{"id":"https://openalex.org/W7165459110","doi":"https://doi.org/10.5281/zenodo.20775746","title":"Erdheim-Chester Disease Mimicking a Precentral Meningioma: A Case of Rapid Parenchymal Recurrence and Multisystemic Progression","display_name":"Erdheim-Chester Disease Mimicking a Precentral Meningioma: A Case of Rapid Parenchymal Recurrence and Multisystemic Progression","publication_year":2026,"publication_date":"2026-02-28","ids":{"openalex":"https://openalex.org/W7165459110","doi":"https://doi.org/10.5281/zenodo.20775746"},"language":"en","primary_location":{"id":"doi:10.5281/zenodo.20775746","doi":"https://doi.org/10.5281/zenodo.20775746","is_oa":true,"landing_page_url":"https://doi.org/10.5281/zenodo.20775746","pdf_url":null,"source":{"id":"https://openalex.org/S4306400562","display_name":"Zenodo (CERN European Organization for Nuclear Research)","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I67311998","host_organization_name":"European Organization for Nuclear Research","host_organization_lineage":["https://openalex.org/I67311998"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":null,"is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":"JournalArticle"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["datacite"],"open_access":{"is_oa":true,"oa_status":"green","oa_url":"https://doi.org/10.5281/zenodo.20775746","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5132672315","display_name":"M. Aabid","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210167424","display_name":"H\u00f4pital Militaire Avicenne","ror":"https://ror.org/02cfbec64","country_code":"MA","type":"healthcare","lineage":["https://openalex.org/I4210167424"]}],"countries":["MA"],"is_corresponding":false,"raw_author_name":"M. Aabid","raw_affiliation_strings":["Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco","institution_ids":["https://openalex.org/I4210167424"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5128768966","display_name":"A. El Hassani","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210167424","display_name":"H\u00f4pital Militaire Avicenne","ror":"https://ror.org/02cfbec64","country_code":"MA","type":"healthcare","lineage":["https://openalex.org/I4210167424"]}],"countries":["MA"],"is_corresponding":false,"raw_author_name":"A. El Hassani","raw_affiliation_strings":["Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco","institution_ids":["https://openalex.org/I4210167424"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5128754884","display_name":"S. Belhend","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210167424","display_name":"H\u00f4pital Militaire Avicenne","ror":"https://ror.org/02cfbec64","country_code":"MA","type":"healthcare","lineage":["https://openalex.org/I4210167424"]}],"countries":["MA"],"is_corresponding":false,"raw_author_name":"S. Belhend","raw_affiliation_strings":["Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco","institution_ids":["https://openalex.org/I4210167424"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5069538259","display_name":"B. Slioui","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210167424","display_name":"H\u00f4pital Militaire Avicenne","ror":"https://ror.org/02cfbec64","country_code":"MA","type":"healthcare","lineage":["https://openalex.org/I4210167424"]}],"countries":["MA"],"is_corresponding":false,"raw_author_name":"B. Slioui","raw_affiliation_strings":["Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco","institution_ids":["https://openalex.org/I4210167424"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5075007333","display_name":"S. Bellasri","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210167424","display_name":"H\u00f4pital Militaire Avicenne","ror":"https://ror.org/02cfbec64","country_code":"MA","type":"healthcare","lineage":["https://openalex.org/I4210167424"]}],"countries":["MA"],"is_corresponding":false,"raw_author_name":"S. Bellasri","raw_affiliation_strings":["Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco","institution_ids":["https://openalex.org/I4210167424"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5036396309","display_name":"A. Mouhsine","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210167424","display_name":"H\u00f4pital Militaire Avicenne","ror":"https://ror.org/02cfbec64","country_code":"MA","type":"healthcare","lineage":["https://openalex.org/I4210167424"]}],"countries":["MA"],"is_corresponding":false,"raw_author_name":"A. Mouhsine","raw_affiliation_strings":["Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco","institution_ids":["https://openalex.org/I4210167424"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5139027903","display_name":"E. Atmane","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210167424","display_name":"H\u00f4pital