{"id":"https://openalex.org/W4387967772","doi":"https://doi.org/10.4103/idoj.idoj_692_22","title":"Barraquer-Simons Syndrome: An Unusual Form of Acquired Partial Lipodystrophy in a Child with Lupus Nephritis","display_name":"Barraquer-Simons Syndrome: An Unusual Form of Acquired Partial Lipodystrophy in a Child with Lupus Nephritis","publication_year":2023,"publication_date":"2023-09-11","ids":{"openalex":"https://openalex.org/W4387967772","doi":"https://doi.org/10.4103/idoj.idoj_692_22","pmid":"https://pubmed.ncbi.nlm.nih.gov/38099047","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/10718111"},"language":"en","primary_location":{"id":"doi:10.4103/idoj.idoj_692_22","doi":"https://doi.org/10.4103/idoj.idoj_692_22","is_oa":true,"landing_page_url":"https://doi.org/10.4103/idoj.idoj_692_22","pdf_url":null,"source":{"id":"https://openalex.org/S2754097677","display_name":"Indian Dermatology Online Journal","issn_l":"2229-5178","issn":["2229-5178","2249-5673"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-d","doyens","ki-jl-1","poland-20","russia-white-list-3"],"host_organization":"https://openalex.org/P4310320448","host_organization_name":"Medknow","host_organization_lineage":["https://openalex.org/P4310320448","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Medknow","Wolters Kluwer"],"type":"journal"},"license":"cc-by-nc-sa","license_id":"https://openalex.org/licenses/cc-by-nc-sa","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Indian Dermatology Online Journal","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj","pubmed"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://doi.org/10.4103/idoj.idoj_692_22","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5109649987","display_name":"Nirjhar Mondal","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210100047","display_name":"Institute of Post Graduate Medical Education and Research","ror":"https://ror.org/00ysvbp68","country_code":"IN","type":"education","lineage":["https://openalex.org/I226431899","https://openalex.org/I4210100047"]}],"countries":["IN"],"is_corresponding":true,"raw_author_name":"Nirjhar Mondal","raw_affiliation_strings":["Department of Dermatology, IPGME and R, SSKM Hospital, Kolkata, West Bengal, India","This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Dermatology, IPGME and R, SSKM Hospital, Kolkata, West Bengal, India","institution_ids":["https://openalex.org/I4210100047"]},{"raw_affiliation_string":"This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms","institution_ids":[]}]},{"author_position":"middle","author":{"id":null,"display_name":"Sudip Mandal","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210100047","display_name":"Institute of Post Graduate Medical Education and Research","ror":"https://ror.org/00ysvbp68","country_code":"IN","type":"education","lineage":["https://openalex.org/I226431899","https://openalex.org/I4210100047"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"Sudip Mandal","raw_affiliation_strings":["Department of Dermatology, IPGME and R, SSKM Hospital, Kolkata, West Bengal, India","This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Dermatology, IPGME and R, SSKM Hospital, Kolkata, West Bengal, India","institution_ids":["https://openalex.org/I4210100047"]},{"raw_affiliation_string":"This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5011591516","display_name":"Pramit Nandy","orcid":"https://orcid.org/0000-0003-1535-6803","observed_orcids":["https://orcid.org/0000-0003-1535-6803"]},"institutions":[{"id":"https://openalex.org/I4210100047","display_name":"Institute of Post Graduate Medical Education and Research","ror":"https://ror.org/00ysvbp68","country_code":"IN","type":"education","lineage":["https://openalex.org/I226431899","https://openalex.org/I4210100047"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"Pramit Nandy","raw_affiliation_strings":["Department of Dermatology, IPGME and R, SSKM Hospital, Kolkata, West Bengal, India","This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Dermatology, IPGME and R, SSKM Hospital, Kolkata, West Bengal, India","institution_ids":["https://openalex.org/I4210100047"]},{"raw_affiliation_string":"This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5035399170","display_name":"Biswanath