{"id":"https://openalex.org/W7204905927","doi":"https://doi.org/10.1016/j.radcr.2026.07.101","title":"An unusual presentation of Moyamoya disease managed conservatively in a resource limited region: A case report","display_name":"An unusual presentation of Moyamoya disease managed conservatively in a resource limited region: A case report","publication_year":2026,"publication_date":"2026-09-01","ids":{"openalex":"https://openalex.org/W7204905927","doi":"https://doi.org/10.1016/j.radcr.2026.07.101","pmid":"https://pubmed.ncbi.nlm.nih.gov/42733476","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/13571123"},"language":"en","primary_location":{"id":"doi:10.1016/j.radcr.2026.07.101","doi":"https://doi.org/10.1016/j.radcr.2026.07.101","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.radcr.2026.07.101","pdf_url":"https://www.sciencedirect.com/science/article/pii/S1930043326007272/pdf","source":{"id":"https://openalex.org/S190549722","display_name":"Radiology Case Reports","issn_l":"1930-0433","issn":["1930-0433"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","norway-1","poland-20"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Radiology Case Reports","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj","pubmed"],"open_access":{"is_oa":true,"oa_status":"gold","oa_url":"https://www.sciencedirect.com/science/article/pii/S1930043326007272/pdf","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5106912499","display_name":"Zareen Tabassum","orcid":"https://orcid.org/0009-0002-7294-6703","observed_orcids":["https://orcid.org/0009-0002-7294-6703"]},"institutions":[{"id":"https://openalex.org/I2800803785","display_name":"Dinajpur Medical College","ror":"https://ror.org/00drqs466","country_code":"BD","type":"healthcare","lineage":["https://openalex.org/I2800803785"]}],"countries":["BD"],"is_corresponding":false,"raw_author_name":"Zareen Tabassum","raw_affiliation_strings":["Medical officer, Department of internal medicine, Dinajpur medical college, Dinajpur 5200, Bangladesh"],"raw_orcid":"https://orcid.org/0009-0002-7294-6703","affiliations":[{"raw_affiliation_string":"Medical officer, Department of internal medicine, Dinajpur medical college, Dinajpur 5200, Bangladesh","institution_ids":["https://openalex.org/I2800803785"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5114742781","display_name":"Md. Deluwar Hussen","orcid":"https://orcid.org/0009-0002-1518-5805","observed_orcids":["https://orcid.org/0009-0002-1518-5805"]},"institutions":[{"id":"https://openalex.org/I2800803785","display_name":"Dinajpur Medical College","ror":"https://ror.org/00drqs466","country_code":"BD","type":"healthcare","lineage":["https://openalex.org/I2800803785"]}],"countries":["BD"],"is_corresponding":true,"raw_author_name":"Md. Deluwar Hussen","raw_affiliation_strings":["Medical officer, Department of internal medicine, Dinajpur medical college, Dinajpur 5200, Bangladesh"],"raw_orcid":"https://orcid.org/0009-0002-1518-5805","affiliations":[{"raw_affiliation_string":"Medical officer, Department of internal medicine, Dinajpur medical college, Dinajpur 5200, Bangladesh","institution_ids":["https://openalex.org/I2800803785"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148843389","display_name":"Afsana Akter Mimi","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I75447333","display_name":"Mymensingh Medical College Hospital","ror":"https://ror.org/000kb2a90","country_code":"BD","type":"healthcare","lineage":["https://openalex.org/I75447333"]}],"countries":["BD"],"is_corresponding":false,"raw_author_name":"Afsana Akter Mimi","raw_affiliation_strings":["Mymensingh Medical College, Mymensingh, Bangladesh"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Mymensingh Medical College, Mymensingh, Bangladesh","institution_ids":["https://openalex.org/I75447333"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148916596","display_name":"Arefa Insan Momo","orcid":"https://orcid.org/0009-0006-1246-3397","observed_orcids":["https://orcid.org/0009-0006-1246-3397"]},"institutions":[{"id":"https://openalex.org/I4400600954","display_name":"Rangpur