{"id":"https://openalex.org/W7224430462","doi":"https://doi.org/10.62856/djcro.v12.87","title":"Extranodal marginal zone lymphoma associated with Vogt-Koyanagi-Harada disease","display_name":"Extranodal marginal zone lymphoma associated with Vogt-Koyanagi-Harada disease","publication_year":2026,"publication_date":"2026-10-29","ids":{"openalex":"https://openalex.org/W7224430462","doi":"https://doi.org/10.62856/djcro.v12.87"},"language":"en","primary_location":{"id":"doi:10.62856/djcro.v12.87","doi":"https://doi.org/10.62856/djcro.v12.87","is_oa":true,"landing_page_url":"https://doi.org/10.62856/djcro.v12.87","pdf_url":"https://djcro.duke.edu/index.php/djcro/article/download/87/46","source":{"id":"https://openalex.org/S7407065198","display_name":"Digital Journal of Case Reports in Ophthalmology","issn_l":"3144-282X","issn":["3144-282X"],"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Digital Journal of Case Reports in Ophthalmology","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref"],"open_access":{"is_oa":true,"oa_status":"bronze","oa_url":"https://djcro.duke.edu/index.php/djcro/article/download/87/46","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5160126181","display_name":"Timothy Kaftan","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I59130452","display_name":"University of Nebraska Medical Center","ror":"https://ror.org/00thqtb16","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I59130452"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Timothy Kaftan","raw_affiliation_strings":["University of Nebraska Medical Center Truhlsen Eye Institute"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Nebraska Medical Center Truhlsen Eye Institute","institution_ids":["https://openalex.org/I59130452"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5160121936","display_name":"Helen Song","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I145608581","display_name":"University of Miami","ror":"https://ror.org/02dgjyy92","country_code":"US","type":"education","lineage":["https://openalex.org/I145608581"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Helen Song","raw_affiliation_strings":["Department of Ophthalmology, University of Miami, Miami, Florida, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Ophthalmology, University of Miami, Miami, Florida, USA","institution_ids":["https://openalex.org/I145608581"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5160097781","display_name":"Thomas Clare","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I59130452","display_name":"University of Nebraska Medical Center","ror":"https://ror.org/00thqtb16","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I59130452"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Thomas Clare","raw_affiliation_strings":["Department of Ophthalmology and Visual Sciences, University of Nebraska Medical Center, Omaha, NE, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Ophthalmology and Visual Sciences, University of Nebraska Medical Center, Omaha, NE, USA","institution_ids":["https://openalex.org/I59130452"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5160111477","display_name":"Nam Nguyen","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I59130452","display_name":"University of Nebraska Medical Center","ror":"https://ror.org/00thqtb16","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I59130452"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Nam Nguyen","raw_affiliation_strings":["Department of Ophthalmology and Visual Sciences, University of Nebraska Medical Center, Omaha, NE, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Ophthalmology and Visual Sciences, University of Nebraska Medical Center, Omaha, NE, USA","institution_ids":["https://openalex.org/I59130452"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5160126796","display_name":"Rao Chundury","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I59130452","display_name":"University of Nebraska Medical Center","ror":"https://ror.org/00thqtb16","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I59130452"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Rao Chundury","raw_affiliation_strings":["Department of Ophthalmology and Visual Sciences, University of Nebraska Medical Center, Omaha, NE, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Ophthalmology and Visual Sciences, University of Nebraska Medical Center, Omaha, NE, USA","institution_ids":["https://openalex.org/I59130452"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5160117949","display_name":"Jeffrey