{"id":"https://openalex.org/W7202253702","doi":"https://doi.org/10.1007/s00277-026-07340-2","title":"Clinical features and prognostic impact of hemophagocytic lymphohistiocytosis in angioimmunoblastic T-cell lymphoma: a single-center retrospective study","display_name":"Clinical features and prognostic impact of hemophagocytic lymphohistiocytosis in angioimmunoblastic T-cell lymphoma: a single-center retrospective study","publication_year":2026,"publication_date":"2026-11-07","ids":{"openalex":"https://openalex.org/W7202253702","doi":"https://doi.org/10.1007/s00277-026-07340-2"},"language":"en","primary_location":{"id":"doi:10.1007/s00277-026-07340-2","doi":"https://doi.org/10.1007/s00277-026-07340-2","is_oa":true,"landing_page_url":"https://doi.org/10.1007/s00277-026-07340-2","pdf_url":null,"source":{"id":"https://openalex.org/S163204731","display_name":"Annals of Hematology","issn_l":"0939-5555","issn":["0939-5555","1432-0584"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","doyens","jufo-1","ki-jl-1","medline","norway-1","oarl","poland-70","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310319900","host_organization_name":"Springer Science+Business Media","host_organization_lineage":["https://openalex.org/P4310319900","https://openalex.org/P4310319965"],"host_organization_lineage_names":["Springer Science+Business Media","Springer Nature"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Annals of Hematology","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj"],"open_access":{"is_oa":true,"oa_status":"gold","oa_url":"https://doi.org/10.1007/s00277-026-07340-2","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5033913146","display_name":"Xiaodan He","orcid":"https://orcid.org/0009-0005-3925-0669","observed_orcids":["https://orcid.org/0009-0005-3925-0669"]},"institutions":[{"id":"https://openalex.org/I183519381","display_name":"Capital Medical University","ror":"https://ror.org/013xs5b60","country_code":"CN","type":"education","lineage":["https://openalex.org/I183519381"]},{"id":"https://openalex.org/I4210147433","display_name":"Beijing Friendship Hospital","ror":"https://ror.org/053qy4437","country_code":"CN","type":"healthcare","lineage":["https://openalex.org/I4210147433"]}],"countries":["CN"],"is_corresponding":false,"raw_author_name":"Xiaodan He","raw_affiliation_strings":["Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China","institution_ids":["https://openalex.org/I183519381","https://openalex.org/I4210147433"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5049888548","display_name":"Jingwei Cao","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I183519381","display_name":"Capital Medical University","ror":"https://ror.org/013xs5b60","country_code":"CN","type":"education","lineage":["https://openalex.org/I183519381"]},{"id":"https://openalex.org/I4210147433","display_name":"Beijing Friendship Hospital","ror":"https://ror.org/053qy4437","country_code":"CN","type":"healthcare","lineage":["https://openalex.org/I4210147433"]}],"countries":["CN"],"is_corresponding":false,"raw_author_name":"Jingwei Cao","raw_affiliation_strings":["Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China","institution_ids":["https://openalex.org/I183519381","https://openalex.org/I4210147433"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5022155984","display_name":"Gaochao Zhang","orcid":"https://orcid.org/0000-0002-9280-4350","observed_orcids":["https://orcid.org/0000-0002-9280-4350"]},"institutions":[{"id":"https://openalex.org/I183519381","display_name":"Capital Medical University","ror":"https://ror.org/013xs5b60","country_code":"CN","type":"education","lineage":["https://openalex.org/I183519381"]},{"id":"https://openalex.org/I4210147433","display_name":"Beijing Friendship Hospital","ror":"https://ror.org/053qy4437","country_code":"CN","type":"healthcare","lineage":["https://openalex.org/I4210147433"]}],"countries":["CN"],"is_corresponding":false,"raw_author_name":"Gaochao Zhang","raw_affiliation_strings":["Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China","institution_ids":["https://openalex.org/I183519381","https://openalex.org/I4210147433"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5141184719","display_name":"Du Yali","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I183519381","display_name":"Capital Medical University","ror":"https://ror.org/013xs5b60","country_code":"CN","type":"education","lineage":["https://openalex.org/I183519381"]},{"id":"https://openalex.org/I4210147433","display_name":"Beijing