{"id":"https://openalex.org/W7223100804","doi":"https://doi.org/10.1016/j.htct.2026.107489","title":"CARACTERIZA\u00c7\u00c3O DA HIPERTENS\u00c3O PULMONAR EM NEOPLASIAS MIELOPROLIFERATIVAS BCR-ABL NEGATIVAS: PRIMEIROS RESULTADOS DE UM ESTUDO TRANSVERSAL NO HUPE/UERJ","display_name":"CARACTERIZA\u00c7\u00c3O DA HIPERTENS\u00c3O PULMONAR EM NEOPLASIAS MIELOPROLIFERATIVAS BCR-ABL NEGATIVAS: PRIMEIROS RESULTADOS DE UM ESTUDO TRANSVERSAL NO HUPE/UERJ","publication_year":2026,"publication_date":"2026-10-01","ids":{"openalex":"https://openalex.org/W7223100804","doi":"https://doi.org/10.1016/j.htct.2026.107489"},"language":"en","primary_location":{"id":"doi:10.1016/j.htct.2026.107489","doi":"https://doi.org/10.1016/j.htct.2026.107489","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.htct.2026.107489","pdf_url":"https://www.sciencedirect.com/science/article/pii/S2531137926012368/pdf","source":{"id":"https://openalex.org/S2898598332","display_name":"Hematology Transfusion and Cell Therapy","issn_l":"2531-1379","issn":["2531-1379","2531-1387"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","ki-jl-1","poland-20","russia-white-list-3","scielo"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Hematology, Transfusion and Cell Therapy","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://www.sciencedirect.com/science/article/pii/S2531137926012368/pdf","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5159214656","display_name":"Carlos Murilo Barbosa JUNIOR","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210099359","display_name":"Hospital Universit\u00e1rio Pedro Ernesto","ror":"https://ror.org/00hrmgq26","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210099359"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Carlos Murilo Barbosa JUNIOR","raw_affiliation_strings":["Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil","institution_ids":["https://openalex.org/I4210099359"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5030082272","display_name":"Camila Gon\u00e7alves Pessanha","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210099359","display_name":"Hospital Universit\u00e1rio Pedro Ernesto","ror":"https://ror.org/00hrmgq26","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210099359"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Camila Gon\u00e7alves PESSANHA","raw_affiliation_strings":["Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil","institution_ids":["https://openalex.org/I4210099359"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5159190231","display_name":"Ariane Leite DE OLIEVIRA","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Ariane Leite DE OLIEVIRA","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5159167173","display_name":"Vinicius Da Cunha LISBOA","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210099359","display_name":"Hospital Universit\u00e1rio Pedro Ernesto","ror":"https://ror.org/00hrmgq26","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210099359"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Vinicius Da Cunha LISBOA","raw_affiliation_strings":["Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil","institution_ids":["https://openalex.org/I4210099359"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5159189101","display_name":"Guilherme George de Souza RODRIGUES","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210099359","display_name":"Hospital Universit\u00e1rio Pedro Ernesto","ror":"https://ror.org/00hrmgq26","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210099359"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Guilherme De Moraes RODRIGUES","raw_affiliation_strings":["Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil","institution_ids":["https://openalex.org/I4210099359"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5159218658","display_name":"Fabio