{"id":"https://openalex.org/W7127045659","doi":"https://doi.org/10.3329/jpsb.v13i1.87412","title":"Mayer-Rokitansky-K\u00fcster-Hauser syndrome: Evaluating how and to what extend management is essential","display_name":"Mayer-Rokitansky-K\u00fcster-Hauser syndrome: Evaluating how and to what extend management is essential","publication_year":2026,"publication_date":"2026-01-31","ids":{"openalex":"https://openalex.org/W7127045659","doi":"https://doi.org/10.3329/jpsb.v13i1.87412"},"language":"en","primary_location":{"id":"doi:10.3329/jpsb.v13i1.87412","doi":"https://doi.org/10.3329/jpsb.v13i1.87412","is_oa":true,"landing_page_url":"https://doi.org/10.3329/jpsb.v13i1.87412","pdf_url":"https://www.banglajol.info/index.php/JPSB/article/download/87412/56827","source":{"id":"https://openalex.org/S2764658643","display_name":"Journal of Paediatric Surgeons of Bangladesh","issn_l":"2077-7469","issn":["2077-7469","2309-1320"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Paediatric Surgeons of Bangladesh","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://www.banglajol.info/index.php/JPSB/article/download/87412/56827","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5124720502","display_name":"Md Nazrul Islam","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I201969901","display_name":"Bangladesh Medical University","ror":"https://ror.org/042mrsz23","country_code":"BD","type":"education","lineage":["https://openalex.org/I201969901"]}],"countries":["BD"],"is_corresponding":false,"raw_author_name":"Md Nazrul Islam","raw_affiliation_strings":["Consultant, Department of Pediatric Surgery Bangabandhu Sheikh Mujib Medical University"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Consultant, Department of Pediatric Surgery Bangabandhu Sheikh Mujib Medical University","institution_ids":["https://openalex.org/I201969901"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5124743780","display_name":"Talima Akter","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4400600910","display_name":"Holy Family Red Crescent Medical College","ror":"https://ror.org/05ayzqh10","country_code":"BD","type":"education","lineage":["https://openalex.org/I4400600910"]}],"countries":["BD"],"is_corresponding":false,"raw_author_name":"Talima Akter","raw_affiliation_strings":["Assistant Professor, Department of Microbiology Holy Family Red Crescent Medical College"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Assistant Professor, Department of Microbiology Holy Family Red Crescent Medical College","institution_ids":["https://openalex.org/I4400600910"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5124705714","display_name":"Pravin Chaudhary","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I201969901","display_name":"Bangladesh Medical University","ror":"https://ror.org/042mrsz23","country_code":"BD","type":"education","lineage":["https://openalex.org/I201969901"]}],"countries":["BD"],"is_corresponding":false,"raw_author_name":"Pravin Chaudhary","raw_affiliation_strings":["Resident, Department of Pediatric Surgery Bangabandhu Sheikh Mujib Medical University"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Resident, Department of Pediatric Surgery Bangabandhu Sheikh Mujib Medical University","institution_ids":["https://openalex.org/I201969901"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5124696672","display_name":"Md Ruhul Amin","orcid":"https://orcid.org/0000-0002-9758-3438","observed_orcids":["https://orcid.org/0000-0002-9758-3438"]},"institutions":[{"id":"https://openalex.org/I201969901","display_name":"Bangladesh Medical University","ror":"https://ror.org/042mrsz23","country_code":"BD","type":"education","lineage":["https://openalex.org/I201969901"]}],"countries":["BD"],"is_corresponding":false,"raw_author_name":"Md Ruhul Amin","raw_affiliation_strings":["Professor, Department of Pediatric Surgery Bangabandhu Sheikh Mujib Medical University"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Professor, Department of Pediatric Surgery Bangabandhu Sheikh Mujib Medical University","institution_ids":["https://openalex.org/I201969901"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5124729581","display_name":"A S M Shahidul Hossain","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I201969901","display_name":"Bangladesh Medical University","ror":"https://ror.org/042mrsz23","country_code":"BD","type":"education","lineage":["https://openalex.org/I201969901"]}],"countries":["BD"],"is_corresponding":false,"raw_author_name":"A S M Shahidul Hossain","raw_affiliation_strings":["Consultant Radiology & Imaging department Bangabandhu Sheikh Mujib Medical University"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Consultant Radiology & Imaging department Bangabandhu Sheikh Mujib Medical University","institution_ids":["https://openalex.org/I201969901"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5124707032","display_name":"Mohammad