Militaire Avicenne","ror":"https://ror.org/02cfbec64","country_code":"MA","type":"healthcare","lineage":["https://openalex.org/I4210167424"]}],"countries":["MA"],"is_corresponding":false,"raw_author_name":"E. Atmane","raw_affiliation_strings":["Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Radiology, Avicenna Military Hospital, Marrakech, Morocco","institution_ids":["https://openalex.org/I4210167424"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":["https://openalex.org/I4210167424"],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":{"value":0.38721579,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11909","display_name":"Histiocytic Disorders and Treatments","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11909","display_name":"Histiocytic Disorders and Treatments","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10975","display_name":"Bone Tumor Diagnosis and Treatments","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2732","display_name":"Orthopedics and Sports Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11571","display_name":"Sarcoidosis and Beryllium Toxicity Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/erdheim-chester-disease","display_name":"Erdheim-Chester disease","score":1.0},{"id":"https://openalex.org/keywords/non-langerhans-cell-histiocytosis","display_name":"non-Langerhans cell histiocytosis","score":0.9330000281333923},{"id":"https://openalex.org/keywords/braf-v600e-mutation","display_name":"BRAF V600E mutation","score":0.9300000071525574},{"id":"https://openalex.org/keywords/thoracic-lesions","display_name":"thoracic lesions","score":0.5770000219345093},{"id":"https://openalex.org/keywords/liver-lesions","display_name":"liver lesions","score":0.8569999933242798},{"id":"https://openalex.org/keywords/cardiac-history","display_name":"cardiac history","score":0.8220000267028809},{"id":"https://openalex.org/keywords/differential-diagnosis","display_name":"differential diagnosis","score":0.6919999718666077},{"id":"https://openalex.org/keywords/unnecessary-surgery","display_name":"unnecessary surgery","score":0.32499998807907104}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9060999751091003},{"id":"https://openalex.org/C126838900","wikidata":"https://www.wikidata.org/wiki/Q77604","display_name":"Radiology","level":1,"score":0.5806000232696533},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.5512999892234802},{"id":"https://openalex.org/C196822366","wikidata":"https://www.wikidata.org/wiki/Q270524","display_name":"Parenchyma","level":2,"score":0.5242000222206116},{"id":"https://openalex.org/C2781156865","wikidata":"https://www.wikidata.org/wiki/Q827023","display_name":"Lesion","level":2,"score":0.5145999789237976},{"id":"https://openalex.org/C2775934546","wikidata":"https://www.wikidata.org/wiki/Q179991","display_name":"Biopsy","level":2,"score":0.4747999906539917},{"id":"https://openalex.org/C2779160599","wikidata":"https://www.wikidata.org/wiki/Q369157","display_name":"Meningioma","level":2,"score":0.4293000102043152},{"id":"https://openalex.org/C2779281540","wikidata":"https://www.wikidata.org/wiki/Q5062122","display_name":"Central nervous system disease","level":2,"score":0.4009000062942505},{"id":"https://openalex.org/C143409427","wikidata":"https://www.wikidata.org/wiki/Q161238","display_name":"Magnetic resonance imaging","level":2,"score":0.38830000162124634},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.37209999561309814},{"id":"https://openalex.org/C2777466421","wikidata":"https://www.wikidata.org/wiki/Q1266890","display_name":"Vascular disease","level":2,"score":0.35929998755455017},{"id":"https://openalex.org/C3020562746","wikidata":"https://www.wikidata.org/wiki/Q7446275","display_name":"Surgical resection","level":2,"score":0.34950000047683716},{"id":"https://openalex.org/C2780801072","wikidata":"https://www.wikidata.org/wiki/Q837512","display_name":"Differential diagnosis","level":2,"score":0.34869998693466187},{"id":"https://openalex.org/C2908871681","wikidata":"https://www.wikidata.org/wiki/Q827023","display_name":"Mass/lesion","level":3,"score":0.3416999876499176},{"id":"https://openalex.org/C2776429142","wikidata":"https://www.wikidata.org/wiki/Q1620189","display_name":"Brain biopsy","level":3,"score":0.3271999955177307},{"id":"https://openalex.org/C2778674544","wikidata":"https://www.wikidata.org/wiki/Q1414805","display_name":"Systemic disease","level":3,"score":0.30970001220703125},{"id":"https://openalex.org/C16568411","wikidata":"https://www.wikidata.org/wiki/Q83042","display_name":"Neurology","level":2,"score":0.29499998688697815},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.29319998621940613},{"id":"https://openalex.org/C2780174970","wikidata":"https://www.wikidata.org/wiki/Q1411740","display_name":"Histiocytosis","level":3,"score":0.289000004529953},{"id":"https://openalex.org/C2778256017","wikidata":"https://www.wikidata.org/wiki/Q3640183","display_name":"Stereotactic