Cannatella","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I59130452","display_name":"University of Nebraska Medical Center","ror":"https://ror.org/00thqtb16","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I59130452"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Jeffrey Cannatella","raw_affiliation_strings":["Department of Pathology, Microbiology, and Immunology, University of Nebraska Medical Center, Omaha, NE, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pathology, Microbiology, and Immunology, University of Nebraska Medical Center, Omaha, NE, USA","institution_ids":["https://openalex.org/I59130452"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5138411030","display_name":"Matthew Lunning","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I59130452","display_name":"University of Nebraska Medical Center","ror":"https://ror.org/00thqtb16","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I59130452"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Matthew Lunning","raw_affiliation_strings":["Department of Internal Medicine, Division of Hematology/Oncology, University of Nebraska Medical Center, Omaha, NE, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Internal Medicine, Division of Hematology/Oncology, University of Nebraska Medical Center, Omaha, NE, USA","institution_ids":["https://openalex.org/I59130452"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5160116120","display_name":"Lindsay Helget","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I59130452","display_name":"University of Nebraska Medical Center","ror":"https://ror.org/00thqtb16","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I59130452"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Lindsay Helget","raw_affiliation_strings":["Department of Internal Medicine, Division of Rheumatology, University of Nebraska Medical Center, Omaha, NE, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Internal Medicine, Division of Rheumatology, University of Nebraska Medical Center, Omaha, NE, USA","institution_ids":["https://openalex.org/I59130452"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5160089087","display_name":"Neha Gupta","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I59130452","display_name":"University of Nebraska Medical Center","ror":"https://ror.org/00thqtb16","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I59130452"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Neha Gupta","raw_affiliation_strings":["Department of Pathology, Microbiology, and Immunology, University of Nebraska Medical Center, Omaha, NE, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pathology, Microbiology, and Immunology, University of Nebraska Medical Center, Omaha, NE, USA","institution_ids":["https://openalex.org/I59130452"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5160089362","display_name":"Steven Yeh","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I59130452","display_name":"University of Nebraska Medical Center","ror":"https://ror.org/00thqtb16","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I59130452"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Steven Yeh","raw_affiliation_strings":["Department of Ophthalmology and Visual Sciences, University of Nebraska Medical Center, Omaha, NE, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Ophthalmology and Visual Sciences, University of Nebraska Medical Center, Omaha, NE, USA","institution_ids":["https://openalex.org/I59130452"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.89163874,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"12","issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11328","display_name":"Ocular Oncology and Treatments","score":0.5375999808311462,"subfield":{"id":"https://openalex.org/subfields/2731","display_name":"Ophthalmology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11328","display_name":"Ocular Oncology and Treatments","score":0.5375999808311462,"subfield":{"id":"https://openalex.org/subfields/2731","display_name":"Ophthalmology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10185","display_name":"Lymphoma Diagnosis and Treatment","score":0.24369999766349792,"subfield":{"id":"https://openalex.org/subfields/2734","display_name":"Pathology and Forensic Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11194","display_name":"Ocular Diseases and Beh\u00e7et\u2019s