{"id":"https://openalex.org/W7140080552","doi":"https://doi.org/10.11648/j.ajp.20261201.15","title":"Challenges in the Management of Cystic Fibrosis in Morocco: A Case Report","display_name":"Challenges in the Management of Cystic Fibrosis in Morocco: A Case Report","publication_year":2026,"publication_date":"2026-03-17","ids":{"openalex":"https://openalex.org/W7140080552","doi":"https://doi.org/10.11648/j.ajp.20261201.15"},"language":"en","primary_location":{"id":"doi:10.11648/j.ajp.20261201.15","doi":"https://doi.org/10.11648/j.ajp.20261201.15","is_oa":true,"landing_page_url":"https://doi.org/10.11648/j.ajp.20261201.15","pdf_url":"http://article.sciencepg.com/pdf/j.ajp.20261201.15","source":{"id":"https://openalex.org/S4210203824","display_name":"American Journal of Pediatrics","issn_l":"2472-0887","issn":["2472-0887","2472-0909"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/P4310319272","host_organization_name":"Science Publishing Group","host_organization_lineage":["https://openalex.org/P4310319272"],"host_organization_lineage_names":["Science Publishing Group"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Pediatrics","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"http://article.sciencepg.com/pdf/j.ajp.20261201.15","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5130361214","display_name":"Ibtissam Merroun","orcid":"https://orcid.org/0009-0008-8865-4813","observed_orcids":["https://orcid.org/0009-0008-8865-4813"]},"institutions":[],"countries":[],"is_corresponding":true,"raw_author_name":"Ibtissam Merroun","raw_affiliation_strings":["Pneumology and Allergology Paediatric Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco"],"raw_orcid":"https://orcid.org/0009-0008-8865-4813","affiliations":[{"raw_affiliation_string":"Pneumology and Allergology Paediatric Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5031587159","display_name":"Fatima Zahra Alaoui-Inboui","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Fatima Alaoui-Inboui","raw_affiliation_strings":["Pneumology and Allergology Paediatric Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Pneumology and Allergology Paediatric Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5117618997","display_name":"Othmane Ahmito","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Othmane Ahmito","raw_affiliation_strings":["Pneumology and Allergology Paediatric Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Pneumology and Allergology Paediatric Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5117415588","display_name":"Meriem El Achiwi","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Meriem Achiwi","raw_affiliation_strings":["Pneumology and Allergology Paediatric Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Pneumology and Allergology Paediatric Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5083589936","display_name":"Kamelia Chbani","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Kamelia Chbani","raw_affiliation_strings":["Pediatric Radiology Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Pediatric Radiology Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5039412853","display_name":"B. Slaoui","orcid":"https://orcid.org/0000-0002-8138-8590","observed_orcids":["https://orcid.org/0000-0002-8138-8590"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Bouchra Slaoui","raw_affiliation_strings":["Pneumology and Allergology Paediatric Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco"],"raw_orcid":"https://orcid.org/0000-0002-8138-8590","affiliations":[{"raw_affiliation_string":"Pneumology and Allergology Paediatric Department, Abderrahim Harrouchi Mother and Child Hospital, Casablanca, Morocco","institution_ids":[]}]}],"institutions":[],"countries_distinct_count":0,"institutions_distinct_count":0,"corresponding_author_ids":["https://openalex.org/A5130361214"],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"12","issue":"1","first_page":"34","last_page":"38"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10665","display_name":"Cystic Fibrosis Research Advances","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10665","display_name":"Cystic Fibrosis Research Advances","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10549","display_name":"Neonatal Respiratory Health Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11725","display_name":"Immunodeficiency and Autoimmune Disorders","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/cystic-fibrosis","display_name":"cystic fibrosis","score":0.9980000257492065},{"id":"https://openalex.org/keywords/recurrent-wheezing","display_name":"recurrent wheezing","score":0.9020000100135803},{"id":"https://openalex.org/keywords/persistent-wheeze","display_name":"persistent