{"id":"https://openalex.org/W7203540546","doi":"https://doi.org/10.7759/cureus.114563","title":"An Uncommon Cause of Cystic Lung Disease","display_name":"An Uncommon Cause of Cystic Lung Disease","publication_year":2026,"publication_date":"2026-08-15","ids":{"openalex":"https://openalex.org/W7203540546","doi":"https://doi.org/10.7759/cureus.114563","pmid":"https://pubmed.ncbi.nlm.nih.gov/42741367"},"language":"en","primary_location":{"id":"doi:10.7759/cureus.114563","doi":"https://doi.org/10.7759/cureus.114563","is_oa":true,"landing_page_url":"https://doi.org/10.7759/cureus.114563","pdf_url":null,"source":{"id":"https://openalex.org/S2738950867","display_name":"Cureus","issn_l":"2168-8184","issn":["2168-8184"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310316779","host_organization_name":"Cureus, Inc.","host_organization_lineage":["https://openalex.org/P4310316779"],"host_organization_lineage_names":["Cureus, Inc."],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Cureus","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://doi.org/10.7759/cureus.114563","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5147241337","display_name":"Keegan Sorensen","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I184840846","display_name":"Virginia Commonwealth University","ror":"https://ror.org/02nkdxk79","country_code":"US","type":"education","lineage":["https://openalex.org/I184840846"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Keegan Sorensen","raw_affiliation_strings":["Internal Medicine, Virginia Commonwealth University, Richmond, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Internal Medicine, Virginia Commonwealth University, Richmond, USA","institution_ids":["https://openalex.org/I184840846"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5091873330","display_name":"Ali Khreisat","orcid":"https://orcid.org/0009-0001-6669-4987","observed_orcids":["https://orcid.org/0009-0001-6669-4987"]},"institutions":[{"id":"https://openalex.org/I184840846","display_name":"Virginia Commonwealth University","ror":"https://ror.org/02nkdxk79","country_code":"US","type":"education","lineage":["https://openalex.org/I184840846"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Ali Khreisat","raw_affiliation_strings":["Pulmonary and Critical Care Medicine, Virginia Commonwealth University, Richmond, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Pulmonary and Critical Care Medicine, Virginia Commonwealth University, Richmond, USA","institution_ids":["https://openalex.org/I184840846"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5139619648","display_name":"Mark Parker","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I184840846","display_name":"Virginia Commonwealth University","ror":"https://ror.org/02nkdxk79","country_code":"US","type":"education","lineage":["https://openalex.org/I184840846"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Mark Parker","raw_affiliation_strings":["Diagnostic Radiology, Thoracic Imaging Division, Virginia Commonwealth University, Richmond, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Diagnostic Radiology, Thoracic Imaging Division, Virginia Commonwealth University, Richmond, USA","institution_ids":["https://openalex.org/I184840846"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5015991699","display_name":"Valentina Robila","orcid":"https://orcid.org/0000-0003-4542-7238","observed_orcids":["https://orcid.org/0000-0003-4542-7238"]},"institutions":[{"id":"https://openalex.org/I184840846","display_name":"Virginia Commonwealth University","ror":"https://ror.org/02nkdxk79","country_code":"US","type":"education","lineage":["https://openalex.org/I184840846"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Valentina Robila","raw_affiliation_strings":["Pathology, Virginia Commonwealth University, Richmond, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Pathology, Virginia Commonwealth University, Richmond, USA","institution_ids":["https://openalex.org/I184840846"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5083578787","display_name":"Apostolos Perelas","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I184840846","display_name":"Virginia Commonwealth University","ror":"https://ror.org/02nkdxk79","country_code":"US","type":"education","lineage":["https://openalex.org/I184840846"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Apostolos Perelas","raw_affiliation_strings":["Pulmonary and Critical Care Medicine, Virginia Commonwealth University, Richmond, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Pulmonary and Critical Care Medicine, Virginia Commonwealth