{"id":"https://openalex.org/W7204538816","doi":"https://doi.org/10.9734/irjgh/2026/v9i1158","title":"Non-cirrhotic Portal Hypertension: Think of Chronic Myelomonocytic Leukemia \u2014 A Case Report","display_name":"Non-cirrhotic Portal Hypertension: Think of Chronic Myelomonocytic Leukemia \u2014 A Case Report","publication_year":2026,"publication_date":"2026-08-28","ids":{"openalex":"https://openalex.org/W7204538816","doi":"https://doi.org/10.9734/irjgh/2026/v9i1158"},"language":"en","primary_location":{"id":"doi:10.9734/irjgh/2026/v9i1158","doi":"https://doi.org/10.9734/irjgh/2026/v9i1158","is_oa":true,"landing_page_url":"https://doi.org/10.9734/irjgh/2026/v9i1158","pdf_url":null,"source":null,"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"International Research Journal of Gastroenterology and Hepatology","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref"],"open_access":{"is_oa":true,"oa_status":"gold","oa_url":"https://doi.org/10.9734/irjgh/2026/v9i1158","any_repository_has_fulltext":null},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5076479615","display_name":"A. A. Bah","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210167424","display_name":"H\u00f4pital Militaire Avicenne","ror":"https://ror.org/02cfbec64","country_code":"MA","type":"healthcare","lineage":["https://openalex.org/I4210167424"]}],"countries":["MA"],"is_corresponding":false,"raw_author_name":"A. A. Bah","raw_affiliation_strings":["Department of Gastroenterology, Avicenne Military Hospital, Marrakech, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Gastroenterology, Avicenne Military Hospital, Marrakech, Morocco","institution_ids":["https://openalex.org/I4210167424"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5137072532","display_name":"K. Gharbi","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210167424","display_name":"H\u00f4pital Militaire Avicenne","ror":"https://ror.org/02cfbec64","country_code":"MA","type":"healthcare","lineage":["https://openalex.org/I4210167424"]}],"countries":["MA"],"is_corresponding":false,"raw_author_name":"K. Gharbi","raw_affiliation_strings":["Department of Gastroenterology, Avicenne Military Hospital, Marrakech, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Gastroenterology, Avicenne Military Hospital, Marrakech, Morocco","institution_ids":["https://openalex.org/I4210167424"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5022175842","display_name":"R. Akka","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210167424","display_name":"H\u00f4pital Militaire Avicenne","ror":"https://ror.org/02cfbec64","country_code":"MA","type":"healthcare","lineage":["https://openalex.org/I4210167424"]}],"countries":["MA"],"is_corresponding":false,"raw_author_name":"R. Akka","raw_affiliation_strings":["Department of Gastroenterology, Avicenne Military Hospital, Marrakech, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Gastroenterology, Avicenne Military Hospital, Marrakech, Morocco","institution_ids":["https://openalex.org/I4210167424"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":["https://openalex.org/I4210167424"],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":{"value":0.58087695,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"9","issue":"1","first_page":"267","last_page":"271"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10337","display_name":"Liver Disease and Transplantation","score":0.5874000191688538,"subfield":{"id":"https://openalex.org/subfields/2721","display_name":"Hepatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10337","display_name":"Liver Disease and