{"id":"https://openalex.org/W7220121237","doi":null,"title":"Acute Chest Syndrome: A Leading Cause of Death in Sickle Cell Disease","display_name":"Acute Chest Syndrome: A Leading Cause of Death in Sickle Cell Disease","publication_year":2023,"publication_date":"2023-08-18","ids":{"openalex":"https://openalex.org/W7220121237"},"language":"en","primary_location":{"id":"pmh:oai:njhaem.org.ng:article/13","doi":null,"is_oa":true,"landing_page_url":"https://njhaem.org.ng/index.php/home/article/view/13","pdf_url":"https://njhaem.org.ng/index.php/home/article/download/13/1","source":{"id":"https://openalex.org/S7407078253","display_name":"Nigerian Journal of Haematology","issn_l":"2635-3024","issn":["2635-3024"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"2635-3024","raw_type":"info:eu-repo/semantics/article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":[],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://njhaem.org.ng/index.php/home/article/download/13/1","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5156993612","display_name":"E. I. Uche","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I126541806","display_name":"Lagos State University","ror":"https://ror.org/01za8fg18","country_code":"NG","type":"education","lineage":["https://openalex.org/I126541806"]}],"countries":["NG"],"is_corresponding":false,"raw_author_name":"Uche, E","raw_affiliation_strings":["Department of Hematology and Blood Transfusion, Lagos State University, College of Medicine PMB"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology and Blood Transfusion, Lagos State University, College of Medicine PMB","institution_ids":["https://openalex.org/I126541806"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5157097422","display_name":"A. A. Akinbami","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I126541806","display_name":"Lagos State University","ror":"https://ror.org/01za8fg18","country_code":"NG","type":"education","lineage":["https://openalex.org/I126541806"]}],"countries":["NG"],"is_corresponding":false,"raw_author_name":"Akinbami, A","raw_affiliation_strings":["Department of Hematology and Blood Transfusion, Lagos State University, College of Medicine PMB"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology and Blood Transfusion, Lagos State University, College of Medicine PMB","institution_ids":["https://openalex.org/I126541806"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5157056567","display_name":"A Dosunmu","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I126541806","display_name":"Lagos State University","ror":"https://ror.org/01za8fg18","country_code":"NG","type":"education","lineage":["https://openalex.org/I126541806"]}],"countries":["NG"],"is_corresponding":false,"raw_author_name":"Dosunmu , A","raw_affiliation_strings":["Department of Hematology and Blood Transfusion, Lagos State University, College of Medicine PMB"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology and Blood Transfusion, Lagos State University, College of Medicine PMB","institution_ids":["https://openalex.org/I126541806"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5157061101","display_name":"A. Adediran","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I197610006","display_name":"University of Lagos","ror":"https://ror.org/05rk03822","country_code":"NG","type":"education","lineage":["https://openalex.org/I197610006"]}],"countries":["NG"],"is_corresponding":false,"raw_author_name":"Adediran , A.","raw_affiliation_strings":["Department of Hematology and Blood Transfusion, Faculty of Clinical Sciences, College of Medicine, University of Lagos, Nigeria"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology and Blood Transfusion, Faculty of Clinical Sciences, College of Medicine, University of Lagos, Nigeria","institution_ids":["https://openalex.org/I197610006"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.4592071,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10554","display_name":"Hemoglobinopathies and Related Disorders","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10554","display_name":"Hemoglobinopathies and Related Disorders","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12845","display_name":"Methemoglobinemia and Tumor Lysis Syndrome","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10041","display_name":"COVID-19 Clinical Research Studies","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2725","display_name":"Infectious Diseases"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/acute-chest-syndrome","display_name":"acute chest syndrome","score":0.9990000128746033},{"id":"https://openalex.org/keywords/sickle-cell-disease","display_name":"sickle cell disease","score":1.0},{"id":"https://openalex.org/keywords/mortality","display_name":"mortality","score":0.8809999823570251},{"id":"https://openalex.org/keywords/vaso-occlusive-crisis","display_name":"vaso-occlusive crisis","score":0.9649999737739563},{"id":"https://openalex.org/keywords/abdominal-surgery","display_name":"abdominal surgery","score":0.5870000123977661},{"id":"https://openalex.org/keywords/respiratory-failure","display_name":"respiratory failure","score":0.8889999985694885},{"id":"https://openalex.org/keywords/diagnosis","display_name":"diagnosis","score":0.7730000019073486}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8988000154495239},{"id":"https://openalex.org/C2780976302","wikidata":"https://www.wikidata.org/wiki/Q4677915","display_name":"Acute chest syndrome","level":4,"score":0.8529000282287598},{"id":"https://openalex.org/C137627325","wikidata":"https://www.wikidata.org/wiki/Q156318","display_name":"Etiology","level":2,"score":0.6638000011444092},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.6535000205039978},{"id":"https://openalex.org/C177713679","wikidata":"https://www.wikidata.org/wiki/Q679690","display_name":"Intensive