University, Richmond, USA","institution_ids":["https://openalex.org/I184840846"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":["https://openalex.org/I184840846"],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.67450364,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"18","issue":"8","first_page":"e114563","last_page":"e114563"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12600","display_name":"Eosinophilic Disorders and Syndromes","score":0.2655999958515167,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12600","display_name":"Eosinophilic Disorders and Syndromes","score":0.2655999958515167,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11305","display_name":"Amyloidosis: Diagnosis, Treatment, Outcomes","score":0.23160000145435333,"subfield":{"id":"https://openalex.org/subfields/1312","display_name":"Molecular Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T13759","display_name":"Medical Imaging and Pathology Studies","score":0.10540000349283218,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/cystic-lung-disease","display_name":"cystic lung disease","score":0.9259999990463257},{"id":"https://openalex.org/keywords/pulmonary-cysts","display_name":"pulmonary cysts","score":0.8230000138282776},{"id":"https://openalex.org/keywords/pulmonary-nodules","display_name":"pulmonary nodules","score":0.8019999861717224},{"id":"https://openalex.org/keywords/sjogren-s-syndrome","display_name":"Sj\u00f6gren's syndrome","score":0.9229999780654907},{"id":"https://openalex.org/keywords/covid-19","display_name":"COVID-19 pandemic","score":0.8949999809265137},{"id":"https://openalex.org/keywords/light-chain-deposition-disease","display_name":"light chain deposition disease","score":0.8930000066757202},{"id":"https://openalex.org/keywords/kappa-light-chain","display_name":"kappa light chain","score":0.7979999780654907},{"id":"https://openalex.org/keywords/hypergammaglobulinemia","display_name":"hypergammaglobulinemia","score":0.9769999980926514},{"id":"https://openalex.org/keywords/mycophenolate","display_name":"mycophenolate","score":0.8859999775886536},{"id":"https://openalex.org/keywords/thoracoscopic-wedge-resection","display_name":"thoracoscopic wedge resection","score":0.7760000228881836},{"id":"https://openalex.org/keywords/transbronchial-biopsy","display_name":"transbronchial biopsy","score":0.7609999775886536}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9836999773979187},{"id":"https://openalex.org/C2779563453","wikidata":"https://www.wikidata.org/wiki/Q6040221","display_name":"Lung biopsy","level":3,"score":0.5311999917030334},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.5203999876976013},{"id":"https://openalex.org/C2777714996","wikidata":"https://www.wikidata.org/wiki/Q7886","display_name":"Lung","level":2,"score":0.4733000099658966},{"id":"https://openalex.org/C126838900","wikidata":"https://www.wikidata.org/wiki/Q77604","display_name":"Radiology","level":1,"score":0.4643999934196472},{"id":"https://openalex.org/C2775934546","wikidata":"https://www.wikidata.org/wiki/Q179991","display_name":"Biopsy","level":2,"score":0.4629000127315521},{"id":"https://openalex.org/C2776053289","wikidata":"https://www.wikidata.org/wiki/Q7979172","display_name":"Wedge resection","level":3,"score":0.44690001010894775},{"id":"https://openalex.org/C75603125","wikidata":"https://www.wikidata.org/wiki/Q1877462","display_name":"Pulmonary function testing","level":2,"score":0.4212999939918518},{"id":"https://openalex.org/C2779758542","wikidata":"https://www.wikidata.org/wiki/Q2106364","display_name":"Eosinophilic","level":2,"score":0.40149998664855957},{"id":"https://openalex.org/C2776178081","wikidata":"https://www.wikidata.org/wiki/Q3286546","display_name":"Respiratory disease","level":3,"score":0.38580000400543213},{"id":"https://openalex.org/C2779701055","wikidata":"https://www.wikidata.org/wiki/Q929833","display_name":"Rare disease","level":3,"score":0.3481999933719635},{"id":"https://openalex.org/C544519230","wikidata":"https://www.wikidata.org/wiki/Q32566","display_name":"Computed tomography","level":2,"score":0.3271999955177307},{"id":"https://openalex.org/C2780007613","wikidata":"https://www.wikidata.org/wiki/Q546523","display_name":"Bone marrow","level":2,"score":0.32109999656677246},{"id":"https://openalex.org/C2777543607","wikidata":"https://www.wikidata.org/wiki/Q1153419","display_name":"Interstitial lung disease","level":3,"score":0.3158000111579895},{"id":"https://openalex.org/C2983914783","wikidata":"https://www.wikidata.org/wiki/Q3286546","display_name":"Lung disease","level":3,"score":0.2777999937534332},{"id":"https://openalex.org/C2776301714","wikidata":"https://www.wikidata.org/wiki/Q259346","display_name":"Sputum","level":3,"score":0.2703000009059906},{"id":"https://openalex.org/C2780514984","wikidata":"https://www.wikidata.org/wiki/Q17146775","display_name":"Hypergammaglobulinemia","level":3,"score":0.26669999957084656},{"id":"https://openalex.org/C2777524225","wikidata":"https://www.wikidata.org/wiki/Q4230125","display_name":"High-resolution