Mahabubul Alam","orcid":"https://orcid.org/0000-0002-8662-2630","observed_orcids":["https://orcid.org/0000-0002-8662-2630"]},"institutions":[{"id":"https://openalex.org/I2799421741","display_name":"Comilla Medical College","ror":"https://ror.org/03q8sfx86","country_code":"BD","type":"healthcare","lineage":["https://openalex.org/I2799421741"]}],"countries":["BD"],"is_corresponding":false,"raw_author_name":"Mohammad Mahabubul Alam","raw_affiliation_strings":["Assistant Professor, Department of Pediatric Surgery, Cumilla Medical College, Cumilla"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Assistant Professor, Department of Pediatric Surgery, Cumilla Medical College, Cumilla","institution_ids":["https://openalex.org/I2799421741"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":3,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":"21","last_page":"24"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11589","display_name":"Gynecological conditions and treatments","score":0.9940999746322632,"subfield":{"id":"https://openalex.org/subfields/2729","display_name":"Obstetrics and Gynecology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11589","display_name":"Gynecological conditions and treatments","score":0.9940999746322632,"subfield":{"id":"https://openalex.org/subfields/2729","display_name":"Obstetrics and Gynecology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11956","display_name":"Sexual Differentiation and Disorders","score":0.00559999980032444,"subfield":{"id":"https://openalex.org/subfields/2712","display_name":"Endocrinology, Diabetes and Metabolism"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11815","display_name":"Urological Disorders and Treatments","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2748","display_name":"Urology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/mayer-rokitansky-kuster-hauser-syndrome","display_name":"Mayer-Rokitansky-Kuster-Hauser syndrome","score":0.9959999918937683},{"id":"https://openalex.org/keywords/primary-amenorrhea","display_name":"primary amenorrhea","score":0.9789999723434448},{"id":"https://openalex.org/keywords/mullerian-anomalies","display_name":"M\u00fcllerian duct anomalies","score":0.7760000228881836},{"id":"https://openalex.org/keywords/surgical-management","display_name":"surgical management","score":0.652999997138977},{"id":"https://openalex.org/keywords/multidisciplinary-management","display_name":"multidisciplinary management","score":0.7080000042915344},{"id":"https://openalex.org/keywords/reproductive-counseling","display_name":"reproductive counseling","score":0.5},{"id":"https://openalex.org/keywords/adolescent-patient","display_name":"adolescent patient","score":0.492000013589859}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.7867000102996826},{"id":"https://openalex.org/C23131810","wikidata":"https://www.wikidata.org/wiki/Q818574","display_name":"Observational study","level":2,"score":0.6312999725341797},{"id":"https://openalex.org/C2911074991","wikidata":"https://www.wikidata.org/wiki/Q1473749","display_name":"Mayer-Rokitansky-Kuster-Hauser Syndrome","level":3,"score":0.6017000079154968},{"id":"https://openalex.org/C2778368355","wikidata":"https://www.wikidata.org/wiki/Q5488","display_name":"Aplasia","level":2,"score":0.5608999729156494},{"id":"https://openalex.org/C2777744392","wikidata":"https://www.wikidata.org/wiki/Q5880","display_name":"Vagina","level":2,"score":0.5410000085830688},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.527999997138977},{"id":"https://openalex.org/C188816634","wikidata":"https://www.wikidata.org/wiki/Q2113324","display_name":"Prospective cohort study","level":2,"score":0.41780000925064087},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.38199999928474426},{"id":"https://openalex.org/C2984752397","wikidata":"https://www.wikidata.org/wiki/Q3259956","display_name":"Primary care","level":2,"score":0.367900013923645},{"id":"https://openalex.org/C61434518","wikidata":"https://www.wikidata.org/wiki/Q932510","display_name":"General surgery","level":1,"score":0.36489999294281006},{"id":"https://openalex.org/C29456083","wikidata":"https://www.wikidata.org/wiki/Q1221899","display_name":"Gynecology","level":1,"score":0.35850000381469727},{"id":"https://openalex.org/C518429986","wikidata":"https://www.wikidata.org/wiki/Q964401","display_name":"Fertility","level":3,"score":0.33009999990463257},{"id":"https://openalex.org/C2779066055","wikidata":"https://www.wikidata.org/wiki/Q9612","display_name":"Uterus","level":2,"score":0.2854999899864197},{"id":"https://openalex.org/C205545832","wikidata":"https://www.wikidata.org/wiki/Q17156455","display_name":"Young adult","level":2,"score":0.2721000015735626},{"id":"https://openalex.org/C2986834420","wikidata":"https://www.wikidata.org/wiki/Q5932254","display_name":"Age