{"id":"https://openalex.org/W7204779225","doi":"https://doi.org/10.1210/clinem/dgag358","title":"Continuous glucose monitoring to track metabolic changes in youths with cystic fibrosis before and after initiation of elexacaftor/tezacaftor/ivacaftor therapy","display_name":"Continuous glucose monitoring to track metabolic changes in youths with cystic fibrosis before and after initiation of elexacaftor/tezacaftor/ivacaftor therapy","publication_year":2026,"publication_date":"2026-08-31","ids":{"openalex":"https://openalex.org/W7204779225","doi":"https://doi.org/10.1210/clinem/dgag358","pmid":"https://pubmed.ncbi.nlm.nih.gov/42671070"},"language":"en","primary_location":{"id":"doi:10.1210/clinem/dgag358","doi":"https://doi.org/10.1210/clinem/dgag358","is_oa":false,"landing_page_url":"https://doi.org/10.1210/clinem/dgag358","pdf_url":null,"source":{"id":"https://openalex.org/S205775358","display_name":"The Journal of Clinical Endocrinology & Metabolism","issn_l":"0021-972X","issn":["0021-972X","1945-7197"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-class-a","anvur-scientific","cwts-core","dongbi-b","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Journal of Clinical Endocrinology &amp; Metabolism","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5076842743","display_name":"Alfonso Galderisi","orcid":"https://orcid.org/0000-0001-8885-3056","observed_orcids":["https://orcid.org/0000-0001-8885-3056"]},"institutions":[{"id":"https://openalex.org/I204730241","display_name":"Universit\u00e9 Paris Cit\u00e9","ror":"https://ror.org/05f82e368","country_code":"FR","type":"education","lineage":["https://openalex.org/I204730241"]},{"id":"https://openalex.org/I32971472","display_name":"Yale University","ror":"https://ror.org/03v76x132","country_code":"US","type":"education","lineage":["https://openalex.org/I32971472"]},{"id":"https://openalex.org/I4210126712","display_name":"H\u00f4pital Robert-Debr\u00e9","ror":"https://ror.org/02dcqy320","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159","https://openalex.org/I4210126712"]}],"countries":["FR","US"],"is_corresponding":true,"raw_author_name":"Alfonso Galderisi","raw_affiliation_strings":["Department of Pediatrics, Yale University , New Haven, CT 06510 ,","Pediatric Endocrinology and Diabetes Service-H\u00f4pital Universitaire Robert-Debr\u00e9, Universit\u00e9 Paris Cite , Paris 75019 ,"],"raw_orcid":"https://orcid.org/0000-0001-8885-3056","affiliations":[{"raw_affiliation_string":"Department of Pediatrics, Yale University , New Haven, CT 06510 ,","institution_ids":["https://openalex.org/I32971472"]},{"raw_affiliation_string":"Pediatric Endocrinology and Diabetes Service-H\u00f4pital Universitaire Robert-Debr\u00e9, Universit\u00e9 Paris Cite , Paris 75019 ,","institution_ids":["https://openalex.org/I204730241","https://openalex.org/I4210126712"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5118144558","display_name":"Hadija Marchiori","orcid":"https://orcid.org/0009-0006-4171-3447","observed_orcids":["https://orcid.org/0009-0006-4171-3447"]},"institutions":[{"id":"https://openalex.org/I138689650","display_name":"University of Padua","ror":"https://ror.org/00240q980","country_code":"IT","type":"education","lineage":["https://openalex.org/I138689650"]},{"id":"https://openalex.org/I32971472","display_name":"Yale University","ror":"https://ror.org/03v76x132","country_code":"US","type":"education","lineage":["https://openalex.org/I32971472"]}],"countries":["IT","US"],"is_corresponding":false,"raw_author_name":"Hadija Marchiori","raw_affiliation_strings":["Department of Information Engineering, University of Padova , Padova 35131 ,","Department of Pediatrics, Yale University , New Haven, CT 06510 ,"],"raw_orcid":"https://orcid.org/0009-0006-4171-3447","affiliations":[{"raw_affiliation_string":"Department of Information Engineering, University of Padova , Padova 35131 ,","institution_ids":["https://openalex.org/I138689650"]},{"raw_affiliation_string":"Department of Pediatrics, Yale University , New Haven, CT 06510 ,","institution_ids":["https://openalex.org/I32971472"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5112736505","display_name":"Laurence Weiss","orcid":"https://orcid.org/0000-0002-1728-915X","observed_orcids":["https://orcid.org/0000-0002-1728-915X"]},"institutions":[{"id":"https://openalex.org/I4210145324","display_name":"H\u00f4pitaux Universitaires de Strasbourg","ror":"https://ror.org/04bckew43","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210145324"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Laurence Weiss","raw_affiliation_strings":["Centre de Ressources et de Comp\u00e9tence de la Mucoviscidose, P\u00e9diatrique-H\u00f4pitaux Universitaires de Strasbourg , Strasbourg 67200 ,"],"raw_orcid":"https://orcid.org/0000-0002-1728-915X","affiliations":[{"raw_affiliation_string":"Centre de Ressources et de Comp\u00e9tence de la Mucoviscidose, P\u00e9diatrique-H\u00f4pitaux Universitaires de Strasbourg , Strasbourg 67200 ,","institution_ids":["https://openalex.org/I4210145324"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5073197835","display_name":"Alix Besan\u00e7on","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1288880153","display_name":"H\u00f4pital Necker-Enfants Malades","ror":"https://ror.org/05tr67282","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I1288880153","https://openalex.org/I4210097159","https://openalex.org/I4210120235"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Alix Besan\u00e7on","raw_affiliation_strings":["Service d'endocrinologie, gyn\u00e9cologie et diab\u00e9tologie p\u00e9diatrique-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Service d'endocrinologie, gyn\u00e9cologie et diab\u00e9tologie p\u00e9diatrique-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,","institution_ids":["https://openalex.org/I1288880153"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5006444836","display_name":"Nathalie Stremler","orcid":"https://orcid.org/0009-0004-8884-0772","observed_orcids":["https://orcid.org/0009-0004-8884-0772"]},"institutions":[{"id":"https://openalex.org/I4210087487","display_name":"Assistance Publique H\u00f4pitaux de Marseille","ror":"https://ror.org/002cp4060","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I21491767","https://openalex.org/I4210087487"]},{"id":"https://openalex.org/I4210162909","display_name":"H\u00f4pital de la Timone","ror":"https://ror.org/05jrr4320","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I21491767","https://openalex.org/I4210087487","https://openalex.org/I4210162909"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Nathalie