{"id":"https://openalex.org/W7223113015","doi":"https://doi.org/10.1016/j.htct.2026.107974","title":"ADES\u00c3O \u00c0 PROFILAXIA EM PESSOAS COM HEMOFILIA: COMPARA\u00c7\u00c3O ENTRE DOIS HEMOCENTROS BRASILEIROS","display_name":"ADES\u00c3O \u00c0 PROFILAXIA EM PESSOAS COM HEMOFILIA: COMPARA\u00c7\u00c3O ENTRE DOIS HEMOCENTROS BRASILEIROS","publication_year":2026,"publication_date":"2026-10-01","ids":{"openalex":"https://openalex.org/W7223113015","doi":"https://doi.org/10.1016/j.htct.2026.107974"},"language":"en","primary_location":{"id":"doi:10.1016/j.htct.2026.107974","doi":"https://doi.org/10.1016/j.htct.2026.107974","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.htct.2026.107974","pdf_url":"https://www.sciencedirect.com/science/article/pii/S2531137926017219/pdf","source":{"id":"https://openalex.org/S2898598332","display_name":"Hematology Transfusion and Cell Therapy","issn_l":"2531-1379","issn":["2531-1379","2531-1387"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","ki-jl-1","poland-20","russia-white-list-3","scielo"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Hematology, Transfusion and Cell Therapy","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://www.sciencedirect.com/science/article/pii/S2531137926017219/pdf","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5159181373","display_name":"Debora Maria do Carmo ROCHA - SANTIAGO","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Debora Maria do Carmo ROCHA - SANTIAGO","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5033744481","display_name":"Margareth C. Ozelo","orcid":"https://orcid.org/0000-0001-5938-0675","observed_orcids":["https://orcid.org/0000-0001-5938-0675"]},"institutions":[{"id":"https://openalex.org/I181391015","display_name":"Universidade Estadual de Campinas (UNICAMP)","ror":"https://ror.org/04wffgt70","country_code":"BR","type":"education","lineage":["https://openalex.org/I181391015"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Margareth Castro OZELO","raw_affiliation_strings":["Centro de Hematologia e Hemoterapia (Hemocentro), Universidade Estadual de Campinas (UNICAMP), Campinas, SP, Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Centro de Hematologia e Hemoterapia (Hemocentro), Universidade Estadual de Campinas (UNICAMP), Campinas, SP, Brasil","institution_ids":["https://openalex.org/I181391015"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5159178266","display_name":"J\u00e9ssica Oliveira FRADE - GUANAES","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"J\u00e9ssica Oliveira FRADE - GUANAES","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5093306812","display_name":"Gabriela G\u00f3es Yamaguti Hayakawa","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Gabriela G\u00f3es YAMAGUTI - HAYAKAWA","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5159169644","display_name":"Genival Araujo SANTOS-J\u00daNIOR","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I51235708","display_name":"Universidade Federal do Esp\u00edrito Santo","ror":"https://ror.org/05sxf4h28","country_code":"BR","type":"education","lineage":["https://openalex.org/I51235708"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Genival Araujo SANTOS-J\u00daNIOR","raw_affiliation_strings":["Universidade Federal do Esp\u00edrito Santo (UFES), Alegre, ES, Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Universidade Federal do Esp\u00edrito Santo (UFES), Alegre, ES, Brasil","institution_ids":["https://openalex.org/I51235708"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5031036531","display_name":"A. Prezotti","orcid":"https://orcid.org/0000-0003-1079-7140","observed_orcids":["https://orcid.org/0000-0003-1079-7140"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Alessandra Nunes Loureiro PREZOTTI","raw_affiliation_strings":["Centro Estadual de Hemoterapia e Hematologia Marcos Daniel Santos (HEMOES), Vit\u00f3ria, ES, Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Centro Estadual de Hemoterapia e Hematologia