Santiago FIGUEIREDO","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210099359","display_name":"Hospital Universit\u00e1rio Pedro Ernesto","ror":"https://ror.org/00hrmgq26","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210099359"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Fabio Santiago FIGUEIREDO","raw_affiliation_strings":["Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil","institution_ids":["https://openalex.org/I4210099359"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5017643164","display_name":"\u00c2ngelo Antunes Salgado","orcid":"https://orcid.org/0009-0001-8253-7535","observed_orcids":["https://orcid.org/0009-0001-8253-7535"]},"institutions":[{"id":"https://openalex.org/I4210099359","display_name":"Hospital Universit\u00e1rio Pedro Ernesto","ror":"https://ror.org/00hrmgq26","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210099359"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Angelo Antunes SALGADO","raw_affiliation_strings":["Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil","institution_ids":["https://openalex.org/I4210099359"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5159211519","display_name":"Luciana Silva RODRIGUES","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210099359","display_name":"Hospital Universit\u00e1rio Pedro Ernesto","ror":"https://ror.org/00hrmgq26","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210099359"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Luciana Silva RODRIGUES","raw_affiliation_strings":["Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil","institution_ids":["https://openalex.org/I4210099359"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5080251195","display_name":"Cristiana Solza","orcid":"https://orcid.org/0000-0002-4543-3630","observed_orcids":["https://orcid.org/0000-0002-4543-3630"]},"institutions":[{"id":"https://openalex.org/I4210099359","display_name":"Hospital Universit\u00e1rio Pedro Ernesto","ror":"https://ror.org/00hrmgq26","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210099359"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Cristiana SOLZA","raw_affiliation_strings":["Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Hospital Universit\u00e1rio Pedro Ernesto, Rio de Janeiro, RJ, Brasil","institution_ids":["https://openalex.org/I4210099359"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5159189579","display_name":"Rogerio Lopes RUFINO ALVES","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210099359","display_name":"Hospital Universit\u00e1rio Pedro Ernesto","ror":"https://ror.org/00hrmgq26","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210099359"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Rogerio Lopes RUFINO ALVES","raw_affiliation_strings":["Hospital Universit ario Pedro Ernesto , Rio de Janeiro , RJ , Brasil"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Hospital Universit ario Pedro Ernesto , Rio de Janeiro , RJ , Brasil","institution_ids":["https://openalex.org/I4210099359"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":{"value":0,"currency":"USD","value_usd":0},"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.78145841,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"48","issue":null,"first_page":"107489","last_page":"107489"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11628","display_name":"Myeloproliferative Neoplasms: Diagnosis and Treatment","score":0.9394999742507935,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11628","display_name":"Myeloproliferative Neoplasms: Diagnosis and Treatment","score":0.9394999742507935,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10728","display_name":"Pulmonary Hypertension Research and Treatments","score":0.05609999969601631,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10309","display_name":"Acute Myeloid