Stremler","raw_affiliation_strings":["Centre de Ressources et de Comp\u00e9tence de la Mucoviscidose P\u00e9diatrique-H\u00f4pital D'enfants de la Timone\u2014Assistance Publique H\u00f4pitaux de Marseille , Marseille 13005 ,"],"raw_orcid":"https://orcid.org/0009-0004-8884-0772","affiliations":[{"raw_affiliation_string":"Centre de Ressources et de Comp\u00e9tence de la Mucoviscidose P\u00e9diatrique-H\u00f4pital D'enfants de la Timone\u2014Assistance Publique H\u00f4pitaux de Marseille , Marseille 13005 ,","institution_ids":["https://openalex.org/I4210087487","https://openalex.org/I4210162909"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5048808407","display_name":"Aline Lustre","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1288880153","display_name":"H\u00f4pital Necker-Enfants Malades","ror":"https://ror.org/05tr67282","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I1288880153","https://openalex.org/I4210097159","https://openalex.org/I4210120235"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Aline Lustre","raw_affiliation_strings":["Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,","institution_ids":["https://openalex.org/I1288880153","https://openalex.org/I4210097159"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5099044365","display_name":"Djouher Sahki","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1288880153","display_name":"H\u00f4pital Necker-Enfants Malades","ror":"https://ror.org/05tr67282","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I1288880153","https://openalex.org/I4210097159","https://openalex.org/I4210120235"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Djouher Sahki","raw_affiliation_strings":["Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,","institution_ids":["https://openalex.org/I1288880153","https://openalex.org/I4210097159"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5052186564","display_name":"Anne-Marie Bonnel","orcid":"https://orcid.org/0009-0002-1475-2492","observed_orcids":["https://orcid.org/0009-0002-1475-2492"]},"institutions":[{"id":"https://openalex.org/I1288880153","display_name":"H\u00f4pital Necker-Enfants Malades","ror":"https://ror.org/05tr67282","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I1288880153","https://openalex.org/I4210097159","https://openalex.org/I4210120235"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4210159263","display_name":"Centre Hospitalier de Versailles","ror":"https://ror.org/053evvt91","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210159263"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Anne-Sophie Bonnel","raw_affiliation_strings":["Centre de R\u00e9f\u00e9rence de la Mucoviscidose-H\u00f4pital Andr\u00e9 Mignot-Centre Hospitalier de Versailles , Versaille 78150 ,","Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,"],"raw_orcid":"https://orcid.org/0009-0002-1475-2492","affiliations":[{"raw_affiliation_string":"Centre de R\u00e9f\u00e9rence de la Mucoviscidose-H\u00f4pital Andr\u00e9 Mignot-Centre Hospitalier de Versailles , Versaille 78150 ,","institution_ids":["https://openalex.org/I4210159263"]},{"raw_affiliation_string":"Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,","institution_ids":["https://openalex.org/I1288880153","https://openalex.org/I4210097159"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5018306210","display_name":"Isabelle Sermet\u2010Gaudelus","orcid":"https://orcid.org/0000-0001-5537-9482","observed_orcids":["https://orcid.org/0000-0001-5537-9482"]},"institutions":[{"id":"https://openalex.org/I1288880153","display_name":"H\u00f4pital Necker-Enfants Malades","ror":"https://ror.org/05tr67282","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I1288880153","https://openalex.org/I4210097159","https://openalex.org/I4210120235"]},{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]},{"id":"https://openalex.org/I4210086369","display_name":"Institut Necker Enfants Malades","ror":"https://ror.org/000nhq538","country_code":"FR","type":"facility","lineage":["https://openalex.org/I1294671590","https://openalex.org/I154526488","https://openalex.org/I204730241","https://openalex.org/I4210086369","https://openalex.org/I4210096427"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4387156277","display_name":"ERN LUNG","ror":"https://ror.org/0279ntc65","country_code":"DE","type":"healthcare","lineage":["https://openalex.org/I1320481043","https://openalex.org/I2800387288","https://openalex.org/I4387155652","https://openalex.org/I4387156277"]}],"countries":["DE","FR"],"is_corresponding":false,"raw_author_name":"Isabelle Sermet-Gaudelus","raw_affiliation_strings":["Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,","European Respiratory Network Lung , Frankfurt 60596 ,","INSERM U1151, Institut Necker Enfants Malades , Paris 75015 ,"],"raw_orcid":"https://orcid.org/0000-0001-5537-9482","affiliations":[{"raw_affiliation_string":"Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,","institution_ids":["https://openalex.org/I1288880153","https://openalex.org/I4210097159"]},{"raw_affiliation_string":"European Respiratory Network Lung , Frankfurt 60596 ,","institution_ids":["https://openalex.org/I4387156277"]},{"raw_affiliation_string":"INSERM U1151, Institut Necker Enfants Malades , Paris 75015 ,","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210086369"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148801716","display_name":"the MODUL-CF group","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"the MODUL-CF group","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5074322264","display_name":"Marianne Alison","orcid":"https://orcid.org/0000-0002-9245-9390","observed_orcids":["https://orcid.org/0000-0002-9245-9390"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Marianne Alison","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5043307931","display_name":"Baptiste Arnouat","orcid":"https://orcid.org/0009-0001-1063-0343","observed_orcids":["https://orcid.org/0009-0001-1063-0343"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Baptiste Arnouat","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5128653190","display_name":"Melissande Baravalle","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Melissande Baravalle","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5106991968","display_name":"Mahassen Barboura","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Mahassen Barboura","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5117758922","display_name":"Jeanne Barillon","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Jeanne Barillon","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5080452799","display_name":"Audrey