{"id":"https://openalex.org/W4384828599","doi":"https://doi.org/10.12688/f1000research.133102.3","title":"Case Report: Case report: An unusual presentation of granulomatosis with polyangiitis","display_name":"Case Report: Case report: An unusual presentation of granulomatosis with polyangiitis","publication_year":2023,"publication_date":"2023-07-19","ids":{"openalex":"https://openalex.org/W4384828599","doi":"https://doi.org/10.12688/f1000research.133102.3"},"language":"en","primary_location":{"id":"doi:10.12688/f1000research.133102.3","doi":"https://doi.org/10.12688/f1000research.133102.3","is_oa":true,"landing_page_url":"https://doi.org/10.12688/f1000research.133102.3","pdf_url":null,"source":{"id":"https://openalex.org/S4210239046","display_name":"F1000Research","issn_l":"2046-1402","issn":["2046-1402"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","jufo-1","ki-jl-1","medline","norway-1","oarl","poland-70","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320357","host_organization_name":"Faculty of 1000","host_organization_lineage":["https://openalex.org/P4310320357","https://openalex.org/P4310320547"],"host_organization_lineage_names":["Faculty of 1000","Taylor & Francis"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"F1000Research","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj"],"open_access":{"is_oa":true,"oa_status":"gold","oa_url":"https://doi.org/10.12688/f1000research.133102.3","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5007254508","display_name":"Ichrak Bannour","orcid":"https://orcid.org/0000-0002-0956-6348","observed_orcids":["https://orcid.org/0000-0002-0956-6348"]},"institutions":[{"id":"https://openalex.org/I166928557","display_name":"University of Monastir","ror":"https://ror.org/00nhtcg76","country_code":"TN","type":"education","lineage":["https://openalex.org/I166928557"]},{"id":"https://openalex.org/I4210167430","display_name":"Hospital Fatuma Bourguiba Monastir","ror":"https://ror.org/05t1yee64","country_code":"TN","type":"healthcare","lineage":["https://openalex.org/I4210167430"]}],"countries":["TN"],"is_corresponding":true,"raw_author_name":"Ichrak Bannour","raw_affiliation_strings":["Immunology Laboratory, Fattouma Bourguiba Universitary Hospital, Universite de Monastir, Monastir, Monastir, 5000","Laboratory of Molecular Immuno-Oncology, Faculty of Medicine, Universite de Monastir, Monastir, Monastir, 5000"],"raw_orcid":"https://orcid.org/0000-0002-0956-6348","affiliations":[{"raw_affiliation_string":"Immunology Laboratory, Fattouma Bourguiba Universitary Hospital, Universite de Monastir, Monastir, Monastir, 5000","institution_ids":["https://openalex.org/I166928557","https://openalex.org/I4210167430"]},{"raw_affiliation_string":"Laboratory of Molecular Immuno-Oncology, Faculty of Medicine, Universite de Monastir, Monastir, Monastir, 5000","institution_ids":["https://openalex.org/I166928557"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5004568704","display_name":"M. Ben Brahim","orcid":"https://orcid.org/0000-0003-1967-0824","observed_orcids":["https://orcid.org/0000-0003-1967-0824"]},"institutions":[{"id":"https://openalex.org/I166928557","display_name":"University of Monastir","ror":"https://ror.org/00nhtcg76","country_code":"TN","type":"education","lineage":["https://openalex.org/I166928557"]}],"countries":["TN"],"is_corresponding":false,"raw_author_name":"Maroi Ben Brahim","raw_affiliation_strings":["Biochemistry Laboratory, LR12ES05 LR-NAFS Nutrition-Functional Food and Vascular Health, Faculty of Medicine, Universite de Monastir, Monastir, Monastir, 5000","Internal Medicine and Endocrinology Department, Tahar Sfar University Hospital, Universite de Monastir, Monastir, Monastir, 5111"],"raw_orcid":"https://orcid.org/0000-0003-1967-0824","affiliations":[{"raw_affiliation_string":"Biochemistry Laboratory, LR12ES05 LR-NAFS Nutrition-Functional Food and Vascular Health, Faculty of Medicine, Universite de Monastir, Monastir, Monastir, 5000","institution_ids":["https://openalex.org/I166928557"]},{"raw_affiliation_string":"Internal Medicine and Endocrinology Department, Tahar Sfar University Hospital, Universite de Monastir, Monastir, Monastir, 5111","institution_ids":["https://openalex.org/I166928557"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5110566272","display_name":"Sondes