{"id":"https://openalex.org/W4390744583","doi":"https://doi.org/10.3324/haematol.2023.283603","title":"Longitudinal, natural history study reveals the disease burden of idiopathic multicentric Castleman disease","display_name":"Longitudinal, natural history study reveals the disease burden of idiopathic multicentric Castleman disease","publication_year":2024,"publication_date":"2024-01-11","ids":{"openalex":"https://openalex.org/W4390744583","doi":"https://doi.org/10.3324/haematol.2023.283603","pmid":"https://pubmed.ncbi.nlm.nih.gov/38205523","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/11217716"},"language":"en","primary_location":{"id":"doi:10.3324/haematol.2023.283603","doi":"https://doi.org/10.3324/haematol.2023.283603","is_oa":true,"landing_page_url":"https://doi.org/10.3324/haematol.2023.283603","pdf_url":"https://haematologica.org/article/download/haematol.2023.283603/76491","source":{"id":"https://openalex.org/S2752781272","display_name":"Haematologica","issn_l":"0390-6078","issn":["0390-6078","1592-8721"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","dongbi-a","doyens","jufo-2","ki-jl-2","medline","norway-2","oarl","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310317774","host_organization_name":"Ferrata Storti Foundation","host_organization_lineage":["https://openalex.org/P4310317774"],"host_organization_lineage_names":["Ferrata Storti Foundation"],"type":"journal"},"license":"cc-by-nc","license_id":"https://openalex.org/licenses/cc-by-nc","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Haematologica","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj","pubmed"],"open_access":{"is_oa":true,"oa_status":"gold","oa_url":"https://haematologica.org/article/download/haematol.2023.283603/76491","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5062019448","display_name":"Mateo Sarmiento Bustamante","orcid":"https://orcid.org/0009-0002-6774-2714","observed_orcids":["https://orcid.org/0009-0002-6774-2714"]},"institutions":[{"id":"https://openalex.org/I79576946","display_name":"University of Pennsylvania","ror":"https://ror.org/00b30xv10","country_code":"US","type":"education","lineage":["https://openalex.org/I79576946"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"Mateo Sarmiento Bustamante","raw_affiliation_strings":["Center for Cytokine Storm Treatment and Laboratory, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Center for Cytokine Storm Treatment and Laboratory, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104","institution_ids":["https://openalex.org/I79576946"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5055932729","display_name":"Sheila K. Pierson","orcid":"https://orcid.org/0000-0002-3736-1411","observed_orcids":["https://orcid.org/0000-0002-3736-1411"]},"institutions":[{"id":"https://openalex.org/I79576946","display_name":"University of Pennsylvania","ror":"https://ror.org/00b30xv10","country_code":"US","type":"education","lineage":["https://openalex.org/I79576946"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"Sheila K. Pierson","raw_affiliation_strings":["Center for Cytokine Storm Treatment and Laboratory, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Center for Cytokine Storm Treatment and Laboratory, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104","institution_ids":["https://openalex.org/I79576946"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5101526663","display_name":"Yue Ren","orcid":"https://orcid.org/0000-0001-6199-1715","observed_orcids":["https://orcid.org/0000-0001-6199-1715"]},"institutions":[{"id":"https://openalex.org/I79576946","display_name":"University of Pennsylvania","ror":"https://ror.org/00b30xv10","country_code":"US","type":"education","lineage":["https://openalex.org/I79576946"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Yue Ren","raw_affiliation_strings":["Department of Biostatistics, Epidemiology, and Informatics, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Biostatistics, Epidemiology, and Informatics, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104","institution_ids":["https://openalex.org/I79576946"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5089634995","display_name":"Adam Bagg","orcid":"https://orcid.org/0000-0002-1669-468X","observed_orcids":["https://orcid.org/0000-0002-1669-468X"]},"institutions":[{"id":"https://openalex.org/I79576946","display_name":"University of Pennsylvania","ror":"https://ror.org/00b30xv10","country_code":"US","type":"education","lineage":["https://openalex.org/I79576946"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Adam