{"id":"https://openalex.org/W45630943","doi":null,"title":"Anesthetic management of a patient with Alagille's syndrome undergoing living donor liver transplantation without blood transfusion.","display_name":"Anesthetic management of a patient with Alagille's syndrome undergoing living donor liver transplantation without blood transfusion.","publication_year":2004,"publication_date":"2004-06-01","ids":{"openalex":"https://openalex.org/W45630943","mag":"45630943","pmid":"https://pubmed.ncbi.nlm.nih.gov/15455546"},"language":"en","primary_location":{"id":"pmid:15455546","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/15455546","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Chang Gung medical journal","raw_type":"Case Reports"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5111695555","display_name":"Kwok-Wai Cheng","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I3020100970","display_name":"Chang Gung Memorial Hospital","ror":"https://ror.org/02verss31","country_code":"TW","type":"healthcare","lineage":["https://openalex.org/I3020100970"]},{"id":"https://openalex.org/I4210093821","display_name":"Kaohsiung Chang Gung Memorial Hospital","ror":"https://ror.org/00k194y12","country_code":"TW","type":"healthcare","lineage":["https://openalex.org/I4210093821"]}],"countries":["TW"],"is_corresponding":false,"raw_author_name":"Kwok-Wai Cheng","raw_affiliation_strings":["Department of Anesthesiology, Chang Gung Memorial Hospital, 123, Dabi Road, Niaosung Shiang, Kaohsiung, Taiwan 833, ROC"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Anesthesiology, Chang Gung Memorial Hospital, 123, Dabi Road, Niaosung Shiang, Kaohsiung, Taiwan 833, ROC","institution_ids":["https://openalex.org/I3020100970","https://openalex.org/I4210093821"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5053900926","display_name":"Jia-Jung Huang","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Jia-Jung Huang","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5048698351","display_name":"Chih\u2010Hsien Wang","orcid":"https://orcid.org/0000-0003-3214-6867","observed_orcids":["https://orcid.org/0000-0003-3214-6867"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Chih-Hsien Wang","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5111371940","display_name":"Chao\u2010Long Chen","orcid":"https://orcid.org/0000-0003-0566-9312","observed_orcids":["https://orcid.org/0000-0003-0566-9312"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Chao-Long Chen","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5035332476","display_name":"Bruno Jawan","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Bruno Jawan","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.716,"has_fulltext":false,"cited_by_count":13,"citation_normalized_percentile":{"value":0.7153911,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":87,"max":96},"biblio":{"volume":"27","issue":"6","first_page":"449","last_page":"53"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10999","display_name":"Organ Transplantation Techniques and Outcomes","score":0.6104000210762024,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10999","display_name":"Organ Transplantation Techniques and Outcomes","score":0.6104000210762024,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12460","display_name":"Pediatric Hepatobiliary Diseases and Treatments","score":0.2890999913215637,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10436","display_name":"Anesthesia and Sedative Agents","score":0.03620000183582306,"subfield":{"id":"https://openalex.org/subfields/2703","display_name":"Anesthesiology and Pain Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/living-donor-liver-transplantation","display_name":"living donor liver transplantation","score":0.9399999976158142},{"id":"https://openalex.org/keywords/anesthetic-management","display_name":"anesthetic