Marcos Daniel Santos (HEMOES), Vit\u00f3ria, ES, Brasil","institution_ids":[]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":{"value":0,"currency":"USD","value_usd":0},"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.78639738,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"48","issue":null,"first_page":"107974","last_page":"107974"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11280","display_name":"Hemophilia Treatment and Research","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11280","display_name":"Hemophilia Treatment and Research","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11620","display_name":"Medication Adherence and Compliance","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2714","display_name":"Family Practice"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10746","display_name":"Platelet Disorders and Treatments","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/hemophilia","display_name":"hemophilia","score":0.8769999742507935},{"id":"https://openalex.org/keywords/prophylaxis-adherence","display_name":"prophylaxis adherence","score":0.9430000185966492},{"id":"https://openalex.org/keywords/factor-viii-concentrate","display_name":"factor VIII concentrate","score":0.8939999938011169},{"id":"https://openalex.org/keywords/factor-ix-concentrate","display_name":"factor IX concentrate","score":0.9980000257492065},{"id":"https://openalex.org/keywords/hemophilia-a","display_name":"hemophilia A","score":0.9649999737739563},{"id":"https://openalex.org/keywords/hemophilia-b","display_name":"hemophilia B","score":1.0},{"id":"https://openalex.org/keywords/severe-hemophilia","display_name":"severe hemophilia","score":0.6259999871253967},{"id":"https://openalex.org/keywords/annualized-bleeding-rate","display_name":"annualized bleeding rate","score":0.6779999732971191},{"id":"https://openalex.org/keywords/bleeding-complications","display_name":"bleeding complications","score":0.37299999594688416},{"id":"https://openalex.org/keywords/hemocenters","display_name":"hemocenters","score":0.597000002861023},{"id":"https://openalex.org/keywords/hemostasis","display_name":"hemostasis","score":0.33799999952316284}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9753000140190125},{"id":"https://openalex.org/C29456083","wikidata":"https://www.wikidata.org/wiki/Q1221899","display_name":"Gynecology","level":1,"score":0.3919999897480011},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.3084000051021576},{"id":"https://openalex.org/C2779473830","wikidata":"https://www.wikidata.org/wiki/Q1540899","display_name":"MEDLINE","level":2,"score":0.23549999296665192},{"id":"https://openalex.org/C81182388","wikidata":"https://www.wikidata.org/wiki/Q353963","display_name":"Complication","level":2,"score":0.18000000715255737},{"id":"https://openalex.org/C3008058167","wikidata":"https://www.wikidata.org/wiki/Q84263196","display_name":"Coronavirus disease 2019 (COVID-19)","level":4,"score":0.16580000519752502},{"id":"https://openalex.org/C3007834351","wikidata":"https://www.wikidata.org/wiki/Q82069695","display_name":"Severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2)","level":5,"score":0.16009999811649323},{"id":"https://openalex.org/C164705383","wikidata":"https://www.wikidata.org/wiki/Q10379","display_name":"Cardiology","level":1,"score":0.15399999916553497},{"id":"https://openalex.org/C15708023","wikidata":"https://www.wikidata.org/wiki/Q80083","display_name":"Humanities","level":1,"score":0.1509999930858612},{"id":"https://openalex.org/C3006700255","wikidata":"https://www.wikidata.org/wiki/Q81068910","display_name":"2019-20 coronavirus outbreak","level":3,"score":0.14239999651908875}],"mesh":[],"locations_count":2,"locations":[{"id":"doi:10.1016/j.htct.2026.107974","doi":"https://doi.org/10.1016/j.htct.2026.107974","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.htct.2026.107974","pdf_url":"https://www.sciencedirect.com/science/article/pii/S2531137926017219/pdf","source":{"id":"https://openalex.org/S2898598332","display_name":"Hematology