Naskar","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210100047","display_name":"Institute of Post Graduate Medical Education and Research","ror":"https://ror.org/00ysvbp68","country_code":"IN","type":"education","lineage":["https://openalex.org/I226431899","https://openalex.org/I4210100047"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"Biswanath Naskar","raw_affiliation_strings":["Department of Dermatology, IPGME and R, SSKM Hospital, Kolkata, West Bengal, India","This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Dermatology, IPGME and R, SSKM Hospital, Kolkata, West Bengal, India","institution_ids":["https://openalex.org/I4210100047"]},{"raw_affiliation_string":"This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms","institution_ids":[]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":["https://openalex.org/A5109649987"],"corresponding_institution_ids":["https://openalex.org/I4210100047"],"apc_list":null,"apc_paid":null,"fwci":0.1742,"has_fulltext":true,"cited_by_count":1,"citation_normalized_percentile":{"value":0.51366039,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":89,"max":93},"biblio":{"volume":"14","issue":"6","first_page":"890","last_page":"892"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10308","display_name":"Systemic Lupus Erythematosus Research","score":0.9390000104904175,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10308","display_name":"Systemic Lupus Erythematosus Research","score":0.9390000104904175,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11330","display_name":"Systemic Sclerosis and Related Diseases","score":0.0142000000923872,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12421","display_name":"Adrenal Hormones and Disorders","score":0.008799999952316284,"subfield":{"id":"https://openalex.org/subfields/2712","display_name":"Endocrinology, Diabetes and Metabolism"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/barraquer-simons-syndrome","display_name":"Barraquer-Simons syndrome","score":0.9980000257492065},{"id":"https://openalex.org/keywords/partial-lipodystrophy","display_name":"partial lipodystrophy","score":0.9390000104904175},{"id":"https://openalex.org/keywords/lupus-nephritis","display_name":"lupus nephritis","score":0.9470000267028809},{"id":"https://openalex.org/keywords/pediatric-systemic-lupus-erythematosus","display_name":"pediatric lupus","score":0.8870000243186951},{"id":"https://openalex.org/keywords/subcutaneous-fat-reduction","display_name":"subcutaneous fat loss","score":0.8069999814033508},{"id":"https://openalex.org/keywords/proximal-myopathy","display_name":"proximal myopathy","score":0.7749999761581421},{"id":"https://openalex.org/keywords/insulin-resistance","display_name":"insulin resistance","score":0.5149999856948853},{"id":"https://openalex.org/keywords/anti-dsdna-antibodies","display_name":"anti-dsDNA antibodies","score":0.5}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9315228462219238},{"id":"https://openalex.org/C2779123688","wikidata":"https://www.wikidata.org/wiki/Q421094","display_name":"Hydroxychloroquine","level":5,"score":0.7527685165405273},{"id":"https://openalex.org/C2779912601","wikidata":"https://www.wikidata.org/wiki/Q1621830","display_name":"Lupus nephritis","level":3,"score":0.5102071762084961},{"id":"https://openalex.org/C2909029107","wikidata":"https://www.wikidata.org/wiki/Q219102","display_name":"Cushingoid","level":2,"score":0.5020854473114014},{"id":"https://openalex.org/C2778751314","wikidata":"https://www.wikidata.org/wiki/Q681160","display_name":"Dermatomyositis","level":2,"score":0.49787068367004395},{"id":"https://openalex.org/C2780941825","wikidata":"https://www.wikidata.org/wiki/Q1538213","display_name":"Lipodystrophy","level":5,"score":0.48707249760627747},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.4804077446460724},{"id":"https://openalex.org/C2779546735","wikidata":"https://www.wikidata.org/wiki/Q3500973","display_name":"Lipoatrophy","level":5,"score":0.47611814737319946},{"id":"https://openalex.org/C2776912625","wikidata":"https://www.wikidata.org/wiki/Q1485","display_name":"Systemic lupus