groups","level":2,"score":0.2630000114440918},{"id":"https://openalex.org/C2780423258","wikidata":"https://www.wikidata.org/wiki/Q1430816","display_name":"Pediatric surgery","level":2,"score":0.25130000710487366}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.3329/jpsb.v13i1.87412","doi":"https://doi.org/10.3329/jpsb.v13i1.87412","is_oa":true,"landing_page_url":"https://doi.org/10.3329/jpsb.v13i1.87412","pdf_url":"https://www.banglajol.info/index.php/JPSB/article/download/87412/56827","source":{"id":"https://openalex.org/S2764658643","display_name":"Journal of Paediatric Surgeons of Bangladesh","issn_l":"2077-7469","issn":["2077-7469","2309-1320"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Paediatric Surgeons of Bangladesh","raw_type":"journal-article"}],"best_oa_location":{"id":"doi:10.3329/jpsb.v13i1.87412","doi":"https://doi.org/10.3329/jpsb.v13i1.87412","is_oa":true,"landing_page_url":"https://doi.org/10.3329/jpsb.v13i1.87412","pdf_url":"https://www.banglajol.info/index.php/JPSB/article/download/87412/56827","source":{"id":"https://openalex.org/S2764658643","display_name":"Journal of Paediatric Surgeons of Bangladesh","issn_l":"2077-7469","issn":["2077-7469","2309-1320"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Paediatric Surgeons of Bangladesh","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":1.0}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W7127045659.pdf","grobid_xml":"https://content.openalex.org/works/W7127045659.grobid-xml"},"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W4361802075","https://openalex.org/W4392125636","https://openalex.org/W1989147216","https://openalex.org/W4206068926","https://openalex.org/W4319811927","https://openalex.org/W4400576863","https://openalex.org/W2903169933","https://openalex.org/W2054880415","https://openalex.org/W2080203083","https://openalex.org/W3104724718"],"abstract_inverted_index":{"Mayer-Rokitansky-K\u00fcster-Hauser":[0],"(MRKH)":[1],"syndrome,":[2],"also":[3],"referred":[4],"to":[5,51,63,83,90,129],"as":[6],"M\u00fcllerian":[7,55],"agenesis,":[8],"is":[9,19,96,222,228],"the":[10,27,31,35,52,231],"second":[11],"most":[12],"common":[13],"cause":[14],"of":[15,26,34,54,74,108,110,210,215,220,247,250],"primary":[16,84],"amenorrhea.":[17,85],"It":[18],"characterized":[20],"by":[21,154],"congenital":[22],"aplasia":[23],"or":[24,70],"absence":[25,73],"uterus,":[28],"cervix,":[29,68],"and":[30,98,114,150,159,198,212,243],"upper":[32],"2/3":[33],"vagina":[36],"in":[37,60,124,224,238],"phenotypically":[38],"normal":[39],"46,":[40],"XX":[41],"females.":[42],"Embryological":[43],"evidence":[44],"shows":[45],"that":[46],"MRKH":[47,111,139,148,193,201,217],"syndrome":[48,149,194,202],"occurs":[49],"due":[50,82],"failure":[53],"ducts":[56],"devel":[57],"opment,":[58],"which":[59],"turn":[61],"leads":[62],"a":[64],"poorly":[65],"developed":[66],"vagina,":[67],"uterus":[69],"even":[71],"an":[72],"either":[75],"organ.":[76],"Usually":[77],"patients":[78,135,144,167,173,195],"present":[79],"at":[80],"puberty":[81],"So,":[86],"mostly":[87],"they":[88],"visit":[89],"gynecological":[91],"department":[92],"but":[93,233],"manage":[94],"ment":[95],"multi-model":[97],"multi-disciplinary.":[99],"In":[100],"this":[101],"study,":[102],"we":[103],"have":[104],"presented":[105],"our":[106],"experience":[107],"management":[109],"syndrome.":[112,140,218],"Materials":[113],"methods:":[115],"A":[116,132,141],"prospective":[117],"observational":[118],"study":[119],"was":[120,188],"being":[121],"carried":[122],"out":[123],"BSMMU":[125],"from":[126,183],"Oct.":[127,130],"2018":[128],"2021.":[131],"total":[133,142,165],"27":[134,143,166],"were":[136,145,168,174,196,203],"diagnosed":[137,146],"with":[138,147],"evaluated":[151,169],"for":[152,161,240],"classification":[153],"X-ray,":[155],"ultrasonography,":[156],"hormonal":[157],"evaluation":[158],"MRI":[160],"selected":[162],"cases.":[163],"Results:A":[164],"among":[170],"them":[171],"9":[172],"operated":[175],"under":[176],"paediatric":[177],"surgery":[178],"department.":[179],"Patients":[180],"age":[181,187],"ranged":[182],"13-18":[184],"years,":[185],"mean":[186],"15.1":[189],"years.":[190],"Type":[191,199],"I":[192],"11":[197],"II":[200],"16.":[204],"We":[205],"had":[206],"treated":[207],"4":[208],"cases":[209,214],"Type-I":[211],"5":[213],"Type-II":[216],"Conclusion:Management":[219],"MRKHS":[221],"challenge":[223],"Bangladesh":[225,251],"perspective.":[226],"Surgery":[227],"not":[229],"only":[230],"treatment":[232],"main":[234],"focus":[235],"should":[236],"be":[237],"counselling":[239],"next":[241],"conjugal":[242],"social":[244],"life.":[245],"Journal":[246],"Paediatric":[248],"Surgeons":[249],"(2022)":[252],"Vol.":[253],"13":[254],"(1":[255],"&":[256],"2):":[257],"21-24":[258]},"counts_by_year":[],"updated_date":"2026-10-28T10:33:24.094632","created_date":"2026-02-03T00:00:00"}