{"id":"https://openalex.org/W4414780697","doi":"https://doi.org/10.1016/j.rmcr.2025.102292","title":"A case of rapidly progressive interstitial lung disease","display_name":"A case of rapidly progressive interstitial lung disease","publication_year":2025,"publication_date":"2025-01-01","ids":{"openalex":"https://openalex.org/W4414780697","doi":"https://doi.org/10.1016/j.rmcr.2025.102292","pmid":"https://pubmed.ncbi.nlm.nih.gov/41036532","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/12481108"},"language":"en","primary_location":{"id":"doi:10.1016/j.rmcr.2025.102292","doi":"https://doi.org/10.1016/j.rmcr.2025.102292","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.rmcr.2025.102292","pdf_url":null,"source":{"id":"https://openalex.org/S2764604413","display_name":"Respiratory Medicine Case Reports","issn_l":"2213-0071","issn":["2213-0071"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","norway-1","poland-40","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Respiratory Medicine Case Reports","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj","pubmed"],"open_access":{"is_oa":true,"oa_status":"gold","oa_url":"https://doi.org/10.1016/j.rmcr.2025.102292","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5050925414","display_name":"Khoa Quy","orcid":"https://orcid.org/0000-0002-1923-7572","observed_orcids":["https://orcid.org/0000-0002-1923-7572"]},"institutions":[{"id":"https://openalex.org/I4210142044","display_name":"VinUniversity","ror":"https://ror.org/052dmdr17","country_code":"VN","type":"education","lineage":["https://openalex.org/I4210142044"]}],"countries":["VN"],"is_corresponding":true,"raw_author_name":"Khoa Quy","raw_affiliation_strings":["College of Health Sciences, VinUniversity, Hanoi, Viet Nam"],"raw_orcid":"https://orcid.org/0000-0002-1923-7572","affiliations":[{"raw_affiliation_string":"College of Health Sciences, VinUniversity, Hanoi, Viet Nam","institution_ids":["https://openalex.org/I4210142044"]}]},{"author_position":"middle","author":{"id":null,"display_name":"Thanh-Mai Vo","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210142044","display_name":"VinUniversity","ror":"https://ror.org/052dmdr17","country_code":"VN","type":"education","lineage":["https://openalex.org/I4210142044"]}],"countries":["VN"],"is_corresponding":false,"raw_author_name":"Thanh-Mai Vo","raw_affiliation_strings":["College of Health Sciences, VinUniversity, Hanoi, Viet Nam"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"College of Health Sciences, VinUniversity, Hanoi, Viet Nam","institution_ids":["https://openalex.org/I4210142044"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5119829521","display_name":"Thai-Hoa Bui-Pham","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210142044","display_name":"VinUniversity","ror":"https://ror.org/052dmdr17","country_code":"VN","type":"education","lineage":["https://openalex.org/I4210142044"]}],"countries":["VN"],"is_corresponding":false,"raw_author_name":"Thai-Hoa Bui-Pham","raw_affiliation_strings":["College of Health Sciences, VinUniversity, Hanoi, Viet Nam"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"College of Health Sciences, VinUniversity, Hanoi, Viet Nam","institution_ids":["https://openalex.org/I4210142044"]}]},{"author_position":"middle","author":{"id":null,"display_name":"Duc-Nhat Nguyen","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210142044","display_name":"VinUniversity","ror":"https://ror.org/052dmdr17","country_code":"VN","type":"education","lineage":["https://openalex.org/I4210142044"]},{"id":"https://openalex.org/I4210159142","display_name":"108 Military Central Hospital","ror":"https://ror.org/04k25m262","country_code":"VN","type":"healthcare","lineage":["https://openalex.org/I4210159142"]}],"countries":["VN"],"is_corresponding":false,"raw_author_name":"Duc-Nhat Nguyen","raw_affiliation_strings":["College of Health Sciences, VinUniversity, Hanoi, Viet