Bagg","raw_affiliation_strings":["Department of Pathology and Laboratory Medicine, University of Pennsylvania, Philadelphia, PA, 19104"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pathology and Laboratory Medicine, University of Pennsylvania, Philadelphia, PA, 19104","institution_ids":["https://openalex.org/I79576946"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5005196958","display_name":"Joshua D. Brandstadter","orcid":"https://orcid.org/0000-0003-0652-5791","observed_orcids":["https://orcid.org/0000-0003-0652-5791"]},"institutions":[{"id":"https://openalex.org/I79576946","display_name":"University of Pennsylvania","ror":"https://ror.org/00b30xv10","country_code":"US","type":"education","lineage":["https://openalex.org/I79576946"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Joshua D. Brandstadter","raw_affiliation_strings":["Division of Hematology/Oncology, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Hematology/Oncology, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104","institution_ids":["https://openalex.org/I79576946"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5070120524","display_name":"Gordan Srkalovi\u0107","orcid":"https://orcid.org/0000-0003-3519-0409","observed_orcids":["https://orcid.org/0000-0003-3519-0409"]},"institutions":[{"id":"https://openalex.org/I87216513","display_name":"Michigan State University","ror":"https://ror.org/05hs6h993","country_code":"US","type":"education","lineage":["https://openalex.org/I87216513"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Gordan Srkalovic","raw_affiliation_strings":["Sparrow Herbert-Herman Cancer Center, Michigan State University College of Human Medicine, Lansing, MI, 48912"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Sparrow Herbert-Herman Cancer Center, Michigan State University College of Human Medicine, Lansing, MI, 48912","institution_ids":["https://openalex.org/I87216513"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5092083368","display_name":"Natalie Mango","orcid":"https://orcid.org/0009-0003-1718-0490","observed_orcids":["https://orcid.org/0009-0003-1718-0490"]},"institutions":[{"id":"https://openalex.org/I79576946","display_name":"University of Pennsylvania","ror":"https://ror.org/00b30xv10","country_code":"US","type":"education","lineage":["https://openalex.org/I79576946"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Natalie Mango","raw_affiliation_strings":["Center for Cytokine Storm Treatment and Laboratory, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Center for Cytokine Storm Treatment and Laboratory, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104","institution_ids":["https://openalex.org/I79576946"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5079003235","display_name":"Daisy V. Alapat","orcid":"https://orcid.org/0000-0002-3414-8375","observed_orcids":["https://orcid.org/0000-0002-3414-8375"]},"institutions":[{"id":"https://openalex.org/I79620101","display_name":"University of Arkansas for Medical Sciences","ror":"https://ror.org/00xcryt71","country_code":"US","type":"education","lineage":["https://openalex.org/I79620101"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Daisy Alapat","raw_affiliation_strings":["Department of Pathology, College of Medicine, University of Arkansas for Medical Sciences, Little Rock, AR, 72205"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pathology, College of Medicine, University of Arkansas for Medical Sciences, Little Rock, AR, 72205","institution_ids":["https://openalex.org/I79620101"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5083914569","display_name":"Mary Jo Lechowicz","orcid":"https://orcid.org/0000-0003-1997-1950","observed_orcids":["https://orcid.org/0000-0003-1997-1950"]},"institutions":[{"id":"https://openalex.org/I150468666","display_name":"Emory University","ror":"https://ror.org/03czfpz43","country_code":"US","type":"education","lineage":["https://openalex.org/I150468666"]},{"id":"https://openalex.org/I4390039307","display_name":"Winship Cancer Institute","ror":"https://ror.org/02gars961","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I132943300","https://openalex.org/I150468666","https://openalex.org/I4390039307"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Mary Jo Lechowicz","raw_affiliation_strings":["Department of Hematology and Medical Oncology, Emory University School of Medicine and Winship Cancer Institute, Atlanta, GA, 30322"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology and Medical Oncology, Emory University School of Medicine and Winship