Medical College","ror":"https://ror.org/053jqyp97","country_code":"BD","type":"education","lineage":["https://openalex.org/I4400600954"]}],"countries":["BD"],"is_corresponding":false,"raw_author_name":"Arefa Insan Momo","raw_affiliation_strings":["Rangpur Medical College, Rangpur, Bangladesh"],"raw_orcid":"https://orcid.org/0009-0006-1246-3397","affiliations":[{"raw_affiliation_string":"Rangpur Medical College, Rangpur, Bangladesh","institution_ids":["https://openalex.org/I4400600954"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148877977","display_name":"Sharmin Akter Riya","orcid":"https://orcid.org/0009-0006-5938-4194","observed_orcids":["https://orcid.org/0009-0006-5938-4194"]},"institutions":[{"id":"https://openalex.org/I2653708","display_name":"Chittagong Medical College","ror":"https://ror.org/01y8zn427","country_code":"BD","type":"healthcare","lineage":["https://openalex.org/I2653708"]}],"countries":["BD"],"is_corresponding":false,"raw_author_name":"Sharmin Akter Riya","raw_affiliation_strings":["Chittagong Medical College, Cumilla, Bangladesh"],"raw_orcid":"https://orcid.org/0009-0006-5938-4194","affiliations":[{"raw_affiliation_string":"Chittagong Medical College, Cumilla, Bangladesh","institution_ids":["https://openalex.org/I2653708"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5128281328","display_name":"Munim Hasan Choudhury","orcid":"https://orcid.org/0009-0006-0097-857X","observed_orcids":["https://orcid.org/0009-0006-0097-857X"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Munim Hasan Choudhury","raw_affiliation_strings":["Anwer Khan Modern Medical College Hospital, Dhaka, Bangladesh"],"raw_orcid":"https://orcid.org/0009-0006-0097-857X","affiliations":[{"raw_affiliation_string":"Anwer Khan Modern Medical College Hospital, Dhaka, Bangladesh","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5143472508","display_name":"Sayema Begum Jahra","orcid":"https://orcid.org/0009-0009-6364-3349","observed_orcids":["https://orcid.org/0009-0009-6364-3349"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Sayema Begum Jahra","raw_affiliation_strings":["Sylhet Womens Medical College and Hospital, Sylhet, Bangladesh"],"raw_orcid":"https://orcid.org/0009-0009-6364-3349","affiliations":[{"raw_affiliation_string":"Sylhet Womens Medical College and Hospital, Sylhet, Bangladesh","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5126924643","display_name":"Anika Tasnim Khan","orcid":"https://orcid.org/0009-0005-5431-4229","observed_orcids":["https://orcid.org/0009-0005-5431-4229"]},"institutions":[{"id":"https://openalex.org/I2653708","display_name":"Chittagong Medical College","ror":"https://ror.org/01y8zn427","country_code":"BD","type":"healthcare","lineage":["https://openalex.org/I2653708"]}],"countries":["BD"],"is_corresponding":false,"raw_author_name":"Anika Tasnim Khan","raw_affiliation_strings":["Medical Officer, Obs and Gynae, Chittagong Medical College, Chattogram 4203, Bangladesh"],"raw_orcid":"https://orcid.org/0009-0005-5499-9598","affiliations":[{"raw_affiliation_string":"Medical Officer, Obs and Gynae, Chittagong Medical College, Chattogram 4203, Bangladesh","institution_ids":["https://openalex.org/I2653708"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":4,"corresponding_author_ids":["https://openalex.org/A5114742781"],"corresponding_institution_ids":["https://openalex.org/I2800803785"],"apc_list":{"value":600,"currency":"USD","value_usd":600},"apc_paid":{"value":600,"currency":"USD","value_usd":600},"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.61113958,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"21","issue":"11","first_page":"5766","last_page":"5770"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12747","display_name":"Moyamoya disease diagnosis and treatment","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12747","display_name":"Moyamoya disease diagnosis and treatment","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12464","display_name":"Neurological Complications and Syndromes","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11402","display_name":"Vascular