Nam","Department of Acute and Emergency Medicine, Institute of Medical Care for Senior Military Officers, 108 Military Central Hospital, Hanoi, Viet Nam"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"College of Health Sciences, VinUniversity, Hanoi, Viet Nam","institution_ids":["https://openalex.org/I4210142044"]},{"raw_affiliation_string":"Department of Acute and Emergency Medicine, Institute of Medical Care for Senior Military Officers, 108 Military Central Hospital, Hanoi, Viet Nam","institution_ids":["https://openalex.org/I4210159142"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5103565254","display_name":"Minh-Hong Nguyen","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210159142","display_name":"108 Military Central Hospital","ror":"https://ror.org/04k25m262","country_code":"VN","type":"healthcare","lineage":["https://openalex.org/I4210159142"]}],"countries":["VN"],"is_corresponding":false,"raw_author_name":"Minh-Hong Nguyen","raw_affiliation_strings":["Department of Acute and Emergency Medicine, Institute of Medical Care for Senior Military Officers, 108 Military Central Hospital, Hanoi, Viet Nam"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Acute and Emergency Medicine, Institute of Medical Care for Senior Military Officers, 108 Military Central Hospital, Hanoi, Viet Nam","institution_ids":["https://openalex.org/I4210159142"]}]},{"author_position":"middle","author":{"id":null,"display_name":"Hai-Ha Thi Dinh","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210142044","display_name":"VinUniversity","ror":"https://ror.org/052dmdr17","country_code":"VN","type":"education","lineage":["https://openalex.org/I4210142044"]},{"id":"https://openalex.org/I4210159142","display_name":"108 Military Central Hospital","ror":"https://ror.org/04k25m262","country_code":"VN","type":"healthcare","lineage":["https://openalex.org/I4210159142"]}],"countries":["VN"],"is_corresponding":false,"raw_author_name":"Hai-Ha Thi Dinh","raw_affiliation_strings":["College of Health Sciences, VinUniversity, Hanoi, Viet Nam","Department of Acute and Emergency Medicine, Institute of Medical Care for Senior Military Officers, 108 Military Central Hospital, Hanoi, Viet Nam"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"College of Health Sciences, VinUniversity, Hanoi, Viet Nam","institution_ids":["https://openalex.org/I4210142044"]},{"raw_affiliation_string":"Department of Acute and Emergency Medicine, Institute of Medical Care for Senior Military Officers, 108 Military Central Hospital, Hanoi, Viet Nam","institution_ids":["https://openalex.org/I4210159142"]}]},{"author_position":"last","author":{"id":null,"display_name":"Van-Luan Pham","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210142044","display_name":"VinUniversity","ror":"https://ror.org/052dmdr17","country_code":"VN","type":"education","lineage":["https://openalex.org/I4210142044"]},{"id":"https://openalex.org/I4210159142","display_name":"108 Military Central Hospital","ror":"https://ror.org/04k25m262","country_code":"VN","type":"healthcare","lineage":["https://openalex.org/I4210159142"]}],"countries":["VN"],"is_corresponding":false,"raw_author_name":"Van-Luan Pham","raw_affiliation_strings":["College of Health Sciences, VinUniversity, Hanoi, Viet Nam","Department and Faculty of Respiratory Medicine, 108 Military Central Hospital, Hanoi, Viet Nam"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"College of Health Sciences, VinUniversity, Hanoi, Viet Nam","institution_ids":["https://openalex.org/I4210142044"]},{"raw_affiliation_string":"Department and Faculty of Respiratory Medicine, 108 Military Central Hospital, Hanoi, Viet