Arfa","orcid":"https://orcid.org/0000-0001-7797-4899","observed_orcids":["https://orcid.org/0000-0001-7797-4899"]},"institutions":[{"id":"https://openalex.org/I166928557","display_name":"University of Monastir","ror":"https://ror.org/00nhtcg76","country_code":"TN","type":"education","lineage":["https://openalex.org/I166928557"]}],"countries":["TN"],"is_corresponding":false,"raw_author_name":"Sondes Arfa","raw_affiliation_strings":["Internal Medicine and Endocrinology Department, Tahar Sfar University Hospital, Universite de Monastir, Monastir, Monastir, 5111"],"raw_orcid":"https://orcid.org/0000-0001-7797-4899","affiliations":[{"raw_affiliation_string":"Internal Medicine and Endocrinology Department, Tahar Sfar University Hospital, Universite de Monastir, Monastir, Monastir, 5111","institution_ids":["https://openalex.org/I166928557"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5031348088","display_name":"Soumaya ben Amor","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Soumaya ben Amor","raw_affiliation_strings":["Department of Gastrology, Tahar Sfar University Hospital, Mahdia"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Gastrology, Tahar Sfar University Hospital, Mahdia","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5084057626","display_name":"Asma Ben Mabrouk","orcid":"https://orcid.org/0000-0001-7150-9515","observed_orcids":["https://orcid.org/0000-0001-7150-9515"]},"institutions":[{"id":"https://openalex.org/I166928557","display_name":"University of Monastir","ror":"https://ror.org/00nhtcg76","country_code":"TN","type":"education","lineage":["https://openalex.org/I166928557"]}],"countries":["TN"],"is_corresponding":false,"raw_author_name":"Asma Ben Mabrouk","raw_affiliation_strings":["Internal Medicine and Endocrinology Department, Tahar Sfar University Hospital, Universite de Monastir, Monastir, Monastir, 5111"],"raw_orcid":"https://orcid.org/0000-0001-7150-9515","affiliations":[{"raw_affiliation_string":"Internal Medicine and Endocrinology Department, Tahar Sfar University Hospital, Universite de Monastir, Monastir, Monastir, 5111","institution_ids":["https://openalex.org/I166928557"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5077900139","display_name":"Olfa Berrich","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I166928557","display_name":"University of Monastir","ror":"https://ror.org/00nhtcg76","country_code":"TN","type":"education","lineage":["https://openalex.org/I166928557"]}],"countries":["TN"],"is_corresponding":false,"raw_author_name":"Olfa Berrich","raw_affiliation_strings":["Biochemistry Laboratory, LR12ES05 LR-NAFS Nutrition-Functional Food and Vascular Health, Faculty of Medicine, Universite de Monastir, Monastir, Monastir, 5000","Internal Medicine and Endocrinology Department, Tahar Sfar University Hospital, Universite de Monastir, Monastir, Monastir, 5111"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Biochemistry Laboratory, LR12ES05 LR-NAFS Nutrition-Functional Food and Vascular Health, Faculty of Medicine, Universite de Monastir, Monastir, Monastir, 5000","institution_ids":["https://openalex.org/I166928557"]},{"raw_affiliation_string":"Internal Medicine and Endocrinology Department, Tahar Sfar University Hospital, Universite de Monastir, Monastir, Monastir, 5111","institution_ids":["https://openalex.org/I166928557"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5071411913","display_name":"Sonia Hammemi","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I166928557","display_name":"University of Monastir","ror":"https://ror.org/00nhtcg76","country_code":"TN","type":"education","lineage":["https://openalex.org/I166928557"]},{"id":"https://openalex.org/I4210167430","display_name":"Hospital Fatuma Bourguiba Monastir","ror":"https://ror.org/05t1yee64","country_code":"TN","type":"healthcare","lineage":["https://openalex.org/I4210167430"]}],"countries":["TN"],"is_corresponding":false,"raw_author_name":"Sonia Hammemi","raw_affiliation_strings":["Biochemistry Laboratory, LR12ES05 LR-NAFS Nutrition-Functional Food and Vascular Health, Faculty of Medicine, Universite de Monastir, Monastir, Monastir, 5000","Internal Medicine and Endocrinology Department, Fattouma Bourguiba University Hospital, Universite de Monastir, Monastir, Monastir, 5000"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Biochemistry