{"id":"https://openalex.org/W7207613271","doi":"https://doi.org/10.70577/1gfsa660","title":"Vasculitis por IgG4 multiorg\u00e1nica: aneurisma disecante de la aorta abdominal, pseudo-tumor renal y p\u00e9rdida visual bilateral fulminante: revisi\u00f3n sistem\u00e1tica","display_name":"Vasculitis por IgG4 multiorg\u00e1nica: aneurisma disecante de la aorta abdominal, pseudo-tumor renal y p\u00e9rdida visual bilateral fulminante: revisi\u00f3n sistem\u00e1tica","publication_year":2026,"publication_date":"2026-09-03","ids":{"openalex":"https://openalex.org/W7207613271","doi":"https://doi.org/10.70577/1gfsa660"},"language":"en","primary_location":{"id":"doi:10.70577/1gfsa660","doi":"https://doi.org/10.70577/1gfsa660","is_oa":true,"landing_page_url":"https://doi.org/10.70577/1gfsa660","pdf_url":"https://smijournal.com/index.php/files/article/download/138/142","source":{"id":"https://openalex.org/S7407055980","display_name":"Salud Medicina e Innovaci\u00f3n Journal","issn_l":"3121-2980","issn":["3121-2980"],"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":["latindex"],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":"cc-by-nc-sa","license_id":"https://openalex.org/licenses/cc-by-nc-sa","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Salud Medicina e Innovaci\u00f3n Journal","raw_type":"journal-article"},"parent_works":[],"lineage":["https://openalex.org/W7207613271"],"child_works_count":0,"type":"article","is_traditional":true,"indexed_in":["crossref"],"open_access":{"is_oa":true,"oa_status":"hybrid","oa_url":"https://smijournal.com/index.php/files/article/download/138/142","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5050726610","display_name":"Diego Roberto Orrala Mendoza","orcid":"https://orcid.org/0009-0009-2778-6334","observed_orcids":["https://orcid.org/0009-0009-2778-6334"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Diego Roberto Orrala Mendoza","raw_affiliation_strings":["Investigador Independiente"],"raw_orcid":"https://orcid.org/0009-0009-2778-6334","affiliations":[{"raw_affiliation_string":"Investigador Independiente","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5149664997","display_name":"Ivana Elizabeth Flores Ram\u00edrez","orcid":"https://orcid.org/0009-0008-1576-3904","observed_orcids":["https://orcid.org/0009-0008-1576-3904"]},"institutions":[{"id":"https://openalex.org/I2405095","display_name":"University of Guayaquil","ror":"https://ror.org/047kyg834","country_code":"EC","type":"education","lineage":["https://openalex.org/I2405095"]},{"id":"https://openalex.org/I4210090927","display_name":"Universidad Estatal de Milagro","ror":"https://ror.org/00gd7ns03","country_code":"EC","type":"education","lineage":["https://openalex.org/I4210090927"]}],"countries":["EC"],"is_corresponding":false,"raw_author_name":"Ivana Elizabeth Flores Ram\u00edrez","raw_affiliation_strings":["Universidad de Guayaquil"],"raw_orcid":"https://orcid.org/0009-0008-1576-3904","affiliations":[{"raw_affiliation_string":"Universidad de Guayaquil","institution_ids":["https://openalex.org/I2405095","https://openalex.org/I4210090927"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5108980564","display_name":"Luis Felipe Oviedo Vasquez","orcid":"https://orcid.org/0009-0002-3067-3575","observed_orcids":["https://orcid.org/0009-0002-3067-3575"]},"institutions":[{"id":"https://openalex.org/I2405095","display_name":"University of Guayaquil","ror":"https://ror.org/047kyg834","country_code":"EC","type":"education","lineage":["https://openalex.org/I2405095"]},{"id":"https://openalex.org/I4210090927","display_name":"Universidad Estatal de Milagro","ror":"https://ror.org/00gd7ns03","country_code":"EC","type":"education","lineage":["https://openalex.org/I4210090927"]}],"countries":["EC"],"is_corresponding":false,"raw_author_name":"Luis Felipe Oviedo V\u00e1squez","raw_affiliation_strings":["Universidad de Guayaquil"],"raw_orcid":"https://orcid.org/0009-0002-3067-3575","affiliations":[{"raw_affiliation_string":"Universidad de Guayaquil","institution_ids":["https://openalex.org/I2405095","https://openalex.org/I4210090927"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5149775338","display_name":"Fernando David Rivera