computed tomography","level":3,"score":0.2623000144958496},{"id":"https://openalex.org/C2777223847","wikidata":"https://www.wikidata.org/wiki/Q407922","display_name":"Air trapping","level":3,"score":0.25699999928474426},{"id":"https://openalex.org/C2910901110","wikidata":"https://www.wikidata.org/wiki/Q35805","display_name":"Productive Cough","level":3,"score":0.2554999887943268},{"id":"https://openalex.org/C3017571381","wikidata":"https://www.wikidata.org/wiki/Q35805","display_name":"Dry cough","level":2,"score":0.2533999979496002}],"mesh":[],"locations_count":3,"locations":[{"id":"doi:10.7759/cureus.114563","doi":"https://doi.org/10.7759/cureus.114563","is_oa":true,"landing_page_url":"https://doi.org/10.7759/cureus.114563","pdf_url":null,"source":{"id":"https://openalex.org/S2738950867","display_name":"Cureus","issn_l":"2168-8184","issn":["2168-8184"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310316779","host_organization_name":"Cureus, Inc.","host_organization_lineage":["https://openalex.org/P4310316779"],"host_organization_lineage_names":["Cureus, Inc."],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Cureus","raw_type":"journal-article"},{"id":"pmid:42741367","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/42741367","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Cureus","raw_type":"Case Reports"},{"id":"pmh:oai:pubmedcentral.nih.gov:13573641","doi":null,"is_oa":true,"landing_page_url":"https://pmc.ncbi.nlm.nih.gov/articles/PMC13573641/","pdf_url":"https://pmc.ncbi.nlm.nih.gov/articles/PMC13573641/pdf/cureus-0018-00000114563.pdf","source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Cureus","raw_type":"Text"}],"best_oa_location":{"id":"doi:10.7759/cureus.114563","doi":"https://doi.org/10.7759/cureus.114563","is_oa":true,"landing_page_url":"https://doi.org/10.7759/cureus.114563","pdf_url":null,"source":{"id":"https://openalex.org/S2738950867","display_name":"Cureus","issn_l":"2168-8184","issn":["2168-8184"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310316779","host_organization_name":"Cureus, Inc.","host_organization_lineage":["https://openalex.org/P4310316779"],"host_organization_lineage_names":["Cureus, Inc."],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Cureus","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":1.0}],"sustainable_development_goals_aurora":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":0.6963598728179932}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":11,"referenced_works":["https://openalex.org/W1761041395","https://openalex.org/W1989199366","https://openalex.org/W2031114868","https://openalex.org/W2168639929","https://openalex.org/W2299010842","https://openalex.org/W2414959792","https://openalex.org/W2954252483","https://openalex.org/W3006188680","https://openalex.org/W4319041223","https://openalex.org/W4394688630","https://openalex.org/W4401968526"],"related_works":[],"abstract_inverted_index":{"A":[0],"59-year-old":[1],"female":[2],"with":[3,7,98,112],"Sj\u00f6gren's":[4],"syndrome":[5],"presented":[6],"a":[8,25,49,65],"three-year":[9],"history":[10],"of":[11,27,116],"dyspnea":[12],"and":[13,34,59,83,96],"cough":[14],"beginning":[15],"after":[16],"COVID-19":[17],"infection.":[18],"Serial":[19],"chest":[20],"computed":[21],"tomography":[22],"scans":[23],"over":[24,40],"course":[26],"three":[28],"years":[29],"revealed":[30,76],"multiple":[31],"pulmonary":[32],"cysts":[33],"nodules,":[35],"including":[36],"one":[37],"that":[38],"enlarged":[39],"time.":[41],"Pulmonary":[42],"function":[43],"was":[44],"largely":[45],"preserved,":[46],"aside":[47],"from":[48],"mildly":[50],"reduced":[51],"diffusing":[52],"capacity,":[53],"while":[54],"laboratory":[55],"studies":[56],"showed":[57],"hypergammaglobulinemia":[58],"elevated":[60],"kappa":[61],"light":[62,87],"chains.":[63],"After":[64],"nondiagnostic":[66],"bronchoscopic":[67],"transbronchial":[68],"biopsy,":[69],"she":[70],"underwent":[71],"thoracoscopic":[72],"wedge":[73],"resection.":[74],"Pathology":[75],"eosinophilic":[77],"deposits":[78],"without":[79],"Congo":[80],"red":[81],"staining,":[82],"mass":[84],"spectrometry":[85],"confirmed":[86],"chain":[88],"deposition":[89],"disease.":[90,119],"Bone":[91],"marrow":[92],"biopsy":[93],"excluded":[94],"malignancy,":[95],"treatment":[97],"mycophenolate":[99],"led":[100],"to":[101],"symptomatic":[102],"improvement.":[103],"This":[104],"case":[105],"highlights":[106],"the":[107],"diagnostic":[108],"challenges":[109],"often":[110],"encountered":[111],"an":[113],"uncommon":[114],"cause":[115],"cystic":[117],"lung":[118]},"counts_by_year":[],"updated_date":"2026-09-26T08:19:03.415552","created_date":"2026-08-16T00:00:00"}