Cancer Institute, Atlanta, GA, 30322","institution_ids":["https://openalex.org/I150468666","https://openalex.org/I4390039307"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5082318113","display_name":"Hongzhe Li","orcid":"https://orcid.org/0000-0003-3662-3907","observed_orcids":["https://orcid.org/0000-0003-3662-3907","https://orcid.org/0009-0005-7695-0533"]},"institutions":[{"id":"https://openalex.org/I79576946","display_name":"University of Pennsylvania","ror":"https://ror.org/00b30xv10","country_code":"US","type":"education","lineage":["https://openalex.org/I79576946"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Hongzhe Li","raw_affiliation_strings":["Department of Biostatistics, Epidemiology, and Informatics, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Biostatistics, Epidemiology, and Informatics, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104","institution_ids":["https://openalex.org/I79576946"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5090044223","display_name":"Frits van Rhee","orcid":"https://orcid.org/0000-0001-9959-1282","observed_orcids":["https://orcid.org/0000-0001-9959-1282"]},"institutions":[{"id":"https://openalex.org/I79620101","display_name":"University of Arkansas for Medical Sciences","ror":"https://ror.org/00xcryt71","country_code":"US","type":"education","lineage":["https://openalex.org/I79620101"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Frits Van Rhee","raw_affiliation_strings":["Myeloma Center, Winthrop P. Rockefeller Cancer Institute, University of Arkansas for Medical Sciences, Little Rock, AR, 72205"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Myeloma Center, Winthrop P. Rockefeller Cancer Institute, University of Arkansas for Medical Sciences, Little Rock, AR, 72205","institution_ids":["https://openalex.org/I79620101"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5041898934","display_name":"Megan S. Lim","orcid":"https://orcid.org/0000-0002-0415-2867","observed_orcids":["https://orcid.org/0000-0002-0415-2867"]},"institutions":[{"id":"https://openalex.org/I1334819555","display_name":"Memorial Sloan Kettering Cancer Center","ror":"https://ror.org/02yrq0923","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1334819555"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Megan S. Lim","raw_affiliation_strings":["Department of Pathology and Laboratory Medicine, Memorial Sloan Kettering Cancer Center, New York City, New York, 10065"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pathology and Laboratory Medicine, Memorial Sloan Kettering Cancer Center, New York City, New York, 10065","institution_ids":["https://openalex.org/I1334819555"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5015042510","display_name":"David C. Fajgenbaum","orcid":"https://orcid.org/0000-0002-7367-8184","observed_orcids":["https://orcid.org/0000-0002-7367-8184"]},"institutions":[{"id":"https://openalex.org/I79576946","display_name":"University of Pennsylvania","ror":"https://ror.org/00b30xv10","country_code":"US","type":"education","lineage":["https://openalex.org/I79576946"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"David C. Fajgenbaum","raw_affiliation_strings":["Center for Cytokine Storm Treatment and Laboratory, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104. davidfa@pennmedicine.upenn.edu","Center for Cytokine Storm Treatment and Laboratory, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Center for Cytokine Storm Treatment and Laboratory, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104. davidfa@pennmedicine.upenn.edu","institution_ids":["https://openalex.org/I79576946"]},{"raw_affiliation_string":"Center for Cytokine Storm Treatment and Laboratory, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104","institution_ids":["https://openalex.org/I79576946"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":6,"corresponding_author_ids":["https://openalex.org/A5015042510","https://openalex.org/A5055932729","https://openalex.org/A5062019448"],"corresponding_institution_ids":["https://openalex.org/I79576946"],"apc_list":{"value":2000,"currency":"EUR","value_usd":2157},"apc_paid":{"value":2000,"currency":"EUR","value_usd":2157},"fwci":4.3388,"has_fulltext":true,"cited_by_count":19,"citation_normalized_percentile":{"value":0.94944679,"is_in_top_1_percent":false,"is_in_top_10_percent":true},"cited_by_percentile_year":{"min":88,"max":99},"biblio":{"volume":"109","issue":"7","first_page":"2196","last_page":"2206"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11576","display_name":"IgG4-Related and Inflammatory