{"id":"https://openalex.org/W4416634554","doi":"https://doi.org/10.1183/13993003.congress-2025.pa1920","title":"Epidemiology of ILD-PH in France: Insights from the French National Health Data System","display_name":"Epidemiology of ILD-PH in France: Insights from the French National Health Data System","publication_year":2025,"publication_date":"2025-09-27","ids":{"openalex":"https://openalex.org/W4416634554","doi":"https://doi.org/10.1183/13993003.congress-2025.pa1920"},"language":"en","primary_location":{"id":"doi:10.1183/13993003.congress-2025.pa1920","doi":"https://doi.org/10.1183/13993003.congress-2025.pa1920","is_oa":false,"landing_page_url":"https://doi.org/10.1183/13993003.congress-2025.pa1920","pdf_url":null,"source":{"id":"https://openalex.org/S4210207896","display_name":"European Respiratory Journal","issn_l":"0903-1936","issn":["0903-1936","1399-3003"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-class-a","anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310317833","host_organization_name":"European Respiratory Society","host_organization_lineage":["https://openalex.org/P4310317833"],"host_organization_lineage_names":["European Respiratory Society"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pulmonary hypertension","raw_type":"proceedings-article"},"volume":null,"type":"conference-abstract","is_traditional":false,"indexed_in":["crossref"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5062669039","display_name":"O. Sitbon","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4210162942","display_name":"Bic\u00eatre Hospital","ror":"https://ror.org/05c9p1x46","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159","https://openalex.org/I4210162942","https://openalex.org/I4405259118"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Olivie Sitbon","raw_affiliation_strings":["1H\u00f4pital Bic\u00eatre, AP-HP, Paris, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"1H\u00f4pital Bic\u00eatre, AP-HP, Paris, France","institution_ids":["https://openalex.org/I4210097159","https://openalex.org/I4210162942"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5014703126","display_name":"Vincent Cottin","orcid":"https://orcid.org/0000-0002-5591-0955","observed_orcids":["https://orcid.org/0000-0002-5591-0955"]},"institutions":[{"id":"https://openalex.org/I4210100596","display_name":"Hospices Civils de Lyon","ror":"https://ror.org/01502ca60","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210100596"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Vincent Cottin","raw_affiliation_strings":["2CHU of Lyon HCL, Lyon, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"2CHU of Lyon HCL, Lyon, France","institution_ids":["https://openalex.org/I4210100596"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5001916649","display_name":"Aur\u00e9lie Chekroun Martinot","orcid":"https://orcid.org/0009-0003-1556-3949","observed_orcids":["https://orcid.org/0009-0003-1556-3949"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Aurelie Chekroun Martinot","raw_affiliation_strings":["3Alira Heal, Paris, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"3Alira Heal, Paris, France","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5055014811","display_name":"N. Petrica","orcid":"https://orcid.org/0009-0007-9372-3687","observed_orcids":["https://orcid.org/0009-0007-9372-3687"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Nicoleta Petrica","raw_affiliation_strings":["4Alira Health, Paris, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"4Alira Health, Paris, France","institution_ids":[]}]},{"author_position":"middle","author":{"id":null,"display_name":"Diego Funes","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Diego Funes","raw_affiliation_strings":["5Ferrer, Barcelona, Spain"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"5Ferrer, Barcelona, Spain","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5049301529","display_name":"Gabriela Bacchini Jeanneret","orcid":"https://orcid.org/0000-0003-3923-3656","observed_orcids":["https://orcid.org/0000-0003-3923-3656"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Gabriela Bacchini Jeanneret","raw_affiliation_strings":["5Ferrer, Barcelona, Spain"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"5Ferrer, Barcelona, Spain","institution_ids":[]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":3,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":null,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":null,"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":"PA1920","last_page":"PA1920"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10728","display_name":"Pulmonary Hypertension Research and Treatments","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10728","display_name":"Pulmonary Hypertension Research and Treatments","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10870","display_name":"Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis","score":0.0003000000142492354,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11330","display_name":"Systemic