{"id":"https://openalex.org/W4389465166","doi":"https://doi.org/10.1212/wnl.92.15_supplement.p5.6-035","title":"Clinical and radiographic mismatch in fat embolism syndrome in hemoglobin SC disease (P5.6-035)","display_name":"Clinical and radiographic mismatch in fat embolism syndrome in hemoglobin SC disease (P5.6-035)","publication_year":2019,"publication_date":"2019-04-09","ids":{"openalex":"https://openalex.org/W4389465166","doi":"https://doi.org/10.1212/wnl.92.15_supplement.p5.6-035"},"language":"en","primary_location":{"id":"doi:10.1212/wnl.92.15_supplement.p5.6-035","doi":"https://doi.org/10.1212/wnl.92.15_supplement.p5.6-035","is_oa":false,"landing_page_url":"http://dx.doi.org/10.1212/wnl.92.15_supplement.p5.6-035","pdf_url":null,"source":{"id":"https://openalex.org/S79704628","display_name":"Neurology","issn_l":"0028-3878","issn":["0028-3878","1526-632X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315671","host_organization_name":"Lippincott Williams & Wilkins","host_organization_lineage":["https://openalex.org/P4310315671","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Lippincott Williams & Wilkins","Wolters Kluwer"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Neurology","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5093444964","display_name":"Shahla Moghbel","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2802534011","display_name":"MedStar Georgetown University Hospital","ror":"https://ror.org/03ja1ak26","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I2802534011","https://openalex.org/I86755215"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Shahla Moghbel","raw_affiliation_strings":["Neurology, Medstar Georgetown University Hospital Washington DC United States"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Neurology, Medstar Georgetown University Hospital Washington DC United States","institution_ids":["https://openalex.org/I2802534011"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5076019069","display_name":"Arathi S. Nandyala","orcid":"https://orcid.org/0000-0001-7907-8676","observed_orcids":["https://orcid.org/0000-0001-7907-8676"]},"institutions":[{"id":"https://openalex.org/I2613432","display_name":"University of South Florida","ror":"https://ror.org/032db5x82","country_code":"US","type":"education","lineage":["https://openalex.org/I2613432"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Arathi Nandyala","raw_affiliation_strings":["University of South Florida College of Medicine Tampa FL United States"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of South Florida College of Medicine Tampa FL United States","institution_ids":["https://openalex.org/I2613432"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5033473555","display_name":"Steven E. Lo","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2802534011","display_name":"MedStar Georgetown University Hospital","ror":"https://ror.org/03ja1ak26","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I2802534011","https://openalex.org/I86755215"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Steven Lo","raw_affiliation_strings":["Medstar Georgetown University Hospital Washington DC United States"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Medstar Georgetown University Hospital Washington DC United States","institution_ids":["https://openalex.org/I2802534011"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"92","issue":"15_supplement","first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10554","display_name":"Hemoglobinopathies and Related Disorders","score":0.9976000189781189,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10554","display_name":"Hemoglobinopathies and Related Disorders","score":0.9976000189781189,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12845","display_name":"Methemoglobinemia and Tumor Lysis