{"id":"https://openalex.org/W4403719695","doi":"https://doi.org/10.14309/01.ajg.0001039908.50271.a9","title":"S2635 A Case of Mistaken Identity: IGG4-SC Mimicking Malignancy","display_name":"S2635 A Case of Mistaken Identity: IGG4-SC Mimicking Malignancy","publication_year":2024,"publication_date":"2024-10-01","ids":{"openalex":"https://openalex.org/W4403719695","doi":"https://doi.org/10.14309/01.ajg.0001039908.50271.a9"},"language":"en","primary_location":{"id":"doi:10.14309/01.ajg.0001039908.50271.a9","doi":"https://doi.org/10.14309/01.ajg.0001039908.50271.a9","is_oa":false,"landing_page_url":"https://doi.org/10.14309/01.ajg.0001039908.50271.a9","pdf_url":null,"source":{"id":"https://openalex.org/S66441642","display_name":"The American Journal of Gastroenterology","issn_l":"0002-9270","issn":["0002-9270","1572-0241"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315671","host_organization_name":"Lippincott Williams & Wilkins","host_organization_lineage":["https://openalex.org/P4310315671","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Lippincott Williams & Wilkins","Wolters Kluwer"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Gastroenterology","raw_type":"journal-article"},"volume":null,"type":"conference-abstract","is_traditional":false,"indexed_in":["crossref"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":null,"display_name":"Alexander Alfaro","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210138718","display_name":"VA Caribbean Healthcare System","ror":"https://ror.org/03tjwy964","country_code":"PR","type":"healthcare","lineage":["https://openalex.org/I1322918889","https://openalex.org/I2799886695","https://openalex.org/I4210119004","https://openalex.org/I4210138718"]}],"countries":["PR"],"is_corresponding":true,"raw_author_name":"Alexander Alfaro","raw_affiliation_strings":["Veterans Affairs Caribbean Healthcare System, San Juan, Puerto Rico;"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Veterans Affairs Caribbean Healthcare System, San Juan, Puerto Rico;","institution_ids":["https://openalex.org/I4210138718"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5076863151","display_name":"Diego Rom\u00e1n-Col\u00f3n","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210138718","display_name":"VA Caribbean Healthcare System","ror":"https://ror.org/03tjwy964","country_code":"PR","type":"healthcare","lineage":["https://openalex.org/I1322918889","https://openalex.org/I2799886695","https://openalex.org/I4210119004","https://openalex.org/I4210138718"]}],"countries":["PR"],"is_corresponding":false,"raw_author_name":"Diego Roman-Colon","raw_affiliation_strings":["Veterans Affairs Caribbean Healthcare System, San Juan, Puerto Rico;"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Veterans Affairs Caribbean Healthcare System, San Juan, Puerto Rico;","institution_ids":["https://openalex.org/I4210138718"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5093011250","display_name":"Jose Irizarry-Garcia","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210138718","display_name":"VA Caribbean Healthcare System","ror":"https://ror.org/03tjwy964","country_code":"PR","type":"healthcare","lineage":["https://openalex.org/I1322918889","https://openalex.org/I2799886695","https://openalex.org/I4210119004","https://openalex.org/I4210138718"]}],"countries":["PR"],"is_corresponding":false,"raw_author_name":"Jose Irizarry-Garcia","raw_affiliation_strings":["Veterans Affairs Caribbean Healthcare System, Guaynabo, Puerto Rico"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Veterans Affairs Caribbean Healthcare System, Guaynabo, Puerto Rico","institution_ids":["https://openalex.org/I4210138718"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5092756142","display_name":"Benjamin A Gonzalez Burgos","orcid":"https://orcid.org/0000-0002-8742-6551","observed_orcids":["https://orcid.org/0000-0002-8742-6551"]},"institutions":[{"id":"https://openalex.org/I4210138718","display_name":"VA Caribbean Healthcare System","ror":"https://ror.org/03tjwy964","country_code":"PR","type":"healthcare","lineage":["https://openalex.org/I1322918889","https://openalex.org/I2799886695","https://openalex.org/I4210119004","https://openalex.org/I4210138718"]}],"countries":["PR"],"is_corresponding":false,"raw_author_name":"Benjamin Gonzalez-Burgos","raw_affiliation_strings":["Veterans Affairs Caribbean Healthcare System, San Juan, Puerto Rico;"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Veterans Affairs Caribbean Healthcare System, San Juan, Puerto Rico;","institution_ids":["https://openalex.org/I4210138718"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5063675139","display_name":"Jos\u00e9 Martin-Ortiz","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210138718","display_name":"VA