Leukemia Research","score":0.0003000000142492354,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/pulmonary-hypertension","display_name":"pulmonary hypertension","score":0.9789999723434448},{"id":"https://openalex.org/keywords/bcr-abl-negative-myeloproliferative-neoplasms","display_name":"BCR-ABL-negative myeloproliferative neoplasms","score":0.9430000185966492},{"id":"https://openalex.org/keywords/myelofibrosis","display_name":"myelofibrosis","score":0.9049999713897705},{"id":"https://openalex.org/keywords/polycythemia-vera","display_name":"polycythemia vera","score":0.9570000171661377},{"id":"https://openalex.org/keywords/essential-thrombocythemia","display_name":"essential thrombocythemia","score":0.9940000176429749},{"id":"https://openalex.org/keywords/tricuspid-regurgitant-velocity","display_name":"tricuspid regurgitation velocity","score":0.9049999713897705},{"id":"https://openalex.org/keywords/pro-inflammatory-cytokines","display_name":"inflammatory cytokines","score":0.5789999961853027},{"id":"https://openalex.org/keywords/driver-mutations","display_name":"driver mutations","score":0.4449999928474426}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9451000094413757},{"id":"https://openalex.org/C29456083","wikidata":"https://www.wikidata.org/wiki/Q1221899","display_name":"Gynecology","level":1,"score":0.5160999894142151},{"id":"https://openalex.org/C2989005","wikidata":"https://www.wikidata.org/wiki/Q214963","display_name":"Nuclear medicine","level":1,"score":0.4413999915122986},{"id":"https://openalex.org/C2780130068","wikidata":"https://www.wikidata.org/wiki/Q2208651","display_name":"Transversal (combinatorics)","level":2,"score":0.2515999972820282},{"id":"https://openalex.org/C3018341830","wikidata":"https://www.wikidata.org/wiki/Q181876","display_name":"Primary cancer","level":3,"score":0.1273999959230423},{"id":"https://openalex.org/C529618451","wikidata":"https://www.wikidata.org/wiki/Q234904","display_name":"Ultrasonography","level":2,"score":0.1266999989748001},{"id":"https://openalex.org/C121608353","wikidata":"https://www.wikidata.org/wiki/Q12078","display_name":"Cancer","level":2,"score":0.11980000138282776},{"id":"https://openalex.org/C15708023","wikidata":"https://www.wikidata.org/wiki/Q80083","display_name":"Humanities","level":1,"score":0.11299999803304672},{"id":"https://openalex.org/C2776178081","wikidata":"https://www.wikidata.org/wiki/Q3286546","display_name":"Respiratory disease","level":3,"score":0.10840000212192535},{"id":"https://openalex.org/C3018130915","wikidata":"https://www.wikidata.org/wiki/Q1752284","display_name":"Neoplasm staging","level":3,"score":0.10729999840259552}],"mesh":[],"locations_count":2,"locations":[{"id":"doi:10.1016/j.htct.2026.107489","doi":"https://doi.org/10.1016/j.htct.2026.107489","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.htct.2026.107489","pdf_url":"https://www.sciencedirect.com/science/article/pii/S2531137926012368/pdf","source":{"id":"https://openalex.org/S2898598332","display_name":"Hematology Transfusion and Cell Therapy","issn_l":"2531-1379","issn":["2531-1379","2531-1387"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","ki-jl-1","poland-20","russia-white-list-3","scielo"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Hematology, Transfusion and Cell Therapy","raw_type":"journal-article"},{"id":"pmh:oai:doaj.org/article:f0de1e50d5f44f2aaafd8df026ffd224","doi":null,"is_oa":false,"landing_page_url":"https://doaj.org/article/f0de1e50d5f44f2aaafd8df026ffd224","pdf_url":null,"source":{"id":"https://openalex.org/S4306401280","display_name":"DOAJ (DOAJ: Directory of Open Access Journals)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Hematology, Transfusion and Cell Therapy, Vol 48, Iss , Pp 