wheezing","score":0.7590000033378601},{"id":"https://openalex.org/keywords/sweat-test","display_name":"sweat test","score":0.8880000114440918},{"id":"https://openalex.org/keywords/diagnostic-challenges","display_name":"diagnostic challenges","score":0.6039999723434448},{"id":"https://openalex.org/keywords/pancreatic-enzyme-replacement-therapy","display_name":"pancreatic enzyme replacement therapy","score":0.7070000171661377},{"id":"https://openalex.org/keywords/vitamin-supplementation","display_name":"vitamin supplementation","score":0.8299999833106995},{"id":"https://openalex.org/keywords/respiratory-physiotherapy","display_name":"respiratory physiotherapy","score":0.9589999914169312},{"id":"https://openalex.org/keywords/newborn-screening","display_name":"newborn screening","score":0.6209999918937683},{"id":"https://openalex.org/keywords/morocco","display_name":"Morocco","score":0.3059999942779541}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9301000237464905},{"id":"https://openalex.org/C2776938444","wikidata":"https://www.wikidata.org/wiki/Q178194","display_name":"Cystic fibrosis","level":2,"score":0.7840999960899353},{"id":"https://openalex.org/C141983124","wikidata":"https://www.wikidata.org/wiki/Q188008","display_name":"Respiratory distress","level":2,"score":0.5622000098228455},{"id":"https://openalex.org/C2779343474","wikidata":"https://www.wikidata.org/wiki/Q3109175","display_name":"Context (archaeology)","level":2,"score":0.5522000193595886},{"id":"https://openalex.org/C137627325","wikidata":"https://www.wikidata.org/wiki/Q156318","display_name":"Etiology","level":2,"score":0.46000000834465027},{"id":"https://openalex.org/C534529494","wikidata":"https://www.wikidata.org/wiki/Q7891","display_name":"Respiratory system","level":2,"score":0.3806999921798706},{"id":"https://openalex.org/C2776178081","wikidata":"https://www.wikidata.org/wiki/Q3286546","display_name":"Respiratory disease","level":3,"score":0.3709000051021576},{"id":"https://openalex.org/C2781047483","wikidata":"https://www.wikidata.org/wiki/Q1525170","display_name":"Stridor","level":3,"score":0.35019999742507935},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.34380000829696655},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.33320000767707825},{"id":"https://openalex.org/C2777714996","wikidata":"https://www.wikidata.org/wiki/Q7886","display_name":"Lung","level":2,"score":0.3228999972343445},{"id":"https://openalex.org/C177713679","wikidata":"https://www.wikidata.org/wiki/Q679690","display_name":"Intensive care medicine","level":1,"score":0.3183000087738037},{"id":"https://openalex.org/C164705383","wikidata":"https://www.wikidata.org/wiki/Q10379","display_name":"Cardiology","level":1,"score":0.28380000591278076},{"id":"https://openalex.org/C2778721537","wikidata":"https://www.wikidata.org/wiki/Q922640","display_name":"Bronchopulmonary dysplasia","level":4,"score":0.2752000093460083},{"id":"https://openalex.org/C2776042228","wikidata":"https://www.wikidata.org/wiki/Q35869","display_name":"Asthma","level":2,"score":0.272599995136261},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.27070000767707825},{"id":"https://openalex.org/C2779644171","wikidata":"https://www.wikidata.org/wiki/Q13400765","display_name":"Respiratory tract","level":3,"score":0.2700999975204468},{"id":"https://openalex.org/C126838900","wikidata":"https://www.wikidata.org/wiki/Q77604","display_name":"Radiology","level":1,"score":0.2696000039577484},{"id":"https://openalex.org/C105922876","wikidata":"https://www.wikidata.org/wiki/Q1423981","display_name":"Airway","level":2,"score":0.25949999690055847},{"id":"https://openalex.org/C2780643987","wikidata":"https://www.wikidata.org/wiki/Q468414","display_name":"Angiography","level":2,"score":0.25760000944137573},{"id":"https://openalex.org/C2776169613","wikidata":"https://www.wikidata.org/wiki/Q2305910","display_name":"Newborn screening","level":2,"score":0.2556000053882599}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.11648/j.ajp.20261201.15","doi":"https://doi.org/10.11648/j.ajp.20261201.15","is_oa":true,"landing_page_url":"https://doi.org/10.11648/j.ajp.20261201.15","pdf_url":"http://article.sciencepg.com/pdf/j.ajp.20261201.15","source":{"id":"https://openalex.org/S4210203824","display_name":"American Journal of Pediatrics","issn_l":"2472-0887","issn":["2472-0887","2472-0909"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/P4310319272","host_organization_name":"Science Publishing Group","host_organization_lineage":["https://openalex.org/P4310319272"],"host_organization_lineage_names":["Science Publishing