Sclerosis and Related Diseases","score":9.999999747378752e-05,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/prevalence","display_name":"prevalence","score":0.7419999837875366},{"id":"https://openalex.org/keywords/incidence","display_name":"incidence","score":1.0},{"id":"https://openalex.org/keywords/right-heart-catheterization","display_name":"right heart catheterization","score":0.9829999804496765},{"id":"https://openalex.org/keywords/icd-10-coding","display_name":"ICD-10 coding","score":0.6439999938011169}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.842199981212616},{"id":"https://openalex.org/C107130276","wikidata":"https://www.wikidata.org/wiki/Q133805","display_name":"Epidemiology","level":2,"score":0.8147000074386597},{"id":"https://openalex.org/C61511704","wikidata":"https://www.wikidata.org/wiki/Q1671857","display_name":"Incidence (geometry)","level":2,"score":0.7330999970436096},{"id":"https://openalex.org/C45827449","wikidata":"https://www.wikidata.org/wiki/Q5270338","display_name":"Diagnosis code","level":3,"score":0.5220999717712402},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.5145000219345093},{"id":"https://openalex.org/C2983914783","wikidata":"https://www.wikidata.org/wiki/Q3286546","display_name":"Lung disease","level":3,"score":0.47279998660087585},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.44269999861717224},{"id":"https://openalex.org/C534262118","wikidata":"https://www.wikidata.org/wiki/Q177719","display_name":"Medical diagnosis","level":2,"score":0.4390000104904175},{"id":"https://openalex.org/C138816342","wikidata":"https://www.wikidata.org/wiki/Q189603","display_name":"Public health","level":2,"score":0.40470001101493835},{"id":"https://openalex.org/C2777543607","wikidata":"https://www.wikidata.org/wiki/Q1153419","display_name":"Interstitial lung disease","level":3,"score":0.39899998903274536},{"id":"https://openalex.org/C81182388","wikidata":"https://www.wikidata.org/wiki/Q353963","display_name":"Complication","level":2,"score":0.3871999979019165},{"id":"https://openalex.org/C160735492","wikidata":"https://www.wikidata.org/wiki/Q31207","display_name":"Health care","level":2,"score":0.3749000132083893},{"id":"https://openalex.org/C3017977704","wikidata":"https://www.wikidata.org/wiki/Q18745135","display_name":"Health data","level":3,"score":0.3732999861240387},{"id":"https://openalex.org/C149923435","wikidata":"https://www.wikidata.org/wiki/Q37732","display_name":"Demography","level":1,"score":0.35109999775886536},{"id":"https://openalex.org/C2988170871","wikidata":"https://www.wikidata.org/wiki/Q11000047","display_name":"Healthcare system","level":3,"score":0.34860000014305115},{"id":"https://openalex.org/C2776178081","wikidata":"https://www.wikidata.org/wiki/Q3286546","display_name":"Respiratory disease","level":3,"score":0.3377000093460083},{"id":"https://openalex.org/C99454951","wikidata":"https://www.wikidata.org/wiki/Q932068","display_name":"Environmental health","level":1,"score":0.33559998869895935},{"id":"https://openalex.org/C2779701055","wikidata":"https://www.wikidata.org/wiki/Q929833","display_name":"Rare disease","level":3,"score":0.3280999958515167},{"id":"https://openalex.org/C2779159551","wikidata":"https://www.wikidata.org/wiki/Q1414874","display_name":"Comorbidity","level":2,"score":0.32190001010894775},{"id":"https://openalex.org/C2779473830","wikidata":"https://www.wikidata.org/wiki/Q1540899","display_name":"MEDLINE","level":2,"score":0.3190000057220459},{"id":"https://openalex.org/C3018822202","wikidata":"https://www.wikidata.org/wiki/Q1324077","display_name":"Patient data","level":2,"score":0.31220000982284546},{"id":"https://openalex.org/C512399662","wikidata":"https://www.wikidata.org/wiki/Q3505712","display_name":"Family medicine","level":1,"score":0.31130000948905945},{"id":"https://openalex.org/C3020672099","wikidata":"https://www.wikidata.org/wiki/Q857354","display_name":"Longitudinal data","level":2,"score":0.3073999881744385},{"id":"https://openalex.org/C2777895361","wikidata":"https://www.wikidata.org/wiki/Q1758614","display_name":"Longitudinal study","level":2,"score":0.3037000000476837},{"id":"https://openalex.org/C186079640","wikidata":"https://www.wikidata.org/wiki/Q719602","display_name":"Prevalence","level":3,"score":0.29260000586509705},{"id":"https://openalex.org/C2780664029","wikidata":"https://www.wikidata.org/wiki/Q5282120","display_name":"Disease burden","level":3,"score":0.29249998927116394},{"id":"https://openalex.org/C2780074459","wikidata":"https://www.wikidata.org/wiki/Q389735","display_name":"Heart disease","level":2,"score":0.2856999933719635},{"id":"https://openalex.org/C177713679","wikidata":"https://www.wikidata.org/wiki/Q679690","display_name":"Intensive care medicine","level":1,"score":0.2816999852657318},{"id":"https://openalex.org/C2780930700","wikidata":"https://www.wikidata.org/wiki/Q1128595","display_name":"Pulmonary