Transfusion and Cell Therapy","issn_l":"2531-1379","issn":["2531-1379","2531-1387"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","ki-jl-1","poland-20","russia-white-list-3","scielo"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Hematology, Transfusion and Cell Therapy","raw_type":"journal-article"},{"id":"pmh:oai:doaj.org/article:f6c944a7b42c490eb48b9aab3d39ecbc","doi":null,"is_oa":false,"landing_page_url":"https://doaj.org/article/f6c944a7b42c490eb48b9aab3d39ecbc","pdf_url":null,"source":{"id":"https://openalex.org/S4306401280","display_name":"DOAJ (DOAJ: Directory of Open Access Journals)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Hematology, Transfusion and Cell Therapy, Vol 48, Iss , Pp 107974- (2026)","raw_type":"article"}],"best_oa_location":{"id":"doi:10.1016/j.htct.2026.107974","doi":"https://doi.org/10.1016/j.htct.2026.107974","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.htct.2026.107974","pdf_url":"https://www.sciencedirect.com/science/article/pii/S2531137926017219/pdf","source":{"id":"https://openalex.org/S2898598332","display_name":"Hematology Transfusion and Cell Therapy","issn_l":"2531-1379","issn":["2531-1379","2531-1387"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","ki-jl-1","poland-20","russia-white-list-3","scielo"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Hematology, Transfusion and Cell Therapy","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":1.0,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7223113015.pdf","grobid_xml":"https://content.openalex.org/works/W7223113015.grobid-xml"},"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W7120830440","https://openalex.org/W7120843408","https://openalex.org/W2529297642","https://openalex.org/W7223113799","https://openalex.org/W4387748665","https://openalex.org/W4415669004","https://openalex.org/W4403554952","https://openalex.org/W2908651886","https://openalex.org/W4404094512","https://openalex.org/W7221233092"],"abstract_inverted_index":{"A":[0,81,126,198,211,263,312,401,432,498],"profilaxia":[1,53,120,175,514],"com":[2,71,79,110,122,170,191,196,217,230],"concentrados":[3,72],"de":[4,14,48,58,73,114,135,144,165,200,203,234,254,298,308,320,326,343,357,391,404,421,427,434,446,484,504,518],"fatores":[5,60,379],"VIII":[6],"(FVIII)":[7],"e":[8,38,57,75,83,96,101,139,176,193,206,251,288,334,347,355,369,388,397,409,438,526],"IX":[9],"(FIX)":[10],"\u00e9":[11],"o":[12,224,362,416,465,489,495,511,523],"padr\u00e3o":[13],"tratamento":[15,69,471,492],"da":[16,22,52,265,383,468,477,479,513],"hemofilia.":[17,533],"Contudo,":[18],"esses":[19],"benef\u00edcios":[20],"dependem":[21],"execu\u00e7\u00e3o":[23],"consistente":[24],"do":[25,29,90,470,530],"regime":[26],"profil\u00e1tico.":[27],"Apesar":[28,476],"acesso":[30,490],"ao":[31,68,142,385,491],"tratamento,":[32],"a":[33,50,66,133,140,214,303,395,413,425,442,473,528],"ades\u00e3o":[34,67,127,154,266,286,291,300,309,327,345,354,396,406,437],"permanece":[35],"um":[36,419],"desafio,":[37],"h\u00e1":[39],"poucas":[40],"evid\u00eancias":[41],"brasileiras":[42],"baseadas":[43],"em":[44,77,87,119,153,174,451,502,515,532],"medidas":[45],"objetivas":[46],"capazes":[47],"quantificar":[49],"implementa\u00e7\u00e3o":[51],"na":[54,99,130,180,449],"pr\u00e1tica":[55,519],"cl\u00ednica":[56],"identificar":[59],"associados":[61],"\u00e0":[62,381,458],"n\u00e3o":[63,158,281,299,344,405,463,485,493],"ades\u00e3o.":[64,159],"Avaliar":[65],"profil\u00e1tico":[70],"FVIII":[74,123],"FIX":[76],"pessoas":[78,109,169],"hemofilia":[80,209,218],"(HA)":[82],"B":[84],"(HB)":[85],"acompanhadas":[86],"dois":[88],"hemocentros":[89,271],"Sudeste":[91],"brasileiro.":[92],"Estudo":[93],"transversal,":[94,460],"descritivo":[95],"explorat\u00f3rio,":[97],"realizado":[98],"UNICAMP":[100,212,304],"no":[102,161],"HEMOES,":[103],"entre":[104,132,269,353,374,407,436],"Jan-Dez":[105],"2024.":[106],"Foram":[107],"inclu\u00eddas":[108,179],"HA":[111,192],"ou":[112,124