Syndrome","score":0.1696999967098236,"subfield":{"id":"https://openalex.org/subfields/2731","display_name":"Ophthalmology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/malt-lymphoma","display_name":"MALT lymphoma","score":0.9559999704360962},{"id":"https://openalex.org/keywords/vogt-koyanagi-harada-disease","display_name":"Vogt-Koyanagi-Harada disease","score":1.0},{"id":"https://openalex.org/keywords/ocular-lymphoma","display_name":"ocular lymphoma","score":0.8799999952316284},{"id":"https://openalex.org/keywords/uveal-inflammation","display_name":"uveal inflammation","score":0.859000027179718},{"id":"https://openalex.org/keywords/panuveitis","display_name":"panuveitis","score":0.8180000185966492},{"id":"https://openalex.org/keywords/serous-retinal-detachment","display_name":"serous retinal detachment","score":0.9929999709129333},{"id":"https://openalex.org/keywords/choroidal-lymphoma","display_name":"choroidal lymphoma","score":0.6430000066757202},{"id":"https://openalex.org/keywords/enucleation","display_name":"enucleation","score":0.9160000085830688},{"id":"https://openalex.org/keywords/mycophenolate-mofetil","display_name":"mycophenolate mofetil","score":0.8550000190734863},{"id":"https://openalex.org/keywords/topical-corticosteroids","display_name":"topical corticosteroids","score":0.6240000128746033}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9179999828338623},{"id":"https://openalex.org/C188261085","wikidata":"https://www.wikidata.org/wiki/Q5380862","display_name":"Enucleation","level":2,"score":0.6841999888420105},{"id":"https://openalex.org/C2779343474","wikidata":"https://www.wikidata.org/wiki/Q3109175","display_name":"Context (archaeology)","level":2,"score":0.5339999794960022},{"id":"https://openalex.org/C2779338263","wikidata":"https://www.wikidata.org/wiki/Q208414","display_name":"Lymphoma","level":2,"score":0.5160999894142151},{"id":"https://openalex.org/C118487528","wikidata":"https://www.wikidata.org/wiki/Q161437","display_name":"Ophthalmology","level":1,"score":0.4957999885082245},{"id":"https://openalex.org/C2778007619","wikidata":"https://www.wikidata.org/wiki/Q6058506","display_name":"Intraocular lymphoma","level":3,"score":0.4855000078678131},{"id":"https://openalex.org/C2778257484","wikidata":"https://www.wikidata.org/wiki/Q555066","display_name":"Visual acuity","level":2,"score":0.4821000099182129},{"id":"https://openalex.org/C2780428090","wikidata":"https://www.wikidata.org/wiki/Q625164","display_name":"Retinal detachment","level":3,"score":0.46950000524520874},{"id":"https://openalex.org/C2776694393","wikidata":"https://www.wikidata.org/wiki/Q271762","display_name":"Choroid","level":3,"score":0.45329999923706055},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.4406000077724457},{"id":"https://openalex.org/C2780827179","wikidata":"https://www.wikidata.org/wiki/Q422001","display_name":"Retinal","level":2,"score":0.42660000920295715},{"id":"https://openalex.org/C2776391266","wikidata":"https://www.wikidata.org/wiki/Q9612","display_name":"Fundus (uterus)","level":2,"score":0.4174000024795532},{"id":"https://openalex.org/C2776194053","wikidata":"https://www.wikidata.org/wiki/Q280027","display_name":"Uveitis","level":2,"score":0.3806000053882599},{"id":"https://openalex.org/C2776148792","wikidata":"https://www.wikidata.org/wiki/Q3041498","display_name":"Eye disease","level":2,"score":0.366100013256073},{"id":"https://openalex.org/C2781092963","wikidata":"https://www.wikidata.org/wiki/Q650050","display_name":"Intraocular pressure","level":2,"score":0.36480000615119934},{"id":"https://openalex.org/C113520495","wikidata":"https://www.wikidata.org/wiki/Q2359854","display_name":"Posterior segment of eyeball","level":2,"score":0.34279999136924744},{"id":"https://openalex.org/C2779526237","wikidata":"https://www.wikidata.org/wiki/Q591256","display_name":"MALT lymphoma","level":3,"score":0.33719998598098755},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.33329999446868896},{"id":"https://openalex.org/C2778434524","wikidata":"https://www.wikidata.org/wiki/Q1048080","display_name":"Ciliary body","level":2,"score":0.32659998536109924},{"id":"https://openalex.org/C2778396096","wikidata":"https://www.wikidata.org/wiki/Q1238645","display_name":"Vogt\u2013Koyanagi\u2013Harada disease","level":3,"score":0.32600000500679016},{"id":"https://openalex.org/C2778024200","wikidata":"https://www.wikidata.org/wiki/Q2346242","display_name":"Retinal pigment epithelium","level":3,"score":0.2872999906539917},{"id":"https://openalex.org/C2779701055","wikidata":"https://www.wikidata.org/wiki/Q929833","display_name":"Rare