Barzic","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Audrey Barzic","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5114813640","display_name":"Lilia Benhalla","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Lilia Benhalla","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5042637279","display_name":"Myriam Benhamida","orcid":"https://orcid.org/0000-0002-0369-2933","observed_orcids":["https://orcid.org/0000-0002-0369-2933"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Myriam Benhamida","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5114813641","display_name":"Khadidja Bennour","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Khadidja Bennour","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5005668807","display_name":"Laureline Berteloot","orcid":"https://orcid.org/0000-0001-9681-3142","observed_orcids":["https://orcid.org/0000-0001-9681-3142"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Laureline Berteloot","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5001349515","display_name":"Katia Bessaci","orcid":"https://orcid.org/0000-0002-7965-5418","observed_orcids":["https://orcid.org/0000-0002-7965-5418"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Katia Bessaci","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5037920967","display_name":"Antoine Bessou","orcid":"https://orcid.org/0009-0000-8770-426X","observed_orcids":["https://orcid.org/0009-0000-8770-426X"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Antoine Bessou","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5034790341","display_name":"Marie Biard","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Marie Biard","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148809691","display_name":"Thiphaine Bihou\u00e9e","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Thiphaine Bihou\u00e9e","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5005021862","display_name":"Aurore Blond\u00e9","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Aurore Blonde","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5052186564","display_name":"Anne-Marie Bonnel","orcid":"https://orcid.org/0009-0002-1475-2492","observed_orcids":["https://orcid.org/0009-0002-1475-2492"]},"institutions":[{"id":"https://openalex.org/I1288880153","display_name":"H\u00f4pital Necker-Enfants Malades","ror":"https://ror.org/05tr67282","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I1288880153","https://openalex.org/I4210097159","https://openalex.org/I4210120235"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4210159263","display_name":"Centre Hospitalier de Versailles","ror":"https://ror.org/053evvt91","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210159263"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Anne-Sophie Bonnel","raw_affiliation_strings":["Centre de R\u00e9f\u00e9rence de la Mucoviscidose-H\u00f4pital Andr\u00e9 Mignot-Centre Hospitalier de Versailles , Versaille 78150 ,","Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Centre de R\u00e9f\u00e9rence de la Mucoviscidose-H\u00f4pital Andr\u00e9 Mignot-Centre Hospitalier de Versailles , Versaille 78150 ,","institution_ids":["https://openalex.org/I4210159263"]},{"raw_affiliation_string":"Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,","institution_ids":["https://openalex.org/I1288880153","https://openalex.org/I4210097159"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5117188245","display_name":"Nesrine Bouleghlem","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Nesrine Bouleghlem","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5038922363","display_name":"Bertrand Bruneau","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Bertrand Bruneau","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5022662991","display_name":"S. Bui","orcid":"https://orcid.org/0000-0003-3576-2518","observed_orcids":["https://orcid.org/0000-0003-3576-2518"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"St\u00e9phanie Bui","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5075355644","display_name":"Aline Carsin-Vu","orcid":"https://orcid.org/0000-0003-2728-6662","observed_orcids":["https://orcid.org/0000-0003-2728-6662"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Aline Carsin-Vu","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5106728810","display_name":"Mathilde Casson-Masselin","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Mathilde Casson-Masselin","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5057094854","display_name":"Justine Chanclud","orcid":"https://orcid.org/0000-0002-9086-1650","observed_orcids":["https://orcid.org/0000-0002-9086-1650"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Justine Chanclud","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5042033628","display_name":"F. Chedevergne","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Fr\u00e9d\u00e9rique Chedevergne","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5113135095","display_name":"Camille Cisterne","orcid":"https://orcid.org/0009-0002-9342-2124","observed_orcids":["https://orcid.org/0009-0002-9342-2124"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Camille Cisterne","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5007768330","display_name":"Harriet Corvol","orcid":"https://orcid.org/0000-0002-7026-7523","observed_orcids":["https://orcid.org/0000-0002-7026-7523"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Harriet Corvol","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5021833257","display_name":"Laure Cosson","orcid":"https://orcid.org/0000-0001-9469-9796","observed_orcids":["https://orcid.org/0000-0001-9469-9796"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Laure Cosson","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5090468696","display_name":"L. Couderc","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Laure Couderc","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5128630057","display_name":"Carole Couette","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Carole Couette","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5031784994","display_name":"Marie\u2010Laure Dalphin","orcid":"https://orcid.org/0000-0002-6429-818X","observed_orcids":["https://orcid.org/0000-0002-6429-818X"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Marie-Laure Dalphin","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5088179873","display_name":"P. De Carli","orcid":"https://orcid.org/0000-0002-2564-1766","observed_orcids":["https://orcid.org/0000-0002-2564-1766"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Paola