{"id":"https://openalex.org/W7222970076","doi":"https://doi.org/10.1093/jscr/rjag924","title":"Delayed diagnosis of congenital pulmonary airway malformation in an infant: diagnostic challenges and surgical implications","display_name":"Delayed diagnosis of congenital pulmonary airway malformation in an infant: diagnostic challenges and surgical implications","publication_year":2026,"publication_date":"2026-10-01","ids":{"openalex":"https://openalex.org/W7222970076","doi":"https://doi.org/10.1093/jscr/rjag924","pmid":"https://pubmed.ncbi.nlm.nih.gov/42899236","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/13679820"},"language":"en","primary_location":{"id":"doi:10.1093/jscr/rjag924","doi":"https://doi.org/10.1093/jscr/rjag924","is_oa":true,"landing_page_url":"https://doi.org/10.1093/jscr/rjag924","pdf_url":null,"source":{"id":"https://openalex.org/S4210198593","display_name":"Journal of Surgical Case Reports","issn_l":"2042-8812","issn":["2042-8812"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","jufo-1","ki-jl-1","norway-1","poland-20","russia-white-list-3"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Surgical Case Reports","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj","pubmed"],"open_access":{"is_oa":true,"oa_status":"gold","oa_url":"https://doi.org/10.1093/jscr/rjag924","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5121864772","display_name":"Nour Srewell","orcid":"https://orcid.org/0009-0006-3735-7400","observed_orcids":["https://orcid.org/0009-0006-3735-7400"]},"institutions":[],"countries":[],"is_corresponding":true,"raw_author_name":"Nour Srewell","raw_affiliation_strings":["Department of Vascular Surgery, Al-Mouwasat University Hospital , Omar Bin Abdul Aziz Street, Mezzeh, Damascus ,"],"raw_orcid":"https://orcid.org/0009-0006-3735-7400","affiliations":[{"raw_affiliation_string":"Department of Vascular Surgery, Al-Mouwasat University Hospital , Omar Bin Abdul Aziz Street, Mezzeh, Damascus ,","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5107613966","display_name":"Youssef Chouman","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Youssef Chouman","raw_affiliation_strings":["Department of Pediatric Surgery, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Surgery, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5159072887","display_name":"Yamama Sharief","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Yamama Sharief","raw_affiliation_strings":["Department of Pediatric Surgery, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Surgery, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5159085741","display_name":"Mohammed Baraa Meqdad","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Mohammed Baraa Meqdad","raw_affiliation_strings":["Department of Pediatric Surgery, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Surgery, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5104431049","display_name":"Mira Hamzeh Rafea","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Mira Hamzeh Rafea","raw_affiliation_strings":["Department of Pediatrics, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatrics, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5159037229","display_name":"Omar Alsalama","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Omar Alsalama","raw_affiliation_strings":["Department of Pediatric Surgery, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Surgery, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5122330246","display_name":"Bushra Alsahan","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Bushra Alsahan","raw_affiliation_strings":["Department of Pediatrics, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatrics, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5111108752","display_name":"Mohammd Abdulkader","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Mohammd Abdulkader","raw_affiliation_strings":["Department of Pediatric Surgery, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Surgery, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5053035020","display_name":"Sawssan Ali","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Sawssan Ali","raw_affiliation_strings":["Department of Pediatrics, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatrics, Children University Hospital , Al-Mouwasat Street, Mezzeh, Damascus ,","institution_ids":[]}]}],"institutions":[],"countries_distinct_count":0,"institutions_distinct_count":0,"corresponding_author_ids":["https://openalex.org/A5121864772"],"corresponding_institution_ids":[],"apc_list":{"value":1000,"currency":"USD","value_usd":1000},"apc_paid":{"value":1000,"currency":"USD","value_usd":1000},"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.81973624,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"2026","issue":"10","first_page":"rjag924","last_page":"rjag924"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11586","display_name":"Congenital Diaphragmatic Hernia Studies","score":0.9984999895095825,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11586","display_name":"Congenital Diaphragmatic Hernia Studies","score":0.9984999895095825,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11260","display_name":"Tracheal and airway disorders","score":0.00039999998989515007,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10549","display_name":"Neonatal Respiratory Health Research","score":0.0003000000142492354,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/congenital-cystic-adenomatoid-malformation","display_name":"congenital cystic adenomatoid malformation","score":1.0},{"id":"https://openalex.org/keywords/delayed-diagnosis","display_name":"delayed diagnosis","score":0.9559999704360962},{"id":"https://openalex.org/keywords/infants","display_name":"infants","score":0.8410000205039978},{"id":"https://openalex.org/keywords/bilobectomy","display_name":"bilobectomy","score":0.7160000205039978},{"id":"https://openalex.org/keywords/chest-ct","display_name":"chest CT","score":0.6819999814033508},{"id":"https://openalex.org/keywords/dyspnea","display_name":"dyspnea","score":0.7490000128746033},{"id":"https://openalex.org/keywords/prenatal-screening","display_name":"prenatal screening","score":0.574999988079071},{"id":"https://openalex.org/keywords/histopathological-diagnosis","display_name":"histopathological diagnosis","score":0.796999990940094}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9836999773979187},{"id":"https://openalex.org/C2777601897","wikidata":"https://www.wikidata.org/wiki/Q3409113","display_name":"Presentation (obstetrics)","level":2,"score":0.713699996471405},{"id":"https://openalex.org/C544855455","wikidata":"https://www.wikidata.org/wiki/Q1070952","display_name":"Histopathology","level":2,"score":0.6229000091552734},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.5253999829292297},{"id":"https://openalex.org/C2778258057","wikidata":"https://www.wikidata.org/wiki/Q1136569","display_name":"Prenatal diagnosis","level":4,"score":0.4934000074863434},{"id":"https://openalex.org/C3019796121","wikidata":"https://www.wikidata.org/wiki/Q5048356","display_name":"Case presentation","level":2,"score":0.4812999963760376},{"id":"https://openalex.org/C105922876","wikidata":"https://www.wikidata.org/wiki/Q1423981","display_name":"Airway","level":2,"score":0.46950000524520874},{"id":"https://openalex.org/C126838900","wikidata":"https://www.wikidata.org/wiki/Q77604","display_name":"Radiology","level":1,"score":0.4399000108242035},{"id":"https://openalex.org/C2777714996","wikidata":"https://www.wikidata.org/wiki/Q7886","display_name":"Lung","level":2,"score":0.38339999318122864},{"id":"https://openalex.org/C3020547009","wikidata":"https://www.wikidata.org/wiki/Q1070952","display_name":"Histopathological examination","level":2,"score":0.3707999885082245},{"id":"https://openalex.org/C2781179581","wikidata":"https://www.wikidata.org/wiki/Q2857712","display_name":"Family history","level":2,"score":0.3628999888896942},{"id":"https://openalex.org/C527108885","wikidata":"https://www.wikidata.org/wiki/Q835153","display_name":"Physical examination","level":2,"score":0.3531000018119812},{"id":"https://openalex.org/C544519230","wikidata":"https://www.wikidata.org/wiki/Q32566","display_name":"Computed tomography","level":2,"score":0.33149999380111694},{"id":"https://openalex.org/C2780597408","wikidata":"https://www.wikidata.org/wiki/Q193211","display_name":"Cyst","level":2,"score":0.26649999618530273},{"id":"https://openalex.org/C2776178081","wikidata":"https://www.wikidata.org/wiki/Q3286546","display_name":"Respiratory disease","level":3,"score":0.25699999928474426},{"id":"https://openalex.org/C206179267","wikidata":"https://www.wikidata.org/wiki/Q188952","display_name":"Medical