Friendship Hospital","ror":"https://ror.org/053qy4437","country_code":"CN","type":"healthcare","lineage":["https://openalex.org/I4210147433"]}],"countries":["CN"],"is_corresponding":false,"raw_author_name":"Yali Du","raw_affiliation_strings":["Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China","institution_ids":["https://openalex.org/I183519381","https://openalex.org/I4210147433"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5107206111","display_name":"Shu Fang","orcid":"https://orcid.org/0009-0003-3103-5046","observed_orcids":["https://orcid.org/0009-0003-3103-5046"]},"institutions":[{"id":"https://openalex.org/I183519381","display_name":"Capital Medical University","ror":"https://ror.org/013xs5b60","country_code":"CN","type":"education","lineage":["https://openalex.org/I183519381"]},{"id":"https://openalex.org/I4210147433","display_name":"Beijing Friendship Hospital","ror":"https://ror.org/053qy4437","country_code":"CN","type":"healthcare","lineage":["https://openalex.org/I4210147433"]}],"countries":["CN"],"is_corresponding":false,"raw_author_name":"Shu Fang","raw_affiliation_strings":["Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China","institution_ids":["https://openalex.org/I183519381","https://openalex.org/I4210147433"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5147039950","display_name":"Jing Wang","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I183519381","display_name":"Capital Medical University","ror":"https://ror.org/013xs5b60","country_code":"CN","type":"education","lineage":["https://openalex.org/I183519381"]},{"id":"https://openalex.org/I4210147433","display_name":"Beijing Friendship Hospital","ror":"https://ror.org/053qy4437","country_code":"CN","type":"healthcare","lineage":["https://openalex.org/I4210147433"]}],"countries":["CN"],"is_corresponding":false,"raw_author_name":"Jing Wang","raw_affiliation_strings":["Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China","institution_ids":["https://openalex.org/I183519381","https://openalex.org/I4210147433"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5147049813","display_name":"Miao Wang","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I183519381","display_name":"Capital Medical University","ror":"https://ror.org/013xs5b60","country_code":"CN","type":"education","lineage":["https://openalex.org/I183519381"]},{"id":"https://openalex.org/I4210147433","display_name":"Beijing Friendship Hospital","ror":"https://ror.org/053qy4437","country_code":"CN","type":"healthcare","lineage":["https://openalex.org/I4210147433"]}],"countries":["CN"],"is_corresponding":false,"raw_author_name":"Miao Wang","raw_affiliation_strings":["Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China","institution_ids":["https://openalex.org/I183519381","https://openalex.org/I4210147433"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5111320874","display_name":"Mengyuan Zhou","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I183519381","display_name":"Capital Medical University","ror":"https://ror.org/013xs5b60","country_code":"CN","type":"education","lineage":["https://openalex.org/I183519381"]},{"id":"https://openalex.org/I4210147433","display_name":"Beijing Friendship Hospital","ror":"https://ror.org/053qy4437","country_code":"CN","type":"healthcare","lineage":["https://openalex.org/I4210147433"]}],"countries":["CN"],"is_corresponding":false,"raw_author_name":"Mengyuan Zhou","raw_affiliation_strings":["Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China","institution_ids":["https://openalex.org/I183519381","https://openalex.org/I4210147433"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5015849563","display_name":"Jingshi Wang","orcid":"https://orcid.org/0000-0001-5050-9225","observed_orcids":["https://orcid.org/0000-0001-5050-9225"]},"institutions":[{"id":"https://openalex.org/I183519381","display_name":"Capital Medical University","ror":"https://ror.org/013xs5b60","country_code":"CN","type":"education","lineage":["https://openalex.org/I183519381"]},{"id":"https://openalex.org/I4210147433","display_name":"Beijing Friendship Hospital","ror":"https://ror.org/053qy4437","country_code":"CN","type":"healthcare","lineage":["https://openalex.org/I4210147433"]}],"countries":["CN"],"is_corresponding":true,"raw_author_name":"Jingshi Wang","raw_affiliation_strings":["Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology, Beijing Friendship Hospital, Capital Medical University, Beijing, 