Nam","institution_ids":["https://openalex.org/I4210159142"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":["https://openalex.org/A5050925414"],"corresponding_institution_ids":["https://openalex.org/I4210142044"],"apc_list":{"value":1200,"currency":"USD","value_usd":1200},"apc_paid":{"value":1200,"currency":"USD","value_usd":1200},"fwci":1.1406,"has_fulltext":false,"cited_by_count":2,"citation_normalized_percentile":{"value":0.79005752,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":95,"max":96},"biblio":{"volume":"58","issue":null,"first_page":"102292","last_page":"102292"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11724","display_name":"Inflammatory Myopathies and Dermatomyositis","score":0.9603999853134155,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11724","display_name":"Inflammatory Myopathies and Dermatomyositis","score":0.9603999853134155,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10870","display_name":"Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis","score":0.030700000002980232,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11330","display_name":"Systemic Sclerosis and Related Diseases","score":0.0020000000949949026,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/rapidly-progressive-interstitial-lung-disease","display_name":"rapidly progressive interstitial lung disease","score":0.9919999837875366},{"id":"https://openalex.org/keywords/dermatomyositis","display_name":"dermatomyositis","score":0.6679999828338623},{"id":"https://openalex.org/keywords/hypoxemic-respiratory-failure","display_name":"hypoxemic respiratory failure","score":0.8669999837875366},{"id":"https://openalex.org/keywords/calcineurin-inhibitors","display_name":"calcineurin inhibitors","score":0.7919999957084656},{"id":"https://openalex.org/keywords/cyclophosphamide","display_name":"cyclophosphamide","score":0.9860000014305115},{"id":"https://openalex.org/keywords/corticosteroid-therapy","display_name":"corticosteroid therapy","score":0.9110000133514404},{"id":"https://openalex.org/keywords/elderly-male","display_name":"elderly man","score":0.5680000185966492}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9496999979019165},{"id":"https://openalex.org/C2777543607","wikidata":"https://www.wikidata.org/wiki/Q1153419","display_name":"Interstitial lung disease","level":3,"score":0.781000018119812},{"id":"https://openalex.org/C2778751314","wikidata":"https://www.wikidata.org/wiki/Q681160","display_name":"Dermatomyositis","level":2,"score":0.6208000183105469},{"id":"https://openalex.org/C2776755627","wikidata":"https://www.wikidata.org/wiki/Q408524","display_name":"Cyclophosphamide","level":3,"score":0.5088000297546387},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.5054000020027161},{"id":"https://openalex.org/C2776888751","wikidata":"https://www.wikidata.org/wiki/Q767485","display_name":"Respiratory failure","level":2,"score":0.482699990272522},{"id":"https://openalex.org/C2777714996","wikidata":"https://www.wikidata.org/wiki/Q7886","display_name":"Lung","level":2,"score":0.4514999985694885},{"id":"https://openalex.org/C2776670291","wikidata":"https://www.wikidata.org/wiki/Q1779300","display_name":"Connective tissue disease","level":4,"score":0.41999998688697815},{"id":"https://openalex.org/C2994364436","wikidata":"https://www.wikidata.org/wiki/Q1153419","display_name":"Interstitial pneumonia","level":3,"score":0.4074999988079071},{"id":"https://openalex.org/C2777405647","wikidata":"https://www.wikidata.org/wiki/Q17147306","display_name":"Usual interstitial pneumonia","level":4,"score":0.392300009727478},{"id":"https://openalex.org/C2776153627","wikidata":"https://www.wikidata.org/wiki/Q1622407","display_name":"Mixed connective tissue disease","level":3,"score":0.3578000068664551},{"id":"https://openalex.org/C2779701055","wikidata":"https://www.wikidata.org/wiki/Q929833","display_name":"Rare disease","level":3,"score":0.34529998898506165},{"id":"https://openalex.org/C534529494","wikidata":"https://www.wikidata.org/wiki/Q7891","display_name":"Respiratory system","level":2,"score":0.3237000107765198},{"id":"https://openalex.org/C518705261","wikidata":"https://www.wikidata.org/wiki/Q25615","display_name":"Connective