care medicine","level":1,"score":0.5587000250816345},{"id":"https://openalex.org/C61511704","wikidata":"https://www.wikidata.org/wiki/Q1671857","display_name":"Incidence (geometry)","level":2,"score":0.47380000352859497},{"id":"https://openalex.org/C2778620579","wikidata":"https://www.wikidata.org/wiki/Q185034","display_name":"Sickle cell anemia","level":3,"score":0.40049999952316284},{"id":"https://openalex.org/C190892606","wikidata":"https://www.wikidata.org/wiki/Q3512464","display_name":"Radiological weapon","level":2,"score":0.37450000643730164},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.3736000061035156},{"id":"https://openalex.org/C2779473830","wikidata":"https://www.wikidata.org/wiki/Q1540899","display_name":"MEDLINE","level":2,"score":0.32199999690055847},{"id":"https://openalex.org/C2777698277","wikidata":"https://www.wikidata.org/wiki/Q266018","display_name":"Acute coronary syndrome","level":3,"score":0.2994000017642975},{"id":"https://openalex.org/C29374701","wikidata":"https://www.wikidata.org/wiki/Q1931388","display_name":"Cause of death","level":3,"score":0.29679998755455017},{"id":"https://openalex.org/C2776178081","wikidata":"https://www.wikidata.org/wiki/Q3286546","display_name":"Respiratory disease","level":3,"score":0.2827000021934509},{"id":"https://openalex.org/C179755657","wikidata":"https://www.wikidata.org/wiki/Q58702","display_name":"Mortality rate","level":2,"score":0.2822999954223633},{"id":"https://openalex.org/C2778384902","wikidata":"https://www.wikidata.org/wiki/Q183134","display_name":"Sepsis","level":2,"score":0.2572999894618988}],"mesh":[],"locations_count":1,"locations":[{"id":"pmh:oai:njhaem.org.ng:article/13","doi":null,"is_oa":true,"landing_page_url":"https://njhaem.org.ng/index.php/home/article/view/13","pdf_url":"https://njhaem.org.ng/index.php/home/article/download/13/1","source":{"id":"https://openalex.org/S7407078253","display_name":"Nigerian Journal of Haematology","issn_l":"2635-3024","issn":["2635-3024"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"2635-3024","raw_type":"info:eu-repo/semantics/article"}],"best_oa_location":{"id":"pmh:oai:njhaem.org.ng:article/13","doi":null,"is_oa":true,"landing_page_url":"https://njhaem.org.ng/index.php/home/article/view/13","pdf_url":"https://njhaem.org.ng/index.php/home/article/download/13/1","source":{"id":"https://openalex.org/S7407078253","display_name":"Nigerian Journal of Haematology","issn_l":"2635-3024","issn":["2635-3024"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"2635-3024","raw_type":"info:eu-repo/semantics/article"},"sustainable_development_goals":[{"display_name":"Good health and well-being","score":1.0,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7220121237.pdf","grobid_xml":"https://content.openalex.org/works/W7220121237.grobid-xml"},"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W4281769813","https://openalex.org/W2796912475","https://openalex.org/W2762571010","https://openalex.org/W2034039634","https://openalex.org/W1978409215","https://openalex.org/W1906580417","https://openalex.org/W2535945527","https://openalex.org/W7202193567","https://openalex.org/W2105956653","https://openalex.org/W4206491903"],"abstract_inverted_index":{"Acute":[0,156],"chest":[1,157],"syndrome":[2,158],"(ACS)":[3],"is":[4,16],"a":[5,188],"leading":[6],"cause":[7],"of":[8,18,22,33,70,84,93,117,165,190],"mortality":[9],"in":[10,65,107,141,152,176],"sickle":[11,23],"cell":[12,24,161],"disease":[13],"(SCD),":[14],"and":[15,59,78,96,114,125,147,159],"one":[17],"the":[19,31,91,112,153],"numerous":[20],"complications":[21],"disease.":[25,162],"The":[26,68,135,163],"aetiological":[27],"factors":[28],"associated":[29,133],"with":[30],"development":[32],"ACS":[34,42,71,106],"could":[35],"either":[36,38],"be":[37,63],"infectious":[39],"or":[40,45,52],"non-infectious.":[41],"develops":[43],"insidiously":[44],"suddenly,":[46],"during":[47],"admission":[48],"for":[49,181],"vaso-occlusive":[50],"crises,":[51],"after":[53],"surgery":[54],"particularly":[55],"abdominal":[56],"surgery.":[57],"Diagnosing":[58],"managing":[60],"it":[61],"may":[62],"challenging":[64],"in-experienced":[66],"hands.":[67],"outcome":[69],"depends":[72],"on":[73,105,111],"rapid":[74],"diagnosis":[75],"(clinical,":[76],"radiological":[77],"laboratory),":[79],"as":[80,82],"well":[81],"institution":[83],"appropriate":[85],"management,":[86],"which":[87],"aims":[88,102],"to":[89,103,109,197],"reduce":[90],"incidence":[92],"respiratory":[94],"failure,":[95],"death.":[97],"Therefore,":[98],"this":[99,142,177,182],"review":[100,143,183],"article":[101,184],"elucidate":[104],"order":[108],"improve":[110],"diagnostic":[113],"management":[115],"skills":[116],"Emergency":[118],"Physicians/":[119],"Surgeons,":[120],"Pediatricians,":[121],"Family":[122],"Physicians,":[123],"Internists":[124],"Haematologists":[126],"who":[127],"manage":[128],"SCD":[129],"patients,":[130],"thus":[131],"reducing":[132],"mortality.":[134],"following":[136],"search":[137,154,180],"engines":[138],"were":[139,174],"used":[140,151],"article:":[144],"Google,":[145],"Pubmed":[146],"UpToDate.":[148],"Key":[149],"words":[150],"were:":[155],"Sickle":[160],"number":[164],"articles":[166,173],"initially":[167],"obtained":[168],"was":[169,185],"53;":[170],"however":[171],"41":[172],"included":[175],"review.":[178],"Literature":[179],"conducted":[186],"over":[187],"period":[189],"four":[191],"(4)":[192],"months":[193],"from":[194],"June":[195],"2016":[196],"October":[198],"2016.":[199]},"counts_by_year":[],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2026-10-05T00:00:00"}