100050, China","institution_ids":["https://openalex.org/I183519381","https://openalex.org/I4210147433"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":["https://openalex.org/A5015849563"],"corresponding_institution_ids":["https://openalex.org/I183519381","https://openalex.org/I4210147433"],"apc_list":{"value":4590,"currency":"USD","value_usd":4590},"apc_paid":{"value":4590,"currency":"USD","value_usd":4590},"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.7813000082969666,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.7813000082969666,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10185","display_name":"Lymphoma Diagnosis and Treatment","score":0.16300000250339508,"subfield":{"id":"https://openalex.org/subfields/2734","display_name":"Pathology and Forensic Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10685","display_name":"Viral-associated cancers and disorders","score":0.04010000079870224,"subfield":{"id":"https://openalex.org/subfields/2730","display_name":"Oncology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/angioimmunoblastic-t-cell-lymphoma","display_name":"angioimmunoblastic T-cell lymphoma","score":0.9860000014305115},{"id":"https://openalex.org/keywords/hemophagocytic-lymphohistiocytosis","display_name":"hemophagocytic lymphohistiocytosis","score":0.9990000128746033},{"id":"https://openalex.org/keywords/hyperinflammation","display_name":"hyperinflammation","score":0.8600000143051147},{"id":"https://openalex.org/keywords/prognostic-factors","display_name":"prognostic factors","score":0.9440000057220459},{"id":"https://openalex.org/keywords/overall-survival","display_name":"overall survival","score":0.7179999947547913},{"id":"https://openalex.org/keywords/progression-free-survival","display_name":"progression-free survival","score":0.8320000171661377},{"id":"https://openalex.org/keywords/hyperferritinemia","display_name":"hyperferritinemia","score":0.8149999976158142},{"id":"https://openalex.org/keywords/bone-marrow-hemophagocytosis","display_name":"bone marrow hemophagocytosis","score":0.9010000228881836},{"id":"https://openalex.org/keywords/performance-status","display_name":"performance status","score":0.621999979019165},{"id":"https://openalex.org/keywords/conjugated-bilirubin","display_name":"direct bilirubin","score":0.8240000009536743},{"id":"https://openalex.org/keywords/platelet-count","display_name":"platelet count","score":0.9480000138282776},{"id":"https://openalex.org/keywords/immune-dysregulation","display_name":"immune dysregulation","score":0.8019999861717224}],"concepts":[{"id":"https://openalex.org/C2779079688","wikidata":"https://www.wikidata.org/wiki/Q1642170","display_name":"Hemophagocytic lymphohistiocytosis","level":3,"score":0.9358000159263611},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9071999788284302},{"id":"https://openalex.org/C2777363875","wikidata":"https://www.wikidata.org/wiki/Q5712526","display_name":"Hemophagocytosis","level":4,"score":0.8522999882698059},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.676800012588501},{"id":"https://openalex.org/C2779338263","wikidata":"https://www.wikidata.org/wiki/Q208414","display_name":"Lymphoma","level":2,"score":0.666700005531311},{"id":"https://openalex.org/C167135981","wikidata":"https://www.wikidata.org/wiki/Q2146302","display_name":"Retrospective cohort study","level":2,"score":0.6560999751091003},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.5284000039100647},{"id":"https://openalex.org/C2776365654","wikidata":"https://www.wikidata.org/wiki/Q4763257","display_name":"Angioimmunoblastic T-cell lymphoma","level":4,"score":0.4580000042915344},{"id":"https://openalex.org/C2780873365","wikidata":"https://www.wikidata.org/wiki/Q496812","display_name":"Leukopenia","level":3,"score":0.4426000118255615},{"id":"https://openalex.org/C197934379","wikidata":"https://www.wikidata.org/wiki/Q2047938","display_name":"Adverse effect","level":2,"score":0.40560001134872437},{"id":"https://openalex.org/C2781214270","wikidata":"https://www.wikidata.org/wiki/Q4692282","display_name":"Aggressive lymphoma","level":4,"score":0.39899998903274536},{"id":"https://openalex.org/C146357865","wikidata":"https://www.wikidata.org/wiki/Q1123245","display_name":"Stage (stratigraphy)","level":2,"score":0.37720000743865967},{"id":"https://openalex.org/C2778559949","wikidata":"https://www.wikidata.org/wiki/Q2626074","display_name":"Diffuse large B-cell lymphoma","level":3,"score":0.35670000314712524},{"id":"https://openalex.org/C3019894029","wikidata":"https://www.wikidata.org/wiki/Q332823","display_name":"Overall