de Carli","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5109438415","display_name":"Eric Deneuville","orcid":"https://orcid.org/0000-0002-4369-0000","observed_orcids":["https://orcid.org/0000-0002-4369-0000"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Eric Deneuville","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5074435025","display_name":"Ga\u00ebl Dournes","orcid":"https://orcid.org/0000-0002-0251-6639","observed_orcids":["https://orcid.org/0000-0002-0251-6639","https://orcid.org/0009-0003-0834-1491"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Gael Dournes","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5054150398","display_name":"Val\u00e9rie Douzal","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Valerie Douzal","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5040751249","display_name":"Hubert Ducou Le Pointe","orcid":"https://orcid.org/0000-0002-6667-8629","observed_orcids":["https://orcid.org/0000-0002-6667-8629"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Hubert Ducou-le-Pointe","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5119462033","display_name":"Cl\u00e9mence Dufour-Barba","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Clemence Dufour-Barba","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5022129306","display_name":"Rapha\u00ebl Enaud","orcid":"https://orcid.org/0000-0001-9493-5218","observed_orcids":["https://orcid.org/0000-0001-9493-5218","https://orcid.org/0000-0002-2277-1004"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Raphael Enaud","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5033305079","display_name":"Mathilde Ferry","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Mathilde Ferry","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5128684179","display_name":"Morgane Floch","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Morgane Floch","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5109073036","display_name":"Pierre Foucaud","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Pierre Foucaud","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5009835620","display_name":"Flaviu Gabor","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Flaviu Gabor","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5028397561","display_name":"Asma Gabsi","orcid":"https://orcid.org/0009-0004-8396-7678","observed_orcids":["https://orcid.org/0009-0004-8396-7678"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Asma Gabsi","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5046801212","display_name":"Elsa Gachelin","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Elsa Gachelin","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5074865537","display_name":"Charlotte Giraud","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Charlotte Giraud","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148429801","display_name":"Fatiha Hassani","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Fatiha Hassani","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5034923999","display_name":"Audrey Herzog","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Audrey Herzog","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5103258152","display_name":"V\u00e9ronique Houdouin","orcid":"https://orcid.org/0000-0002-6062-1293","observed_orcids":["https://orcid.org/0000-0002-6062-1293","https://orcid.org/0000-0002-0119-2628"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"V\u00e9ronique Houdouin","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148814663","display_name":"Antoine Delval","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Antoine Delval","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5113643418","display_name":"Anne Houzel-Charavel","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Anne Houzel","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5075759858","display_name":"Fr\u00e9d\u00e9ric Huet","orcid":"https://orcid.org/0009-0003-0252-1264","observed_orcids":["https://orcid.org/0009-0003-0252-1264","https://orcid.org/0000-0002-4510-7093"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Fr\u00e9d\u00e9ric Huet","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5054180064","display_name":"Antoine Hutt","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Antoine Hutt","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5004508232","display_name":"Ahmed Kheniche","orcid":"https://orcid.org/0000-0002-2217-6731","observed_orcids":["https://orcid.org/0000-0002-2217-6731"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Ahmed Kheniche","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5017097106","display_name":"Marie Jamin","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Marie Jamin","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5083986984","display_name":"Kadiatou Kaba","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Kadiatou Kaba","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5030636109","display_name":"S\u00e9bastien Kiefer","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"S\u00e9bastien Kiefer","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5112864913","display_name":"Guillaume Labb\u00e9","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Guillaume Labb\u00e9","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5033094217","display_name":"Alice Ladaurade","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Alice Ladaurade","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5075041815","display_name":"Jane Languepin","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Jane Languepin","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5019478431","display_name":"Muriel Laurans","orcid":"https://orcid.org/0000-0003-4936-3251","observed_orcids":["https://orcid.org/0000-0003-4936-3251"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Muriel Laurans","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5128667587","display_name":"Laurence Leclainche-Viala","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Laurence Leclainche-Viala","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148779371","display_name":"Faustine Lefebvre","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Faustine Lefebvre","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5079254006","display_name":"T. Lefran\u00e7ois","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Thomas Lefrancois","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5085972134","display_name":"Servane Lelez-Soquet","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Servane