erythematosus","level":3,"score":0.4590766131877899},{"id":"https://openalex.org/C2776715498","wikidata":"https://www.wikidata.org/wiki/Q11426176","display_name":"Prednisolone","level":2,"score":0.44107598066329956},{"id":"https://openalex.org/C527108885","wikidata":"https://www.wikidata.org/wiki/Q835153","display_name":"Physical examination","level":2,"score":0.4192083477973938},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.3627723455429077},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.3351421356201172},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.17813122272491455},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.0},{"id":"https://openalex.org/C2993143319","wikidata":"https://www.wikidata.org/wiki/Q583050","display_name":"Antiretroviral therapy","level":4,"score":0.0},{"id":"https://openalex.org/C3008058167","wikidata":"https://www.wikidata.org/wiki/Q84263196","display_name":"Coronavirus disease 2019 (COVID-19)","level":4,"score":0.0},{"id":"https://openalex.org/C524204448","wikidata":"https://www.wikidata.org/wiki/Q788926","display_name":"Infectious disease (medical specialty)","level":3,"score":0.0},{"id":"https://openalex.org/C142462285","wikidata":"https://www.wikidata.org/wiki/Q2528140","display_name":"Viral load","level":3,"score":0.0},{"id":"https://openalex.org/C3013748606","wikidata":"https://www.wikidata.org/wiki/Q15787","display_name":"Human immunodeficiency virus (HIV)","level":2,"score":0.0}],"mesh":[],"locations_count":4,"locations":[{"id":"doi:10.4103/idoj.idoj_692_22","doi":"https://doi.org/10.4103/idoj.idoj_692_22","is_oa":true,"landing_page_url":"https://doi.org/10.4103/idoj.idoj_692_22","pdf_url":null,"source":{"id":"https://openalex.org/S2754097677","display_name":"Indian Dermatology Online Journal","issn_l":"2229-5178","issn":["2229-5178","2249-5673"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-d","doyens","ki-jl-1","poland-20","russia-white-list-3"],"host_organization":"https://openalex.org/P4310320448","host_organization_name":"Medknow","host_organization_lineage":["https://openalex.org/P4310320448","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Medknow","Wolters Kluwer"],"type":"journal"},"license":"cc-by-nc-sa","license_id":"https://openalex.org/licenses/cc-by-nc-sa","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Indian Dermatology Online Journal","raw_type":"journal-article"},{"id":"pmh:oai:pubmedcentral.nih.gov:10718111","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/10718111","pdf_url":"https://pmc.ncbi.nlm.nih.gov/articles/PMC10718111/pdf/IDOJ-14-890.pdf","source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-nc-sa","license_id":"https://openalex.org/licenses/cc-by-nc-sa","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Indian Dermatol Online J","raw_type":"Text"},{"id":"pmid:38099047","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/38099047","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Indian dermatology online journal","raw_type":"Journal Article"},{"id":"pmh:oai:doaj.org/article:079d6691f1604fc094253efb7c360e44","doi":null,"is_oa":true,"landing_page_url":"https://doaj.org/article/079d6691f1604fc094253efb7c360e44","pdf_url":null,"source":{"id":"https://openalex.org/S4306401280","display_name":"DOAJ (DOAJ: Directory of Open Access Journals)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-sa","license_id":"https://openalex.org/licenses/cc-by-sa","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Indian Dermatology Online Journal, Vol 14, Iss 6, Pp 890-892 (2023)","raw_type":"article"}],"best_oa_location":{"id":"doi:10.4103/idoj.idoj_692_22","doi":"https://doi.org/10.4103/idoj.idoj_692_22","is_oa":true,"landing_page_url":"https://doi.org/10.4103/idoj.idoj_692_22","pdf_url":null,"source":{"id":"https://openalex.org/S2754097677","display_name":"Indian Dermatology Online Journal","issn_l":"2229-5178","issn":["2229-5178","2249-5673"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-d","doyens","ki-jl-1","poland-20","russia-white-list-3"],"host_organization":"https://openalex.org/P4310320448","host_organization_name":"Medknow","host_organization_lineage":["https://openalex.org/P4310320448","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Medknow","Wolters