Diseases","score":0.43849998712539673,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11576","display_name":"IgG4-Related and Inflammatory Diseases","score":0.43849998712539673,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.20350000262260437,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10685","display_name":"Viral-associated cancers and disorders","score":0.16539999842643738,"subfield":{"id":"https://openalex.org/subfields/2730","display_name":"Oncology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/idiopathic-multicentric-castleman-disease","display_name":"idiopathic multicentric Castleman disease","score":1.0},{"id":"https://openalex.org/keywords/disease-burden","display_name":"disease burden","score":0.781000018119812},{"id":"https://openalex.org/keywords/natural-history-disease","display_name":"natural history (disease)","score":0.9779999852180481},{"id":"https://openalex.org/keywords/tafro-syndrome","display_name":"TAFRO syndrome","score":0.8220000267028809},{"id":"https://openalex.org/keywords/hospitalization","display_name":"hospitalization","score":0.7599999904632568},{"id":"https://openalex.org/keywords/disease-flares","display_name":"disease flares","score":0.6740000247955322},{"id":"https://openalex.org/keywords/acute-kidney-injury","display_name":"acute kidney injury","score":0.7749999761581421},{"id":"https://openalex.org/keywords/sepsis","display_name":"sepsis","score":0.9670000076293945},{"id":"https://openalex.org/keywords/pneumonia","display_name":"pneumonia","score":0.9559999704360962},{"id":"https://openalex.org/keywords/dialysis","display_name":"dialysis","score":0.6990000009536743},{"id":"https://openalex.org/keywords/mechanical-ventilation","display_name":"mechanical ventilation","score":0.9819999933242798},{"id":"https://openalex.org/keywords/quality-of-life","display_name":"quality of life","score":0.9539999961853027}],"concepts":[{"id":"https://openalex.org/C2778551932","wikidata":"https://www.wikidata.org/wiki/Q285115","display_name":"Organomegaly","level":3,"score":0.9382692575454712},{"id":"https://openalex.org/C2776548574","wikidata":"https://www.wikidata.org/wiki/Q486485","display_name":"Anasarca","level":2,"score":0.9200741052627563},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8530165553092957},{"id":"https://openalex.org/C163276114","wikidata":"https://www.wikidata.org/wiki/Q484591","display_name":"Natural history","level":2,"score":0.7033397555351257},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.5595340132713318},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.5009720325469971},{"id":"https://openalex.org/C2776054410","wikidata":"https://www.wikidata.org/wiki/Q1947302","display_name":"Castleman disease","level":3,"score":0.45704489946365356}],"mesh":[{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000368","descriptor_name":"Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005871","descriptor_name":"Castleman Disease","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D005871","descriptor_name":"Castleman Disease","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":true},{"descriptor_ui":"D005871","descriptor_name":"Castleman Disease","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":true},{"descriptor_ui":"D005871","descriptor_name":"Castleman Disease","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":true},{"descriptor_ui":"D006760","descriptor_name":"Hospitalization","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008137","descriptor_name":"Longitudinal Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D012042","descriptor_name":"Registries","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D017281","descriptor_name":"Cost of Illness","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":5,"locations":[{"id":"doi:10.3324/haematol.2023.283603","doi":"https://doi.org/10.3324/haematol.2023.283603","is_oa":true,"landing_page_url":"https://doi.org/10.3324/haematol.2023.283603","pdf_url":"https://haematologica.org/article/download/haematol.2023.283603/76491","source":{"id":"https://openalex.org/S2752781272","display_name":"Haematologica","issn_l":"0390-6078","issn":["0390-6078","1592-8721"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","dongbi-a","doyens","jufo-2","ki-jl-2","medline","norway-2","oarl","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310317774","host_organization_name":"Ferrata Storti Foundation","host_organization_lineage":["https://openalex.org/P4310317774"],"host_organization_lineage_names":["Ferrata Storti