management","score":0.8600000143051147},{"id":"https://openalex.org/keywords/anemia","display_name":"anemia","score":0.621999979019165},{"id":"https://openalex.org/keywords/pediatric-patients","display_name":"pediatric patients","score":0.6019999980926514},{"id":"https://openalex.org/keywords/aortic-stenosis","display_name":"aortic stenosis","score":0.7860000133514404},{"id":"https://openalex.org/keywords/pulmonary-artery-stenosis","display_name":"pulmonary artery stenosis","score":0.972000002861023},{"id":"https://openalex.org/keywords/albumin-infusion","display_name":"albumin infusion","score":0.46000000834465027},{"id":"https://openalex.org/keywords/central-venous-pressure","display_name":"central venous pressure","score":0.7409999966621399},{"id":"https://openalex.org/keywords/normothermia","display_name":"normothermia","score":0.6579999923706055},{"id":"https://openalex.org/keywords/hemodynamic-stability","display_name":"hemodynamic stability","score":0.5320000052452087},{"id":"https://openalex.org/keywords/chronic-cholestasis","display_name":"chronic cholestasis","score":0.6990000009536743}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9842798113822937},{"id":"https://openalex.org/C2780971011","wikidata":"https://www.wikidata.org/wiki/Q1544408","display_name":"Alagille syndrome","level":3,"score":0.6873621940612793},{"id":"https://openalex.org/C2779609443","wikidata":"https://www.wikidata.org/wiki/Q1368191","display_name":"Liver transplantation","level":3,"score":0.5831797122955322},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.5393175482749939},{"id":"https://openalex.org/C2780014101","wikidata":"https://www.wikidata.org/wiki/Q183605","display_name":"Blood transfusion","level":2,"score":0.5188361406326294},{"id":"https://openalex.org/C42219234","wikidata":"https://www.wikidata.org/wiki/Q131130","display_name":"Anesthesia","level":1,"score":0.4916444420814514},{"id":"https://openalex.org/C178853913","wikidata":"https://www.wikidata.org/wiki/Q1642137","display_name":"Hemodynamics","level":2,"score":0.4803089499473572},{"id":"https://openalex.org/C2780496750","wikidata":"https://www.wikidata.org/wiki/Q193889","display_name":"Ascites","level":2,"score":0.47366151213645935},{"id":"https://openalex.org/C2911091166","wikidata":"https://www.wikidata.org/wiki/Q106419912","display_name":"Transplantation","level":2,"score":0.4558202028274536},{"id":"https://openalex.org/C2779243279","wikidata":"https://www.wikidata.org/wiki/Q659033","display_name":"Biliary atresia","level":4,"score":0.42236456274986267},{"id":"https://openalex.org/C2777728312","wikidata":"https://www.wikidata.org/wiki/Q7232210","display_name":"Portopulmonary hypertension","level":4,"score":0.4205438196659088},{"id":"https://openalex.org/C2780007028","wikidata":"https://www.wikidata.org/wiki/Q2343082","display_name":"Stenosis","level":2,"score":0.4125465750694275},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.24652734398841858},{"id":"https://openalex.org/C164705383","wikidata":"https://www.wikidata.org/wiki/Q10379","display_name":"Cardiology","level":1,"score":0.23728087544441223},{"id":"https://openalex.org/C2778593092","wikidata":"https://www.wikidata.org/wiki/Q1075923","display_name":"Cholestasis","level":2,"score":0.2279193103313446}],"mesh":[{"descriptor_ui":"D000758","descriptor_name":"Anesthesia","qualifier_ui":"Q000379","qualifier_name":"methods","is_major_topic":true},{"descriptor_ui":"D001803","descriptor_name":"Blood Transfusion","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true},{"descriptor_ui":"D002675","descriptor_name":"Child, Preschool","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D016031","descriptor_name":"Liver Transplantation","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true},{"descriptor_ui":"D016738","descriptor_name":"Alagille Syndrome","qualifier_ui":"Q000601","qualifier_name":"surgery","is_major_topic":true},{"descriptor_ui":"D019520","descriptor_name":"Living