{"id":"https://openalex.org/W4385398277","doi":"https://doi.org/10.1136/jnis-2023-snis.231","title":"E-131 The association between moyamoya disease and coexisting autoimmune conditions: overview of clinical and epidemiological characteristics","display_name":"E-131 The association between moyamoya disease and coexisting autoimmune conditions: overview of clinical and epidemiological characteristics","publication_year":2023,"publication_date":"2023-07-01","ids":{"openalex":"https://openalex.org/W4385398277","doi":"https://doi.org/10.1136/jnis-2023-snis.231"},"language":"en","primary_location":{"id":"doi:10.1136/jnis-2023-snis.231","doi":"https://doi.org/10.1136/jnis-2023-snis.231","is_oa":true,"landing_page_url":"http://dx.doi.org/10.1136/jnis-2023-snis.231","pdf_url":"https://jnis.bmj.com/content/neurintsurg/15/Suppl_1/A156.1.full.pdf","source":{"id":"https://openalex.org/S66405466","display_name":"Journal of NeuroInterventional Surgery","issn_l":"1759-8478","issn":["1759-8478","1759-8486"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-a","doyens","jufo-2","ki-jl-1","medline","norway-1","poland-100","russia-white-list-1"],"host_organization":"https://openalex.org/P4310319945","host_organization_name":"BMJ","host_organization_lineage":["https://openalex.org/P4310319945"],"host_organization_lineage_names":["BMJ"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"SNIS 20th annual meeting electronic poster abstracts","raw_type":"proceedings-article"},"volume":null,"type":"conference-abstract","indexed_in":["crossref"],"open_access":{"is_oa":true,"oa_status":"bronze","oa_url":"https://jnis.bmj.com/content/neurintsurg/15/Suppl_1/A156.1.full.pdf","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5011627807","display_name":"David Glenn Harrison","orcid":"https://orcid.org/0000-0001-9363-6451","observed_orcids":["https://orcid.org/0000-0001-9363-6451"]},"institutions":[{"id":"https://openalex.org/I1330342723","display_name":"Mayo Clinic","ror":"https://ror.org/02qp3tb03","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"D Harrison","raw_affiliation_strings":["Mayo Clinic, Rochester, MN, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Mayo Clinic, Rochester, MN, USA","institution_ids":["https://openalex.org/I1330342723"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5065112919","display_name":"Mitchel D. Bauman","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1330342723","display_name":"Mayo Clinic","ror":"https://ror.org/02qp3tb03","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"M Bauman","raw_affiliation_strings":["Mayo Clinic, Rochester, MN, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Mayo Clinic, Rochester, MN, USA","institution_ids":["https://openalex.org/I1330342723"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5055618165","display_name":"Nancy Jeanne Brown","orcid":"https://orcid.org/0000-0001-7109-3142","observed_orcids":["https://orcid.org/0000-0001-7109-3142"]},"institutions":[{"id":"https://openalex.org/I204250578","display_name":"University of California, Irvine","ror":"https://ror.org/04gyf1771","country_code":"US","type":"education","lineage":["https://openalex.org/I204250578"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"N Brown","raw_affiliation_strings":["UC Irvine, Newport Beach, CA, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"UC Irvine, Newport Beach, CA, USA","institution_ids":["https://openalex.org/I204250578"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5079777523","display_name":"Renu Singh","orcid":"https://orcid.org/0000-0003-2616-6618","observed_orcids":["https://orcid.org/0000-0003-2616-6618"]},"institutions":[{"id":"https://openalex.org/I5388228","display_name":"University of Rochester","ror":"https://ror.org/022kthw22","country_code":"US","type":"education","lineage":["https://openalex.org/I5388228"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"R Singh","raw_affiliation_strings":["University of Rochester, Rochester, NY, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Rochester, Rochester, NY, USA","institution_ids":["https://openalex.org/I5388228"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5053360172","display_name":"Julian Lassiter Gendreau","orcid":"https://orcid.org/0000-0001-8412-0437","observed_orcids":["https://orcid.org/0000-0001-8412-0437"]},"institutions":[{"id":"https://openalex.org/I145311948","display_name":"Johns Hopkins University","ror":"https://ror.org/00za53h95","country_code":"US","type":"education","lineage":["https://openalex.org/I145311948"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"J Gendreau","raw_affiliation_strings":["Johns Hopkins Whiting School of