Lelez-Soquet","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5033738124","display_name":"Marion Lenoir","orcid":"https://orcid.org/0000-0001-5936-9070","observed_orcids":["https://orcid.org/0000-0001-5936-9070"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Marion Lenoir","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148818464","display_name":"Louis-Marie Lieber","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Louis-Marie Lieber","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5058718820","display_name":"Clotilde Livrozet","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Clotilde Livrozet","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5128637238","display_name":"Catthy Ll\u00e9r\u00e9na","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Catthy Ll\u00e9r\u00e9na","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5083408711","display_name":"Alexia Letierce","orcid":"https://orcid.org/0000-0001-6679-5772","observed_orcids":["https://orcid.org/0000-0001-6679-5772"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Alexia Letierce","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5018628953","display_name":"Damien Mandry","orcid":"https://orcid.org/0000-0003-2127-7538","observed_orcids":["https://orcid.org/0000-0003-2127-7538"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Damien Mandry","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5112523868","display_name":"Sarah Marchal","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Sarah Marchal","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5110818892","display_name":"Christophe Marguet","orcid":"https://orcid.org/0000-0002-1545-1184","observed_orcids":["https://orcid.org/0000-0002-1545-1184"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Christophe Marguet","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5106502757","display_name":"Sophie Mayer","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Sophie Mayer","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5012385926","display_name":"St\u00e9phane Mazur","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"St\u00e9phane Mazur","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5006649224","display_name":"Laurent M\u00e9ly","orcid":"https://orcid.org/0000-0002-3790-085X","observed_orcids":["https://orcid.org/0000-0002-3790-085X"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Laurent M\u00e9ly","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5128631968","display_name":"Rania Messaoudi","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Rania Messaoudi","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5058402654","display_name":"Marie Mittaine","orcid":"https://orcid.org/0000-0003-2385-495X","observed_orcids":["https://orcid.org/0000-0003-2385-495X"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Marie Mittaine","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5034957361","display_name":"Baptiste Morel","orcid":"https://orcid.org/0000-0002-2872-6423","observed_orcids":["https://orcid.org/0000-0002-2872-6423"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Baptiste Morel","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5022861381","display_name":"Camille Ohlmann","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Camille Ohlmann","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5039483976","display_name":"Jocelyne Pengam","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Jocelyne Pengam","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5076046482","display_name":"St\u00e9phanie Perrez","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"St\u00e9phanie Perrez","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5043078952","display_name":"Caroline P\u00e9risson","orcid":"https://orcid.org/0009-0000-6606-0821","observed_orcids":["https://orcid.org/0009-0000-6606-0821"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Caroline P\u00e9risson","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5085244309","display_name":"Thomas Perrin","orcid":"https://orcid.org/0000-0002-5974-3269","observed_orcids":["https://orcid.org/0000-0002-5974-3269"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Thomas Perrin","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5128675400","display_name":"Isabelle Petit","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Isabelle Petit","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148808330","display_name":"Philippe Petit","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Philippe Petit","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5017870838","display_name":"Juliette Pezron","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Juliette Pezron","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5016558981","display_name":"C. Piccini-Bailly","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Carole Piccini-Bailly","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5092846435","display_name":"Delphine Pouradier","orcid":"https://orcid.org/0009-0007-8749-7732","observed_orcids":["https://orcid.org/0009-0007-8749-7732"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Delphine Pouradier","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5028167914","display_name":"Cinthia Rames","orcid":"https://orcid.org/0009-0002-6962-0796","observed_orcids":["https://orcid.org/0009-0002-6962-0796"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Cinthia Rames","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5065039765","display_name":"Ad\u00e9la\u00efde Rega","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Adelaide Rega","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5022125342","display_name":"Philippe Reix","orcid":"https://orcid.org/0000-0002-9192-8335","observed_orcids":["https://orcid.org/0000-0002-9192-8335","https://orcid.org/0000-0003-2711-8319"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Philippe Reix","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148808890","display_name":"Martine Remy","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Martine Remy","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5075798246","display_name":"Natascha Remus","orcid":"https://orcid.org/0000-0003-4849-9034","observed_orcids":["https://orcid.org/0000-0003-4849-9034"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Natacha R\u00e9mus","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5080011937","display_name":"Marine Revillion","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Marine Revillion","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5092130210","display_name":"Anna Ronayette","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Anna