Laboratory, LR12ES05 LR-NAFS Nutrition-Functional Food and Vascular Health, Faculty of Medicine, Universite de Monastir, Monastir, Monastir, 5000","institution_ids":["https://openalex.org/I166928557"]},{"raw_affiliation_string":"Internal Medicine and Endocrinology Department, Fattouma Bourguiba University Hospital, Universite de Monastir, Monastir, Monastir, 5000","institution_ids":["https://openalex.org/I166928557","https://openalex.org/I4210167430"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":["https://openalex.org/A5007254508"],"corresponding_institution_ids":["https://openalex.org/I166928557","https://openalex.org/I4210167430"],"apc_list":{"value":1350,"currency":"USD","value_usd":1350},"apc_paid":{"value":1350,"currency":"USD","value_usd":1350},"fwci":0.1742,"has_fulltext":true,"cited_by_count":1,"citation_normalized_percentile":{"value":0.48441283,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":93},"biblio":{"volume":"12","issue":null,"first_page":"430","last_page":"430"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10697","display_name":"Vasculitis and related conditions","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10697","display_name":"Vasculitis and related conditions","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12328","display_name":"Autoimmune and Inflammatory Disorders","score":0.00019999999494757503,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T14015","display_name":"Otitis Media and Relapsing Polychondritis","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/granulomatosis-with-polyangiitis","display_name":"granulomatosis with polyangiitis","score":1.0},{"id":"https://openalex.org/keywords/liver-involvement","display_name":"liver involvement","score":0.7080000042915344},{"id":"https://openalex.org/keywords/anca-associated-vasculitis","display_name":"ANCA-associated vasculitis","score":0.7770000100135803},{"id":"https://openalex.org/keywords/pr3-anca","display_name":"PR3-ANCA","score":0.8700000047683716},{"id":"https://openalex.org/keywords/sinusitis","display_name":"sinusitis","score":0.7329999804496765},{"id":"https://openalex.org/keywords/hepatomegaly","display_name":"hepatomegaly","score":0.8629999756813049},{"id":"https://openalex.org/keywords/alveolar-hemorrhage","display_name":"alveolar hemorrhage","score":0.7770000100135803},{"id":"https://openalex.org/keywords/heart-failure","display_name":"heart failure","score":0.718999981880188},{"id":"https://openalex.org/keywords/cyclophosphamide-pulse-therapy","display_name":"cyclophosphamide pulse therapy","score":0.7350000143051147},{"id":"https://openalex.org/keywords/atypical-presentation","display_name":"atypical presentation","score":0.515999972820282}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8403197526931763},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.5873478055000305}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.12688/f1000research.133102.3","doi":"https://doi.org/10.12688/f1000research.133102.3","is_oa":true,"landing_page_url":"https://doi.org/10.12688/f1000research.133102.3","pdf_url":null,"source":{"id":"https://openalex.org/S4210239046","display_name":"F1000Research","issn_l":"2046-1402","issn":["2046-1402"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","jufo-1","ki-jl-1","medline","norway-1","oarl","poland-70","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320357","host_organization_name":"Faculty of 1000","host_organization_lineage":["https://openalex.org/P4310320357","https://openalex.org/P4310320547"],"host_organization_lineage_names":["Faculty of 1000","Taylor & Francis"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"F1000Research","raw_type":"journal-article"}],"best_oa_location":{"id":"doi:10.12688/f1000research.133102.3","doi":"https://doi.org/10.12688/f1000research.133102.3","is_oa":true,"landing_page_url":"https://doi.org/10.12688/f1000research.133102.3","pdf_url":null,"source":{"id":"https://openalex.org/S4210239046","display_name":"F1000Research","issn_l":"2046-1402","issn":["2046-1402"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","jufo-1","ki-jl-1","medline","norway-1","oarl","poland-70","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320357","host_organization_name":"Faculty of 