survival","level":2,"score":0.34950000047683716},{"id":"https://openalex.org/C205545832","wikidata":"https://www.wikidata.org/wiki/Q17156455","display_name":"Young adult","level":2,"score":0.34049999713897705},{"id":"https://openalex.org/C194409129","wikidata":"https://www.wikidata.org/wiki/Q103824","display_name":"Hematology","level":2,"score":0.32019999623298645},{"id":"https://openalex.org/C8891405","wikidata":"https://www.wikidata.org/wiki/Q1059","display_name":"Immune system","level":2,"score":0.31859999895095825},{"id":"https://openalex.org/C146304588","wikidata":"https://www.wikidata.org/wiki/Q961652","display_name":"Case-control study","level":2,"score":0.31529998779296875},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.3109000027179718},{"id":"https://openalex.org/C10515644","wikidata":"https://www.wikidata.org/wiki/Q543310","display_name":"Survival analysis","level":2,"score":0.30720001459121704},{"id":"https://openalex.org/C2776283816","wikidata":"https://www.wikidata.org/wiki/Q332823","display_name":"Survival rate","level":2,"score":0.3046000003814697},{"id":"https://openalex.org/C2780194698","wikidata":"https://www.wikidata.org/wiki/Q6005429","display_name":"Immune dysregulation","level":3,"score":0.29760000109672546},{"id":"https://openalex.org/C2780366003","wikidata":"https://www.wikidata.org/wiki/Q246147","display_name":"Cytopenia","level":3,"score":0.2605000138282776},{"id":"https://openalex.org/C2776015282","wikidata":"https://www.wikidata.org/wiki/Q644318","display_name":"Vasculitis","level":3,"score":0.25609999895095825},{"id":"https://openalex.org/C2778476033","wikidata":"https://www.wikidata.org/wiki/Q1667625","display_name":"International Prognostic Index","level":4,"score":0.25189998745918274}],"mesh":[],"locations_count":2,"locations":[{"id":"doi:10.1007/s00277-026-07340-2","doi":"https://doi.org/10.1007/s00277-026-07340-2","is_oa":true,"landing_page_url":"https://doi.org/10.1007/s00277-026-07340-2","pdf_url":null,"source":{"id":"https://openalex.org/S163204731","display_name":"Annals of Hematology","issn_l":"0939-5555","issn":["0939-5555","1432-0584"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","doyens","jufo-1","ki-jl-1","medline","norway-1","oarl","poland-70","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310319900","host_organization_name":"Springer Science+Business Media","host_organization_lineage":["https://openalex.org/P4310319900","https://openalex.org/P4310319965"],"host_organization_lineage_names":["Springer Science+Business Media","Springer Nature"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Annals of Hematology","raw_type":"journal-article"},{"id":"doi:10.21203/rs.3.rs-10537209/v1","doi":"https://doi.org/10.21203/rs.3.rs-10537209/v1","is_oa":true,"landing_page_url":"https://doi.org/10.21203/rs.3.rs-10537209/v1","pdf_url":"https://www.researchsquare.com/article/rs-10537209/latest.pdf","source":{"id":"https://openalex.org/S4306525896","display_name":"Research Square","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Research Square","raw_type":"posted-content"}],"best_oa_location":{"id":"doi:10.1007/s00277-026-07340-2","doi":"https://doi.org/10.1007/s00277-026-07340-2","is_oa":true,"landing_page_url":"https://doi.org/10.1007/s00277-026-07340-2","pdf_url":null,"source":{"id":"https://openalex.org/S163204731","display_name":"Annals of Hematology","issn_l":"0939-5555","issn":["0939-5555","1432-0584"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","doyens","jufo-1","ki-jl-1","medline","norway-1","oarl","poland-70","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310319900","host_organization_name":"Springer Science+Business Media","host_organization_lineage":["https://openalex.org/P4310319900","https://openalex.org/P4310319965"],"host_organization_lineage_names":["Springer Science+Business Media","Springer Nature"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Annals of Hematology","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":1.0,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[],"funders":[{"id":"https://openalex.org/F4320321001","display_name":"National Natural Science Foundation of