,157,364],"HB,":[113],"qualquer":[115],"idade,":[116],"sem":[117],"inibidor,":[118],"regular":[121],"FIX.":[125],"foi":[128,202],"baseada":[129,501],"rela\u00e7\u00e3o":[131],"quantidade":[134],"fator":[136],"(UI)":[137],"prescrita":[138],"dispensada":[141],"longo":[143],"12":[145],"meses,":[146],"sendo":[147,188],"classificada,":[148],"segundo":[149],"Schrijvers":[150],"et":[151],"al.,":[152],"\u00f3tima,":[155],"sub\u00f3tima":[156,287],"An\u00e1lises":[160],"SPSS,":[162],"v24.0,":[163],"signific\u00e2ncia":[164],"5%.":[166],"Entre":[167],"941":[168],"hemofilia,":[171,358],"270":[172],"estavam":[173],"224":[177],"foram":[178,278],"an\u00e1lise":[181,264,459],"(UNICAMP":[182],"=":[183,186,249,261,273,317,367],"103;":[184],"HEMOES":[185,225,294],"121),":[187],"176":[189],"(78,6%)":[190],"48":[194],"(21,4%)":[195],"HB.":[197],"mediana":[199,238,246],"idade":[201,313],"27":[204],"anos":[205,322],"83%":[207],"apresentavam":[208],"grave.":[210],"apresentou":[213,226,295,305],"maior":[215,227,252,296,306,324,402,422],"propor\u00e7\u00e3o":[216,307,325],"grave":[219],"(95,1%;":[220],"p":[221,240,248,260],"<":[222,241],"0,0001),":[223,242],"carga":[228],"hemorr\u00e1gica,":[229],"maiores":[231,341],"taxas":[232,342],"anualizadas":[233],"sangramento":[235,243],"total":[236],"(ABR":[237],"1;":[239],"articular":[244],"(AJBR":[245],"0;":[247],"0,001)":[250],"frequ\u00eancia":[253,297,444,483],"hemartroses":[255],"espont\u00e2neas":[256],"(36,4%":[257],"vs.":[258],"16,5%;":[259],"0,001).":[262],"revelou":[267],"heterogeneidade":[268],"os":[270,375,398],"(p":[272,316,366],"0,027):":[274],"118":[275],"participantes":[276],"(52,7%)":[277],"classificados":[279],"como":[280,418,454],"aderentes,":[282],"28":[283],"(12,5%)":[284],"apresentaram":[285,323,339],"78":[289],"(34,8%)":[290],"\u00f3tima.":[292],"O":[293],"(60,3%),":[301],"enquanto":[302,330],"\u00f3tima":[310,328],"(43,7%).":[311],"mostrou":[314],"associa\u00e7\u00e3o":[315,352,435],"0,003):":[318],"crian\u00e7as":[319],"0\u20139":[321],"(63,6%),":[329],"adolescentes":[331,408],"(10\u201319":[332],"anos)":[333,338],"adultos":[335,410],"jovens":[336,411],"(20\u201339":[337],"as":[340,455],"(56,3%":[346],"66,7%,":[348],"respectivamente).":[349],"N\u00e3o":[350],"houve":[351],"tipo":[356],"escolaridade,":[359],"dist\u00e2ncia":[360],"at\u00e9":[361],"hemocentro":[363],"ABR":[365],"0,785)":[368],"AJBR":[370],"(0,936).":[371],"As":[372],"diferen\u00e7as":[373],"hemocentros,":[376],"sugerem":[377],"que":[378,461,488],"relacionados":[380],"organiza\u00e7\u00e3o":[382],"assist\u00eancia,":[384],"acompanhamento":[386],"multiprofissional":[387],"\u00e0s":[389],"estrat\u00e9gias":[390],"monitoramento":[392,512],"podem":[393],"influenciar":[394],"desfechos":[399],"cl\u00ednicos.":[400],"taxa":[403],"refor\u00e7a":[412],"transi\u00e7\u00e3o":[414],"para":[415,510,522,527],"autocuidado":[417],"per\u00edodo":[420],"vulnerabilidade,":[423],"indicando":[424],"necessidade":[426],"interven\u00e7\u00f5es":[428],"direcionadas":[429],"nessa":[430],"fase.":[431],"aus\u00eancia":[433],"ABR/AJBR":[439],"provavelmente":[440],"reflete":[441],"baixa":[443],"global":[445],"eventos":[447],"hemorr\u00e1gicos":[448],"popula\u00e7\u00e3o":[450],"profilaxia,":[452,480],"bem":[453],"limita\u00e7\u00f5es":[456],"inerentes":[457],"pode":[462],"captar":[464],"impacto":[466],"cumulativo":[467],"irregularidade":[469],"sobre":[472],"sa\u00fade":[474],"articular.":[475],"disponibilidade":[478],"observou-se":[481],"elevada":[482],"ades\u00e3o,":[486],"demonstrando":[487],"garante":[494],"uso":[496],"adequado.":[497],"avalia\u00e7\u00e3o":[499],"objetiva":[500],"dados":[503],"dispensa\u00e7\u00e3o":[505],"mostrou-se":[506],"uma":[507],"estrat\u00e9gia":[508],"aplic\u00e1vel":[509],"condi\u00e7\u00f5es":[516],"reais":[517],"cl\u00ednica,":[520],"contribuindo":[521],"aprimoramento":[524],"assistencial":[525],"qualidade":[529],"cuidado":[531]},"counts_by_year":[],"updated_date":"2026-11-08T12:12:28.789561","created_date":"2026-10-22T00:00:00"}