Caribbean Healthcare System","ror":"https://ror.org/03tjwy964","country_code":"PR","type":"healthcare","lineage":["https://openalex.org/I1322918889","https://openalex.org/I2799886695","https://openalex.org/I4210119004","https://openalex.org/I4210138718"]}],"countries":["PR"],"is_corresponding":false,"raw_author_name":"Jose Martin-Ortiz","raw_affiliation_strings":["Veterans Affairs Caribbean Healthcare System, San Juan, Puerto Rico;"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Veterans Affairs Caribbean Healthcare System, San Juan, Puerto Rico;","institution_ids":["https://openalex.org/I4210138718"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":["https://openalex.org/I4210138718"],"apc_list":{"value":4390,"currency":"USD","value_usd":4390},"apc_paid":null,"fwci":null,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":null,"cited_by_percentile_year":null,"biblio":{"volume":"119","issue":"10S","first_page":"S1843","last_page":"S1843"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11576","display_name":"IgG4-Related and Inflammatory Diseases","score":0.9984999895095825,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11576","display_name":"IgG4-Related and Inflammatory Diseases","score":0.9984999895095825,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11834","display_name":"Liver Diseases and Immunity","score":0.0006000000284984708,"subfield":{"id":"https://openalex.org/subfields/2721","display_name":"Hepatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10518","display_name":"Gallbladder and Bile Duct Disorders","score":9.999999747378752e-05,"subfield":{"id":"https://openalex.org/subfields/2715","display_name":"Gastroenterology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/igg4-related-sclerosing-cholangitis","display_name":"IgG4-related sclerosing cholangitis","score":0.9789999723434448},{"id":"https://openalex.org/keywords/obstructive-jaundice","display_name":"obstructive jaundice","score":0.7260000109672546},{"id":"https://openalex.org/keywords/mimicking-malignancy","display_name":"mimicking malignancy","score":0.8090000152587891},{"id":"https://openalex.org/keywords/cholecystectomy","display_name":"cholecystectomy","score":0.7549999952316284},{"id":"https://openalex.org/keywords/ca19-9","display_name":"CA19-9","score":0.8809999823570251},{"id":"https://openalex.org/keywords/serum-igg4-elevation","display_name":"serum IgG4 elevation","score":0.8799999952316284},{"id":"https://openalex.org/keywords/differential-diagnosis","display_name":"differential diagnosis","score":0.6520000100135803},{"id":"https://openalex.org/keywords/immunohistochemistry","display_name":"immunohistochemistry","score":0.7960000038146973},{"id":"https://openalex.org/keywords/corticosteroid-therapy","display_name":"corticosteroid therapy","score":0.9850000143051147},{"id":"https://openalex.org/keywords/autoimmune-cholangitis","display_name":"autoimmune cholangitis","score":0.6840000152587891},{"id":"https://openalex.org/keywords/magnetic-resonance-cholangiopancreatography","display_name":"magnetic resonance cholangiopancreatography","score":0.8339999914169312},{"id":"https://openalex.org/keywords/endoscopic-retrograde-cholangiopancreatography","display_name":"endoscopic retrograde cholangiopancreatography","score":0.949999988079071}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9606033563613892},{"id":"https://openalex.org/C2779399171","wikidata":"https://www.wikidata.org/wiki/Q1483951","display_name":"Malignancy","level":2,"score":0.7397240400314331},{"id":"https://openalex.org/C2778355321","wikidata":"https://www.wikidata.org/wiki/Q17079427","display_name":"Identity (music)","level":2,"score":0.5295884013175964},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.39583781361579895},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.290438711643219},{"id":"https://openalex.org/C107038049","wikidata":"https://www.wikidata.org/wiki/Q35986","display_name":"Aesthetics","level":1,"score":0.13193097710609436},{"id":"https://openalex.org/C138885662","wikidata":"https://www.wikidata.org/wiki/Q5891","display_name":"Philosophy","level":0,"score":0.0}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.14309/01.ajg.0001039908.50271.a9","doi":"https://doi.org/10.14309/01.ajg.0001039908.50271.a9","is_oa":false,"landing_page_url":"https://doi.org/10.14309/01.ajg.0001039908.50271.a9","pdf_url":null,"source":{"id":"https://openalex.org/S66441642","display_name":"The American Journal of Gastroenterology","issn_l":"0002-9270","issn":["0002-9270","1572-0241"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315671","host_organization_name":"Lippincott Williams & Wilkins","host_organization_lineage":["https://openalex.org/P4310315671","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Lippincott Williams & Wilkins","Wolters Kluwer"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Gastroenterology","raw_type":"journal-article"}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":0.9940000176429749,"display_name":"Good health and well-being"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W7138880531","https://openalex.org/W7220680137","https://openalex.org/W4403719886","https://openalex.org/W4417239213","https://openalex.org/W3130932833","https://openalex.org/W2494415010","https://openalex.org/W7153820047","https://openalex.org/W7154691846","https://openalex.org/W2912768755","https://openalex.org/W4387750660"],"abstract_inverted_index":{"Introduction:":[0],"IGG4-related":[1],"sclerosing":[2,233],"cholangitis":[3],"(IgG4-SC)":[4],"is":[5,47,259],"a":[6,67,76,96,169,185,204,260,268,285,293],"rare":[7],"autoimmune":[8,322],"disease":[9],"affecting":[10],"the":[11,165,182,190,214,225,237,244,250,321],"bile":[12,125],"ducts":[13],"in":[14,18,110,249,275,328],"fewer":[15],"than":[16],"1":[17],"100,000":[19],"people.":[20],"This":[21,100,207,241],"condition":[22],"primarily":[23],"strikes":[24],"men":[25],"over":[26],"40,":[27],"and":[28,52,71,85,117,131,146,184,266,284,301,312,324],"its":[29],"ability":[30],"to":[31,236,319],"mimic":[32],"other":[33],"illnesses,":[34],"especially":[35,256],"malignancy,":[36],"makes":[37],"accurate":[38,308],"diagnosis":[39,51,252,311],"particularly":[40],"challenging.":[41],"A":[42,63,277],"high":[43,278],"index":[44,279],"of":[45,69,79,98,104,124,143,168,224,231,246,253,270,280,287,314],"suspicion":[46,281],"crucial":[48,306],"for":[49,282,307],"timely":[50],"treatment,":[53],"as":[54,334],"IgG4-SC":[55,248,283],"can":[56,272,331],"significantly":[57,201,294],"impact":[58],"patient":[59,170,326],"outcomes.":[60],"Case":[61],"Description/Methods:":[62],"72-year-old":[64],"man":[65],"with":[66,75,128,155,160,171,221],"history":[68,97,269],"tobacco":[70],"alcohol":[72],"use":[73],"presented":[74],"concerning":[77],"trio":[78],"symptoms:":[80],"abdominal":[81],"pain,":[82],"dark":[83],"urine,":[84],"weight":[86],"loss.":[87],"Interestingly,":[88],"he":[89],"had":[90],"no":[91],"prior":[92,105],"biliary":[93,106],"complications":[94],"despite":[95],"cholecystectomy.":[99],"detail,":[101],"often":[102],"suggestive":[103,123],"issues,":[107],"was":[108,122,137,153,187,200],"misleading":[109,274],"this":[111],"case.":[112],"Physical":[113],"examination":[114,220],"revealed":[115,228],"jaundice":[116],"mild":[118],"discomfort.":[119],"Laboratory":[120],"workup":[121],"duct":[126,158],"obstruction":[127],"elevated":[129,139,202,295],"bilirubin":[130],"alkaline":[132],"phosphatase":[133],"levels.":[134],"Furthermore,":[135],"there":[136],"also":[138],"CA":[140,264],"19-9,":[141],"anemia":[142],"chronic":[144],"disease,":[145],"transaminitis.":[147],"magnetic":[148],"resonance":[149,151],"imaging/magnetic":[150],"cholangiopancreatography":[152,180],"consistent":[154],"common":[156],"hepatic":[157],"stricture":[159],"intrahepatic":[161],"ductal":[162],"dilation.":[163],"In":[164],"clinical":[166,288],"setting":[167],"cholecystectomy,":[172],"these":[173],"findings":[174],"strongly":[175],"suggested":[176],"malignancy.":[177,335],"Endoscopic":[178],"retrograde":[179],"confirmed":[181],"stricture,":[183],"biopsy":[186,217,226],"performed.":[188],"However,":[189],"plot":[191],"took":[192],"an":[193],"unexpected":[194,208],"turn:":[195],"his":[196],"serum":[197,296],"IgG4":[198,232,297],"level":[199],"at":[203],"staggering":[205],"940.3.":[206],"finding":[209],"prompted":[210],"further":[211],"investigation":[212],"beyond":[213],"initial":[215],"inconclusive":[216],"results.":[218],"Follow-up":[219],"immunohistochemical":[222,303],"staining":[223,304],"specimen":[227],"characteristic":[229],"features":[230],"cholangitis,":[234],"leading":[235,261],"definitive":[238],"diagnosis.":[239,309],"Discussion:":[240],"case":[242],"exemplifies":[243],"importance":[245],"considering":[247],"differential":[251],"obstructive":[254],"jaundice,":[255],"when":[257],"malignancy":[258],"suspect.":[262],"Elevated":[263],"19-9":[265],"even":[267],"cholecystectomy":[271],"be":[273],"IgG4-SC.":[276],"combination":[286],"features,":[289],"laboratory":[290],"findings,":[291],"including":[292],"level,":[298],"imaging":[299],"studies,":[300],"potentially":[302],"are":[305,317],"Early":[310],"initiation":[313],"corticosteroid":[315],"therapy":[316],"essential":[318],"manage":[320],"response":[323],"improve":[325],"outcomes":[327],"IgG4-SC,":[329],"which":[330],"effectively":[332],"masquerade":[333]},"counts_by_year":[],"updated_date":"2026-09-29T14:09:16.559479","created_date":"2024-10-25T00:00:00"}
