{"id":"https://openalex.org/W4381686593","doi":"https://doi.org/10.53855/bjt.v26i1.497_port","title":"Hepatite Fulminante como Primeira Apresenta\u00e7\u00e3o da Doen\u00e7a de Wilson","display_name":"Hepatite Fulminante como Primeira Apresenta\u00e7\u00e3o da Doen\u00e7a de Wilson","publication_year":2023,"publication_date":"2023-06-19","ids":{"openalex":"https://openalex.org/W4381686593","doi":"https://doi.org/10.53855/bjt.v26i1.497_port"},"language":"pt","primary_location":{"id":"doi:10.53855/bjt.v26i1.497_port","doi":"https://doi.org/10.53855/bjt.v26i1.497_port","is_oa":true,"landing_page_url":"https://doi.org/10.53855/bjt.v26i1.497_port","pdf_url":"https://bjt.emnuvens.com.br/revista/article/download/497/559/1122","source":{"id":"https://openalex.org/S4210196417","display_name":"Brazilian Journal of Transplantation","issn_l":"2764-1589","issn":["2764-1589"],"is_oa":true,"is_in_doaj":true,"is_core":false,"listed_in":["doaj","latindex","scielo"],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Brazilian Journal of Transplantation","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://bjt.emnuvens.com.br/revista/article/download/497/559/1122","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5031244220","display_name":"Djulia Adriani Frainer","orcid":"https://orcid.org/0000-0003-4465-1019","observed_orcids":["https://orcid.org/0000-0003-4465-1019"]},"institutions":[{"id":"https://openalex.org/I4210124925","display_name":"Hospital Municipal S\u00e3o Jos\u00e9","ror":"https://ror.org/03cn5jj91","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210124925"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Djulia Adriani Frainer","raw_affiliation_strings":["Hospital Municipal S\u00e3o Jos\u00e9"],"raw_orcid":"https://orcid.org/0000-0003-4465-1019","affiliations":[{"raw_affiliation_string":"Hospital Municipal S\u00e3o Jos\u00e9","institution_ids":["https://openalex.org/I4210124925"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5024839682","display_name":"Carolina da Silveira Welter","orcid":"https://orcid.org/0000-0002-4864-9605","observed_orcids":["https://orcid.org/0000-0002-4864-9605"]},"institutions":[{"id":"https://openalex.org/I4210124925","display_name":"Hospital Municipal S\u00e3o Jos\u00e9","ror":"https://ror.org/03cn5jj91","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210124925"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Carolina da Silveira Welter","raw_affiliation_strings":["Hospital Municipal S\u00e3o Jos\u00e9"],"raw_orcid":"https://orcid.org/0000-0002-4864-9605","affiliations":[{"raw_affiliation_string":"Hospital Municipal S\u00e3o Jos\u00e9","institution_ids":["https://openalex.org/I4210124925"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5011219419","display_name":"Claudia Theis","orcid":"https://orcid.org/0000-0002-1303-298X","observed_orcids":["https://orcid.org/0000-0002-1303-298X"]},"institutions":[{"id":"https://openalex.org/I4210124925","display_name":"Hospital Municipal S\u00e3o Jos\u00e9","ror":"https://ror.org/03cn5jj91","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210124925"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Claudia Theis","raw_affiliation_strings":["Hospital Municipal S\u00e3o Jos\u00e9"],"raw_orcid":"https://orcid.org/0000-0002-1303-298X","affiliations":[{"raw_affiliation_string":"Hospital Municipal S\u00e3o Jos\u00e9","institution_ids":["https://openalex.org/I4210124925"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5103145596","display_name":"Raquel Francine Liermann Garcia","orcid":"https://orcid.org/0009-0005-2600-6640","observed_orcids":["https://orcid.org/0009-0005-2600-6640"]},"institutions":[{"id":"https://openalex.org/I4210124925","display_name":"Hospital