Syndrome","score":0.00019999999494757503,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10227","display_name":"Acute Ischemic Stroke Management","score":9.999999747378752e-05,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/fat-embolism-syndrome","display_name":"fat embolism syndrome","score":0.9980000257492065},{"id":"https://openalex.org/keywords/hemoglobin-sc-disease","display_name":"hemoglobin SC disease","score":0.9879999756813049},{"id":"https://openalex.org/keywords/sickle-cell-disease","display_name":"sickle cell disease","score":0.921999990940094},{"id":"https://openalex.org/keywords/brain-mri","display_name":"brain MRI","score":0.6420000195503235},{"id":"https://openalex.org/keywords/susceptibility-weighted-imaging","display_name":"susceptibility-weighted imaging","score":0.8479999899864197},{"id":"https://openalex.org/keywords/restricted-diffusion","display_name":"restricted diffusion","score":0.8050000071525574},{"id":"https://openalex.org/keywords/cerebral-edema","display_name":"cerebral edema","score":0.6850000023841858},{"id":"https://openalex.org/keywords/microhemorrhages","display_name":"microhemorrhages","score":0.8259999752044678},{"id":"https://openalex.org/keywords/exchange-transfusion","display_name":"exchange transfusion","score":0.8840000033378601},{"id":"https://openalex.org/keywords/retinal-angiography","display_name":"retinal angiography","score":0.6499999761581421},{"id":"https://openalex.org/keywords/vaso-occlusive-crisis","display_name":"vaso-occlusive crisis","score":0.7229999899864197},{"id":"https://openalex.org/keywords/vegetative-state","display_name":"vegetative state","score":0.5720000267028809}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.7754557132720947},{"id":"https://openalex.org/C2909315519","wikidata":"https://www.wikidata.org/wiki/Q950760","display_name":"Fat embolism syndrome","level":3,"score":0.6703638434410095},{"id":"https://openalex.org/C36454342","wikidata":"https://www.wikidata.org/wiki/Q245341","display_name":"Radiography","level":2,"score":0.5972853899002075},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.4951907694339752},{"id":"https://openalex.org/C2778917026","wikidata":"https://www.wikidata.org/wiki/Q43041","display_name":"Hemoglobin","level":2,"score":0.45932409167289734},{"id":"https://openalex.org/C126838900","wikidata":"https://www.wikidata.org/wiki/Q77604","display_name":"Radiology","level":1,"score":0.3980496823787689},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.33203497529029846},{"id":"https://openalex.org/C2778298768","wikidata":"https://www.wikidata.org/wiki/Q950760","display_name":"Fat embolism","level":2,"score":0.25550055503845215}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.1212/wnl.92.15_supplement.p5.6-035","doi":"https://doi.org/10.1212/wnl.92.15_supplement.p5.6-035","is_oa":false,"landing_page_url":"http://dx.doi.org/10.1212/wnl.92.15_supplement.p5.6-035","pdf_url":null,"source":{"id":"https://openalex.org/S79704628","display_name":"Neurology","issn_l":"0028-3878","issn":["0028-3878","1526-632X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315671","host_organization_name":"Lippincott Williams & Wilkins","host_organization_lineage":["https://openalex.org/P4310315671","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Lippincott Williams & Wilkins","Wolters Kluwer"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Neurology","raw_type":"journal-article"}],"best_oa_location":null,"sustainable_development_goals":[{"score":1.0,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W2599921221","https://openalex.org/W4319294343","https://openalex.org/W3205998639","https://openalex.org/W2507806713","https://openalex.org/W3036727134","https://openalex.org/W2794332261","https://openalex.org/W7128920753","https://openalex.org/W7165624339","https://openalex.org/W2901864536","https://openalex.org/W2009675325"],"abstract_inverted_index":{"Objective:":[0],"NA":[1],"Background:":[2],"Fat":[3],"embolism":[4,211,238],"syndrome":[5,239],"has":[6,252,304,310,316],"been":[7,58,229,253],"reported":[8,129,230],"mostly":[9],"in":[10,18,221,231,259,291,296],"cases":[11],"of":[12,31,41,44,65,111,198,264,287],"long":[13],"bone":[14,22],"fractures":[15],"and":[16,91,106,144,201,204,215,284,295],"rarely":[17],"hemoglobinopathies":[19],"due":[20],"to":[21,151,255,306,312,318],"marrow":[23,181],"infarction.":[24],"Nevertheless,":[25],"it":[26],"encompasses":[27],"a":[28,63,66,261,292],"wide":[29],"range":[30],"multi-organ":[32],"complications,":[33],"including":[34,131],"neurological,":[35],"with":[36,50,71,74,116,138,209,236,243],"devastating":[37],"outcome.":[38],"MRI":[39,123,189,290],"findings":[40],"\u201cstarfield":[42],"\u201cpattern":[43],"innumerable":[45],"restricted":[46,199],"diffusion":[47,200],"punctate":[48,196],"foci":[49,197],"concordant":[51],"decreased":[52],"signal":[53],"on":[54,190],"ADC":[55],"map":[56],"have":[57,228],"reported.":[59],"Design/Methods:":[60],"We":[61],"report":[62],"case":[64,270],"40-year":[67],"old":[68],"Nigerian":[69],"male":[70],"hemoglobin":[72,170],"SC":[73,171],"no":[75],"previous":[76],"crisis":[77],"or":[78],"complications":[79],"who":[80,240],"develops":[81],"acute":[82,117],"painful":[83],"episodes":[84],"likely":[85],"vaso-occlusive":[86],"pain":[87],"minutes":[88],"after":[89,281],"fluorescein":[90],"indocyanine":[92],"dye":[93],"injection":[94],"for":[95,156],"retinal":[96,100],"angiography":[97],"status":[98],"post":[99],"detachment":[101],"repair,":[102],"requiring":[103,120],"PCA":[104],"pump":[105],"hospitalization.":[107],"Within":[108],"1":[109],"day":[110,191],"hospitalization,":[112],"he":[113],"became":[114],"unresponsive":[115],"respiratory":[118],"failure":[119],"intubation.":[121],"Results:":[122],"brain":[124,188,289],"at":[125],"7.5":[126],"hour":[127],"was":[128,136,148],"insignificant":[130],"susceptibility":[132,249,274],"weighted":[133,250,275],"images.":[134],"EEG":[135],"consistent":[137,208],"diffuse":[139,194,205],"encephalopathy.":[140],"He":[141],"developed":[142],"anemia":[143],"severe":[145],"thrombocytopenia.":[146],"Patient":[147],"then":[149],"transferred":[150],"our":[152,269],"institution.":[153],"Empiric":[154],"antibiotics":[155],"possible":[157],"CNS":[158],"infection":[159],"were":[160,165],"initiated.":[161],"CSF":[162],"studies":[163],"however":[164],"grossly":[166],"unremarkable.":[167],"Electrophoresis":[168],"confirmed":[169],"disease.":[172],"Peripheral":[173],"smear":[174],"showed":[175,183,193],"numerous":[176,195,202],"immature":[177],"nucleated":[178],"RBCs.":[179],"Bone":[180],"biopsy":[182],"extensive":[184],"fat":[185,210,237],"necrosis.":[186],"Repeat":[187],"12":[192],"microhemorrhages":[203],"cerebral":[206],"edema":[207],"syndrome.":[212],"Despite":[213],"RBC":[214],"multiple":[216],"exchange":[217,246],"transfusions,":[218],"patient":[219],"remained":[220],"persistent":[222],"vegetative":[223],"state.":[224],"Conclusions:":[225],"Successful":[226],"outcomes":[227],"sickle":[232],"cell":[233],"disease":[234],"patients":[235],"are":[241],"treated":[242],"early":[244],"aggressive":[245],"transfusions.":[247],"Furthermore,":[248],"imaging":[251,276],"shown":[254],"be":[256,278],"very":[257],"sensitive":[258],"detecting":[260],"small":[262],"amounts":[263],"deoxygenated":[265],"blood":[266],"products.":[267],"However,":[268],"demonstrates":[271],"that":[272],"the":[273,285,297],"can":[277],"normal":[279],"hours":[280],"initial":[282],"insult":[283],"importance":[286],"repeating":[288],"timely":[293],"manner":[294],"appropriate":[298],"clinical":[299],"setting.":[300],"Disclosure:":[301],"Dr.":[302,308,314],"Moghbel":[303],"nothing":[305,311,317],"disclose.":[307,313,319],"Nandyala":[309],"Lo":[315]},"counts_by_year":[],"updated_date":"2026-11-08T12:12:28.789561","created_date":"2023-12-08T00:00:00"}