tissue","level":2,"score":0.31769999861717224},{"id":"https://openalex.org/C2777601897","wikidata":"https://www.wikidata.org/wiki/Q3409113","display_name":"Presentation (obstetrics)","level":2,"score":0.31040000915527344},{"id":"https://openalex.org/C9418649","wikidata":"https://www.wikidata.org/wiki/Q5275407","display_name":"Diffuse alveolar damage","level":4,"score":0.3073999881744385},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.30140000581741333},{"id":"https://openalex.org/C2779563453","wikidata":"https://www.wikidata.org/wiki/Q6040221","display_name":"Lung biopsy","level":3,"score":0.2906999886035919},{"id":"https://openalex.org/C2777914695","wikidata":"https://www.wikidata.org/wiki/Q12192","display_name":"Pneumonia","level":2,"score":0.29010000824928284},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.2849999964237213},{"id":"https://openalex.org/C75603125","wikidata":"https://www.wikidata.org/wiki/Q1877462","display_name":"Pulmonary function testing","level":2,"score":0.28369998931884766},{"id":"https://openalex.org/C2775998817","wikidata":"https://www.wikidata.org/wiki/Q1509367","display_name":"Rapidly progressive glomerulonephritis","level":4,"score":0.26499998569488525},{"id":"https://openalex.org/C2778720950","wikidata":"https://www.wikidata.org/wiki/Q424972","display_name":"Prednisone","level":2,"score":0.2547000050544739},{"id":"https://openalex.org/C2776760755","wikidata":"https://www.wikidata.org/wiki/Q18939","display_name":"Azathioprine","level":3,"score":0.25440001487731934}],"mesh":[],"locations_count":5,"locations":[{"id":"doi:10.1016/j.rmcr.2025.102292","doi":"https://doi.org/10.1016/j.rmcr.2025.102292","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.rmcr.2025.102292","pdf_url":null,"source":{"id":"https://openalex.org/S2764604413","display_name":"Respiratory Medicine Case Reports","issn_l":"2213-0071","issn":["2213-0071"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","norway-1","poland-40","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Respiratory Medicine Case Reports","raw_type":"journal-article"},{"id":"pmh:oai:europepmc.org:11291952","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/12481108","pdf_url":null,"source":{"id":"https://openalex.org/S4306400806","display_name":"Europe PMC (PubMed Central)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1303153112","host_organization_name":"European Bioinformatics Institute","host_organization_lineage":["https://openalex.org/I1303153112"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":null,"raw_type":"Text"},{"id":"pmid:41036532","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/41036532","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Respiratory medicine case reports","raw_type":"Case Reports"},{"id":"pmh:oai:pubmedcentral.nih.gov:12481108","doi":null,"is_oa":true,"landing_page_url":"https://pmc.ncbi.nlm.nih.gov/articles/PMC12481108/","pdf_url":null,"source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Respir Med Case Rep","raw_type":"Text"},{"id":"pmh:oai:doaj.org/article:df4f51629ef1414eb6dea3f69f4fced8","doi":null,"is_oa":true,"landing_page_url":"https://doaj.org/article/df4f51629ef1414eb6dea3f69f4fced8","pdf_url":null,"source":{"id":"https://openalex.org/S4306401280","display_name":"DOAJ (DOAJ: Directory of Open Access Journals)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-sa","license_id":"https://openalex.org/licenses/cc-by-sa","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Respiratory Medicine Case Reports, Vol 58, Iss , Pp 102292- (2025)","raw_type":"article"}],"best_oa_location":{"id":"doi:10.1016/j.rmcr.2025.102292","doi":"https://doi.org/10.1016/j.rmcr.2025.102292","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.rmcr.2025.102292","pdf_url":null,"source":{"id":"https://openalex.org/S2764604413","display_name":"Respiratory Medicine