Transplantation","score":0.5874000191688538,"subfield":{"id":"https://openalex.org/subfields/2721","display_name":"Hepatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11628","display_name":"Myeloproliferative Neoplasms: Diagnosis and Treatment","score":0.3334999978542328,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11625","display_name":"Abdominal vascular conditions and treatments","score":0.013299999758601189,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/non-cirrhotic-portal-hypertension","display_name":"non-cirrhotic portal hypertension","score":0.9980000257492065},{"id":"https://openalex.org/keywords/chronic-myelomonocytic-leukemia","display_name":"chronic myelomonocytic leukemia","score":0.9649999737739563},{"id":"https://openalex.org/keywords/esophageal-varices","display_name":"esophageal varices","score":0.847000002861023},{"id":"https://openalex.org/keywords/variceal-bleeding","display_name":"variceal bleeding","score":0.9869999885559082},{"id":"https://openalex.org/keywords/hematemesis","display_name":"hematemesis","score":0.8999999761581421},{"id":"https://openalex.org/keywords/splenomegaly","display_name":"splenomegaly","score":0.9760000109672546},{"id":"https://openalex.org/keywords/monocytosis","display_name":"monocytosis","score":0.8489999771118164},{"id":"https://openalex.org/keywords/myelodysplastic-syndrome","display_name":"myelodysplastic syndrome","score":0.8040000200271606},{"id":"https://openalex.org/keywords/hydroxyurea","display_name":"hydroxyurea","score":0.7570000290870667},{"id":"https://openalex.org/keywords/beta-blockers","display_name":"beta-blockers","score":0.8600000143051147},{"id":"https://openalex.org/keywords/hematologic-malignancies","display_name":"hematologic malignancies","score":0.597000002861023}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.958299994468689},{"id":"https://openalex.org/C2778923028","wikidata":"https://www.wikidata.org/wiki/Q974869","display_name":"Leukocytosis","level":2,"score":0.7545999884605408},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.5703999996185303},{"id":"https://openalex.org/C2781087989","wikidata":"https://www.wikidata.org/wiki/Q1682044","display_name":"Monocytosis","level":3,"score":0.5436999797821045},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.5375999808311462},{"id":"https://openalex.org/C2777928532","wikidata":"https://www.wikidata.org/wiki/Q1088072","display_name":"Chronic myelomonocytic leukemia","level":4,"score":0.5375000238418579},{"id":"https://openalex.org/C2778808290","wikidata":"https://www.wikidata.org/wiki/Q124604","display_name":"Portal hypertension","level":3,"score":0.517300009727478},{"id":"https://openalex.org/C2778800853","wikidata":"https://www.wikidata.org/wiki/Q1704044","display_name":"Portal vein thrombosis","level":3,"score":0.5109000205993652},{"id":"https://openalex.org/C2779102576","wikidata":"https://www.wikidata.org/wiki/Q5113984","display_name":"Chronic liver disease","level":3,"score":0.46630001068115234},{"id":"https://openalex.org/C2780007613","wikidata":"https://www.wikidata.org/wiki/Q546523","display_name":"Bone marrow","level":2,"score":0.4472000002861023},{"id":"https://openalex.org/C2778080469","wikidata":"https://www.wikidata.org/wiki/Q1495657","display_name":"Gastrointestinal bleeding","level":2,"score":0.37310001254081726},{"id":"https://openalex.org/C2778219007","wikidata":"https://www.wikidata.org/wiki/Q1777322","display_name":"Bone marrow examination","level":3,"score":0.37049999833106995},{"id":"https://openalex.org/C2776309230","wikidata":"https://www.wikidata.org/wiki/Q580383","display_name":"Splenectomy","level":3,"score":0.36809998750686646},{"id":"https://openalex.org/C2779399171","wikidata":"https://www.wikidata.org/wiki/Q1483951","display_name":"Malignancy","level":2,"score":0.36059999465942383},{"id":"https://openalex.org/C2779195621","wikidata":"https://www.wikidata.org/wiki/Q5526797","display_name":"Gastric