1000","host_organization_lineage":["https://openalex.org/P4310320357","https://openalex.org/P4310320547"],"host_organization_lineage_names":["Faculty of 1000","Taylor & Francis"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"F1000Research","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":0.9940000176429749,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":15,"referenced_works":["https://openalex.org/W62137374","https://openalex.org/W2017834760","https://openalex.org/W2027483935","https://openalex.org/W2035918387","https://openalex.org/W2083370638","https://openalex.org/W2153246360","https://openalex.org/W2210324041","https://openalex.org/W2312733380","https://openalex.org/W2313056848","https://openalex.org/W2590413745","https://openalex.org/W2599563415","https://openalex.org/W2761016571","https://openalex.org/W3124008823","https://openalex.org/W4226268557","https://openalex.org/W4283724020"],"related_works":["https://openalex.org/W4366771880","https://openalex.org/W2412042616","https://openalex.org/W7171733444","https://openalex.org/W4213326159","https://openalex.org/W3036659842","https://openalex.org/W2290467067","https://openalex.org/W4365520329","https://openalex.org/W4394858052","https://openalex.org/W3126020125","https://openalex.org/W7154728626"],"abstract_inverted_index":{"Aim:":[0],"We":[1],"are":[2],"reporting":[3],"a":[4,41,121,176,210],"case":[5],"of":[6,10,147,198,225,236],"an":[7,52,60,73],"unusual":[8],"presentation":[9],"granulomatosis":[11,124],"with":[12,15,25,126,155,175,196],"polyangiitis":[13],"(GPA)":[14],"liver":[16,119],"involvement.":[17],"Case":[18],"presentation:":[19],"A":[20,110,187],"45-year-old":[21],"male":[22],"patient":[23,39,150],"presented":[24,174],"erythematous":[26],"plaques":[27],"on":[28,45,158],"the":[29,38,46,78,114,118,145,183,199,219],"face":[30],"and":[31,72,84,92,101,108,117,141,162,164,179,201,214],"bilateral":[32],"nasal":[33,115,188,192,203],"obstruction.":[34],"On":[35],"physical":[36],"examination,":[37],"had":[40],"ring-shaped":[42],"squamous":[43],"plaque":[44],"face.":[47],"The":[48,82,137,149],"laboratory":[49],"findings":[50,143],"revealed":[51],"accelerated":[53],"erythrocyte":[54],"sedimentation":[55],"rate":[56],"at":[57,64],"100":[58],"mm/h,":[59],"elevated":[61,74],"C-reactive":[62],"protein":[63],"66":[65],"mg/L,":[66],"hyper":[67],"gamma":[68],"globulinemia":[69],"16":[70],"g/L":[71],"alkaline":[75],"phosphatase":[76],"(twice":[77],"upper":[79],"normal":[80],"limit).":[81],"craniofacial":[83],"thoracoabdominal":[85],"computed":[86],"tomography":[87],"(CT)":[88],"-scans":[89],"showed":[90,120,191],"ethmoid":[91],"maxillary":[93],"sinusitis,":[94],"low":[95],"facial":[96],"bone":[97],"density,":[98],"multiple":[99],"mediastinal":[100],"hilar":[102],"lymphadenopathy,":[103],"diffuse":[104,211],"small":[105],"pulmonary":[106],"nodules,":[107],"hepatomegaly.":[109],"cutaneous":[111],"lesion":[112],"biopsy,":[113],"mucosa,":[116],"chronic":[122],"inflammatory":[123],"process":[125],"necrosis.":[127],"Serum":[128],"anti-neutrophil":[129],"cytoplasmic":[130],"antibody":[131],"(ANCA)":[132],"against":[133],"PR3":[134],"was":[135,167,215],"positive.":[136],"clinical,":[138],"biological,":[139],"radiological,":[140],"histological":[142],"substantiated":[144],"diagnosis":[146],"GPA.":[148],"received":[151],"systemic":[152],"steroids":[153],"combined":[154],"cyclophosphamide":[156],"pulses":[157],"days":[159,229],"1,":[160],"14":[161],"28":[163],"then":[165],"he":[166,173,208],"lost":[168],"to":[169,218],"follow-up.":[170],"Two-years":[171],"later,":[172,207],"cardiac":[177],"failure":[178,227],"skin":[180],"ulcer":[181],"in":[182],"right":[184],"lower":[185],"limb.":[186],"endoscopic":[189],"exam":[190],"septum":[193],"cartilage":[194],"perforation":[195],"resorption":[197],"middle":[200],"inferior":[202],"concha.":[204],"Two":[205],"weeks":[206],"developed":[209],"alveolar":[212],"hemorrhage":[213],"therefore":[216],"transferred":[217],"intensive":[220],"care":[221],"unit":[222],"but":[223],"died":[224],"respiratory":[226],"3":[228],"later.":[230],"Conclusion:":[231],"Clinicians":[232],"should":[233],"be":[234],"aware":[235],"GPA":[237],"atypical":[238],"clinical":[239],"manifestations.":[240]},"counts_by_year":[{"year":2024,"cited_by_count":1}],"updated_date":"2026-10-13T10:08:12.033832","created_date":"2023-07-21T00:00:00"}