P\u00e9rez","orcid":"https://orcid.org/0009-0006-5302-6361","observed_orcids":["https://orcid.org/0009-0006-5302-6361"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Fernando David Rivera P\u00e9rez","raw_affiliation_strings":["GAD Municipal de Pastaza"],"raw_orcid":"https://orcid.org/0009-0006-5302-6361","affiliations":[{"raw_affiliation_string":"GAD Municipal de Pastaza","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5149920668","display_name":"Arleth Bianka S\u00e1nchez Pacheco","orcid":"https://orcid.org/0009-0005-3727-4800","observed_orcids":["https://orcid.org/0009-0005-3727-4800"]},"institutions":[{"id":"https://openalex.org/I4210125208","display_name":"Hospital de S\u00e3o Marcos","ror":"https://ror.org/040bb8882","country_code":"PT","type":"healthcare","lineage":["https://openalex.org/I4210125208"]}],"countries":["PT"],"is_corresponding":false,"raw_author_name":"Arleth Bianka S\u00e1nchez Pacheco","raw_affiliation_strings":["Hospital San Marcos"],"raw_orcid":"https://orcid.org/0009-0005-3727-4800","affiliations":[{"raw_affiliation_string":"Hospital San Marcos","institution_ids":["https://openalex.org/I4210125208"]}]}],"institutions":[],"countries_distinct_count":2,"institutions_distinct_count":3,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"4","issue":"3","first_page":"851","last_page":"870"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11576","display_name":"IgG4-Related and Inflammatory Diseases","score":0.9990000128746033,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11576","display_name":"IgG4-Related and Inflammatory Diseases","score":0.9990000128746033,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10697","display_name":"Vasculitis and related conditions","score":0.0006000000284984708,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11892","display_name":"Kawasaki Disease and Coronary Complications","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2735","display_name":"Pediatrics, Perinatology and Child Health"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/igg4-related-disease","display_name":"IgG4-related disease","score":0.9539999961853027},{"id":"https://openalex.org/keywords/igg4-related-vasculitis","display_name":"IgG4-related vasculitis","score":0.9649999737739563},{"id":"https://openalex.org/keywords/renal-pseudotumor","display_name":"renal pseudotumor","score":0.8650000095367432},{"id":"https://openalex.org/keywords/bilateral-vision-loss","display_name":"bilateral vision loss","score":0.7609999775886536},{"id":"https://openalex.org/keywords/optic-neuropathy","display_name":"optic neuropathy","score":0.7829999923706055},{"id":"https://openalex.org/keywords/orbital-involvement","display_name":"orbital involvement","score":0.8769999742507935},{"id":"https://openalex.org/keywords/multisystem-involvement","display_name":"multisystem involvement","score":0.8769999742507935},{"id":"https://openalex.org/keywords/igg4-positive-plasma-cells","display_name":"IgG4-positive plasma cells","score":0.7429999709129333},{"id":"https://openalex.org/keywords/corticosteroid-therapy","display_name":"corticosteroid therapy","score":0.9020000100135803},{"id":"https://openalex.org/keywords/early-diagnosis","display_name":"early diagnosis","score":0.5370000004768372},{"id":"https://openalex.org/keywords/cardiovascular-complications","display_name":"cardiovascular complications","score":0.5379999876022339},{"id":"https://openalex.org/keywords/renal-complications","display_name":"renal complications","score":0.45399999618530273}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9275000095367432},{"id":"https://openalex.org/C2781107259","wikidata":"https://www.wikidata.org/wiki/Q5508364","display_name":"Fulminant","level":2,"score":0.7226999998092651},{"id":"https://openalex.org/C2776015282","wikidata":"https://www.wikidata.org/wiki/Q644318","display_name":"Vasculitis","level":3,"score":0.6432999968528748},{"id":"https://openalex.org/C24040308","wikidata":"https://www.wikidata.org/wiki/Q574727","display_name":"Anti-neutrophil cytoplasmic antibody","level":4,"score":0.47929999232292175},{"id":"https://openalex.org/C126838900","wikidata":"https://www.wikidata.org/wiki/Q77604","display_name":"Radiology","level":1,"score":0.41999998688697815},{"id":"https://openalex.org/C2779993142","wikidata":"https://www.wikidata.org/wiki/Q594660","display_name":"Aortic