Donors","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true}],"locations_count":2,"locations":[{"id":"pmid:15455546","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/15455546","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Chang Gung medical journal","raw_type":"Case Reports"},{"id":"mag:45630943","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/15455546","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":"PubMed","raw_type":null}],"best_oa_location":null,"sustainable_development_goals":[{"score":1.0,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":18,"referenced_works":["https://openalex.org/W10822334","https://openalex.org/W60562296","https://openalex.org/W1573504947","https://openalex.org/W1987170442","https://openalex.org/W2005642726","https://openalex.org/W2024998938","https://openalex.org/W2027355176","https://openalex.org/W2036389645","https://openalex.org/W2040947899","https://openalex.org/W2049004325","https://openalex.org/W2049948540","https://openalex.org/W2054114450","https://openalex.org/W2062074309","https://openalex.org/W2082822767","https://openalex.org/W2117031212","https://openalex.org/W2140748591","https://openalex.org/W2176529779","https://openalex.org/W2418488748"],"related_works":["https://openalex.org/W4283374570","https://openalex.org/W7096715620","https://openalex.org/W2586322635","https://openalex.org/W3092105765","https://openalex.org/W2352958177","https://openalex.org/W2149172036","https://openalex.org/W2977823896","https://openalex.org/W4402796936","https://openalex.org/W2036389645","https://openalex.org/W5628203"],"abstract_inverted_index":{"Alagille's":[0],"syndrome":[1],"(AGS),":[2],"which":[3],"has":[4],"five":[5],"main":[6],"characteristics":[7],"including":[8],"chronic":[9],"cholestasis;":[10],"typical":[11],"peculiar":[12],"facies;":[13],"posterior":[14],"embryotoxon;":[15],"butterfly-like":[16],"vertebral-arch":[17],"defects;":[18],"and":[19,56,61,90,100,107,117],"cardiovascular":[20,88],"malformations,":[21],"is":[22],"rarely":[23],"seen":[24],"in":[25,28],"Taiwan,":[26],"especially":[27],"a":[29,40,50,135],"liver":[30,70,169],"transplantation":[31,71],"setting.":[32],"We":[33],"present":[34],"the":[35,87,121,143,155,164,167],"successful":[36,79],"anesthetic":[37,80],"management":[38,81],"of":[39,53,78,86,93,166],"3-year-11-month-old":[41],"boy":[42],"with":[43,49,114],"AGS.":[44],"The":[45,75],"patient":[46,153],"was":[47,132,146],"anemic":[48],"preoperative":[51],"hemoglobin":[52,136],"9.1":[54],"g/dl":[55],"had":[57],"mild":[58,62],"aortic":[59],"stenosis":[60],"pulmonary":[63],"artery":[64],"stenosis.":[65],"He":[66],"underwent":[67],"living":[68],"donor":[69],"without":[72],"blood":[73,104,130],"transfusion.":[74],"key":[76],"points":[77],"included":[82],"complete":[83],"pre-operative":[84],"evaluation":[85],"system,":[89],"intra-operative":[91],"maintenance":[92],"normothermia,":[94],"normal":[95,98],"ionized":[96],"calcium,":[97],"pH":[99],"stable":[101,150],"hemodynamics.":[102,151],"Surgical":[103],"loss,":[105],"ascites":[106],"intraoperative":[108],"transudate":[109],"loss":[110],"were":[111],"primarily":[112],"replaced":[113],"5%":[115],"albumin":[116],"crystalloids":[118],"to":[119,148,162],"maintain":[120,149],"central":[122],"venous":[123],"pressure":[124],"around":[125],"10":[126],"cm":[127],"H2O.":[128],"No":[129],"transfusion":[131],"given":[133],"for":[134],"level":[137],"higher":[138],"than":[139],"6-7":[140],"g/dl,":[141],"but":[142],"intravascular":[144],"volume":[145],"sufficient":[147],"Our":[152],"tolerated":[154],"anemia":[156],"well,":[157],"it":[158],"did":[159],"not":[160],"seem":[161],"affect":[163],"recovery":[165],"new":[168],"allograft":[170],"postoperatively.":[171]},"counts_by_year":[{"year":2022,"cited_by_count":3},{"year":2021,"cited_by_count":1},{"year":2020,"cited_by_count":1},{"year":2018,"cited_by_count":2},{"year":2014,"cited_by_count":1},{"year":2012,"cited_by_count":1}],"updated_date":"2026-11-03T10:50:19.383937","created_date":"2016-06-24T00:00:00"}