Municipal S\u00e3o Jos\u00e9","ror":"https://ror.org/03cn5jj91","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210124925"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Raquel Francine Liermann Garcia","raw_affiliation_strings":["Hospital Municipal S\u00e3o Jos\u00e9"],"raw_orcid":"https://orcid.org/0009-0005-2600-6640","affiliations":[{"raw_affiliation_string":"Hospital Municipal S\u00e3o Jos\u00e9","institution_ids":["https://openalex.org/I4210124925"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5101741305","display_name":"R. Rodr\u00edguez Lemos","orcid":"https://orcid.org/0000-0002-1925-1083","observed_orcids":["https://orcid.org/0000-0002-1925-1083"]},"institutions":[{"id":"https://openalex.org/I4210124925","display_name":"Hospital Municipal S\u00e3o Jos\u00e9","ror":"https://ror.org/03cn5jj91","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210124925"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Ricardo Lemos","raw_affiliation_strings":["Hospital Municipal S\u00e3o Jos\u00e9"],"raw_orcid":"https://orcid.org/0000-0002-1925-1083","affiliations":[{"raw_affiliation_string":"Hospital Municipal S\u00e3o Jos\u00e9","institution_ids":["https://openalex.org/I4210124925"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5024052889","display_name":"Franco Haritsch","orcid":"https://orcid.org/0000-0002-4944-3588","observed_orcids":["https://orcid.org/0000-0002-4944-3588"]},"institutions":[{"id":"https://openalex.org/I4210124925","display_name":"Hospital Municipal S\u00e3o Jos\u00e9","ror":"https://ror.org/03cn5jj91","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210124925"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Franco Haritsch","raw_affiliation_strings":["Hospital Municipal S\u00e3o Jos\u00e9"],"raw_orcid":"https://orcid.org/0000-0002-4944-3588","affiliations":[{"raw_affiliation_string":"Hospital Municipal S\u00e3o Jos\u00e9","institution_ids":["https://openalex.org/I4210124925"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5010001494","display_name":"Andr\u00e9 Carminati Lima","orcid":"https://orcid.org/0000-0003-1752-062X","observed_orcids":["https://orcid.org/0000-0003-1752-062X"]},"institutions":[{"id":"https://openalex.org/I4210124925","display_name":"Hospital Municipal S\u00e3o Jos\u00e9","ror":"https://ror.org/03cn5jj91","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210124925"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Andre Carminati Lima","raw_affiliation_strings":["Hospital Municipal S\u00e3o Jos\u00e9"],"raw_orcid":"https://orcid.org/0000-0003-1752-062X","affiliations":[{"raw_affiliation_string":"Hospital Municipal S\u00e3o Jos\u00e9","institution_ids":["https://openalex.org/I4210124925"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5036757639","display_name":"Christian Evangelista Garcia","orcid":"https://orcid.org/0000-0002-8563-4728","observed_orcids":["https://orcid.org/0000-0002-8563-4728"]},"institutions":[{"id":"https://openalex.org/I4210124925","display_name":"Hospital Municipal S\u00e3o Jos\u00e9","ror":"https://ror.org/03cn5jj91","country_code":"BR","type":"healthcare","lineage":["https://openalex.org/I4210124925"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Christian Evangelista Garcia","raw_affiliation_strings":["Hospital Municipal S\u00e3o Jos\u00e9"],"raw_orcid":"https://orcid.org/0000-0002-8563-4728","affiliations":[{"raw_affiliation_string":"Hospital Municipal S\u00e3o Jos\u00e9","institution_ids":["https://openalex.org/I4210124925"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":["https://openalex.org/I4210124925"],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"26","issue":"1","first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10337","display_name":"Liver