China","ror":"https://ror.org/01h0zpd94"}],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7202253702.pdf","grobid_xml":"https://content.openalex.org/works/W7202253702.grobid-xml"},"referenced_works_count":29,"referenced_works":["https://openalex.org/W1997628957","https://openalex.org/W2009471409","https://openalex.org/W2015684600","https://openalex.org/W2049185125","https://openalex.org/W2053459660","https://openalex.org/W2064037171","https://openalex.org/W2067041786","https://openalex.org/W2076119473","https://openalex.org/W2133201432","https://openalex.org/W2159987792","https://openalex.org/W2162251899","https://openalex.org/W2282446718","https://openalex.org/W2283832635","https://openalex.org/W2416844197","https://openalex.org/W2582914277","https://openalex.org/W2838817294","https://openalex.org/W2936019126","https://openalex.org/W2991426900","https://openalex.org/W3043913681","https://openalex.org/W3142342531","https://openalex.org/W3208600129","https://openalex.org/W4223504540","https://openalex.org/W4226466846","https://openalex.org/W4320519485","https://openalex.org/W4380264769","https://openalex.org/W4390976585","https://openalex.org/W4394622628","https://openalex.org/W4404512863","https://openalex.org/W7130525254"],"related_works":["https://openalex.org/W4320519485","https://openalex.org/W7216319563","https://openalex.org/W2027364993","https://openalex.org/W2006711107","https://openalex.org/W2589728206","https://openalex.org/W2015895130","https://openalex.org/W2125847997","https://openalex.org/W3148092621","https://openalex.org/W2554453433","https://openalex.org/W2409813451"],"abstract_inverted_index":{"Angioimmunoblastic":[0],"T-cell":[1],"lymphoma":[2,123],"(AITL)":[3],"is":[4],"characterized":[5],"by":[6],"immune":[7],"dysregulation,":[8],"but":[9,148,233],"the":[10,119,229,234],"clinical":[11,37,219],"impact":[12],"of":[13],"associated":[14,136,176,215,224],"hemophagocytic":[15],"lymphohistiocytosis":[16],"(HLH)":[17],"remains":[18],"unclear.":[19],"We":[20],"retrospectively":[21],"analyzed":[22],"70":[23],"consecutive":[24],"patients":[25,47,65,249],"with":[26,64,69,137,151,177,183,216,225,250],"AITL":[27,50,61,211],"diagnosed":[28],"between":[29],"January":[30,33],"2015":[31],"and":[32,35,40,54,88,107,171,213,267],"2025":[34],"compared":[36],"features,":[38],"treatment,":[39],"outcomes":[41],"according":[42],"to":[43,210],"HLH":[44,70,120,133,184,202,221],"status.":[45],"23(32.9%)":[46],"hadAITL-HLH,5":[48],"before":[49],"diagnosis,":[51],"9":[52,55],"synchronously,":[53],"more":[56,71,217,246],"than":[57],"30":[58],"days":[59],"after":[60,187,240],"diagnosis.":[62],"Compared":[63],"without":[66],"HLH,":[67,251],"those":[68],"frequently":[72],"had":[73],"fever,":[74],"B":[75],"symptoms,":[76],"Ann":[77],"Arbor":[78],"stage":[79],"IV":[80],"disease,":[81],"bone-marrow":[82],"hemophagocytosis,":[83],"anemia,":[84],"thrombocytopenia,":[85],"hypoalbuminemia,":[86],"hyperferritinemia,":[87],"peripheral-blood":[89],"EBV-DNA":[90,243],"positivity":[91,244],"(":[92],"P":[93,104,113,145,158,199],"<":[94],"0.05).":[95],"Fixed-group":[96],"comparisions":[97],"showed":[98],"OS":[99,139,181,227],"(19.2":[100],"vs.":[101,110],"46.1":[102],"months;":[103,112],"=":[105,114,146,159,200],"0.037)":[106],"PFS":[108,152],"(9.6":[109],"31.6":[111],"0.038)":[115],"were":[116,126,175],"shorter":[117],"in":[118,228,264,270],"group,":[121],"whereas":[122,252],"response":[124],"rates":[125],"similar.":[127],"In":[128],"time-dependent":[129,231],"Cox":[130],"sensitivity":[131],"analysis,":[132,232],"onset":[134,222],"was":[135,185,214,223,236,245],"inferior":[138,178,226],"(HR":[140,153],"2.50,":[141],"95%":[142,155,196],"CI":[143,156,197],"1.19\u20135.26;":[144],"0.016),":[147],"not":[149,237,257],"significantly":[150],"1.87,":[154],"0.93\u20133.75;":[157],"0.078).":[160],"Multivariable":[161],"analysis":[162],"identified":[163],"poorer":[164],"ECOG":[165],"performance":[166],"status,":[167],"higher":[168],"direct":[169],"bilirubin,":[170],"lower":[172],"platelet":[173],"count":[174],"OS.":[179],"The":[180],"association":[182,235],"attenuated":[186],"adjustment":[188],"for":[189],"these":[190],"baseline":[191],"factors":[192],"(adjusted":[193],"HR":[194],"1.92,":[195],"0.83\u20134.41;":[198],"0.127).":[201],"can":[203],"occur":[204],"at":[205],"different":[206],"time":[207],"points":[208],"relative":[209],"diagnosis":[212],"adverse":[218],"features.":[220],"unadjusted":[230],"statistically":[238],"significant":[239],"adjustment;":[241],"Peripheral-blood":[242],"frequent":[247],"among":[248],"quantitative":[253],"viral":[254],"loads":[255],"did":[256],"differ":[258],"significantly.":[259],"These":[260],"findings":[261],"describe":[262],"associations":[263],"this":[265],"cohort":[266],"require":[268],"confirmation":[269],"larger":[271],"multicenter":[272],"studies.":[273]},"counts_by_year":[],"updated_date":"2026-11-11T12:16:26.678958","created_date":"2026-08-13T00:00:00"}
