{"id":"https://openalex.org/W7211879024","doi":"https://doi.org/10.2169/internalmedicine.7871-26","title":"Vasculitis Syndromes with Renal Involvement: A Review from a Case Series","display_name":"Vasculitis Syndromes with Renal Involvement: A Review from a Case Series","publication_year":2026,"publication_date":"2026-01-01","ids":{"openalex":"https://openalex.org/W7211879024","doi":"https://doi.org/10.2169/internalmedicine.7871-26","pmid":"https://pubmed.ncbi.nlm.nih.gov/42716747"},"language":"en","primary_location":{"id":"doi:10.2169/internalmedicine.7871-26","doi":"https://doi.org/10.2169/internalmedicine.7871-26","is_oa":true,"landing_page_url":"https://doi.org/10.2169/internalmedicine.7871-26","pdf_url":"https://www.jstage.jst.go.jp/article/internalmedicine/advpub/0/advpub_7871-26/_pdf","source":{"id":"https://openalex.org/S154471048","display_name":"Internal Medicine","issn_l":"0918-2918","issn":["0918-2918","1349-7235"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-1","medline","norway-1","poland-40","russia-white-list-2"],"host_organization":"https://openalex.org/P4310313351","host_organization_name":"The Japanese Society of Internal Medicine","host_organization_lineage":["https://openalex.org/P4310313351"],"host_organization_lineage_names":["The Japanese Society of Internal Medicine"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Internal Medicine","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://www.jstage.jst.go.jp/article/internalmedicine/advpub/0/advpub_7871-26/_pdf","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5004884368","display_name":"Yoshifumi Ubara","orcid":"https://orcid.org/0000-0003-2322-8203","observed_orcids":["https://orcid.org/0000-0003-2322-8203"]},"institutions":[{"id":"https://openalex.org/I4210166463","display_name":"Toranomon Hospital","ror":"https://ror.org/05rkz5e28","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210166463"]},{"id":"https://openalex.org/I4399598392","display_name":"Okinaka Memorial Institute for Medical Research","ror":"https://ror.org/03ge26363","country_code":"JP","type":"facility","lineage":["https://openalex.org/I4399598392"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"Yoshifumi Ubara","raw_affiliation_strings":["Department of Nephrology and Rheumatology, Toranomon Hospital, Japan","The Okinaka Memorial Institute for Medical Research, Toranomon Hospital, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Nephrology and Rheumatology, Toranomon Hospital, Japan","institution_ids":["https://openalex.org/I4210166463"]},{"raw_affiliation_string":"The Okinaka Memorial Institute for Medical Research, Toranomon Hospital, Japan","institution_ids":["https://openalex.org/I4210166463","https://openalex.org/I4399598392"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5044514866","display_name":"Kei Kono","orcid":"https://orcid.org/0009-0000-5097-3538","observed_orcids":["https://orcid.org/0009-0000-5097-3538"]},"institutions":[{"id":"https://openalex.org/I4210166463","display_name":"Toranomon Hospital","ror":"https://ror.org/05rkz5e28","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210166463"]},{"id":"https://openalex.org/I4399598392","display_name":"Okinaka Memorial Institute for Medical Research","ror":"https://ror.org/03ge26363","country_code":"JP","type":"facility","lineage":["https://openalex.org/I4399598392"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"Kei Kono","raw_affiliation_strings":["Department of Pathology, Toranomon Hospital, Japan","The Okinaka Memorial Institute for Medical Research, Toranomon Hospital, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pathology, Toranomon Hospital, Japan","institution_ids":["https://openalex.org/I4210166463"]},{"raw_affiliation_string":"The Okinaka Memorial Institute for Medical Research, Toranomon Hospital, Japan","institution_ids":["https://openalex.org/I4210166463","https://openalex.org/I4399598392"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5016304823","display_name":"Naoki Sawa","orcid":"https://orcid.org/0000-0003-2092-4094","observed_orcids":["https://orcid.org/0000-0003-2092-4094"]},"institutions":[{"id":"https://openalex.org/I4210166463","display_name":"Toranomon Hospital","ror":"https://ror.org/05rkz5e28","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210166463"]},{"id":"https://openalex.org/I4399598392","display_name":"Okinaka Memorial Institute for Medical Research","ror":"https://ror.org/03ge26363","country_code":"JP","type":"facility","lineage":["https://openalex.org/I4399598392"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"Naoki Sawa","raw_affiliation_strings":["Department of Nephrology and Rheumatology, Toranomon Hospital, Japan","The Okinaka Memorial Institute for Medical