history","level":2,"score":0.2508000135421753}],"mesh":[],"locations_count":3,"locations":[{"id":"doi:10.1093/jscr/rjag924","doi":"https://doi.org/10.1093/jscr/rjag924","is_oa":true,"landing_page_url":"https://doi.org/10.1093/jscr/rjag924","pdf_url":null,"source":{"id":"https://openalex.org/S4210198593","display_name":"Journal of Surgical Case Reports","issn_l":"2042-8812","issn":["2042-8812"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","jufo-1","ki-jl-1","norway-1","poland-20","russia-white-list-3"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Surgical Case Reports","raw_type":"journal-article"},{"id":"pmh:oai:pubmedcentral.nih.gov:13679820","doi":null,"is_oa":true,"landing_page_url":"https://pmc.ncbi.nlm.nih.gov/articles/PMC13679820/","pdf_url":"https://pmc.ncbi.nlm.nih.gov/articles/PMC13679820/pdf/rjag924.pdf","source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"J Surg Case Rep","raw_type":"Text"},{"id":"pmid:42899236","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/42899236","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of surgical case reports","raw_type":"Case Reports"}],"best_oa_location":{"id":"doi:10.1093/jscr/rjag924","doi":"https://doi.org/10.1093/jscr/rjag924","is_oa":true,"landing_page_url":"https://doi.org/10.1093/jscr/rjag924","pdf_url":null,"source":{"id":"https://openalex.org/S4210198593","display_name":"Journal of Surgical Case Reports","issn_l":"2042-8812","issn":["2042-8812"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","jufo-1","ki-jl-1","norway-1","poland-20","russia-white-list-3"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Surgical Case Reports","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":0.9922999739646912}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7222970076.pdf","grobid_xml":"https://content.openalex.org/works/W7222970076.grobid-xml"},"referenced_works_count":8,"referenced_works":["https://openalex.org/W2112907352","https://openalex.org/W2963473599","https://openalex.org/W3103171760","https://openalex.org/W3150729545","https://openalex.org/W4388231738","https://openalex.org/W4399041371","https://openalex.org/W4401146083","https://openalex.org/W7130657806"],"related_works":["https://openalex.org/W4404392760","https://openalex.org/W7203953139","https://openalex.org/W4313140718","https://openalex.org/W2795635582","https://openalex.org/W4404414901","https://openalex.org/W4382982351","https://openalex.org/W3015017640","https://openalex.org/W7204498134","https://openalex.org/W7155420542","https://openalex.org/W4402322650"],"abstract_inverted_index":{"Although":[0],"congenital":[1],"pulmonary":[2],"airway":[3],"malformation":[4],"(CPAM)":[5],"is":[6],"usually":[7],"diagnosed":[8,31],"during":[9],"prenatal":[10,57],"screening,":[11],"delayed":[12,132],"presentation":[13,133],"may":[14],"increase":[15],"diagnostic":[16],"uncertainty":[17],"and":[18,32,49,101,104,109,122,127],"operative":[19,135],"complexity.":[20,136],"We":[21],"report,":[22],"to":[23],"our":[24],"knowledge,":[25],"the":[26,53,70,115],"first":[27],"case":[28,113],"of":[29,46,55,118],"CPAM":[30,108,126],"surgically":[33],"managed":[34],"in":[35,37,52,69,124],"Syria":[36],"a":[38,43,66,83],"4-month-old":[39],"infant":[40],"presenting":[41],"with":[42,82],"1-month":[44],"history":[45],"dyspnea,":[47],"fever,":[48],"poor":[50],"feeding":[51],"absence":[54],"routine":[56],"screening.":[58],"Initial":[59],"chest":[60,75],"radiography,":[61],"although":[62],"technically":[63],"limited,":[64],"demonstrated":[65],"rounded":[67],"opacity":[68],"right":[71,99],"hemithorax,":[72],"while":[73],"non-contrast":[74],"computed":[76],"tomography":[77],"(CT)":[78],"revealed":[79],"multicystic":[80],"lesions":[81],"hyperattenuating":[84],"intralesional":[85],"component,":[86],"raising":[87],"suspicion":[88],"for":[89],"secondary":[90],"infection":[91],"or":[92],"pleuropulmonary":[93],"blastoma":[94],"(PPB).":[95],"The":[96],"patient":[97],"underwent":[98],"upper":[100],"middle":[102],"bilobectomy,":[103],"histopathological":[105],"examination":[106],"confirmed":[107],"excluded":[110],"PPB.":[111],"This":[112],"highlights":[114],"complementary":[116],"roles":[117],"postnatal":[119],"CT,":[120],"surgery,":[121],"histopathology":[123],"confirming":[125],"excluding":[128],"PPB,":[129],"particularly":[130],"when":[131],"increases":[134]},"counts_by_year":[],"updated_date":"2026-11-08T12:12:28.789561","created_date":"2026-10-20T00:00:00"}