Ronayette","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5014207726","display_name":"Flavie Sadones","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Flavie Sadones","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5099044365","display_name":"Djouher Sahki","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1288880153","display_name":"H\u00f4pital Necker-Enfants Malades","ror":"https://ror.org/05tr67282","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I1288880153","https://openalex.org/I4210097159","https://openalex.org/I4210120235"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Djouher Sahki","raw_affiliation_strings":["Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,","institution_ids":["https://openalex.org/I1288880153","https://openalex.org/I4210097159"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5104188758","display_name":"Floriane Sauvage","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Floriane Sauvage","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5022814475","display_name":"Manuela Scalbert","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Manuela Scalbert","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148795882","display_name":"Consuelo Sebastiasancho","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Consuelo Sebastiasancho","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5018306210","display_name":"Isabelle Sermet\u2010Gaudelus","orcid":"https://orcid.org/0000-0001-5537-9482","observed_orcids":["https://orcid.org/0000-0001-5537-9482"]},"institutions":[{"id":"https://openalex.org/I1288880153","display_name":"H\u00f4pital Necker-Enfants Malades","ror":"https://ror.org/05tr67282","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I1288880153","https://openalex.org/I4210097159","https://openalex.org/I4210120235"]},{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]},{"id":"https://openalex.org/I4210086369","display_name":"Institut Necker Enfants Malades","ror":"https://ror.org/000nhq538","country_code":"FR","type":"facility","lineage":["https://openalex.org/I1294671590","https://openalex.org/I154526488","https://openalex.org/I204730241","https://openalex.org/I4210086369","https://openalex.org/I4210096427"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4387156277","display_name":"ERN LUNG","ror":"https://ror.org/0279ntc65","country_code":"DE","type":"healthcare","lineage":["https://openalex.org/I1320481043","https://openalex.org/I2800387288","https://openalex.org/I4387155652","https://openalex.org/I4387156277"]}],"countries":["DE","FR"],"is_corresponding":false,"raw_author_name":"Isabelle Sermet-Gaudelus","raw_affiliation_strings":["Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,","European Respiratory Network Lung , Frankfurt 60596 ,","INSERM U1151, Institut Necker Enfants Malades , Paris 75015 ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Centre de R\u00e9f\u00e9rences Maladies Rares, Mucoviscidose et Maladies, Apparent\u00e9e-H\u00f4pital Universitaire Necker-Enfants Malades\u2014APHP , Paris 75015 ,","institution_ids":["https://openalex.org/I1288880153","https://openalex.org/I4210097159"]},{"raw_affiliation_string":"European Respiratory Network Lung , Frankfurt 60596 ,","institution_ids":["https://openalex.org/I4387156277"]},{"raw_affiliation_string":"INSERM U1151, Institut Necker Enfants Malades , Paris 75015 ,","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210086369"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148783078","display_name":"Chiara Sielo","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Chiara Sielo","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148772488","display_name":"Sophie Simon","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Sophie Simon","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5034508646","display_name":"Ana\u00eblle Simonneau","orcid":"https://orcid.org/0000-0001-6194-4812","observed_orcids":["https://orcid.org/0000-0001-6194-4812"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Anaelle Simonneau","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5014940090","display_name":"Floriane Socchi","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Floriane Socchi","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5006444836","display_name":"Nathalie Stremler","orcid":"https://orcid.org/0009-0004-8884-0772","observed_orcids":["https://orcid.org/0009-0004-8884-0772"]},"institutions":[{"id":"https://openalex.org/I4210087487","display_name":"Assistance Publique H\u00f4pitaux de Marseille","ror":"https://ror.org/002cp4060","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I21491767","https://openalex.org/I4210087487"]},{"id":"https://openalex.org/I4210162909","display_name":"H\u00f4pital de la Timone","ror":"https://ror.org/05jrr4320","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I21491767","https://openalex.org/I4210087487","https://openalex.org/I4210162909"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Nathalie Stremler","raw_affiliation_strings":["Centre de Ressources et de Comp\u00e9tence de la Mucoviscidose P\u00e9diatrique-H\u00f4pital D'enfants de la Timone\u2014Assistance Publique H\u00f4pitaux de Marseille , Marseille 13005 ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Centre de Ressources et de Comp\u00e9tence de la Mucoviscidose P\u00e9diatrique-H\u00f4pital D'enfants de la Timone\u2014Assistance Publique H\u00f4pitaux de Marseille , Marseille 13005 ,","institution_ids":["https://openalex.org/I4210087487","https://openalex.org/I4210162909"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5036567805","display_name":"Aur\u00e9lie Tatopoulos","orcid":"https://orcid.org/0000-0001-6195-9555","observed_orcids":["https://orcid.org/0000-0001-6195-9555"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Aur\u00e9lie Tatopoulos","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5037776758","display_name":"Matthieu Thimmesch","orcid":"https://orcid.org/0000-0001-6058-3373","observed_orcids":["https://orcid.org/0000-0001-6058-3373"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Matthieu Thimmesch","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5019704464","display_name":"Diane Abdel-Latif Thomasson","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Diane Thomassonabdel-Latif","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5061804250","display_name":"Guillaume Thouvenin","orcid":"https://orcid.org/0000-0003-0528-5458","observed_orcids":["https://orcid.org/0000-0003-0528-5458"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Guillaume