107489- (2026)","raw_type":"article"}],"best_oa_location":{"id":"doi:10.1016/j.htct.2026.107489","doi":"https://doi.org/10.1016/j.htct.2026.107489","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.htct.2026.107489","pdf_url":"https://www.sciencedirect.com/science/article/pii/S2531137926012368/pdf","source":{"id":"https://openalex.org/S2898598332","display_name":"Hematology Transfusion and Cell Therapy","issn_l":"2531-1379","issn":["2531-1379","2531-1387"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","ki-jl-1","poland-20","russia-white-list-3","scielo"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Hematology, Transfusion and Cell Therapy","raw_type":"journal-article"},"sustainable_development_goals":[{"score":1.0,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7223100804.pdf","grobid_xml":"https://content.openalex.org/works/W7223100804.grobid-xml"},"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W7217919031","https://openalex.org/W7151118463","https://openalex.org/W329970212","https://openalex.org/W7046992270","https://openalex.org/W2577241301","https://openalex.org/W4200329430","https://openalex.org/W7133077417","https://openalex.org/W3187860377","https://openalex.org/W7125461923","https://openalex.org/W2921167672"],"abstract_inverted_index":{"Introdu\u00e7\u00e3o":[0],"A":[1,393,437,502],"hipertens\u00e3o":[2],"pulmonar":[3],"(HP)":[4],"em":[5,71,82,113,231,264,267,274,304,421,461],"pacientes":[6,167,233,414,489,506],"com":[7,124,217,288,342,354],"neoplasias":[8],"mieloproliferativas":[9],"(NMP)":[10],"BCR-ABL":[11,77,463],"negativas":[12],"apresenta":[13],"impacto":[14],"progn\u00f3stico":[15],"negativo,":[16],"associando-se":[17],"a":[18,54,310,355,375,379,402,425,476,508],"maior":[19,380],"risco":[20,481],"cardiovascular,":[21],"progress\u00e3o":[22],"para":[23,47,101,131,362],"mielofibrose":[24],"(MF)":[25],"ou":[26,306,417,450],"leucemia":[27],"mieloide":[28],"aguda":[29],"(LMA)":[30],"e":[31,61,68,109,118,134,162,178,186,200,214,257,270,284,326,368,474,507,512],"menor":[32,339,400],"sobrevida.":[33],"Dados":[34],"nacionais":[35],"sobre":[36,459,517],"essa":[37],"complica\u00e7\u00e3o":[38,426],"ainda":[39],"s\u00e3o":[40,92],"escassos,":[41],"tornando":[42],"fundamental":[43],"caracterizar":[44],"coortes":[45],"locais":[46],"refinar":[48],"o":[49,485,518],"manejo":[50],"cl\u00ednico.":[51],"Objetivo":[52],"Avaliar":[53],"preval\u00eancia":[55,394,469],"de":[56,59,64,75,103,106,111,138,144,154,156,164,219,221,227,244,247,293,313,335,364,370,382,396,411,413,430,447,472,480,488,505,510],"alta":[57],"probabilidade":[58,137,226],"HP":[60,139,228,289,343,383,397,460],"identificar":[62],"fatores":[63],"risco/marcadores":[65],"cl\u00ednicos,":[66],"laboratoriais":[67],"moleculares":[69],"associados":[70],"uma":[72],"coorte":[73,204],"brasileira":[74],"NMP":[76,462],"negativas.":[78,464],"Metodologia":[79],"Estudo":[80],"transversal":[81],"andamento":[83],"no":[84,340,428,470],"Hospital":[85],"Universit\u00e1rio":[86],"Pedro":[87],"Ernesto":[88],"(HUPE/UERJ).":[89],"Pacientes":[90,123],"ambulatoriais":[91],"submetidos":[93],"\u00e0":[94,98,190,255],"avalia\u00e7\u00e3o":[95],"ecocardiogr\u00e1fica":[96],"pareada":[97],"coleta":[99],"sangu\u00ednea":[100],"exames":[102],"rotina,":[104],"dosagem":[105],"citocinas":[107,511],"inflamat\u00f3rias":[108],"citometria":[110,513],"fluxo":[112],"sangue":[114],"perif\u00e9rico":[115],"(blastos":[116],"CD34+/CD117+":[117],"c\u00e9lulas":[119],"endoteliais":[120],"precursoras":[121],"CD34+/CD133+).":[122],"MF":[125,180,184,188,245,431,473],"realizam":[126],"Next":[127],"Generation":[128],"Sequencing":[129],"(NGS)":[130],"muta\u00e7\u00f5es":[132,277],"driver":[133],"adicionais.":[135],"Alta":[136,225],"foi":[140,229,337,399],"definida":[141],"por":[142,197,279,409],"velocidade":[143],"regurgita\u00e7\u00e3o":[145],"tric\u00faspide":[146],"(TRV)":[147],">":[148],"2,8":[149],"m/s":[150,238],"ao":[151,242],"ecocardiograma.":[152],"Registro":[153],"comit\u