Kluwer"],"type":"journal"},"license":"cc-by-nc-sa","license_id":"https://openalex.org/licenses/cc-by-nc-sa","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Indian Dermatology Online Journal","raw_type":"journal-article"},"sustainable_development_goals":[{"score":1.0,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W4387967772.pdf","grobid_xml":"https://content.openalex.org/works/W4387967772.grobid-xml"},"referenced_works_count":6,"referenced_works":["https://openalex.org/W1998985018","https://openalex.org/W2027542164","https://openalex.org/W2528176296","https://openalex.org/W2778285506","https://openalex.org/W4230281200","https://openalex.org/W4249944699"],"related_works":["https://openalex.org/W2408935969","https://openalex.org/W2001755576","https://openalex.org/W2908132904","https://openalex.org/W2297511804","https://openalex.org/W2018904159","https://openalex.org/W4400056462","https://openalex.org/W2469205311","https://openalex.org/W2143834835","https://openalex.org/W2947028548","https://openalex.org/W3146799365"],"abstract_inverted_index":{"Dear":[0],"Editor,":[1],"The":[2,46,60,138,177,191,318,407,441,520,535,642],"Barraquer\u2013Simons":[3],"syndrome":[4,330,395,529,558,624],"is":[5,22,32,420,537,552,562,617],"a":[6,49,53,74,81,371,378,581,618],"rare":[7,372],"type":[8],"of":[9,17,28,58,76,113,117,124,156,168,179,188,197,225,253,264,269,337,374,381,410,433,475,490,494,507,516,522,533,544,576,584,593,596,610,639,644,677,683],"partial":[10,78,350,398,418,518],"symmetric":[11],"lipodystrophy":[12,79,362,368,399,419,476],"characterized":[13,376],"by":[14,377,436],"the":[15,29,99,121,189,332,348,471,513,542,545,591,645,669],"loss":[16,116,167,413],"subcutaneous":[18,169],"adipose":[19,382],"tissue":[20,38,383,455],"and":[21,44,67,107,110,127,136,153,175,185,218,221,245,280,285,296,314,322,341,404,428,452,462,478,492,504,547,571,574,604,625,655,673],"primarily":[23,400,563],"limited":[24],"to":[25,55,98,327,357,512,526,541,568,636,648],"upper":[26],"part":[27,123],"body.":[30,190],"It":[31],"often":[33,63,538],"associated":[34,445,498],"with":[35,52,83,91,105,115,143,256,416,431,446,608],"autoimmune":[36,453],"connective":[37,454],"disorders":[39,375,456],"like":[40,389,457],"systemic":[41,458,577],"lupus":[42,84,93,207,459,499,613],"erythematosus":[43],"dermatomyositis.[1]":[45],"condition":[47,442,546,654],"has":[48,587,656],"female":[50,54],"predisposition":[51],"male":[56,88],"ratio":[57],"4:1.[2]":[59],"affected":[61],"patients":[62,415,626],"have":[64,438],"insulin":[65],"resistance":[66],"other":[68,226,365,386,479,495,531],"metabolic":[69,447,594],"complications.":[70,578],"Here,":[71],"we":[72],"describe":[73],"case":[75],"acquired":[77,397,417,517],"in":[80,364,414,622,668],"child":[82,89,139,192],"nephritis.":[85,614],"A":[86],"11\u2013year-old":[87],"diagnosed":[90],"focal":[92],"nephritis":[94,208],"class":[95],"III":[96],"presented":[97],"skin":[100],"out":[101],"patient":[102,599,640,646],"department":[103],"(OPD)":[104],"muscle":[106],"joint":[108,213],"pain":[109],"progressive":[111],"swelling":[112],"face":[114,491],"fat":[118,170,180,338,412],"predominantly":[119],"from":[120,172,201,339,530],"lower":[122,186],"face,":[125],"cheek,":[126],"temple":[128,342],"area":[129],"for":[130,206,310,556,590,612,631],"last":[131],"six":[132],"months":[133],"[Figures":[134],"1":[135],"2].":[137],"was":[140,166,228,238,248,307,316,600],"on":[141],"treatment":[142,555,592],"prednisolone":[144],"35":[145],"mg,":[146,149,152],"hydroxychloroquine":[147],"200":[148],"enalapril":[150],"5":[151],"monthly":[154],"injection":[155],"cyclophosphamide":[157],"at":[158,565],"500":[159],"mg/m2":[160],"dose.":[161],"On":[162,230],"clinical":[163,320,514],"examination,":[164],"there":[165],"pad":[171],"bilateral":[173,276],"cheek":[174],"temples.":[176],"repartition":[178],"did":[181],"not":[182,664],"affect":[183],"trunk":[184],"parts":[187],"had":[193,212],"developed":[194],"some":[195],"degree":[196],"cushingoid":[198],"body":[199,354,366,496],"habitus":[200,355],"long-standing":[202],"oral":[203],"steroid":[204,359],"therapy":[205,509],"[Figure":[209],"3].":[210],"He":[211],"tenderness":[214],"involving":[215,275],"both":[216],"small":[217],"large":[219],"joints":[220],"proximal":[222],"myopathy.":[223,265],"Examination":[224],"systems":[227],"unremarkable.":