hypertension","level":2,"score":0.2662000060081482},{"id":"https://openalex.org/C194828623","wikidata":"https://www.wikidata.org/wiki/Q2861470","display_name":"Emergency medicine","level":1,"score":0.2660999894142151},{"id":"https://openalex.org/C47344431","wikidata":"https://www.wikidata.org/wiki/Q1519812","display_name":"Health policy","level":3,"score":0.25529998540878296},{"id":"https://openalex.org/C205545832","wikidata":"https://www.wikidata.org/wiki/Q17156455","display_name":"Young adult","level":2,"score":0.2524000108242035},{"id":"https://openalex.org/C2780877353","wikidata":"https://www.wikidata.org/wiki/Q2518253","display_name":"Health services research","level":3,"score":0.25189998745918274},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.25130000710487366}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.1183/13993003.congress-2025.pa1920","doi":"https://doi.org/10.1183/13993003.congress-2025.pa1920","is_oa":false,"landing_page_url":"https://doi.org/10.1183/13993003.congress-2025.pa1920","pdf_url":null,"source":{"id":"https://openalex.org/S4210207896","display_name":"European Respiratory Journal","issn_l":"0903-1936","issn":["0903-1936","1399-3003"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-class-a","anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310317833","host_organization_name":"European Respiratory Society","host_organization_lineage":["https://openalex.org/P4310317833"],"host_organization_lineage_names":["European Respiratory Society"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pulmonary hypertension","raw_type":"proceedings-article"}],"best_oa_location":null,"sustainable_development_goals":[{"score":1.0,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W4387981754","https://openalex.org/W4416634925","https://openalex.org/W7131828388","https://openalex.org/W4416101669","https://openalex.org/W4416634329","https://openalex.org/W3217331330","https://openalex.org/W1894528780","https://openalex.org/W4387980615","https://openalex.org/W4416637217","https://openalex.org/W4416759390"],"abstract_inverted_index":{"The":[0,149],"epidemiology":[1],"of":[2,31,37,52,68,119,183,193,211,243],"Pulmonary":[3],"Hypertension":[4],"with":[5,14,77,111,141,145,180],"Lung":[6,16],"Disease":[7,17],"(LD-PH,":[8],"Group":[9,114],"3":[10,197],"PH),":[11],"including":[12],"PH":[13,78,104,113],"Interstitial":[15],"(ILD-PH),":[18],"remains":[19],"poorly":[20],"understood.":[21],"This":[22,200],"study":[23,178],"aimed":[24],"at":[25,156],"estimating":[26],"the":[27,50,69,103,127,177],"prevalence":[28,151,182],"and":[29,58,87,90,117,143,163,190],"incidence":[30,164,192],"ILD-PH":[32,146,153,170,206],"in":[33,74,215],"France":[34],"as":[35,208],"part":[36],"a":[38,60,181,209,212],"pan-European":[39],"real-world":[40],"evidence":[41],"study.":[42],"In":[43],"this":[44],"retrospective,":[45],"longitudinal":[46],"study,":[47],"due":[48],"to":[49,56,98,224],"absence":[51],"ICD-10":[53],"codes":[54],"specific":[55],"LD-PH":[57,142],"ILD-PH,":[59],"clinician-informed":[61],"algorithm":[62],"was":[63,154],"developed":[64],"through":[65],"preliminary":[66],"analysis":[67,203],"French":[70,128,137],"hospitalizations":[71],"database":[72],"(PMSI)":[73],"2022.":[75],"Patients":[76],"diagnoses":[79],"(ICD-10:":[80],"I27.0,":[81],"I27.2)":[82],"recorded":[83],"between":[84],"January":[85],"2017":[86],"December":[88],"2019":[89],"concurrent":[91],"lung":[92],"disease":[93,214],"within":[94],"24":[95],"months":[96],"prior":[97],"or":[99],"60":[100],"days":[101],"after":[102],"index":[105],"date":[106],"were":[107,124,147],"included,":[108],"excluding":[109],"those":[110],"other":[112],"records.":[115],"Comorbidities":[116],"use":[118],"right":[120],"heart":[121],"catheterization":[122],"(RHC)":[123],"identified":[125],"using":[126],"National":[129],"Health":[130],"Data":[131],"System":[132],"(SNDS).":[133],"Among":[134,169],"51.1":[135],"million":[136,159],"adults,":[138],"2,615":[139],"patients":[140,218],"1,119":[144],"identified.":[148],"annual":[150],"for":[152,237],"estimated":[155],"7.3":[157],"per":[158],"(/M)":[160],"(95%CI,":[161,167,186,196],"6.6\u20138.1)":[162],"5.0":[165],"/M/yr":[166,195],"4.4\u20135.6).":[168],"patients,":[171],"857":[172],"(76.6%)":[173],"underwent":[174,219],"RHC":[175,220],"during":[176],"period,":[179],"5.6":[184],"/M":[185],"4.9":[187],"\u2013":[188,198],"6.2)":[189],"an":[191],"3.6":[194],"4.1).":[199],"first":[201],"nationwide":[202],"highlights":[204],"that":[205],"occurs":[207],"complication":[210],"rare":[213],"France.":[216],"Most":[217],"evaluation,":[221],"demonstrating":[222],"adherence":[223],"diagnostic":[225],"guidelines":[226],"despite":[227],"limited":[228],"therapeutic":[229],"options.":[230],"These":[231],"findings":[232],"provide":[233],"critical":[234],"baseline":[235],"data":[236],"healthcare":[238],"planning":[239],"while":[240],"acknowledging":[241],"limitations":[242],"claims":[244],"data.":[245]},"counts_by_year":[],"updated_date":"2026-11-01T11:40:01.658920","created_date":"2025-11-25T00:00:00"}