Malformations Diagnosis and Treatment","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/moyamoya-disease","display_name":"moyamoya disease","score":0.9980000257492065},{"id":"https://openalex.org/keywords/pediatric-moyamoya-disease","display_name":"pediatric moyamoya disease","score":0.9779999852180481},{"id":"https://openalex.org/keywords/cortical-blindness","display_name":"cortical blindness","score":0.7689999938011169},{"id":"https://openalex.org/keywords/encephalomalacia","display_name":"encephalomalacia","score":0.7799999713897705},{"id":"https://openalex.org/keywords/conservative-treatment","display_name":"conservative treatment","score":0.578000009059906},{"id":"https://openalex.org/keywords/resource-limited-settings","display_name":"resource-limited settings","score":0.9580000042915344},{"id":"https://openalex.org/keywords/surgical-revascularization","display_name":"surgical revascularization","score":0.6669999957084656}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9319999814033508},{"id":"https://openalex.org/C2777601897","wikidata":"https://www.wikidata.org/wiki/Q3409113","display_name":"Presentation (obstetrics)","level":2,"score":0.8180999755859375},{"id":"https://openalex.org/C2776548475","wikidata":"https://www.wikidata.org/wiki/Q1951267","display_name":"Moyamoya disease","level":2,"score":0.7958999872207642},{"id":"https://openalex.org/C3019252630","wikidata":"https://www.wikidata.org/wiki/Q6549547","display_name":"Limited resources","level":2,"score":0.603600025177002},{"id":"https://openalex.org/C3019796121","wikidata":"https://www.wikidata.org/wiki/Q5048356","display_name":"Case presentation","level":2,"score":0.4397999942302704},{"id":"https://openalex.org/C61434518","wikidata":"https://www.wikidata.org/wiki/Q932510","display_name":"General surgery","level":1,"score":0.4262000024318695},{"id":"https://openalex.org/C177713679","wikidata":"https://www.wikidata.org/wiki/Q679690","display_name":"Intensive care medicine","level":1,"score":0.40790000557899475},{"id":"https://openalex.org/C206345919","wikidata":"https://www.wikidata.org/wiki/Q20380951","display_name":"Resource (disambiguation)","level":2,"score":0.4052000045776367},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.3869999945163727},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.38589999079704285},{"id":"https://openalex.org/C126838900","wikidata":"https://www.wikidata.org/wiki/Q77604","display_name":"Radiology","level":1,"score":0.367000013589859},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.3555999994277954},{"id":"https://openalex.org/C545542383","wikidata":"https://www.wikidata.org/wiki/Q2751242","display_name":"Medical emergency","level":1,"score":0.3303999900817871},{"id":"https://openalex.org/C2779701055","wikidata":"https://www.wikidata.org/wiki/Q929833","display_name":"Rare disease","level":3,"score":0.30570000410079956},{"id":"https://openalex.org/C2779473830","wikidata":"https://www.wikidata.org/wiki/Q1540899","display_name":"MEDLINE","level":2,"score":0.301800012588501},{"id":"https://openalex.org/C2780724011","wikidata":"https://www.wikidata.org/wiki/Q1295316","display_name":"Emergency department","level":2,"score":0.29330000281333923}],"mesh":[],"locations_count":3,"locations":[{"id":"doi:10.1016/j.radcr.2026.07.101","doi":"https://doi.org/10.1016/j.radcr.2026.07.101","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.radcr.2026.07.101","pdf_url":"https://www.sciencedirect.com/science/article/pii/S1930043326007272/pdf","source":{"id":"https://openalex.org/S190549722","display_name":"Radiology Case Reports","issn_l":"1930-0433","issn":["1930-0433"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","norway-1","poland-20"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Radiology Case Reports","raw_type":"journal-article"},{"id":"pmh:oai:pubmedcentral.nih.gov:13571123","doi":null,"is_oa":true,"landing_page_url":"https://pmc.ncbi.nlm.nih.gov/articles/PMC13571123/","pdf_url":"https://pmc.ncbi.nlm.nih.gov/articles/PMC13571123/pdf/main.pdf","source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Radiol