{"id":"https://openalex.org/W4409955464","doi":"https://doi.org/10.34257/ljmhrvol25is3pg61","title":"Urogenital Anomalies in Anorectal Malformations and Hirschsprung\u2019s Disease: Prevalence, Diagnosis, and Management","display_name":"Urogenital Anomalies in Anorectal Malformations and Hirschsprung\u2019s Disease: Prevalence, Diagnosis, and Management","publication_year":2025,"publication_date":"2025-04-07","ids":{"openalex":"https://openalex.org/W4409955464","doi":"https://doi.org/10.34257/ljmhrvol25is3pg61"},"language":"en","primary_location":{"id":"doi:10.34257/ljmhrvol25is3pg61","doi":"https://doi.org/10.34257/ljmhrvol25is3pg61","is_oa":true,"landing_page_url":"https://doi.org/10.34257/ljmhrvol25is3pg61","pdf_url":"https://doi.org/10.34257/ljmhrvol25is3pg61","source":{"id":"https://openalex.org/S4210169248","display_name":"Global Journal of Medical Research","issn_l":"0975-5888","issn":["0975-5888","2249-4618"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310321940","host_organization_name":"Global Journals","host_organization_lineage":["https://openalex.org/P4310321940"],"host_organization_lineage_names":["Global Journals"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Global Journal of Medical Research","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://doi.org/10.34257/ljmhrvol25is3pg61","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5087890261","display_name":"Ir\u00e8ne Nadine Kouna Tsala","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Ir\u00e8ne Nadine Kouna Tsala","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5062579024","display_name":"Pierre Lingier","orcid":"https://orcid.org/0000-0002-9351-8970","observed_orcids":["https://orcid.org/0000-0002-9351-8970"]},"institutions":[{"id":"https://openalex.org/I3019103622","display_name":"Temple Street Children's University Hospital","ror":"https://ror.org/0527gjc91","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I3019103622"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Pierre Lingier","raw_affiliation_strings":["Children's University Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Children's University Hospital","institution_ids":["https://openalex.org/I3019103622"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5047571919","display_name":"Tobie Eric Ntsobe","orcid":"https://orcid.org/0000-0002-6520-865X","observed_orcids":["https://orcid.org/0000-0002-6520-865X"]},"institutions":[{"id":"https://openalex.org/I4210113195","display_name":"Gannan Medical University","ror":"https://ror.org/01tjgw469","country_code":"CN","type":"education","lineage":["https://openalex.org/I4210113195"]}],"countries":["CN"],"is_corresponding":false,"raw_author_name":"Tobie Eric Ntsobe","raw_affiliation_strings":[": General Hospital of Garoua , Cameroon / Gannan Medical University - China"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":": General Hospital of Garoua , Cameroon / Gannan Medical University - China","institution_ids":["https://openalex.org/I4210113195"]}]},{"author_position":"middle","author":{"id":null,"display_name":"Eduardo Vieira Cardoso","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I3019103622","display_name":"Temple Street Children's University Hospital","ror":"https://ror.org/0527gjc91","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I3019103622"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Eduardo Vieira Cardoso","raw_affiliation_strings":["Children's University Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Children's University Hospital","institution_ids":["https://openalex.org/I3019103622"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5027557348","display_name":"Cyrille Abega","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I3019103622","display_name":"Temple Street Children's University Hospital","ror":"https://ror.org/0527gjc91","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I3019103622"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Cyrille Abega","raw_affiliation_strings":["Children's University Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Children's University Hospital","institution_ids":["https://openalex.org/I3019103622"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5008714325","display_name":"Nasroola Damry","orcid":"https://orcid.org/0000-0001-7517-6703","observed_orcids":["https://orcid.org/0000-0001-7517-6703"]},"institutions":[{"id":"https://openalex.org/I3019103622","display_name":"Temple Street Children's University Hospital","ror":"https://ror.org/0527gjc91","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I3019103622"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Nasroola Damry","raw_affiliation_strings":["Children's University Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Children's University