Group"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Pediatrics","raw_type":"journal-article"}],"best_oa_location":{"id":"doi:10.11648/j.ajp.20261201.15","doi":"https://doi.org/10.11648/j.ajp.20261201.15","is_oa":true,"landing_page_url":"https://doi.org/10.11648/j.ajp.20261201.15","pdf_url":"http://article.sciencepg.com/pdf/j.ajp.20261201.15","source":{"id":"https://openalex.org/S4210203824","display_name":"American Journal of Pediatrics","issn_l":"2472-0887","issn":["2472-0887","2472-0909"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/P4310319272","host_organization_name":"Science Publishing Group","host_organization_lineage":["https://openalex.org/P4310319272"],"host_organization_lineage_names":["Science Publishing Group"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Pediatrics","raw_type":"journal-article"},"sustainable_development_goals":[{"display_name":"Good health and well-being","score":1.0,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7140080552.pdf","grobid_xml":"https://content.openalex.org/works/W7140080552.grobid-xml"},"referenced_works_count":16,"referenced_works":["https://openalex.org/W113949224","https://openalex.org/W1971558827","https://openalex.org/W1976996051","https://openalex.org/W2044824352","https://openalex.org/W2045909517","https://openalex.org/W2046799830","https://openalex.org/W2059978108","https://openalex.org/W2079697020","https://openalex.org/W2092440322","https://openalex.org/W2126809978","https://openalex.org/W2584373275","https://openalex.org/W2589573357","https://openalex.org/W3214383389","https://openalex.org/W4393098602","https://openalex.org/W4393298033","https://openalex.org/W4402845150"],"related_works":["https://openalex.org/W2325417198","https://openalex.org/W2043117854","https://openalex.org/W2418279055","https://openalex.org/W4410275774","https://openalex.org/W2895358402","https://openalex.org/W4313652329","https://openalex.org/W2314989174","https://openalex.org/W4394818681","https://openalex.org/W4415513814","https://openalex.org/W2283109076"],"abstract_inverted_index":{"Recurrent":[0],"wheezing":[1,14,85,198],"is":[2,23],"common":[3,28],"in":[4,75,114,178,193,199],"infants,":[5],"most":[6],"often":[7],"triggered":[8],"by":[9],"respiratory":[10,95,169],"viral":[11],"infections.":[12],"When":[13],"begins":[15],"early":[16],"and":[17,40,69,86,119,125,129,168,181,185],"persists":[18],"without":[19,88],"symptom-free":[20,89],"intervals,":[21],"it":[22],"crucial":[24],"to":[25,65,182],"first":[26],"exclude":[27],"underlying":[29],"conditions":[30],"such":[31],"as":[32],"gastroesophageal":[33],"reflux":[34],"disease,":[35],"bronchopulmonary":[36],"or":[37],"vascular":[38],"malformations,":[39],"decompensated":[41],"cardiac":[42],"disease.":[43],"Once":[44],"these":[45],"etiologies":[46],"have":[47],"been":[48],"ruled":[49],"out,":[50],"less":[51],"frequent":[52],"disorders\u2014most":[53],"notably":[54],"cystic":[55,73,188],"fibrosis\u2014should":[56],"be":[57,191],"considered.":[58],"Through":[59],"this":[60],"case":[61,195],"report,":[62],"we":[63],"aim":[64],"highlight":[66],"the":[67,115,120,172],"diagnostic":[68],"management":[70],"challenges":[71],"of":[72,174,196],"fibrosis":[74,189],"our":[76,179],"setting.":[77],"A":[78,140],"4-month-old":[79],"infant":[80],"was":[81],"hospitalized":[82],"for":[83],"recurrent":[84],"dyspnea":[87],"intervals.":[90],"Clinical":[91],"examination":[92],"revealed":[93],"severe":[94,184],"distress":[96],"with":[97,101,160],"diffuse":[98],"wheezing,":[99],"along":[100],"growth":[102],"faltering":[103],"(\u20133":[104],"SD).":[105],"Chest":[106],"X-ray":[107],"demonstrated":[108],"perihilar":[109],"atelectasis,":[110],"bronchial":[111],"wall":[112],"thickening":[113],"left":[116],"lower":[117],"lobe":[118],"right":[121],"apical":[122],"basal":[123],"segment,":[124],"left-sided":[126],"thoracic":[127],"hyperinflation":[128],"chest":[130],"CT":[131],"angiography":[132],"showed":[133,153],"bilateral":[134],"pneumonia.":[135],"Immunological":[136],"investigations":[137],"were":[138],"unremarkable.":[139],"sweat":[141],"chloride":[142,149],"test,":[143],"performed":[144],"twice,":[145],"confirmed":[146],"markedly":[147],"elevated":[148],"concentrations.":[150],"The":[151],"patient":[152],"a":[154],"favorable":[155],"clinical":[156],"evolution":[157],"following":[158],"treatment":[159],"antibiotic":[161],"therapy,":[162],"pancreatic":[163],"enzyme":[164],"replacement,":[165],"vitamin":[166],"supplementation,":[167],"physiotherapy.":[170],"In":[171],"absence":[173],"systematic":[175],"neonatal":[176],"screening":[177],"context":[180],"prevent":[183],"fatal":[186],"complications,":[187],"should":[190],"considered":[192],"any":[194],"persistent":[197],"an":[200],"infant.":[201]},"counts_by_year":[],"updated_date":"2026-10-12T09:40:04.860316","created_date":"2026-03-24T00:00:00"}