Case Rep","raw_type":"Text"},{"id":"pmid:42733476","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/42733476","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Radiology case reports","raw_type":"Case Reports"}],"best_oa_location":{"id":"doi:10.1016/j.radcr.2026.07.101","doi":"https://doi.org/10.1016/j.radcr.2026.07.101","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.radcr.2026.07.101","pdf_url":"https://www.sciencedirect.com/science/article/pii/S1930043326007272/pdf","source":{"id":"https://openalex.org/S190549722","display_name":"Radiology Case Reports","issn_l":"1930-0433","issn":["1930-0433"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","norway-1","poland-20"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Radiology Case Reports","raw_type":"journal-article"},"sustainable_development_goals":[{"score":0.9940000176429749,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7204905927.pdf","grobid_xml":"https://content.openalex.org/works/W7204905927.grobid-xml"},"referenced_works_count":10,"referenced_works":["https://openalex.org/W2108841441","https://openalex.org/W2148940134","https://openalex.org/W2291528898","https://openalex.org/W2292199645","https://openalex.org/W3196099352","https://openalex.org/W4210842132","https://openalex.org/W4390722242","https://openalex.org/W4404643591","https://openalex.org/W4410871235","https://openalex.org/W4411533024"],"related_works":["https://openalex.org/W2315644818","https://openalex.org/W2312419841","https://openalex.org/W4404902347","https://openalex.org/W7128216310","https://openalex.org/W4414877781","https://openalex.org/W3150482649","https://openalex.org/W2165926973","https://openalex.org/W4390722242","https://openalex.org/W2292756561","https://openalex.org/W2810272896"],"abstract_inverted_index":{"Moyamoya":[0,134,153],"disease":[1,6,135],"is":[2,171],"a":[3,33,36,131],"rare":[4],"cerebrovascular":[5],"of":[7,17,20,25,35,64,108,126],"chronic":[8],"and":[9,15,23,56,68,87,96,106,145,160],"progressive":[10,142],"nature,":[11],"characterized":[12],"by":[13,51,82],"stenosis":[14],"occlusion":[16],"the":[18,65,109,113,180],"Circle":[19],"Willis":[21],"vessels":[22],"formation":[24,99],"compensatory":[26,97],"collateral":[27],"circulation.":[28],"Here":[29],"we":[30],"have":[31,71],"reported":[32],"case":[34,79,139],"10":[37],"year":[38,48],"old":[39],"male":[40],"patient":[41,132],"who":[42],"first":[43],"developed":[44],"seizure,":[45],"hemiparesis":[46,60],"1":[47],"ago,":[49],"followed":[50],"deteriorating":[52],"hemiparesis,":[53],"prolonged":[54,69],"fever":[55,70],"blindness.":[57],"Although":[58],"seizure":[59],"are":[61],"common":[62],"presentations":[63],"disease,":[66],"blindness":[67,144],"been":[72,123],"rarely":[73],"reported.":[74],"The":[75],"diagnosis":[76,166],"in":[77,112,130,136,151],"this":[78],"was":[80,117],"established":[81],"Magnetic":[83,88],"Resonance":[84,89],"Imaging":[85],"(MRI)":[86],"Angiogram":[90],"(MRA),":[91],"where":[92],"vessel":[93],"occlusion,":[94],"encephalomalacia":[95],"circulation":[98,147],"were":[100],"detected.":[101],"Due":[102],"to":[103],"financial":[104],"hardships":[105],"limitations":[107],"surgical":[110],"settings":[111],"hospital,":[114],"conservative":[115],"treatment":[116],"provided.":[118],"In":[119,155],"fact,":[120],"there":[121],"has":[122],"no":[124],"report":[125],"performing":[127],"revascularization":[128,177],"surgery":[129,178],"with":[133,176],"Bangladesh.":[137],"This":[138],"highlights":[140],"that":[141],"cortical":[143],"posterior":[146],"involvement":[148],"may":[149],"occur":[150],"pediatric":[152],"disease.":[154],"resource-limited":[156],"settings,":[157],"characteristic":[158],"MRI":[159],"MRA":[161],"findings":[162],"can":[163],"facilitate":[164],"early":[165],"when":[167],"Digital":[168],"Subtraction":[169],"Angiography":[170],"unavailable,":[172],"although":[173],"definitive":[174],"management":[175],"remains":[179],"preferred":[181],"treatment.":[182]},"counts_by_year":[],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2026-09-02T00:00:00"}