Case Reports","issn_l":"2213-0071","issn":["2213-0071"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","norway-1","poland-40","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Respiratory Medicine Case Reports","raw_type":"journal-article"},"sustainable_development_goals":[{"display_name":"Good health and well-being","score":1.0,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":9,"referenced_works":["https://openalex.org/W2141262625","https://openalex.org/W2573087089","https://openalex.org/W2589034377","https://openalex.org/W2890697585","https://openalex.org/W2974327724","https://openalex.org/W3119166515","https://openalex.org/W4200214266","https://openalex.org/W4313406819","https://openalex.org/W4407425444"],"related_works":["https://openalex.org/W7161586787","https://openalex.org/W3093084622","https://openalex.org/W4303984220","https://openalex.org/W2901650494","https://openalex.org/W2909746150","https://openalex.org/W4387247963","https://openalex.org/W4410275418","https://openalex.org/W3092690478","https://openalex.org/W4410414161","https://openalex.org/W4410275376"],"abstract_inverted_index":{"We":[0],"describe":[1],"a":[2],"rare":[3],"presentation":[4],"of":[5,33,70,119,131,161],"rapidly":[6,83,162],"progressive":[7,84,163,206],"interstitial":[8,56,85,172,207],"pneumonia":[9],"with":[10,15,41,81,96,170,210],"autoimmune":[11,202],"features":[12],"(IPAF)":[13],"associated":[14],"MDA5":[16],"autoantibodies.":[17],"Unlike":[18],"typical":[19],"MDA5-positive":[20,82,121,164],"dermatomyositis,":[21],"this":[22,34,132],"patient":[23,78,112],"lacked":[24],"skin":[25],"or":[26,67,72],"muscle":[27],"involvement,":[28],"expanding":[29],"the":[30,111,147],"clinical":[31,66],"spectrum":[32],"antibody-associated":[35],"disease.":[36],"An":[37],"elderly":[38],"male":[39,168],"presented":[40,169],"acute-onset":[42],"dyspnea":[43],"and":[44,55,101,110,134,152,175],"hypoxemic":[45],"respiratory":[46,107,115,211],"failure.":[47,212],"High-resolution":[48],"computed":[49],"tomography":[50],"revealed":[51],"diffuse":[52],"ground-glass":[53],"opacities":[54],"changes.":[57],"Autoimmune":[58],"screening":[59],"identified":[60],"strongly":[61],"positive":[62],"anti-MDA5":[63],"antibodies,":[64],"without":[65,125],"laboratory":[68],"evidence":[69],"dermatomyositis":[71,127],"other":[73],"connective":[74],"tissue":[75],"diseases.":[76],"The":[77],"was":[79,103],"diagnosed":[80],"lung":[86,173,208],"disease":[87,174,193,209],"(RP-ILD)":[88],"manifesting":[89],"as":[90],"IPAF.":[91,165],"Aggressive":[92,189],"combination":[93],"immunosuppressive":[94],"therapy":[95,137,191],"high-dose":[97],"corticosteroids,":[98],"calcineurin":[99],"inhibitor,":[100],"cyclophosphamide":[102],"initiated.":[104],"Despite":[105],"treatment,":[106],"function":[108],"deteriorated,":[109],"succumbed":[113],"to":[114],"failure":[116],"within":[117],"weeks":[118],"presentation.":[120],"RP-ILD":[122],"can":[123],"present":[124],"classic":[126],"features.":[128],"Early":[129],"recognition":[130],"antibody":[133,182],"prompt":[135],"aggressive":[136],"are":[138],"critical,":[139],"though":[140],"prognosis":[141],"remains":[142],"poor.":[143],"This":[144],"case":[145],"underscores":[146],"need":[148,199],"for":[149,200],"heightened":[150],"awareness":[151],"research":[153],"into":[154],"tailored":[155],"treatment":[156],"strategies.":[157],"\u2022":[158,166,178,188,196],"First":[159],"report":[160],"Elderly":[167],"fulminant":[171],"severe":[176],"hypoxemia.":[177],"Diagnosis":[179],"required":[180],"myositis-specific":[181],"panel":[183],"after":[184],"negative":[185],"infectious":[186],"workup.":[187],"initial":[190],"failed,":[192],"progressed":[194],"rapidly.":[195],"Case":[197],"highlights":[198],"early":[201],"testing":[203],"in":[204],"unexplained":[205]},"counts_by_year":[{"year":2026,"cited_by_count":2}],"updated_date":"2026-10-28T10:33:24.094632","created_date":"2025-10-10T00:00:00"}