Thouvenin","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5016850961","display_name":"C. Thumerelle","orcid":"https://orcid.org/0000-0002-3365-2035","observed_orcids":["https://orcid.org/0000-0002-3365-2035"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Caroline Thumerelle","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5128675856","display_name":"C\u00e9lia Thilliard","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"C\u00e9lia Thilliard","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5074084611","display_name":"Jean\u2010Yves Travers","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Jean-Yves Travers","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5054314419","display_name":"Fran\u00e7oise Troussier","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Fran\u00e7oise Troussier","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5017366178","display_name":"Sophie Valois","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Sophie Vallois","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148779235","display_name":"Saskia Vandeperre","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Saskia Vandeperre","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5148823952","display_name":"Julie Vial","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Julie Vial","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5159307160","display_name":"Philippe Vigneron","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Philippe Vigneron","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5112736505","display_name":"Laurence Weiss","orcid":"https://orcid.org/0000-0002-1728-915X","observed_orcids":["https://orcid.org/0000-0002-1728-915X"]},"institutions":[{"id":"https://openalex.org/I4210145324","display_name":"H\u00f4pitaux Universitaires de Strasbourg","ror":"https://ror.org/04bckew43","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210145324"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Laurence Weiss","raw_affiliation_strings":["Centre de Ressources et de Comp\u00e9tence de la Mucoviscidose, P\u00e9diatrique-H\u00f4pitaux Universitaires de Strasbourg , Strasbourg 67200 ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Centre de Ressources et de Comp\u00e9tence de la Mucoviscidose, P\u00e9diatrique-H\u00f4pitaux Universitaires de Strasbourg , Strasbourg 67200 ,","institution_ids":["https://openalex.org/I4210145324"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5025213413","display_name":"Marie\u2010Christine Werck\u2010Gallois","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Marie-Christine Werck-Gallois","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5107910215","display_name":"Nathalie Wizla","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Nathalie Wizla","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":4,"institutions_distinct_count":13,"corresponding_author_ids":["https://openalex.org/A5076842743"],"corresponding_institution_ids":["https://openalex.org/I204730241","https://openalex.org/I32971472","https://openalex.org/I4210126712"],"apc_list":{"value":3750,"currency":"USD","value_usd":3750},"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10665","display_name":"Cystic Fibrosis Research Advances","score":0.9926999807357788,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10665","display_name":"Cystic Fibrosis Research Advances","score":0.9926999807357788,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10560","display_name":"Diabetes Management and Research","score":0.0012000000569969416,"subfield":{"id":"https://openalex.org/subfields/2712","display_name":"Endocrinology, Diabetes and Metabolism"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10839","display_name":"Pancreatic function and diabetes","score":0.00039999998989515007,"subfield":{"id":"https://openalex.org/subfields/2712","display_name":"Endocrinology, Diabetes and Metabolism"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/cystic-fibrosis","display_name":"cystic fibrosis","score":1.0},{"id":"https://openalex.org/keywords/elexacaftor-tezacaftor-ivacaftor","display_name":"elexacaftor/tezacaftor/ivacaftor","score":0.9779999852180481},{"id":"https://openalex.org/keywords/cftr-modulators","display_name":"CFTR modulators","score":0.9020000100135803},{"id":"https://openalex.org/keywords/continuous-glucose-monitoring","display_name":"continuous glucose monitoring","score":0.8769999742507935},{"id":"https://openalex.org/keywords/glucose-tolerance","display_name":"glucose tolerance","score":0.8370000123977661},{"id":"https://openalex.org/keywords/hyperglycemia","display_name":"hyperglycemia","score":0.8100000023841858},{"id":"https://openalex.org/keywords/glycemic-variability","display_name":"glycemic variability","score":0.8050000071525574},{"id":"https://openalex.org/keywords/pediatric-patients","display_name":"pediatric patients","score":0.578000009059906},{"id":"https://openalex.org/keywords/adolescents","display_name":"adolescents","score":0.9240000247955322},{"id":"https://openalex.org/keywords/weight-gain","display_name":"weight gain","score":0.7429999709129333},{"id":"https://openalex.org/keywords/lung-function","display_name":"lung function","score":0.9900000095367432}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.876800000667572},{"id":"https://openalex.org/C2776938444","wikidata":"https://www.wikidata.org/wiki/Q178194","display_name":"Cystic fibrosis","level":2,"score":0.7886999845504761},{"id":"https://openalex.org/C72563966","wikidata":"https://www.wikidata.org/wiki/Q1303415","display_name":"Cohort","level":2,"score":0.6830000281333923},{"id":"https://openalex.org/C2986379492","wikidata":"https://www.wikidata.org/wiki/Q1638492","display_name":"Continuous glucose monitoring","level":4,"score":0.5629000067710876},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.47279998660087585},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.44530001282691956},{"id":"https://openalex.org/C3020574416","wikidata":"https://www.wikidata.org/wiki/Q275157","display_name":"Plasma glucose","level":3,"score":0.4124000072479248},{"id":"https://openalex.org/C3018587741","wikidata":"https://www.wikidata.org/wiki/Q7886","display_name":"Lung function","level":3,"score":0.4099000096321106},{"id":"https://openalex.org/C2780520431","wikidata":"https://www.wikidata.org/wiki/Q5201210","display_name":"Cystic fibrosis-related diabetes","level":5,"score":0.367900013923645},{"id":"https://openalex.org/C201903717","wikidata":"https://www.wikidata.org/wiki/Q1778788","display_name":"Cohort study","level":2,"score":0.3287999927997589},{"id":"https://openalex.org/C555293320","wikidata":"https://www.wikidata.org/wiki/Q12206","display_name":"Diabetes