Disease and Transplantation","score":0.5615000128746033,"subfield":{"id":"https://openalex.org/subfields/2721","display_name":"Hepatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10337","display_name":"Liver Disease and Transplantation","score":0.5615000128746033,"subfield":{"id":"https://openalex.org/subfields/2721","display_name":"Hepatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10915","display_name":"Trace Elements in Health","score":0.23350000381469727,"subfield":{"id":"https://openalex.org/subfields/2916","display_name":"Nutrition and Dietetics"},"field":{"id":"https://openalex.org/fields/29","display_name":"Nursing"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10999","display_name":"Organ Transplantation Techniques and Outcomes","score":0.04410000145435333,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/wilson-s-disease","display_name":"Wilson's disease","score":0.9509999752044678},{"id":"https://openalex.org/keywords/fulminant-hepatitis","display_name":"fulminant hepatitis","score":0.8820000290870667},{"id":"https://openalex.org/keywords/herpetic-encephalitis","display_name":"herpetic encephalitis","score":0.8230000138282776},{"id":"https://openalex.org/keywords/septic-shock","display_name":"septic shock","score":0.8769999742507935},{"id":"https://openalex.org/keywords/bleeding-duodenal-ulcer","display_name":"duodenal ulcer bleeding","score":0.8479999899864197},{"id":"https://openalex.org/keywords/hepatic-artery-pseudoaneurysm","display_name":"hepatic artery pseudoaneurysm","score":0.968999981880188},{"id":"https://openalex.org/keywords/neuropsychiatric-symptoms","display_name":"neuropsychiatric symptoms","score":0.6549999713897705},{"id":"https://openalex.org/keywords/young-adult-patient","display_name":"young adult patient","score":0.4740000069141388}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.7748199105262756},{"id":"https://openalex.org/C29456083","wikidata":"https://www.wikidata.org/wiki/Q1221899","display_name":"Gynecology","level":1,"score":0.4113216996192932}],"mesh":[],"locations_count":3,"locations":[{"id":"doi:10.53855/bjt.v26i1.497_port","doi":"https://doi.org/10.53855/bjt.v26i1.497_port","is_oa":true,"landing_page_url":"https://doi.org/10.53855/bjt.v26i1.497_port","pdf_url":"https://bjt.emnuvens.com.br/revista/article/download/497/559/1122","source":{"id":"https://openalex.org/S4210196417","display_name":"Brazilian Journal of Transplantation","issn_l":"2764-1589","issn":["2764-1589"],"is_oa":true,"is_in_doaj":true,"is_core":false,"listed_in":["doaj","latindex","scielo"],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Brazilian Journal of Transplantation","raw_type":"journal-article"},{"id":"pmh:oai:ojs3.emnuvens.com.br:article/497","doi":null,"is_oa":true,"landing_page_url":"https://bjt.emnuvens.com.br/revista/article/view/497","pdf_url":"https://bjt.emnuvens.com.br/revista/article/download/497/558","source":{"id":"https://openalex.org/S4306402641","display_name":"LA Referencia (Red Federada de Repositorios Institucionales de Publicaciones Cient\u00edficas)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I4383465926","host_organization_name":"LA Referencia","host_organization_lineage":["https://openalex.org/I4383465926"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"instacron:ABTO","raw_type":"info:eu-repo/semantics/article"},{"id":"pmh:oai:doaj.org/article:a62b40f63b034c119d4dfb55ceb87efb","doi":null,"is_oa":true,"landing_page_url":"https://doaj.org/article/a62b40f63b034c119d4dfb55ceb87efb","pdf_url":null,"source":{"id":"https://openalex.org/S4306401280","display_name":"DOAJ (DOAJ: Directory of Open Access Journals)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-sa","license_id":"https://openalex.org/licenses/cc-by-sa","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Brazilian Journal of Transplantation, Vol 26 (2023)","raw_type":"article"}],"best_oa_location":{"id":"doi:10.53855/bjt.v26i1.497_port","doi":"https://doi.org/10.53855/bjt.v26i1.497_port","is_oa":true,"landing_page_url":"https://doi.org/10.53855/bjt.v26i1.497_port","pdf_url":"https://bjt.emnuvens.com.br/revista/article/download/497/559/1122","source":{"id":"https://openalex.org/S4210196417","display_name":"Brazilian Journal of Transplantation","issn_l":"2764-1589","issn":["2764-1589"],"is_oa":true,"is_in_doaj":true,"is_core":false,"listed_in":["doaj","latindex","scielo"],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Brazilian Journal of Transplantation","raw_type":"journal-article"},"sustainable_development_goals":[{"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3","score":1.0}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W4381686593.pdf","grobid_xml":"https://content.openalex.org/works/W4381686593.grobid-xml"},"referenced_works_count":6,"referenced_works":["https://openalex.org/W2089526291","https://openalex.org/W2433487518","https://openalex.org/W2889837648","https://openalex.org/W2995277871","https://openalex.org/W3123621871","https://openalex.org/W4312129944"],"related_works":["https://openalex.org/W4381681039","https://openalex.org/W2401313349","https://openalex.org/W2062331704","https://openalex.org/W4409118612","https://openalex.org/W2416409058","https://openalex.org/W4405738828","https://openalex.org/W430425203","https://openalex.org/W2443755914","https://openalex.org/W2361196890","https://openalex.org/W2265282686"],"abstract_inverted_index":{"A":[0,95],"doen\u00e7a":[1],"de":[2,16,19,25,56,67,73,77,90,93,113,124],"Wilson":[3],"\u00e9":[4,63],"uma":[5,68],"rara":[6],"patologia,":[7],"por\u00e9m,":[8],"que":[9],"engloba":[10],"6\u201312%":[11],"dos":[12],"pacientes":[13,50],"com":[14,37,75,83,100,108],"indica\u00e7\u00e3o":[15],"transplante":[17,91],"hep\u00e1tico":[18,92],"urg\u00eancia.":[20,94],"As":[21],"principais":[22],"manifesta\u00e7\u00f5es,":[23],"al\u00e9m":[24],"hep\u00e1ticas,":[26],"s\u00e3o":[27],"as":[28],"neurol\u00f3gicas":[29],"e":[30,81,88,111,121],"psiqui\u00e1tricas,":[31],"sendo":[32],"mais":[33],"raro":[34],"a":[35,127],"evolu\u00e7\u00e3o":[36,84],"hepatite":[38,86],"fulminante":[39,87],"sem":[40],"sintomas":[41],"neuropsiqui\u00e1tricos.":[42],"Apesar":[43,116],"da":[44],"urg\u00eancia,":[45],"o":[46,65],"progn\u00f3stico":[47],"para":[48,85,119,130],"os":[49],"p\u00f3s-transplante":[51],"\u00e9,":[52],"em":[53,58],"m\u00e9dia,":[54],"85%":[55],"sobreviv\u00eancia":[57],"cinco":[59],"anos.":[60],"Neste":[61],"relato,":[62],"apresentado":[64],"caso":[66],"paciente":[69,96,128],"mulher,":[70],"18":[71],"anos":[72],"idade,":[74],"in\u00edcio":[76],"dor":[78],"abdominal,":[79],"icter\u00edcia":[80],"col\u00faria":[82],"necessidade":[89],"evoluiu":[97,129],"no":[98],"p\u00f3s-operat\u00f3rio":[99],"choque":[101],"s\u00e9ptico":[102],"devido":[103],"encefalite":[104],"herp\u00e9tica,":[105],"\u00falcera":[106],"duodenal":[107],"sangramento":[109],"ativo":[110],"pseudoaneurisma":[112],"art\u00e9ria":[114],"hep\u00e1tica.":[115],"das":[117],"medidas":[118],"estabiliza\u00e7\u00e3o":[120],"solicita\u00e7\u00e3o,":[122],"novamente,":[123],"um":[125],"transplante,":[126],"\u00f3bito.":[131]},"counts_by_year":[],"updated_date":"2026-09-26T08:19:03.415552","created_date":"2023-06-23T00:00:00"}