Engineering, Baltimore, MD, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Johns Hopkins Whiting School of Engineering, Baltimore, MD, USA","institution_ids":["https://openalex.org/I145311948"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":4,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":null,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":null,"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":"A156.1","last_page":"A156"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12747","display_name":"Moyamoya disease diagnosis and treatment","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12747","display_name":"Moyamoya disease diagnosis and treatment","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10697","display_name":"Vasculitis and related conditions","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/moyamoya-disease","display_name":"moyamoya disease","score":0.9909999966621399},{"id":"https://openalex.org/keywords/autoimmune-disease","display_name":"autoimmune disease","score":0.6809999942779541},{"id":"https://openalex.org/keywords/graves-disease","display_name":"Graves' disease","score":0.949999988079071},{"id":"https://openalex.org/keywords/lupus","display_name":"lupus","score":0.8199999928474426},{"id":"https://openalex.org/keywords/antiphospholipid-syndrome","display_name":"antiphospholipid syndrome","score":0.9990000128746033},{"id":"https://openalex.org/keywords/type-1-diabetes","display_name":"type 1 diabetes","score":0.9959999918937683},{"id":"https://openalex.org/keywords/multiple-sclerosis","display_name":"multiple sclerosis","score":0.996999979019165},{"id":"https://openalex.org/keywords/ischemic-stroke","display_name":"ischemic stroke","score":0.8349999785423279},{"id":"https://openalex.org/keywords/hemorrhagic-stroke","display_name":"hemorrhagic stroke","score":0.9309999942779541},{"id":"https://openalex.org/keywords/bilateral-disease","display_name":"bilateral disease","score":0.6499999761581421},{"id":"https://openalex.org/keywords/autoimmune-disease-etiology","display_name":"autoimmune etiology","score":0.4749999940395355}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8715837001800537},{"id":"https://openalex.org/C2776548475","wikidata":"https://www.wikidata.org/wiki/Q1951267","display_name":"Moyamoya disease","level":2,"score":0.8052422404289246},{"id":"https://openalex.org/C107130276","wikidata":"https://www.wikidata.org/wiki/Q133805","display_name":"Epidemiology","level":2,"score":0.6062812805175781},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.5905308723449707},{"id":"https://openalex.org/C137627325","wikidata":"https://www.wikidata.org/wiki/Q156318","display_name":"Etiology","level":2,"score":0.5751935243606567},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.5280095934867859},{"id":"https://openalex.org/C2776874634","wikidata":"https://www.wikidata.org/wiki/Q582207","display_name":"Antiphospholipid syndrome","level":3,"score":0.4283002018928528},{"id":"https://openalex.org/C2908647359","wikidata":"https://www.wikidata.org/wiki/Q2625603","display_name":"Population","level":2,"score":0.42664772272109985},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.4265033006668091},{"id":"https://openalex.org/C2780868729","wikidata":"https://www.wikidata.org/wiki/Q261327","display_name":"Thrombosis","level":2,"score":0.05972674489021301},{"id":"https://openalex.org/C99454951","wikidata":"https://www.wikidata.org/wiki/Q932068","display_name":"Environmental health","level":1,"score":0.0}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.1136/jnis-2023-snis.231","doi":"https://doi.org/10.1136/jnis-2023-snis.231","is_oa":true,"landing_page_url":"http://dx.doi.org/10.1136/jnis-2023-snis.231","pdf_url":"https://jnis.bmj.com/content/neurintsurg/15/Suppl_1/A156.1.full.pdf","source":{"id":"https://openalex.org/S66405466","display_name":"Journal of NeuroInterventional Surgery","issn_l":"1759-8478","issn":["1759-8478","1759-8486"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-a","doyens","jufo-2","ki-jl-1","medline","norway-1","poland-100","russia-white-list-1"],"host_organization":"https://openalex.org/P4310319945","host_organization_name":"BMJ","host_organization_lineage":["https://openalex.org/P4310319945"],"host_organization_lineage_names":["BMJ"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"SNIS 20th annual meeting electronic poster abstracts","raw_type":"proceedings-article"}],"best_oa_location":{"id":"doi:10.1136/jnis-2023-snis.231","doi":"https://doi.org/10.1136/jnis-2023-snis.231","is_oa":true,"landing_page_url":"http://dx.doi.org/10.1136/jnis-2023-snis.231","pdf_url":"https://jnis.bmj.com/content/neurintsurg/15/Suppl_1/A156.1.full.pdf","source":{"id":"https://openalex.org/S66405466","display_name":"Journal