00ea":[155],"\u00e9tica:":[157],"93471225.7.0000.5259":[158],"Resultados":[159],"Entre":[160],"mar\u00e7o":[161],"agosto":[163],"2026,":[165],"29":[166],"foram":[168,201],"inclu\u00eddos":[169],"(10":[170],"Policitemia":[171],"Vera":[172],"[PV],":[173],"5":[174,187],"Trombocitemia":[175],"Essencial":[176],"[TE]":[177],"10":[179],"[2":[181],"pr\u00e9-fibr\u00f3tica,":[182,252],"3":[183,232],"prim\u00e1ria":[185],"secund\u00e1ria":[189,254],"PV]);":[191],"4":[192],"apresentaram":[193],"TRV":[194,235,356],"n\u00e3o":[195],"mensur\u00e1vel":[196],"limita\u00e7\u00f5es":[198],"t\u00e9cnicas":[199],"exclu\u00eddos.":[202],"Na":[203],"analisada":[205],"(n":[206],"=":[207,299,318,324,331,348,358,390],"25),":[208],"64%":[209],"eram":[210],"homens,":[211],"48%":[212,215],"brancos":[213],"pretos/pardos,":[216],"mediana":[218,236],"idade":[220],"66":[222],"anos":[223],"(43\u201387).":[224],"observada":[230],"(12%;":[234],"3,0":[237],"[2,9\u20133,3]),":[239],"todos":[240],"pertencentes":[241],"subgrupo":[243,429,471],"(preval\u00eancia":[246],"30%":[248],"na":[249,404],"MF:":[250],"1":[251,253,258,275],"PV":[256],"prim\u00e1ria).":[259],"Nestes":[260],"pacientes,":[261],"identificou-se":[262],"muta\u00e7\u00e3o":[263],"JAK2":[265],"V617F":[266],"2":[268,273],"(67%)":[269],"CALR":[271],"tipo":[272],"(33%);":[276],"adicionais":[278],"NGS":[280],"inclu\u00edram":[281],"DNMT3A,":[282],"TET2":[283],"CBL.":[285],"O":[286,333],"grupo":[287,341],"apresentou":[290],"maiores":[291,311],"valores":[292],"sPAP":[294],"(mediana":[295,344],"39,0":[296],"mmHg;":[297],"p":[298,317,323,330,347,389],"0,007),":[300],"sem":[301],"diferen\u00e7a":[302],"significativa":[303],"FAC":[305],"TAPSE.":[307],"Observou-se":[308],"tend\u00eancia":[309],"n\u00edveis":[312],"PCR":[314],"(7,4":[315],"mg/L;":[316],"0,44),":[319],"LDH":[320],"(963,5":[321],"U/L;":[322],"0,26)":[325],"NT-proBNP":[327],"(1299,0":[328],"pg/mL;":[329],"0,20).":[332],"n\u00edvel":[334],"hemoglobina":[336],"significativamente":[338],"9,6":[345],"g/dL;":[346],"0,0122),":[349],"mantendo":[350],"correla\u00e7\u00e3o":[351],"cont\u00ednua":[352,504],"negativa":[353],"(p":[357],"0,0145).":[359],"Ap\u00f3s":[360],"ajuste":[361],"tempo":[363,446],"doen\u00e7a,":[365,448],"escores":[366],"progn\u00f3sticos":[367],"presen\u00e7a":[369],"doen\u00e7a":[371],"card\u00edaca":[372],"estrutural":[373],"esquerda,":[374],"anemia":[376,438,477],"manteve-se":[377],"associada":[378],"chance":[381],"(OR":[384],"0,33;":[385],"IC":[386],"95%:":[387],"0,03\u20130,75;":[388],"0,083).":[391],"Discuss\u00e3o":[392],"geral":[395],"(12%)":[398],"que":[401],"descrita":[403],"literatura":[405],"internacional":[406],"(\u223c30%),":[407],"possivelmente":[408],"vi\u00e9s":[410],"sele\u00e7\u00e3o":[412],"menos":[415,499],"idosos":[416],"graves":[418],"atendidos":[419],"ambulatorialmente":[420],"dia":[422],"espec\u00edfico.":[423],"Contudo,":[424],"concentrou-se":[427],"(30%),":[432],"alinhando-se":[433],"aos":[434],"dados":[435,491,515],"globais.":[436],"emergiu":[439],"como":[440,478],"importante":[441],"marcador":[442],"associado,":[443],"independente":[444],"do":[445,455],"gravidade":[449],"cardiopatia":[451],"estrutural.":[452],"Conclus\u00e3o":[453],"Trata-se":[454],"primeiro":[456],"estudo":[457],"brasileiro":[458],"Os":[465],"achados":[466],"mostram":[467],"expressiva":[468],"apontam":[475],"fator":[479],"independente.":[482],"Por":[483],"ora,":[484],"n\u00famero":[486],"limitado":[487],"restringe":[490],"mais":[492],"conclusivos,":[493],"nossa":[494],"expectativa":[495],"\u00e9":[496],"avaliar":[497],"pelo":[498],"114":[500],"participantes.":[501],"inclus\u00e3o":[503],"an\u00e1lise":[509],"trar\u00e3o":[514],"in\u00e9ditos":[516],"entendimento":[519],"dessa":[520],"complica\u00e7\u00e3o.":[521]},"counts_by_year":[],"updated_date":"2026-11-08T12:12:28.789561","created_date":"2026-10-22T00:00:00"}