mellitus","level":2,"score":0.298799991607666},{"id":"https://openalex.org/C134018914","wikidata":"https://www.wikidata.org/wiki/Q162606","display_name":"Endocrinology","level":1,"score":0.2800000011920929},{"id":"https://openalex.org/C2779306644","wikidata":"https://www.wikidata.org/wiki/Q2002370","display_name":"Insulin","level":2,"score":0.2800000011920929},{"id":"https://openalex.org/C2780833929","wikidata":"https://www.wikidata.org/wiki/Q1501412","display_name":"Glucose tolerance test","level":4,"score":0.27129998803138733},{"id":"https://openalex.org/C2777714996","wikidata":"https://www.wikidata.org/wiki/Q7886","display_name":"Lung","level":2,"score":0.2565999925136566},{"id":"https://openalex.org/C2986834420","wikidata":"https://www.wikidata.org/wiki/Q5932254","display_name":"Age groups","level":2,"score":0.2517000138759613},{"id":"https://openalex.org/C2776178081","wikidata":"https://www.wikidata.org/wiki/Q3286546","display_name":"Respiratory disease","level":3,"score":0.2502000033855438}],"mesh":[],"locations_count":2,"locations":[{"id":"doi:10.1210/clinem/dgag358","doi":"https://doi.org/10.1210/clinem/dgag358","is_oa":false,"landing_page_url":"https://doi.org/10.1210/clinem/dgag358","pdf_url":null,"source":{"id":"https://openalex.org/S205775358","display_name":"The Journal of Clinical Endocrinology & Metabolism","issn_l":"0021-972X","issn":["0021-972X","1945-7197"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-class-a","anvur-scientific","cwts-core","dongbi-b","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Journal of Clinical Endocrinology &amp; Metabolism","raw_type":"journal-article"},{"id":"pmid:42671070","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/42671070","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Journal of clinical endocrinology and metabolism","raw_type":"Journal Article"}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":1.0}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[{"id":"https://openalex.org/G6410698471","display_name":null,"funder_award_id":"003341121","funder_id":"https://openalex.org/F4320306168","funder_display_name":"Cystic Fibrosis Foundation"}],"funders":[{"id":"https://openalex.org/F4320306168","display_name":"Cystic Fibrosis Foundation","ror":"https://ror.org/00ax59295"}],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":34,"referenced_works":["https://openalex.org/W1821102469","https://openalex.org/W1974313427","https://openalex.org/W2049236612","https://openalex.org/W2099449365","https://openalex.org/W2099468197","https://openalex.org/W2125568531","https://openalex.org/W2148495167","https://openalex.org/W2158418727","https://openalex.org/W2302984431","https://openalex.org/W2496297269","https://openalex.org/W2793208351","https://openalex.org/W2891476211","https://openalex.org/W2941246007","https://openalex.org/W2985326824","https://openalex.org/W3121759962","https://openalex.org/W3199130498","https://openalex.org/W3214022819","https://openalex.org/W4225808778","https://openalex.org/W4311596863","https://openalex.org/W4312179122","https://openalex.org/W4362661734","https://openalex.org/W4367600780","https://openalex.org/W4385329903","https://openalex.org/W4392756877","https://openalex.org/W4401250977","https://openalex.org/W4401691376","https://openalex.org/W4405219856","https://openalex.org/W4405286280","https://openalex.org/W4407190350","https://openalex.org/W4407365690","https://openalex.org/W4407767640","https://openalex.org/W4415339801","https://openalex.org/W4415582952","https://openalex.org/W4416411754"],"related_works":["https://openalex.org/W4308138022","https://openalex.org/W4407767640","https://openalex.org/W4410998238","https://openalex.org/W4410999467","https://openalex.org/W3199130498","https://openalex.org/W7211918681","https://openalex.org/W4364376796","https://openalex.org/W4416675250","https://openalex.org/W7163143436","https://openalex.org/W4309337649"],"abstract_inverted_index":{"INTRODUCTION:":[0],"Glucose":[1],"tolerance":[2],"abnormalities":[3],"can":[4],"be":[5],"detected":[6],"in":[7,83,132,208],"preschool":[8,117],"and":[9,35,70,95,105,123,169,188,210],"school-age":[10],"children":[11,122,209],"with":[12,58,111,140,162,180,197,203,212],"cystic":[13],"fibrosis.":[14],"There":[15],"is":[16,201],"limited":[17],"data":[18,65],"on":[19,27,87],"the":[20,49,88,143,195,220],"impact":[21,219],"of":[22,63,68,137,142,148,155,166,190,205,222],"CFTR":[23],"modulator":[24],"elexacaftor/tezacaftor/ivacaftor":[25],"(ETI)":[26],"their":[28],"trajectories.":[29],"We":[30,45],"examined":[31],"CGM":[32,64,73,98,206],"metrics":[33,101],"before":[34,66,104,215],"after":[36,106],"ETI":[37,69,77,91,200,216],"initiation":[38,67,217],"across":[39],"different":[40],"pediatric":[41],"age":[42,89,121],"groups.":[43],"METHODS:":[44],"included":[46],"participants":[47,128],"from":[48],"French":[50],"MODUL-CF":[51],"real":[52],"world":[53],"study":[54],"aged":[55],"2-18":[56],"years":[57],"at":[59,90,182],"least":[60],"24":[61],"hours":[62],"a":[71,130,163,170],"2nd":[72],"12\u00b13":[74],"months":[75],"following":[76],"start.":[78],"The":[79],"cohort":[80,145],"was":[81,160],"stratified":[82],"3":[84],"groups":[85],"based":[86],"initiation:":[92],"<6,":[93],"6-12":[94],">12":[96],"years.":[97],"derived":[99],"glucose":[100,134,207],"were":[102,113],"compared":[103],"ETI.":[107],"RESULTS:":[108],"98":[109],"patients":[110],"CF":[112],"enrolled,":[114],"including":[115],"13":[116],"children,":[118],"55":[119],"school":[120],"32":[124],"adolescents.":[125],"At":[126],"baseline,":[127],"displayed":[129,184],"time":[131],"tight":[133],"range":[135],"(TITR)":[136],"89.8%(84.1,":[138],"93.4)":[139],"34%":[141],"whole":[144],"spending":[146],">10%":[147],"time>140mg/dL":[149],"(TA140).":[150],"Following":[151],"treatment,":[152],"TITR":[153],"increased":[154],"\u223c2%(+1.8[-1.8,":[156],"+6.0]%)":[157],"(p=0.004).":[158],"This":[159],"associated":[161,202],"0.4%":[164],"reduction":[165],"mild-hyperglycemia":[167],"(>140mg/dL)":[168],"lower":[171],"CV":[172],"(21.5%(19.0,":[173],"24.7)":[174],"vs":[175],"19.6%(17.0,":[176],"22.6),":[177],"p<0.001).":[178],"Those":[179],"TA140\u226410%":[181],"baseline":[183],"greater":[185],"weight":[186],"gain":[187],"improvement":[189,204],"lung":[191],"function":[192],"respect":[193],"to":[194],"group":[196],"TA140>10%.":[198],"CONCLUSION:":[199],"adolescents":[211],"CF.":[213],"TA140":[214],"may":[218],"trajectory":[221],"clinically":[223],"relevant":[224],"outcomes.":[225]},"counts_by_year":[],"updated_date":"2026-11-01T11:40:01.658920","created_date":"2026-09-01T00:00:00"}