disease","level":3,"score":0.2799000144004822},{"id":"https://openalex.org/C2775934546","wikidata":"https://www.wikidata.org/wiki/Q179991","display_name":"Biopsy","level":2,"score":0.2669999897480011},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.25699999928474426},{"id":"https://openalex.org/C509974204","wikidata":"https://www.wikidata.org/wiki/Q180507","display_name":"Radiation therapy","level":2,"score":0.2542000114917755}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.62856/djcro.v12.87","doi":"https://doi.org/10.62856/djcro.v12.87","is_oa":true,"landing_page_url":"https://doi.org/10.62856/djcro.v12.87","pdf_url":"https://djcro.duke.edu/index.php/djcro/article/download/87/46","source":{"id":"https://openalex.org/S7407065198","display_name":"Digital Journal of Case Reports in Ophthalmology","issn_l":"3144-282X","issn":["3144-282X"],"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Digital Journal of Case Reports in Ophthalmology","raw_type":"journal-article"}],"best_oa_location":{"id":"doi:10.62856/djcro.v12.87","doi":"https://doi.org/10.62856/djcro.v12.87","is_oa":true,"landing_page_url":"https://doi.org/10.62856/djcro.v12.87","pdf_url":"https://djcro.duke.edu/index.php/djcro/article/download/87/46","source":{"id":"https://openalex.org/S7407065198","display_name":"Digital Journal of Case Reports in Ophthalmology","issn_l":"3144-282X","issn":["3144-282X"],"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Digital Journal of Case Reports in Ophthalmology","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":0.98580002784729,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[{"id":"https://openalex.org/G8912971467","display_name":null,"funder_award_id":"R01 EY029594","funder_id":"https://openalex.org/F4320306085","funder_display_name":"U.S. Department of Health and Human Services"}],"funders":[{"id":"https://openalex.org/F4320306085","display_name":"U.S. Department of Health and Human Services","ror":"https://ror.org/033jnv181"},{"id":"https://openalex.org/F4320332161","display_name":"National Institutes of Health","ror":"https://ror.org/01cwqze88"}],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7224430462.pdf","grobid_xml":"https://content.openalex.org/works/W7224430462.grobid-xml"},"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W2022443232","https://openalex.org/W2592733388","https://openalex.org/W4392752157","https://openalex.org/W2026736553","https://openalex.org/W4403888948","https://openalex.org/W3113186674","https://openalex.org/W1998104756","https://openalex.org/W1999407691","https://openalex.org/W7160848083","https://openalex.org/W1982299513"],"abstract_inverted_index":{"This":[0],"case":[1],"report":[2],"highlights":[3],"a":[4,107],"potential":[5],"association":[6],"between":[7],"ocular":[8],"lymphoma":[9,127],"and":[10,47,59,72,78,93,115,145],"recurrent":[11,146],"uveal":[12,147],"inflammation":[13],"secondary":[14],"to":[15,88],"Vogt-Koyanagi-Harada":[16],"(VKH)":[17],"disease.":[18],"A":[19,100],"61-year-old":[20],"male":[21],"with":[22,69,75,85,110],"history":[23],"of":[24,31,96,106,128,143],"bilateral":[25],"panuveitis":[26],"was":[27,42,53,67,73,119],"referred":[28],"for":[29,55],"management":[30],"exudative":[32,61],"retinal":[33,62,113],"detachment":[34,63,114],"in":[35,140],"the":[36,141],"left":[37],"eye":[38,45],"(OS).":[39],"Visual":[40],"acuity":[41],"20/20":[43],"right":[44],"(OD)":[46],"light":[48,90],"perception":[49,91],"OS.":[50,64,99],"Funduscopic":[51],"examination":[52],"significant":[54],"pigmentary":[56],"changes":[57],"OD":[58],"inferior":[60],"The":[65],"patient":[66],"diagnosed":[68],"VKH":[70],"disease":[71],"treated":[74],"topical":[76],"steroids":[77],"mycophenolate":[79],"mofetil.":[80],"He":[81],"later":[82],"presented":[83],"acutely":[84],"reduced":[86],"vision":[87],"no":[89],"OS":[92,103],"intraocular":[94],"pressure":[95],"71":[97],"mmHg":[98],"B-scan":[101],"ultrasound":[102],"showed":[104],"presence":[105],"posterior":[108],"mass":[109],"an":[111],"overlying":[112],"choroid":[116],"thickening.":[117],"Enucleation":[118],"performed.":[120],"Histologic":[121],"findings":[122],"confirmed":[123],"extranodal":[124],"marginal":[125],"zone":[126],"mucosa-associated":[129],"lymphoid":[130],"tissue":[131],"(EMZL).":[132],"We":[133],"hypothesize":[134],"that":[135],"EMZL":[136],"may":[137],"have":[138],"evolved":[139],"context":[142],"chronic":[144],"inflammation.":[148]},"counts_by_year":[],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2026-10-30T00:00:00"}