Research, Toranomon Hospital, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Nephrology and Rheumatology, Toranomon Hospital, Japan","institution_ids":["https://openalex.org/I4210166463"]},{"raw_affiliation_string":"The Okinaka Memorial Institute for Medical Research, Toranomon Hospital, Japan","institution_ids":["https://openalex.org/I4210166463","https://openalex.org/I4399598392"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.65627034,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10697","display_name":"Vasculitis and related conditions","score":0.9937000274658203,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10697","display_name":"Vasculitis and related conditions","score":0.9937000274658203,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11029","display_name":"Renal Diseases and Glomerulopathies","score":0.00559999980032444,"subfield":{"id":"https://openalex.org/subfields/2727","display_name":"Nephrology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11735","display_name":"Peripheral Neuropathies and Disorders","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/vasculitis","display_name":"vasculitis","score":0.8989999890327454},{"id":"https://openalex.org/keywords/renal-involvement","display_name":"renal involvement","score":0.972000002861023},{"id":"https://openalex.org/keywords/kidney-biopsy","display_name":"renal biopsy","score":0.8339999914169312},{"id":"https://openalex.org/keywords/microscopic-polyangiitis","display_name":"microscopic polyangiitis","score":0.9869999885559082},{"id":"https://openalex.org/keywords/granulomatosis-with-polyangiitis","display_name":"granulomatosis with polyangiitis","score":1.0},{"id":"https://openalex.org/keywords/eosinophilic-granulomatosis-with-polyangiitis","display_name":"eosinophilic granulomatosis with polyangiitis","score":0.9929999709129333},{"id":"https://openalex.org/keywords/goodpasture-syndrome","display_name":"Goodpasture's syndrome","score":0.9160000085830688},{"id":"https://openalex.org/keywords/henoch-schonlein-purpura","display_name":"IgA vasculitis","score":0.9240000247955322},{"id":"https://openalex.org/keywords/iga-nephropathy","display_name":"IgA nephropathy","score":0.9919999837875366},{"id":"https://openalex.org/keywords/crescentic-glomerulonephritis","display_name":"crescentic glomerulonephritis","score":0.9629999995231628},{"id":"https://openalex.org/keywords/end-stage-renal-disease","display_name":"end-stage renal disease","score":0.7680000066757202},{"id":"https://openalex.org/keywords/immune-complex-vasculitis","display_name":"immune complex vasculitis","score":0.8240000009536743},{"id":"https://openalex.org/keywords/small-vessel-vasculitis","display_name":"small vessel vasculitis","score":0.8460000157356262}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9731000065803528},{"id":"https://openalex.org/C2776015282","wikidata":"https://www.wikidata.org/wiki/Q644318","display_name":"Vasculitis","level":3,"score":0.6578999757766724},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.5073999762535095},{"id":"https://openalex.org/C143724316","wikidata":"https://www.wikidata.org/wiki/Q312468","display_name":"Series (stratigraphy)","level":2,"score":0.47929999232292175},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.3637999892234802},{"id":"https://openalex.org/C2780368995","wikidata":"https://www.wikidata.org/wiki/Q605006","display_name":"Glomerulonephritis","level":3,"score":0.33480000495910645},{"id":"https://openalex.org/C2778653478","wikidata":"https://www.wikidata.org/wiki/Q1054718","display_name":"Kidney disease","level":2,"score":0.32910001277923584},{"id":"https://openalex.org/C2779473830","wikidata":"https://www.wikidata.org/wiki/Q1540899","display_name":"MEDLINE","level":2,"score":0.3192000091075897},{"id":"https://openalex.org/C126838900","wikidata":"https://www.wikidata.org/wiki/Q77604","display_name":"Radiology","level":1,"score":0.31630000472068787},{"id":"https://openalex.org/C2910998276","wikidata":"https://www.wikidata.org/wiki/Q7148839","display_name":"ANCA-Associated Vasculitis","level":4,"score":0.3160000145435333},{"id":"https://openalex.org/C2780091579","wikidata":"https://www.wikidata.org/wiki/Q9377","display_name":"Kidney","level":2,"score":0.301800012588501},{"id":"https://openalex.org/C2777374719","wikidata":"https://www.wikidata.org/wiki/Q7663822","display_name":"Systemic vasculitis","level":4,"score":0.27810001373291016},{"id":"https://openalex.org/C2777466421","wikidata":"https://www.wikidata.org/wiki/Q1266890","display_name":"Vascular disease","level":2,"score":0.2662000060081482},{"id":"https://openalex.org/C2781184683","wikidata":"https://www.wikidata.org/wiki/Q1054718","display_name":"Nephropathy","level":3,"score":0.2524000108242035},{"id":"https://openalex.org/C2776263479","wikidata":"https://www.wikidata.org/wiki/Q32811","display_name":"Churg-strauss