5018144065","display_name":"Chandramohan Kudligi","orcid":"https://orcid.org/0009-0003-4703-9607","observed_orcids":["https://orcid.org/0009-0003-4703-9607"]},"institutions":[{"id":"https://openalex.org/I77799889","display_name":"Karnataka Institute of Medical Sciences","ror":"https://ror.org/03d6dzy78","country_code":"IN","type":"healthcare","lineage":["https://openalex.org/I77799889"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"Chandramohan Kudligi","raw_affiliation_strings":["From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India","institution_ids":["https://openalex.org/I77799889"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5087771923","display_name":"Meghana Patil","orcid":"https://orcid.org/0000-0002-2141-7919","observed_orcids":["https://orcid.org/0000-0002-2141-7919"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Meghana Patil","raw_affiliation_strings":["Department of Pathology, Employees State Insurance Corporation, Gulburga, Karnataka, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pathology, Employees State Insurance Corporation, Gulburga, Karnataka, India","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5122365899","display_name":"Tejaswini Mukundraj","orcid":"https://orcid.org/0009-0001-4403-3563","observed_orcids":["https://orcid.org/0009-0001-4403-3563"]},"institutions":[{"id":"https://openalex.org/I77799889","display_name":"Karnataka Institute of Medical Sciences","ror":"https://ror.org/03d6dzy78","country_code":"IN","type":"healthcare","lineage":["https://openalex.org/I77799889"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"Tejaswini Mukundraj","raw_affiliation_strings":["From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India","institution_ids":["https://openalex.org/I77799889"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5160227265","display_name":"Navya K. Gopinathan","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I77799889","display_name":"Karnataka Institute of Medical Sciences","ror":"https://ror.org/03d6dzy78","country_code":"IN","type":"healthcare","lineage":["https://openalex.org/I77799889"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"Navya K. Gopinathan","raw_affiliation_strings":["From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India","institution_ids":["https://openalex.org/I77799889"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5149458050","display_name":"Tejashwini Badarli","orcid":"https://orcid.org/0009-0007-0328-1409","observed_orcids":["https://orcid.org/0009-0007-0328-1409"]},"institutions":[{"id":"https://openalex.org/I77799889","display_name":"Karnataka Institute of Medical Sciences","ror":"https://ror.org/03d6dzy78","country_code":"IN","type":"healthcare","lineage":["https://openalex.org/I77799889"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"Tejashwini Badarli","raw_affiliation_strings":["From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India","institution_ids":["https://openalex.org/I77799889"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5111110607","display_name":"S. M. Choukimath","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I77799889","display_name":"Karnataka Institute of Medical Sciences","ror":"https://ror.org/03d6dzy78","country_code":"IN","type":"healthcare","lineage":["https://openalex.org/I77799889"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"Sharanabasava M. Choukimath","raw_affiliation_strings":["Department of Pathology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pathology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India","institution_ids":["https://openalex.org/I77799889"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5123489613","display_name":"Meghana Ravi Kumar","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I77799889","display_name":"Karnataka Institute of Medical Sciences","ror":"https://ror.org/03d6dzy78","country_code":"IN","type":"healthcare","lineage":["https://openalex.org/I77799889"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"Meghana R. Kumar","raw_affiliation_strings":["From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India","institution_ids":["https://openalex.org/I77799889"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5160235884","display_name":"Arpita F. Chavan","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I77799889","display_name":"Karnataka Institute of Medical Sciences","ror":"https://ror.org/03d6dzy78","country_code":"IN","type":"healthcare","lineage":["https://openalex.org/I77799889"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"Arpita F. Chavan","raw_affiliation_strings":["From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"From the Department of Dermatology Venereology and Leprology, Karnataka Medical College and Research Institute, Hubballi, Karnataka, India","institution_ids":["https://openalex.org/I77799889"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":{"value":0.84895883,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12355","display_name":"Genetic and rare skin diseases.","score":1.0,"subfield":{"id":"https://openalex.org/subfields/1311","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T12355","display_name":"Genetic and rare skin diseases.","score":1.0,"subfield":{"id":"https://openalex.org/subfields/1311","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T11868","display_name":"Cancer and Skin Lesions","score":9.999999747378752e-05,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11650","display_name":"Skin and Cellular Biology Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/1307","display_name":"Cell Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/blaschko-lines","display_name":"Blaschko lines","score":0.8420000076293945},{"id":"https://openalex.org/keywords/genetic-counseling","display_name":"genetic