dissection","level":3,"score":0.414900004863739},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.38760000467300415},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.3521000146865845},{"id":"https://openalex.org/C2779701055","wikidata":"https://www.wikidata.org/wiki/Q929833","display_name":"Rare disease","level":3,"score":0.34540000557899475},{"id":"https://openalex.org/C2777374719","wikidata":"https://www.wikidata.org/wiki/Q7663822","display_name":"Systemic vasculitis","level":4,"score":0.30959999561309814},{"id":"https://openalex.org/C2778674544","wikidata":"https://www.wikidata.org/wiki/Q1414805","display_name":"Systemic disease","level":3,"score":0.3075999915599823},{"id":"https://openalex.org/C2780520971","wikidata":"https://www.wikidata.org/wiki/Q2264329","display_name":"Abdominal aorta","level":3,"score":0.30239999294281006},{"id":"https://openalex.org/C2776634560","wikidata":"https://www.wikidata.org/wiki/Q707540","display_name":"Renal artery","level":3,"score":0.2996000051498413},{"id":"https://openalex.org/C2776098176","wikidata":"https://www.wikidata.org/wiki/Q189389","display_name":"Aneurysm","level":2,"score":0.2897000014781952},{"id":"https://openalex.org/C2777601897","wikidata":"https://www.wikidata.org/wiki/Q3409113","display_name":"Presentation (obstetrics)","level":2,"score":0.2896000146865845},{"id":"https://openalex.org/C2777323849","wikidata":"https://www.wikidata.org/wiki/Q616003","display_name":"Aortic aneurysm","level":3,"score":0.2888000011444092},{"id":"https://openalex.org/C2779993416","wikidata":"https://www.wikidata.org/wiki/Q2256736","display_name":"Abdominal aortic aneurysm","level":3,"score":0.28839999437332153},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.28519999980926514},{"id":"https://openalex.org/C2779980429","wikidata":"https://www.wikidata.org/wiki/Q101004","display_name":"Aorta","level":2,"score":0.27880001068115234},{"id":"https://openalex.org/C2778257484","wikidata":"https://www.wikidata.org/wiki/Q555066","display_name":"Visual acuity","level":2,"score":0.2667999863624573},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.26579999923706055},{"id":"https://openalex.org/C2781343717","wikidata":"https://www.wikidata.org/wiki/Q1751810","display_name":"Arteritis","level":2,"score":0.257999986410141},{"id":"https://openalex.org/C2780714102","wikidata":"https://www.wikidata.org/wiki/Q616071","display_name":"Aortic valve","level":2,"score":0.2508000135421753}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.70577/1gfsa660","doi":"https://doi.org/10.70577/1gfsa660","is_oa":true,"landing_page_url":"https://doi.org/10.70577/1gfsa660","pdf_url":"https://smijournal.com/index.php/files/article/download/138/142","source":{"id":"https://openalex.org/S7407055980","display_name":"Salud Medicina e Innovaci\u00f3n Journal","issn_l":"3121-2980","issn":["3121-2980"],"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":["latindex"],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":"cc-by-nc-sa","license_id":"https://openalex.org/licenses/cc-by-nc-sa","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Salud Medicina e Innovaci\u00f3n Journal","raw_type":"journal-article"}],"best_oa_location":{"id":"doi:10.70577/1gfsa660","doi":"https://doi.org/10.70577/1gfsa660","is_oa":true,"landing_page_url":"https://doi.org/10.70577/1gfsa660","pdf_url":"https://smijournal.com/index.php/files/article/download/138/142","source":{"id":"https://openalex.org/S7407055980","display_name":"Salud Medicina e Innovaci\u00f3n Journal","issn_l":"3121-2980","issn":["3121-2980"],"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":["latindex"],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":"cc-by-nc-sa","license_id":"https://openalex.org/licenses/cc-by-nc-sa","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Salud Medicina e Innovaci\u00f3n Journal","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":0.9940000176429749,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/systematic-review","display_name":"Systematic