Hospital","institution_ids":["https://openalex.org/I3019103622"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5010874118","display_name":"Basile Essola","orcid":"https://orcid.org/0000-0001-5361-9358","observed_orcids":["https://orcid.org/0000-0001-5361-9358"]},"institutions":[{"id":"https://openalex.org/I163423212","display_name":"University of Douala","ror":"https://ror.org/02zr5jr81","country_code":"CM","type":"education","lineage":["https://openalex.org/I163423212"]}],"countries":["CM"],"is_corresponding":false,"raw_author_name":"Basile Essola","raw_affiliation_strings":[": Department of Surgery , University of Douala - Cameroun"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":": Department of Surgery , University of Douala - Cameroun","institution_ids":["https://openalex.org/I163423212"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5090469267","display_name":"Anna Poupalou","orcid":"https://orcid.org/0009-0006-5325-1075","observed_orcids":["https://orcid.org/0009-0006-5325-1075"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Anna Poupalou","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":3,"institutions_distinct_count":3,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":"61","last_page":"67"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12237","display_name":"Congenital gastrointestinal and neural anomalies","score":0.98580002784729,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12237","display_name":"Congenital gastrointestinal and neural anomalies","score":0.98580002784729,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11815","display_name":"Urological Disorders and Treatments","score":0.01269999984651804,"subfield":{"id":"https://openalex.org/subfields/2748","display_name":"Urology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11174","display_name":"Pediatric Urology and Nephrology Studies","score":0.00039999998989515007,"subfield":{"id":"https://openalex.org/subfields/2735","display_name":"Pediatrics, Perinatology and Child Health"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/genitourinary-anomalies","display_name":"genitourinary anomalies","score":0.9980000257492065},{"id":"https://openalex.org/keywords/anorectal-malformation","display_name":"anorectal malformation","score":0.9980000257492065},{"id":"https://openalex.org/keywords/hirschsprung-disease","display_name":"Hirschsprung disease","score":0.9829999804496765},{"id":"https://openalex.org/keywords/vesicoureteral-reflux","display_name":"vesicoureteral reflux","score":0.9319999814033508},{"id":"https://openalex.org/keywords/multicystic-dysplastic-kidney","display_name":"multicystic dysplastic kidney","score":0.8889999985694885},{"id":"https://openalex.org/keywords/renal-dysplasia","display_name":"renal dysplasia","score":0.9229999780654907},{"id":"https://openalex.org/keywords/megaureter","display_name":"megaureter","score":0.9340000152587891},{"id":"https://openalex.org/keywords/hydronephrosis","display_name":"hydronephrosis","score":1.0},{"id":"https://openalex.org/keywords/conservative-treatment","display_name":"conservative treatment","score":0.5619999766349792},{"id":"https://openalex.org/keywords/antibiotic-prophylaxis","display_name":"antibiotic prophylaxis","score":0.9660000205039978},{"id":"https://openalex.org/keywords/pediatric-urology","display_name":"pediatric urology","score":0.7879999876022339}],"concepts":[{"id":"https://openalex.org/C133507102","wikidata":"https://www.wikidata.org/wiki/Q4712977","display_name":"Genitourinary system","level":2,"score":0.8291023969650269},{"id":"https://openalex.org/C2779089422","wikidata":"https://www.wikidata.org/wiki/Q1343645","display_name":"Hirschsprung's disease","level":3,"score":0.7673966884613037},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.6334853172302246},{"id":"https://openalex.org/C2779318624","wikidata":"https://www.wikidata.org/wiki/Q4770166","display_name":"Anorectal anomalies","level":2,"score":0.52284175157547},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.38015517592430115},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.26370158791542053},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.23707365989685059},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.23115476965904236}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.34257/ljmhrvol25is3pg61","doi":"https://doi.org/10.34257/ljmhrvol25is3pg61","is_oa":true,"landing_page_url":"https://doi.org/10.34257/ljmhrvol25is3pg61","pdf_url":"https://doi.org/10.34257/ljmhrvol25is3pg61","source":{"id":"https://openalex.org/S4210169248","display_name":"Global Journal of Medical Research","issn_l":"0975-5888","issn":["0975-5888","2249-4618"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310321940","host_organization_name":"Global Journals","host_organization_lineage":["https://openalex.org/P4310321940"],"host_organization_lineage_names":["Global