counseling","score":0.6520000100135803}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.824999988079071},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.7245000004768372},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.5776000022888184},{"id":"https://openalex.org/C2777216303","wikidata":"https://www.wikidata.org/wiki/Q866324","display_name":"Hair follicle","level":2,"score":0.5771999955177307},{"id":"https://openalex.org/C2776292323","wikidata":"https://www.wikidata.org/wiki/Q523893","display_name":"Ichthyosis","level":2,"score":0.48750001192092896},{"id":"https://openalex.org/C3020547009","wikidata":"https://www.wikidata.org/wiki/Q1070952","display_name":"Histopathological examination","level":2,"score":0.478300005197525},{"id":"https://openalex.org/C81241287","wikidata":"https://www.wikidata.org/wiki/Q189474","display_name":"Keratin","level":2,"score":0.4090999960899353},{"id":"https://openalex.org/C2779915019","wikidata":"https://www.wikidata.org/wiki/Q1640998","display_name":"Hyperkeratosis","level":2,"score":0.3928999900817871},{"id":"https://openalex.org/C2780713498","wikidata":"https://www.wikidata.org/wiki/Q2897327","display_name":"Dyskeratosis","level":3,"score":0.26840001344680786},{"id":"https://openalex.org/C2780801072","wikidata":"https://www.wikidata.org/wiki/Q837512","display_name":"Differential diagnosis","level":2,"score":0.25450000166893005}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.4103/ijd.ijd_908_24","doi":"https://doi.org/10.4103/ijd.ijd_908_24","is_oa":true,"landing_page_url":"https://doi.org/10.4103/ijd.ijd_908_24","pdf_url":null,"source":{"id":"https://openalex.org/S40624954","display_name":"Indian Journal of Dermatology","issn_l":"0019-5154","issn":["0019-5154","1998-3611"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-b","doyens","norway-1","poland-40","russia-white-list-3"],"host_organization":"https://openalex.org/P4310320448","host_organization_name":"Medknow","host_organization_lineage":["https://openalex.org/P4310320448","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Medknow","Wolters Kluwer"],"type":"journal"},"license":"cc-by-nc-sa","license_id":"https://openalex.org/licenses/cc-by-nc-sa","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Indian Journal of Dermatology","raw_type":"journal-article"}],"best_oa_location":{"id":"doi:10.4103/ijd.ijd_908_24","doi":"https://doi.org/10.4103/ijd.ijd_908_24","is_oa":true,"landing_page_url":"https://doi.org/10.4103/ijd.ijd_908_24","pdf_url":null,"source":{"id":"https://openalex.org/S40624954","display_name":"Indian Journal of Dermatology","issn_l":"0019-5154","issn":["0019-5154","1998-3611"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-b","doyens","norway-1","poland-40","russia-white-list-3"],"host_organization":"https://openalex.org/P4310320448","host_organization_name":"Medknow","host_organization_lineage":["https://openalex.org/P4310320448","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Medknow","Wolters Kluwer"],"type":"journal"},"license":"cc-by-nc-sa","license_id":"https://openalex.org/licenses/cc-by-nc-sa","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Indian Journal of Dermatology","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":0.8999999761581421}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":8,"referenced_works":["https://openalex.org/W1944031341","https://openalex.org/W2009843196","https://openalex.org/W2030493623","https://openalex.org/W2050084118","https://openalex.org/W2056953744","https://openalex.org/W2112358483","https://openalex.org/W2117827348","https://openalex.org/W2774164002"],"related_works":["https://openalex.org/W2086522373","https://openalex.org/W1944031341","https://openalex.org/W4233762068","https://openalex.org/W1976449841","https://openalex.org/W2112358483","https://openalex.org/W2117827348","https://openalex.org/W2774164002","https://openalex.org/W2810607453","https://openalex.org/W3090800150","https://openalex.org/W2036036668"],"abstract_inverted_index":{"Abstract":[0],"Porokeratotic":[1],"eccrine":[2,18],"and":[3,19,56,70,90,108,111],"hair":[4,20],"follicle":[5,21],"nevus":[6,143],"(PEHFN)":[7],"is":[8],"an":[9],"extremely":[10],"rare,":[11],"non-hereditary":[12],"disorder":[13],"of":[14,38,63,103],"keratinization":[15],"characterized":[16],"by":[17],"involvement.":[22],"To":[23],"date,":[24],"only":[25],"11":[26],"cases":[27],"have":[28],"been":[29,85],"reported":[30],"in":[31],"literature.":[32],"We":[33],"present":[34],"a":[35,94],"rare":[36,95],"case":[37,99],"systematized":[39],"Blaschko-linear":[40],"PEHFN":[41,83],"presenting":[42],"as":[43],"widespread":[44],"hyperkeratotic":[45],"verrucous":[46],"filiform":[47],"papules":[48],"since":[49],"birth,":[50],"affecting":[51],"the":[52,79,101,128,137],"face,":[53],"scalp,":[54],"trunk,":[55],"limbs.":[57],"Histopathological":[58],"examination":[59],"revealed":[60],"characteristic":[61],"features":[62,110],"PEHFN,":[64,132],"including":[65],"basket-weave":[66],"hyperkeratosis,":[67],"coronoid":[68],"lamella,":[69],"parakeratotic":[71,80],"columns.":[72],"The":[73],"granular":[74],"layer":[75],"was":[76],"absent":[77],"beneath":[78],"column.":[81],"Notably,":[82],"has":[84],"associated":[86],"with":[87,115],"keratitis":[88],"ichthyosis":[89],"deafness":[91],"(KID)":[92],"syndrome,":[93,117],"genetic":[96,119],"disorder.":[97],"Our":[98],"highlights":[100],"importance":[102],"recognizing":[104],"PEHFN\u2019s":[105],"distinctive":[106],"clinical":[107],"histopathological":[109],"its":[112,134],"potential":[113],"association":[114],"KID":[116],"emphasizing":[118],"counselling":[120],"for":[121],"affected":[122],"individuals.":[123],"This":[124],"report":[125],"contributes":[126],"to":[127],"limited":[129],"literature":[130],"on":[131],"underscoring":[133],"classification":[135],"under":[136],"unified":[138],"term":[139],"porokeratotic":[140],"adnexal":[141],"ostial":[142],"(PAON).":[144]},"counts_by_year":[],"updated_date":"2026-11-01T11:40:01.658920","created_date":"2026-10-31T00:00:00"}