varices","level":4,"score":0.36039999127388},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.3490999937057495},{"id":"https://openalex.org/C2780955771","wikidata":"https://www.wikidata.org/wiki/Q183425","display_name":"Abdominal pain","level":2,"score":0.34769999980926514},{"id":"https://openalex.org/C2781143854","wikidata":"https://www.wikidata.org/wiki/Q938957","display_name":"Esophagogastroduodenoscopy","level":3,"score":0.3249000012874603},{"id":"https://openalex.org/C126838900","wikidata":"https://www.wikidata.org/wiki/Q77604","display_name":"Radiology","level":1,"score":0.3091999888420105},{"id":"https://openalex.org/C2779788118","wikidata":"https://www.wikidata.org/wiki/Q1542410","display_name":"Thrombocytosis","level":3,"score":0.30309998989105225},{"id":"https://openalex.org/C2778248108","wikidata":"https://www.wikidata.org/wiki/Q5445","display_name":"Anemia","level":2,"score":0.30300000309944153},{"id":"https://openalex.org/C2777595160","wikidata":"https://www.wikidata.org/wiki/Q298278","display_name":"Esophageal varices","level":4,"score":0.29760000109672546},{"id":"https://openalex.org/C2778012290","wikidata":"https://www.wikidata.org/wiki/Q2624485","display_name":"Varices","level":3,"score":0.2962999939918518},{"id":"https://openalex.org/C2779282312","wikidata":"https://www.wikidata.org/wiki/Q1956561","display_name":"Myeloid","level":2,"score":0.290800005197525},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.28839999437332153},{"id":"https://openalex.org/C2778729363","wikidata":"https://www.wikidata.org/wiki/Q11688946","display_name":"Myeloid leukemia","level":2,"score":0.2854999899864197},{"id":"https://openalex.org/C2778608605","wikidata":"https://www.wikidata.org/wiki/Q4677943","display_name":"Acute myelomonocytic leukemia","level":3,"score":0.2847000062465668},{"id":"https://openalex.org/C2776345487","wikidata":"https://www.wikidata.org/wiki/Q3144956","display_name":"Upper gastrointestinal bleeding","level":3,"score":0.27219998836517334},{"id":"https://openalex.org/C2777655228","wikidata":"https://www.wikidata.org/wiki/Q590460","display_name":"Abdominal ultrasonography","level":3,"score":0.27160000801086426},{"id":"https://openalex.org/C2777424391","wikidata":"https://www.wikidata.org/wiki/Q1163908","display_name":"Melena","level":2,"score":0.2680000066757202},{"id":"https://openalex.org/C2777075537","wikidata":"https://www.wikidata.org/wiki/Q929737","display_name":"Liver disease","level":2,"score":0.26330000162124634},{"id":"https://openalex.org/C2778451229","wikidata":"https://www.wikidata.org/wiki/Q212809","display_name":"Endoscopy","level":2,"score":0.25429999828338623}],"mesh":[],"locations_count":2,"locations":[{"id":"doi:10.9734/irjgh/2026/v9i1158","doi":"https://doi.org/10.9734/irjgh/2026/v9i1158","is_oa":true,"landing_page_url":"https://doi.org/10.9734/irjgh/2026/v9i1158","pdf_url":null,"source":null,"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"International Research Journal of Gastroenterology and Hepatology","raw_type":"journal-article"},{"id":"pmh:oai:HAL:hal-05730968v1","doi":null,"is_oa":false,"landing_page_url":"https://hal.science/hal-05730968","pdf_url":null,"source":{"id":"https://openalex.org/S4306402512","display_name":"HAL","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I4405252976","host_organization_name":"Centre pour la Communication Scientifique Directe","host_organization_lineage":["https://openalex.org/I4405252976"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"International Research Journal of Gastroenterology and Hepatology, 2026, 9 (1), pp.267-271","raw_type":"info:eu-repo/semantics/article"}],"best_oa_location":{"id":"doi:10.9734/irjgh/2026/v9i1158","doi":"https://doi.org/10.9734/irjgh/2026/v9i1158","is_oa":true,"landing_page_url":"https://doi.org/10.9734/irjgh/2026/v9i1158","pdf_url":null,"source":null,"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"International Research Journal of Gastroenterology and Hepatology","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":1.0,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W7204713643","https://openalex.org/W4381332997","https://openalex.org/W2978884773","https://openalex.org/W4417202407","https://openalex.org/W4409459650","https://openalex.org/W7113897583","https://openalex.org/W2977305267","https://openalex.org/W4384567497","https://openalex.org/W2978649315","https://openalex.org/W4412467669"],"abstract_inverted_index":{"Non-cirrhotic":[0],"portal":[1,51,127,136],"hypertension":[2],"is":[3,26,54],"an":[4],"uncommon":[5],"cause":[6],"of":[7,42,60,68,99,104,196],"variceal":[8],"bleeding":[9,213],"and":[10,20,38,80,94,126,147,150,174,189,205,210],"requires":[11],"careful":[12],"evaluation":[13],"for":[14],"vascular,":[15],"hepatic,":[16],"infectious,":[17],"autoimmune,":[18],"metabolic,":[19],"haematological":[21,29,208],"causes.":[22],"Chronic":[23],"myelomonocytic":[24,198],"leukaemia":[25],"a":[27,39,61,134],"clonal":[28],"malignancy":[30],"characterised":[31],"by":[32,118],"persistent":[33,163],"monocytosis,":[34],"bone":[35],"marrow":[36,181],"dysplasia,":[37,186],"variable":[40],"risk":[41],"progression":[43],"to":[44],"acute":[45],"myeloid":[46,185],"leukaemia.":[47,199],"A":[48],"hepatic":[49],"or":[50,102],"hypertensive":[52],"presentation":[53],"unusual.":[55],"We":[56],"report":[57],"the":[58,92,194],"case":[59],"68-year-old":[62],"man":[63],"with":[64,73,77,114,207],"no":[65,211],"known":[66],"history":[67],"liver":[69],"disease":[70],"who":[71],"presented":[72],"massive":[74,88],"haematemesis":[75],"associated":[76],"progressive":[78],"asthenia":[79],"long-standing":[81],"abdominal":[82],"heaviness.":[83],"Clinical":[84],"examination":[85],"revealed":[86,157],"pallor,":[87],"splenomegaly":[89,125],"extending":[90],"beyond":[91],"umbilicus,":[93],"moderate":[95],"hepatomegaly,":[96],"without":[97,138],"signs":[98],"hepatocellular":[100],"insufficiency":[101],"stigmata":[103],"cirrhosis.":[105],"Upper":[106],"gastrointestinal":[107],"endoscopy":[108],"showed":[109,133],"grade":[110],"II":[111],"oesophageal":[112],"varices":[113],"red":[115],"signs,":[116],"treated":[117],"endoscopic":[119],"band":[120],"ligation.":[121],"Abdominal":[122],"ultrasound":[123,132],"confirmed":[124],"vein":[128],"dilatation,":[129],"while":[130],"Doppler":[131],"patent":[135],"trunk":[137],"thrombosis.":[139],"Liver":[140],"elastography":[141],"did":[142],"not":[143],"show":[144],"advanced":[145],"fibrosis,":[146],"hepatitis":[148],"B":[149],"C":[151],"serologies":[152],"were":[153],"negative.":[154],"Laboratory":[155],"tests":[156],"leukocytosis":[158],"at":[159,165,171,176,214],"32":[160],"\u00d7":[161,167,178],"10\u2079/L,":[162,168],"monocytosis":[164],"4.5":[166],"normocytic":[169],"anaemia":[170],"9":[172],"g/dL,":[173],"thrombocytopenia":[175],"95":[177],"10\u2079/L.":[179],"Bone":[180],"aspiration":[182],"demonstrated":[183],"hypercellularity,":[184],"monocytic":[187],"proliferation,":[188],"blasts":[190],"below":[191],"5%,":[192],"supporting":[193],"diagnosis":[195],"chronic":[197],"The":[200],"patient":[201],"received":[202],"non-selective":[203],"beta-blockers":[204],"hydroxyurea,":[206],"stabilisation":[209],"recurrent":[212],"six":[215],"months.":[216]},"counts_by_year":[],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2026-08-29T00:00:00"}