Review"}],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7207613271.pdf","grobid_xml":"https://content.openalex.org/works/W7207613271.grobid-xml"},"referenced_works_count":10,"referenced_works":["https://openalex.org/W2001706185","https://openalex.org/W2044900656","https://openalex.org/W2094480061","https://openalex.org/W2313707615","https://openalex.org/W2567362164","https://openalex.org/W2781903683","https://openalex.org/W3118615836","https://openalex.org/W4214640472","https://openalex.org/W4241964765","https://openalex.org/W4402543868"],"related_works":["https://openalex.org/W3044499108","https://openalex.org/W2463145992","https://openalex.org/W4405456221","https://openalex.org/W2799894235","https://openalex.org/W4392799365","https://openalex.org/W3024158286","https://openalex.org/W2417910829","https://openalex.org/W7161546143","https://openalex.org/W2077027340","https://openalex.org/W4366590653"],"abstract_inverted_index":{"Introduction:":[0],"Immunoglobulin":[1],"G4-related":[2],"disease":[3],"(IgG4-RD)":[4],"is":[5,216,257],"a":[6,58,225],"systemic":[7,206],"fibroinflammatory":[8],"disorder":[9],"characterized":[10],"by":[11],"infiltration":[12],"of":[13,81,183,228,232,245],"IgG4-positive":[14],"plasma":[15],"cells":[16],"in":[17,109,162],"multiple":[18],"organs,":[19],"which":[20,202],"can":[21,52,193],"affect":[22],"the":[23,72,137,153,243],"cardiovascular":[24],"system":[25],"with":[26,79,125,159,198,250],"life-threatening":[27],"complications":[28],"such":[29],"as":[30],"aneurysms":[31],"and":[32,49,88,113,120,129,141,144,156,237,247,253,264,268],"aortic":[33,84,126,233],"dissection":[34],"(Zen":[35],"et":[36,41,62,66,101,167,171,187,209],"al.,":[37,42,63,67,102,168,172,188,210],"2012;":[38],"Ghaffari":[39],"Jolfayi":[40,166],"2025).":[43],"Multiorgan":[44,213],"involvement,":[45,51,127],"including":[46],"renal":[47,86,143,235],"pseudotumors":[48,128,175],"orbital":[50,145],"present":[53],"synchronously":[54],"or":[55],"metachronously,":[56],"posing":[57],"diagnostic":[59],"challenge":[60],"(Maccagno":[61,186],"2022;":[64],"Haraguchi":[65],"2012).":[68,173,211],"Objective:":[69],"To":[70],"synthesize":[71],"available":[73],"evidence":[74],"on":[75,122],"multiorgan":[76],"IgG4-related":[77,123,149,174,214],"vasculitis":[78,124,215],"manifestations":[80,146],"dissecting":[82],"abdominal":[83,154],"aneurysm,":[85,234],"pseudotumor":[87,236],"fulminant":[89,199],"bilateral":[90,238],"visual":[91,200,239],"loss.":[92],"Methodology:":[93],"Systematic":[94],"review":[95],"following":[96],"PRISMA":[97],"2020":[98],"guidelines":[99],"(Page":[100],"2021).":[103],"A":[104],"systematic":[105],"search":[106],"was":[107],"conducted":[108],"PubMed,":[110],"LILACS,":[111],"SciELO":[112],"Cochrane":[114],"for":[115],"studies":[116,135,252],"published":[117],"between":[118,139],"2000":[119],"2026":[121],"ophthalmological":[130],"manifestations.":[131],"Results:":[132],"Eight":[133],"relevant":[134],"documenting":[136],"association":[138],"IgG4-RD":[140],"cardiovascular,":[142],"were":[147],"identified.":[148],"aortitis/periaortitis":[150],"predominantly":[151],"affects":[152],"aorta":[155],"iliac":[157],"arteries,":[158],"higher":[160],"prevalence":[161],"elderly":[163],"males":[164],"(Ghaffari":[165],"2025;":[169],"Zen":[170],"are":[176],"extremely":[177],"rare":[178],"lesions,":[179],"representing":[180],"approximately":[181],"0.05%":[182],"evaluated":[184],"lesions":[185],"2022).":[189],"Orbital":[190],"IgG4":[191,255],"involvement":[192],"cause":[194],"compressive":[195],"optic":[196],"neuropathy":[197],"loss,":[201],"responds":[203],"favorably":[204],"to":[205,259],"corticosteroids":[207],"(Haraguchi":[208],"Conclusion:":[212],"an":[217],"exceptional":[218],"but":[219],"potentially":[220],"lethal":[221],"entity":[222],"that":[223],"requires":[224],"high":[226],"index":[227],"suspicion.":[229],"Synchronous":[230],"presentation":[231],"loss":[240],"should":[241],"suggest":[242],"possibility":[244],"IgG4-RD,":[246],"early":[248],"diagnosis":[249],"imaging":[251],"serum":[254],"measurement":[256],"essential":[258],"initiate":[260],"timely":[261],"immunosuppressive":[262],"therapy":[263],"reduce":[265],"associated":[266],"morbidity":[267],"mortality.":[269]},"counts_by_year":[],"updated_date":"2026-10-28T10:33:24.094632","created_date":"2026-09-04T00:00:00"}