of NeuroInterventional Surgery","issn_l":"1759-8478","issn":["1759-8478","1759-8486"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-a","doyens","jufo-2","ki-jl-1","medline","norway-1","poland-100","russia-white-list-1"],"host_organization":"https://openalex.org/P4310319945","host_organization_name":"BMJ","host_organization_lineage":["https://openalex.org/P4310319945"],"host_organization_lineage_names":["BMJ"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"SNIS 20th annual meeting electronic poster abstracts","raw_type":"proceedings-article"},"sustainable_development_goals":[{"score":1.0,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W4385398277.pdf","grobid_xml":"https://content.openalex.org/works/W4385398277.grobid-xml"},"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W4367150617","https://openalex.org/W4386392860","https://openalex.org/W4367152106","https://openalex.org/W2089747891","https://openalex.org/W2145513525","https://openalex.org/W2102011809","https://openalex.org/W1991909138","https://openalex.org/W2269030863","https://openalex.org/W2574302326","https://openalex.org/W2579163468"],"abstract_inverted_index":{"Introduction":[0],"Moyamoya":[1,18,77,115,245,261],"disease":[2,57,78,118,182,215],"was":[3,68,140,183],"first":[4,111],"described":[5],"in":[6,36,107,120,177,185,189],"the":[7,14,37,49,62,181,255],"1950\u2019s.":[8],"While":[9],"six":[10],"decades":[11],"have":[12,243],"passed,":[13],"underlying":[15,26],"etiology":[16],"of":[17,39,54,76,102,113,122,143,154,180],"remains":[19],"unknown.":[20],"It":[21],"has":[22],"been":[23],"postulated":[24],"that":[25],"inflammatory":[27],"or":[28,275],"autoimmune":[29,81,117,248,257],"(AI)":[30],"processes":[31],"may":[32],"play":[33],"a":[34,141],"role":[35],"development":[38],"this":[40,108],"condition.":[41],"Objectives":[42],"This":[43],"systematic":[44,66],"review":[45,67],"aims":[46],"to":[47],"characterize":[48],"clinical":[50],"and":[51,58,79,94,116,136,162,204,234,260],"epidemiological":[52],"attributes":[53],"concurrent":[55,114],"moyamoya":[56],"AI":[59,211],"conditions":[60,212],"among":[61],"population.":[63],"Methods":[64],"A":[65,152],"performed":[69],"including":[70],"studies":[71,84],"reporting":[72,89],"patient":[73],"level":[74],"data":[75],"concomitant":[80],"disease.":[82,128],"Relevant":[83],"were":[85,99,105,119,130,157,164,171,197,213],"identified":[86],"using":[87],"Preferred":[88],"Items":[90],"for":[91],"Systematic":[92],"Reviews":[93],"Meta-Analysis":[95],"criteria.":[96],"Results":[97],"There":[98,139],"739":[100],"results":[101,268],"which":[103],"149":[104],"included":[106],"study.":[109],"The":[110,192,208,250],"reports":[112],"1991":[121],"2":[123],"cases":[124,156,170],"with":[125,132,246,254],"associated":[126],"Graves\u2019":[127,214],"They":[129],"treated":[131],"antithyroid":[133],"medication":[134],"alone":[135],"showed":[137],"improvement.":[138],"total":[142,153],"257":[144],"patients":[145],"(192":[146],"females,":[147],"48":[148],"males,":[149],"17":[150],"unspecified).":[151],"158":[155],"reported":[158,165,184,195,244],"as":[159,166],"\u2018Moyamoya":[160,167],"Disease\u2019":[161],"99":[163],"Syndrome/Vasculopathy.\u2019":[168],"Most":[169],"ischemic":[172],"(175":[173],"ischemic,":[174],"15":[175],"hemorrhagic)":[176],"nature.":[178],"Bilaterality":[179],"130":[186],"cases,":[187,217,221,226,232,238],"unilaterality":[188],"34":[190],"cases.":[191],"most":[193,209],"commonly":[194],"ethnicities":[196],"Chinese":[198],"(26":[199,220],"cases),":[200,203],"Japanese":[201],"(17":[202,206],"Korean":[205],"cases).":[207],"common":[210,256],"(150":[216],"58.4%),":[218],"Lupus":[219],"10.1%),":[222],"antiphospholipid":[223],"syndrome":[224],"(19":[225,231],"7.4%),":[227,233],"Type":[228],"1":[229],"Diabetes":[230],"Multiple":[235],"Sclerosis":[236],"(7":[237],"2.7%).":[239],"Conclusions":[240],"Numerous":[241],"publications":[242],"coexisting":[247],"conditions.":[249],"demographic":[251],"characteristics":[252],"align":[253],"(female":[258],"predominance)":[259],"(high":[262],"east":[263],"Asian":[264],"prevalence)":[265],"attributes.":[266],"These":[267],"warrant":[269],"further":[270],"investigation":[271],"into":[272],"possible":[273],"causal":[274],"synergistic":[276],"mechanisms.":[277],"Disclosures":[278],"D.":[279],"Harrison:":[280],"None.":[281,284,287,290,293],"M.":[282],"Bauman:":[283],"N.":[285],"Brown:":[286],"R.":[288],"Singh:":[289],"J.":[291],"Gendreau:":[292]},"counts_by_year":[],"updated_date":"2026-11-02T09:45:03.842371","created_date":"2023-07-31T00:00:00"}