Journals"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Global Journal of Medical Research","raw_type":"journal-article"}],"best_oa_location":{"id":"doi:10.34257/ljmhrvol25is3pg61","doi":"https://doi.org/10.34257/ljmhrvol25is3pg61","is_oa":true,"landing_page_url":"https://doi.org/10.34257/ljmhrvol25is3pg61","pdf_url":"https://doi.org/10.34257/ljmhrvol25is3pg61","source":{"id":"https://openalex.org/S4210169248","display_name":"Global Journal of Medical Research","issn_l":"0975-5888","issn":["0975-5888","2249-4618"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310321940","host_organization_name":"Global Journals","host_organization_lineage":["https://openalex.org/P4310321940"],"host_organization_lineage_names":["Global Journals"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Global Journal of Medical Research","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":1.0,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W4409955464.pdf","grobid_xml":"https://content.openalex.org/works/W4409955464.grobid-xml"},"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W1987241967","https://openalex.org/W4404051015","https://openalex.org/W7140043118","https://openalex.org/W2089055741","https://openalex.org/W2982020242","https://openalex.org/W7216560933","https://openalex.org/W4387631877","https://openalex.org/W4409746897","https://openalex.org/W7216809777","https://openalex.org/W2907081236"],"abstract_inverted_index":{"Introduction:":[0],"Urogenital":[1],"anomalies":[2,30,156,213],"are":[3,283],"responsible":[4],"of":[5,8,28,39,75,94,103,151,154,181,188,211,242,255,260],"approximately":[6],"50%":[7],"end-stage":[9],"renal":[10,35,236],"disease":[11,55,127,249],"in":[12,83,176,206,272],"children":[13,104],"[5].":[14],"It":[15],"is":[16,278,297],"important":[17],"to":[18,31,34,43,117,202,216,247,269,286],"make":[19],"an":[20],"early":[21],"clinical":[22],"diagnosis":[23],"and":[24,50,53,56,62,110,128,157,168,185,200,235,257],"provide":[25],"prompt":[26],"management":[27],"these":[29],"prevent":[32],"progression":[33],"failure.":[36],"The":[37,220,262],"aim":[38],"this":[40],"study":[41,69,277],"was":[42,204],"establish":[44],"the":[45,71,76,91,295],"correlation":[46],"between":[47],"urinary":[48,155,223],"pathologies":[49],"anorectal":[51,108,132,140,183,217,287],"malformations":[52,109,184,218,244,288],"Hirschsprung's":[54,189,248,290],"present":[57],"their":[58],"therapeutic":[59],"particularities.":[60],"Means":[61],"Methods:":[63],"We":[64,85,121,134,172],"retrospectively":[65],"conducted":[66],"a":[67,87],"descriptive":[68],"at":[70,250],"Pediatric":[72],"Surgery":[73],"Department":[74],"Queen":[77],"Fabiola":[78],"Children's":[79],"University":[80],"Hospital":[81],"(HUDERF)":[82],"Brussels.":[84],"got":[86],"clearance":[88],"consent":[89],"from":[90,113],"ethical":[92],"committee":[93],"our":[95,177],"hospital.":[96],"During":[97],"one":[98],"month,":[99],"we":[100,145],"retrieved":[101],"files":[102],"who":[105,137],"consulted":[106],"for":[107],"Hirschsprung\u2019s":[111,126],"diseases":[112],"August":[114],"1,":[115],"2011":[116],"June":[118],"31,":[119],"2024.":[120],"Included":[122],"all":[123],"patients":[124,136,175,195],"presenting":[125],"those":[129],"with":[130,162],"upper":[131,182],"malformations.":[133,141],"excluded":[135],"presented":[138],"lower":[139],"Clinical":[142],"parameters":[143],"that":[144,280],"recorded":[146],"included:":[147],"age,":[148],"sex,":[149],"type":[150,153],"imaging,":[152],"treatment.":[158],"Data":[159],"were":[160,214,226,245],"analyzed":[161],"Microsoft":[163],"Of":[164],"ice":[165],"Excel":[166],"2010":[167],"SPSS":[169],"software.":[170],"Results:":[171],"included":[173],"50":[174],"study;":[178],"16":[179],"cases":[180,187,210,241,254,259,294],"34":[186],"disease.":[190,291],"For":[191],"radiologic":[192],"assessments,":[193],"30":[194],"underwent":[196],"abdominal":[197],"ultrasound":[198],"(US)":[199],"urethrocys":[201],"graphy":[203],"done":[205],"8":[207],"patients.":[208],"Seven":[209],"urologic":[212,243],"associated":[215,246,268,285],"43.8%.":[219],"dif":[221],"erent":[222],"abnormalities":[224,282],"found":[225],"multicystic":[227],"kidney":[228],"(3":[229],"cases),":[230],"vesicoureteral":[231],"reflux":[232],"(2":[233,238,253],"cases)":[234],"dysplasia":[237],"cases).":[239],"Four":[240],"least":[251],"11.8%":[252],"megaureter":[256],"2":[258],"hydronephrosis).":[261],"conservative":[263,298],"treatment":[264,296],"has":[265],"been":[266],"practiced":[267],"antibiotic":[270],"prophylaxis":[271],"10":[273],"cases.":[274],"Conclusion:":[275],"This":[276],"showing":[279],"urogenital":[281],"mostly":[284],"than":[289],"In":[292],"many":[293]},"counts_by_year":[],"updated_date":"2026-10-26T11:51:55.731654","created_date":"2025-04-30T00:00:00"}