Foundation"],"type":"journal"},"license":"cc-by-nc","license_id":"https://openalex.org/licenses/cc-by-nc","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Haematologica","raw_type":"journal-article"},{"id":"pmh:oai:pubmedcentral.nih.gov:11217716","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/11217716","pdf_url":"https://pmc.ncbi.nlm.nih.gov/articles/PMC11217716/pdf/1092196.pdf","source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-nc","license_id":"https://openalex.org/licenses/cc-by-nc","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Haematologica","raw_type":"Text"},{"id":"pmid:38205523","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/38205523","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Haematologica","raw_type":"Journal Article"},{"id":"pmh:oai:doaj.org/article:a0b5c548ab2a492e8be1f2a507e118d0","doi":null,"is_oa":true,"landing_page_url":"https://doaj.org/article/a0b5c548ab2a492e8be1f2a507e118d0","pdf_url":null,"source":{"id":"https://openalex.org/S4306401280","display_name":"DOAJ (DOAJ: Directory of Open Access Journals)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-sa","license_id":"https://openalex.org/licenses/cc-by-sa","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Haematologica, Vol 999, Iss 1 (2024)","raw_type":"article"},{"id":"pmh:oai:jupiter.its.unimelb.edu.au:11343/348916","doi":null,"is_oa":true,"landing_page_url":"https://hdl.handle.net/11343/348916","pdf_url":null,"source":{"id":"https://openalex.org/S4377196259","display_name":"Minerva Access (University of Melbourne)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I165779595","host_organization_name":"The University of Melbourne","host_organization_lineage":["https://openalex.org/I165779595"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-nc","license_id":"https://openalex.org/licenses/cc-by-nc","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":"Journal Article"}],"best_oa_location":{"id":"doi:10.3324/haematol.2023.283603","doi":"https://doi.org/10.3324/haematol.2023.283603","is_oa":true,"landing_page_url":"https://doi.org/10.3324/haematol.2023.283603","pdf_url":"https://haematologica.org/article/download/haematol.2023.283603/76491","source":{"id":"https://openalex.org/S2752781272","display_name":"Haematologica","issn_l":"0390-6078","issn":["0390-6078","1592-8721"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","dongbi-a","doyens","jufo-2","ki-jl-2","medline","norway-2","oarl","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310317774","host_organization_name":"Ferrata Storti Foundation","host_organization_lineage":["https://openalex.org/P4310317774"],"host_organization_lineage_names":["Ferrata Storti Foundation"],"type":"journal"},"license":"cc-by-nc","license_id":"https://openalex.org/licenses/cc-by-nc","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Haematologica","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":1.0}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[{"id":"https://openalex.org/G3799784065","display_name":null,"funder_award_id":"2018-2022","funder_id":"https://openalex.org/F4320330792","funder_display_name":"EUSA Pharma"},{"id":"https://openalex.org/G3847497847","display_name":null,"funder_award_id":"R01FD007632","funder_id":"https://openalex.org/F4320332163","funder_display_name":"U.S. Food and Drug Administration"},{"id":"https://openalex.org/G9000856728","display_name":"Cancer Center Support Grant","funder_award_id":"P30CA008748","funder_id":"https://openalex.org/F4320337351","funder_display_name":"National Cancer Institute"},{"id":"https://openalex.org/G9000892529","display_name":"JAK1/2 as a Central Regulator of iMCD Pathogenesis and Novel Therapeutic Target","funder_award_id":"R01HL141408","funder_id":"https://openalex.org/F4320337338","funder_display_name":"National Heart, Lung, and Blood Institute"}],"funders":[{"id":"https://openalex.org/F4320317461","display_name":"Recordati Rare Diseases","ror":"https://ror.org/00x68eg25"},{"id":"https://openalex.org/F4320330792","display_name":"EUSA Pharma","ror":"https://ror.org/01p7jrr32"},{"id":"https://openalex.org/F4320332163","display_name":"U.S. Food and Drug Administration","ror":"https://ror.org/034xvzb47"},{"id":"https://openalex.org/F4320337338","display_name":"National Heart, Lung, and Blood Institute","ror":"https://ror.org/012pb6c26"},{"id":"https://openalex.org/F4320337351","display_name":"National Cancer Institute","ror":"https://ror.org/040gcmg81"},{"id":"https://openalex.org/F4320337601","display_name":"Janssen