[229],"biochemical":[231,323],"evaluation,":[232],"anti":[233],"nuclear":[234],"antibody":[235],"test":[236],"(ANA)":[237],"positive":[239],"4+":[240],"(1:160":[241],"titer)":[242],"homogenous":[243],"pattern":[244],"anti-ds":[246],"DNA":[247],"positive.":[249],"Echocardiography":[250],"revealed":[251],"chink":[252],"pericardial":[254],"effusion":[255],"mild":[257],"aortic":[258],"regurgitation.":[259],"Electromyography":[260],"features":[261],"were":[262,288,300],"suggestive":[263],"Magnetic":[266],"resonance":[267],"imaging":[268],"brain":[270],"showed":[271],"symmetrical":[272],"confluent":[273],"calcification":[274],"lentiform":[277],"nuclei,":[278],"thalamus,":[279],"cerebral":[281],"gyri.":[282],"Serum":[283,304],"urea":[284],"creatinine":[286],"levels":[287],"marginally":[289],"elevated.":[290],"Lipid":[291],"profile,":[292],"liver":[293],"function":[294],"test,":[295],"blood":[297],"glucose":[298],"level":[299,306],"within":[301],"normal":[302],"limit.":[303],"C3":[305,429,502,524],"low.":[308],"Serology":[309],"hepatitis":[311],"B,":[312],"C,":[313],"HIV":[315],"negative.":[317],"overall":[319],"presentation":[321],"parameters":[324],"led":[325,510],"us":[326,511],"consider":[328],"Barraquer-Simons":[329,394,528,557,623],"as":[331],"main":[333],"diagnosis.Figure":[334],"1:":[335],"Loss":[336],"check":[340],"areaFigure":[343],"2:":[344],"Lateral":[345],"view":[346],"showing":[347],"characteristic":[349],"lipodystrophyFigure":[351],"3:":[352],"Cushingoid":[353],"due":[356,635],"prolonged":[358],"therapy,":[360],"no":[361,553,681],"seen":[363],"partsThe":[367],"syndromes":[369],"constitute":[370],"group":[373],"selective":[379,411],"deficiency":[380],"without":[384],"any":[385],"explainable":[387],"cause":[388,474],"inflammation":[390],"or":[391,396],"nutritional":[392],"deficiency.[3,4]":[393],"occurs":[401],"among":[402],"children":[403],"young":[405],"adults.":[406],"exact":[408],"pathogenesis":[409],"largely":[421],"unknown.":[422],"However,":[423],"alternate":[424],"complement":[425],"pathway":[426],"activation":[427],"hypocomplementemia":[430],"lysis":[432],"adipocytes":[434],"induced":[435],"C3NeF":[437],"been":[439,588,657],"implicated.[5]":[440],"can":[443],"be":[444,665],"syndrome,":[448],"acanthosis":[449],"nigricans,":[450],"hirsutism,":[451],"erythematosus,":[460],"dermatomyositis,":[461],"localized":[463],"scleroderma.":[464],"Currently,":[465],"highly":[466],"active":[467],"antiretroviral":[468,508],"therapies":[469],"are":[470,481,680],"most":[472],"common":[473],"worldwide":[477],"causes":[480],"much":[482],"rarer.":[483],"In":[484],"our":[485],"case,":[486],"childhood":[487],"onset,":[488],"involvement":[489,616],"sparing":[493],"parts,":[497],"nephritis,":[500],"low":[501,523],"level,":[503],"negative":[505],"history":[506],"diagnosis":[515,536,573],"lipodystrophy.":[519,534,597],"presence":[521],"helps":[525],"differentiate":[527],"forms":[532],"difficult":[539],"owing":[540],"rarity":[543],"its":[548],"insidious":[549],"course.":[550],"There":[551,679],"effective":[554],"currently.":[559],"Therapeutic":[560],"approach":[561],"aimed":[564],"plastic":[566],"surgery":[567],"improve":[569],"aesthetics":[570],"early":[572],"management":[575],"Recently,":[579],"metreleptin,":[580],"recombinant":[582],"analogue":[583],"human":[585],"leptin,":[586],"approved":[589],"derangements":[595],"Our":[598],"prescribed":[601],"hypolipidemic":[602],"diet":[603],"regular":[605],"exercise":[606],"along":[607],"continuation":[609],"medications":[611],"Renal":[615],"major":[619],"prognostic":[620],"factor":[621],"may":[627],"require":[628],"renal":[629,633],"transplantation":[630],"end-stage":[632],"disease":[634],"glomerulonephritis.":[637],"Declaration":[638],"consent":[641],"guardian":[643],"consented":[647],"publish":[649],"data":[650],"regarding":[651],"his":[652,660],"medical":[653],"assured":[658],"that":[659],"child's":[661],"identity":[662],"will":[663],"disclosed":[666],"anywhere":[667],"process.":[670],"Financial":[671],"support":[672],"sponsorship":[674],"Nil.":[675],"Conflicts":[676],"interest":[678],"conflicts":[682],"interest.":[684]},"counts_by_year":[{"year":2025,"cited_by_count":1}],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2023-10-28T00:00:00"}