biopsy","level":3,"score":0.2825999855995178},{"id":"https://openalex.org/C2780645631","wikidata":"https://www.wikidata.org/wiki/Q671554","display_name":"Stroke (engine)","level":2,"score":0.27309998869895935},{"id":"https://openalex.org/C159110652","wikidata":"https://www.wikidata.org/wiki/Q17078201","display_name":"Resection","level":2,"score":0.26899999380111694},{"id":"https://openalex.org/C2909554025","wikidata":"https://www.wikidata.org/wiki/Q179991","display_name":"Incisional biopsy","level":3,"score":0.251800000667572}],"mesh":[],"locations_count":2,"locations":[{"id":"doi:10.5281/zenodo.20775746","doi":"https://doi.org/10.5281/zenodo.20775746","is_oa":true,"landing_page_url":"https://doi.org/10.5281/zenodo.20775746","pdf_url":null,"source":{"id":"https://openalex.org/S4306400562","display_name":"Zenodo (CERN European Organization for Nuclear Research)","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I67311998","host_organization_name":"European Organization for Nuclear Research","host_organization_lineage":["https://openalex.org/I67311998"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":null,"is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":"JournalArticle"},{"id":"doi:10.5281/zenodo.20775747","doi":"https://doi.org/10.5281/zenodo.20775747","is_oa":true,"landing_page_url":"https://doi.org/10.5281/zenodo.20775747","pdf_url":null,"source":{"id":"https://openalex.org/S4306400562","display_name":"Zenodo (CERN European Organization for Nuclear Research)","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I67311998","host_organization_name":"European Organization for Nuclear Research","host_organization_lineage":["https://openalex.org/I67311998"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":null,"is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":"JournalArticle"}],"best_oa_location":{"id":"doi:10.5281/zenodo.20775746","doi":"https://doi.org/10.5281/zenodo.20775746","is_oa":true,"landing_page_url":"https://doi.org/10.5281/zenodo.20775746","pdf_url":null,"source":{"id":"https://openalex.org/S4306400562","display_name":"Zenodo (CERN European Organization for Nuclear Research)","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I67311998","host_organization_name":"European Organization for Nuclear Research","host_organization_lineage":["https://openalex.org/I67311998"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":null,"is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":"JournalArticle"},"sustainable_development_goals":[{"score":0.9537000060081482,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W7160260665","https://openalex.org/W4409227276","https://openalex.org/W2770752653","https://openalex.org/W7222972650","https://openalex.org/W7204730307","https://openalex.org/W4404881655","https://openalex.org/W4416059595","https://openalex.org/W4410697289","https://openalex.org/W2734968108","https://openalex.org/W4413324185"],"abstract_inverted_index":{"Abstract:":[0],"Erdheim-Chester":[1],"disease":[2],"(ECD)":[3],"is":[4,95],"a":[5,11,28,34,40,57,65,79,87,92,96],"rare":[6],"non-Langerhans":[7],"histiocytosis":[8],"that":[9,86],"remains":[10],"significant":[12],"diagnostic":[13],"challenge,":[14],"particularly":[15],"when":[16],"it":[17],"presents":[18],"with":[19,107],"dural":[20,41,93,118],"involvement.":[21],"We":[22],"describe":[23],"the":[24,54,71,75,108],"clinical":[25,98],"course":[26],"of":[27,74],"50-year-old":[29],"male,":[30],"originally":[31],"treated":[32],"for":[33],"presumed":[35],"precentral":[36],"meningioma":[37],"based":[38],"on":[39],"mass":[42,94],"showing":[43],"intense":[44],"enhancement":[45],"and":[46,62,120],"an":[47],"atypical":[48],"T2-hypointense":[49],"signal.":[50],"Following":[51],"surgical":[52],"resection,":[53],"patient":[55],"experienced":[56],"multisystemic":[58],"flare":[59],"(thoracic,":[60],"hepatic,":[61],"adrenal)":[63],"alongside":[64],"rapid":[66],"multifocal":[67],"parenchymal":[68],"recurrence":[69],"in":[70,91],"brain.":[72],"Biopsy":[73],"thoracic":[76],"lesion":[77],"confirmed":[78],"BRAF":[80],"V600E-mutated":[81],"ECD.":[82],"This":[83],"report":[84],"emphasizes":[85],"\"black\"":[88],"T2":[89],"signal":[90],"major":[97],"red":[99],"flag.":[100],"Radiologists":[101],"should":[102],"systematically":[103],"correlate":[104],"such":[105],"findings":[106],"patient's":[109],"cardiac":[110],"history":[111],"to":[112],"distinguish":[113],"ECD":[114],"from":[115],"more":[116],"common":[117],"tumors":[119],"avoid":[121],"unnecessary":[122],"surgery.":[123]},"counts_by_year":[],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2026-06-21T00:00:00"}