Pharmaceuticals","ror":"https://ror.org/03qd7mz70"}],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W4390744583.pdf","grobid_xml":"https://content.openalex.org/works/W4390744583.grobid-xml"},"referenced_works_count":26,"referenced_works":["https://openalex.org/W1632068222","https://openalex.org/W2039067114","https://openalex.org/W2169031812","https://openalex.org/W2171799063","https://openalex.org/W2296827990","https://openalex.org/W2328705550","https://openalex.org/W2572250031","https://openalex.org/W2890680400","https://openalex.org/W2914866238","https://openalex.org/W2968883182","https://openalex.org/W3012641818","https://openalex.org/W3092636925","https://openalex.org/W3112902030","https://openalex.org/W3114598105","https://openalex.org/W3147692682","https://openalex.org/W3151324750","https://openalex.org/W3170481589","https://openalex.org/W3182651380","https://openalex.org/W3193351641","https://openalex.org/W3199859575","https://openalex.org/W4251550924","https://openalex.org/W4285292727","https://openalex.org/W4296794128","https://openalex.org/W4297990875","https://openalex.org/W4360873421","https://openalex.org/W4379281909"],"related_works":["https://openalex.org/W4310103285","https://openalex.org/W4297990875","https://openalex.org/W3211772795","https://openalex.org/W4281905115","https://openalex.org/W3097608910","https://openalex.org/W4417012332","https://openalex.org/W4405042741","https://openalex.org/W7154035329","https://openalex.org/W3211388776","https://openalex.org/W4391838472"],"abstract_inverted_index":{"Idiopathic":[0],"multicentric":[1],"Castleman":[2,91],"disease":[3,54,98,173,179,217,234],"(iMCD)":[4],"is":[5],"a":[6,83,110,166,176,215],"rare":[7],"hematologic":[8],"disorder":[9],"with":[10,29,50,90,160],"heterogeneous":[11],"presentations":[12],"ranging":[13],"from":[14,81],"moderate":[15,48],"constitutional":[16],"symptoms":[17,49],"to":[18,60,93,232],"life-threatening":[19],"multiorgan":[20],"system":[21],"involvement.":[22],"There":[23],"are":[24,73],"vastly":[25],"different":[26],"clinical":[27],"subtypes,":[28],"some":[30],"patients":[31,89,108,122,222],"demonstrating":[32],"thrombocytopenia,":[33],"anasarca,":[34],"fever/elevated":[35],"C-reactive":[36],"protein,":[37],"reticulin":[38],"fibrosis/renal":[39],"failure,":[40,196],"and":[41,44,63,68,150,198,223],"organomegaly":[42],"(TAFRO)":[43],"others":[45],"having":[46],"milder/more":[47],"potential":[51],"for":[52],"severe":[53,189],"(not":[55],"otherwise":[56],"specified,":[57],"NOS).":[58],"Due":[59],"its":[61],"rarity":[62],"heterogeneity,":[64],"the":[65,96,118,124,207,225],"natural":[66,85],"history":[67,86],"long-term":[69,97],"burden":[70,99,218],"of":[71,88,170,178,210,227],"iMCD":[72,156,204,221,231],"poorly":[74],"understood.":[75],"We":[76,104],"investigated":[77],"real-world":[78],"medical":[79],"data":[80,213],"ACCELERATE,":[82],"large":[84],"registry":[87],"disease,":[92],"better":[94],"characterize":[95],"experienced":[100,219],"by":[101,220],"these":[102],"patients.":[103],"found":[105,142],"that":[106],"iMCD-TAFRO":[107],"face":[109],"significant":[111],"hospitalization":[112],"burden,":[113],"requiring":[114],"more":[115],"time":[116,171],"in":[117,175],"hospital":[119],"than":[120],"iMCDNOS":[121],"during":[123],"year":[125],"surrounding":[126],"diagnosis":[127],"(median":[128,181],"[interquartile":[129],"range]:":[130],"36":[131],"[18-61]":[132],"days":[133],"vs.":[134,183],"0":[135],"[0-4]":[136],"days;":[137],"P<0.001).":[138],"In":[139],"addition,":[140],"we":[141,187],"life-sustaining":[143],"interventions,":[144],"such":[145,192],"as":[146,193],"mechanical":[147],"ventilation":[148],"(17%)":[149],"dialysis":[151],"(27%),":[152],"were":[153],"required":[154],"among":[155,200],"patients,":[157,163],"predominantly":[158],"those":[159],"iMCD-TAFRO.":[161],"iMCD-NOS":[162],"however,":[164],"spent":[165],"significantly":[167],"greater":[168],"proportion":[169],"following":[172],"onset":[174],"state":[177],"flare":[180],"52.3%":[182],"18.9%;":[184],"P=0.004).":[185],"Lastly,":[186],"observed":[188],"iMCD-related":[190],"morbidities,":[191],"acute":[194],"renal":[195],"sepsis":[197],"pneumonia,":[199],"others,":[201],"arising":[202],"after":[203],"diagnosis,":[205],"impairing":[206],"patients'":[208],"quality":[209],"life.":[211],"These":[212],"demonstrate":[214],"substantial":[216],"emphasize":[224],"importance":[226],"ongoing":[228],"research":[229],"into":[230],"aid":[233],"control.":[235]},"counts_by_year":[{"year":2026,"cited_by_count":7},{"year":2025,"cited_by_count":5},{"year":2024,"cited_by_count":6},{"year":2020,"cited_by_count":1}],"updated_date":"2026-11-12T12:28:57.059296","created_date":"2024-01-13T00:00:00"}