syndrome","level":4,"score":0.25040000677108765}],"mesh":[],"locations_count":2,"locations":[{"id":"doi:10.2169/internalmedicine.7871-26","doi":"https://doi.org/10.2169/internalmedicine.7871-26","is_oa":true,"landing_page_url":"https://doi.org/10.2169/internalmedicine.7871-26","pdf_url":"https://www.jstage.jst.go.jp/article/internalmedicine/advpub/0/advpub_7871-26/_pdf","source":{"id":"https://openalex.org/S154471048","display_name":"Internal Medicine","issn_l":"0918-2918","issn":["0918-2918","1349-7235"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-1","medline","norway-1","poland-40","russia-white-list-2"],"host_organization":"https://openalex.org/P4310313351","host_organization_name":"The Japanese Society of Internal Medicine","host_organization_lineage":["https://openalex.org/P4310313351"],"host_organization_lineage_names":["The Japanese Society of Internal Medicine"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Internal Medicine","raw_type":"journal-article"},{"id":"pmid:42716747","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/42716747","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Internal medicine (Tokyo, Japan)","raw_type":"Journal Article"}],"best_oa_location":{"id":"doi:10.2169/internalmedicine.7871-26","doi":"https://doi.org/10.2169/internalmedicine.7871-26","is_oa":true,"landing_page_url":"https://doi.org/10.2169/internalmedicine.7871-26","pdf_url":"https://www.jstage.jst.go.jp/article/internalmedicine/advpub/0/advpub_7871-26/_pdf","source":{"id":"https://openalex.org/S154471048","display_name":"Internal Medicine","issn_l":"0918-2918","issn":["0918-2918","1349-7235"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-1","medline","norway-1","poland-40","russia-white-list-2"],"host_organization":"https://openalex.org/P4310313351","host_organization_name":"The Japanese Society of Internal Medicine","host_organization_lineage":["https://openalex.org/P4310313351"],"host_organization_lineage_names":["The Japanese Society of Internal Medicine"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Internal Medicine","raw_type":"journal-article"},"sustainable_development_goals":[{"display_name":"Good health and well-being","score":0.9763000011444092,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7211879024.pdf","grobid_xml":"https://content.openalex.org/works/W7211879024.grobid-xml"},"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W2006221964","https://openalex.org/W2272763330","https://openalex.org/W4308189242","https://openalex.org/W4399386681","https://openalex.org/W363257329","https://openalex.org/W2182321004","https://openalex.org/W6949496615","https://openalex.org/W2028099374","https://openalex.org/W1979406074","https://openalex.org/W4297519921"],"abstract_inverted_index":{"This":[0],"review":[1],"describes":[2],"vasculitis":[3,131],"syndromes":[4],"that":[5,105],"can":[6],"be":[7],"diagnosed":[8],"by":[9,80,139],"kidney":[10,45,61,69],"biopsy.":[11,46],"Microscopic":[12],"polyangiitis":[13,18,76],"(MPA)":[14],"and":[15,54,83,86],"granulomatosis":[16,74],"with":[17,36,52,75,115],"(GPA)":[19],"typically":[20],"follow":[21],"a":[22,33,44,68,99,112],"rapidly":[23],"progressive":[24,103],"course,":[25],"often":[26,91],"leading":[27],"to":[28,107,133],"end-stage":[29,108],"renal":[30,88,109],"failure":[31,110],"within":[32,111],"few":[34,113],"months,":[35],"crescentic":[37],"glomerulonephritis":[38,97,104],"being":[39],"the":[40,60,87],"predominant":[41],"finding":[42],"on":[43],"However,":[47],"some":[48],"types":[49],"primarily":[50],"present":[51],"fever":[53],"elevated":[55],"C-reactive":[56],"protein":[57],"levels,":[58],"while":[59],"function":[62],"is":[63,78,90,98],"preserved;":[64],"in":[65],"such":[66],"cases,":[67],"biopsy":[70],"shows":[71],"arteriolitis.":[72],"Eosinophilic":[73],"(EGPA)":[77],"characterized":[79],"eosinophil":[81],"infiltration":[82],"small-artery":[84],"arteritis,":[85],"prognosis":[89],"favorable.":[92],"Anti-glomerular":[93],"basement":[94],"membrane":[95],"(GBM)":[96],"hyperacute":[100],"form":[101],"of":[102,129],"leads":[106],"weeks,":[114],"most":[116],"glomeruli":[117],"exhibiting":[118],"synchronous":[119],"necrotizing":[120],"glomerulitis.":[121],"Among":[122],"immune":[123],"complex-mediated":[124],"small-vessel":[125],"vasculitides,":[126],"many":[127],"cases":[128,137],"IgA":[130,134],"correspond":[132],"nephropathy;":[135],"however,":[136],"accompanied":[138],"endocapillary":[140],"hypercellularity":[141],"have":[142],"also":[143],"been":[144],"observed.":[145]},"counts_by_year":[],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2026-09-08T00:00:00"}
