{"id":"https://openalex.org/W4320073399","doi":"https://doi.org/10.15406/joentr.2022.14.00506","title":"PFAPA syndrome: A practical review","display_name":"PFAPA syndrome: A practical review","publication_year":2022,"publication_date":"2022-08-29","ids":{"openalex":"https://openalex.org/W4320073399","doi":"https://doi.org/10.15406/joentr.2022.14.00506"},"language":"en","primary_location":{"id":"doi:10.15406/joentr.2022.14.00506","doi":"https://doi.org/10.15406/joentr.2022.14.00506","is_oa":true,"landing_page_url":"https://doi.org/10.15406/joentr.2022.14.00506","pdf_url":"https://medcraveonline.com/JOENTR/JOENTR-14-00506.pdf","source":{"id":"https://openalex.org/S2764820234","display_name":"Journal of Otolaryngology-ENT Research","issn_l":"2379-6359","issn":["2379-6359"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310320093","host_organization_name":"MedCrave Group","host_organization_lineage":["https://openalex.org/P4310320093"],"host_organization_lineage_names":["MedCrave Group"],"type":"journal"},"license":"cc-by-nc","license_id":"https://openalex.org/licenses/cc-by-nc","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Otolaryngology-ENT Research","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref"],"open_access":{"is_oa":true,"oa_status":"hybrid","oa_url":"https://medcraveonline.com/JOENTR/JOENTR-14-00506.pdf","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5077797007","display_name":"Tiago Caneira","orcid":"https://orcid.org/0000-0003-1977-4818","observed_orcids":["https://orcid.org/0000-0003-1977-4818"]},"institutions":[{"id":"https://openalex.org/I4403386557","display_name":"Hospital CUF Descobertas","ror":"https://ror.org/05gsnx339","country_code":"PT","type":"healthcare","lineage":["https://openalex.org/I4403386557"]}],"countries":["PT"],"is_corresponding":false,"raw_author_name":"Tiago Caneira","raw_affiliation_strings":["Department of Otorhinolaryngology, Hospital CUF Descobertas, Portugal","Hospital CUF Descobertas -Otorhinolaryngology Head and Neck Department R. M\u00e1rio Botas, Lisboa, 1998-018, Portugal,"],"raw_orcid":"https://orcid.org/0000-0003-1977-4818","affiliations":[{"raw_affiliation_string":"Department of Otorhinolaryngology, Hospital CUF Descobertas, Portugal","institution_ids":["https://openalex.org/I4403386557"]},{"raw_affiliation_string":"Hospital CUF Descobertas -Otorhinolaryngology Head and Neck Department R. M\u00e1rio Botas, Lisboa, 1998-018, Portugal,","institution_ids":["https://openalex.org/I4403386557"]}]},{"author_position":"middle","author":{"id":null,"display_name":"Jo\u00e3o Subtil","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4403386557","display_name":"Hospital CUF Descobertas","ror":"https://ror.org/05gsnx339","country_code":"PT","type":"healthcare","lineage":["https://openalex.org/I4403386557"]}],"countries":["PT"],"is_corresponding":false,"raw_author_name":"Jo\u00e3o Subtil","raw_affiliation_strings":["Department of Otorhinolaryngology, Hospital CUF Descobertas, Portugal"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Otorhinolaryngology, Hospital CUF Descobertas, Portugal","institution_ids":["https://openalex.org/I4403386557"]}]},{"author_position":"last","author":{"id":null,"display_name":"Jos\u00e9 Saraiva","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4403386557","display_name":"Hospital CUF Descobertas","ror":"https://ror.org/05gsnx339","country_code":"PT","type":"healthcare","lineage":["https://openalex.org/I4403386557"]}],"countries":["PT"],"is_corresponding":false,"raw_author_name":"Jos\u00e9 Saraiva","raw_affiliation_strings":["Department of Otorhinolaryngology, Hospital CUF Descobertas, Portugal"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Otorhinolaryngology, Hospital CUF Descobertas, Portugal","institution_ids":["https://openalex.org/I4403386557"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":["https://openalex.org/I4403386557"],"apc_list":null,"apc_paid":null,"fwci":0.073,"has_fulltext":true,"cited_by_count":1,"citation_normalized_percentile":{"value":0.23495427,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":93},"biblio":{"volume":"14","issue":"2","first_page":"52","last_page":"55"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11078","display_name":"Inflammasome and immune disorders","score":0.8457000255584717,"subfield":{"id":"https://openalex.org/subfields/1312","display_name":"Molecular Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T11078","display_name":"Inflammasome and immune disorders","score":0.8457000255584717,"subfield":{"id":"https://openalex.org/subfields/1312","display_name":"Molecular Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.032499998807907104,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11153","display_name":"Streptococcal Infections and Treatments","score":0.014299999922513962,"subfield":{"id":"https://openalex.org/subfields/2725","display_name":"Infectious Diseases"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/pfapa-syndrome","display_name":"PFAPA syndrome","score":0.9919999837875366},{"id":"https://openalex.org/keywords/periodic-fever","display_name":"periodic fever","score":0.9210000038146973},{"id":"https://openalex.org/keywords/aphthous-stomatitis","display_name":"aphthous stomatitis","score":0.9779999852180481},{"id":"https://openalex.org/keywords/pharyngitis","display_name":"pharyngitis","score":0.9860000014305115},{"id":"https://openalex.org/keywords/cervical-lymphadenitis","display_name":"cervical lymphadenitis","score":0.8659999966621399},{"id":"https://openalex.org/keywords/diagnostic-criteria","display_name":"diagnostic criteria","score":0.6890000104904175},{"id":"https://openalex.org/keywords/differential-diagnosis","display_name":"differential diagnosis","score":0.9940000176429749},{"id":"https://openalex.org/keywords/pathogenesis","display_name":"pathogenesis","score":0.8399999737739563},{"id":"https://openalex.org/keywords/natural-history-disease","display_name":"natural history (disease)","score":0.8650000095367432},{"id":"https://openalex.org/keywords/treatment","display_name":"treatment","score":0.7020000219345093}],"concepts":[{"id":"https://openalex.org/C2779279270","wikidata":"https://www.wikidata.org/wiki/Q2085267","display_name":"Pharyngitis","level":2,"score":0.9158283472061157},{"id":"https://openalex.org/C137627325","wikidata":"https://www.wikidata.org/wiki/Q156318","display_name":"Etiology","level":2,"score":0.8047353625297546},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.7513822317123413},{"id":"https://openalex.org/C2781233496","wikidata":"https://www.wikidata.org/wiki/Q355981","display_name":"Adenitis","level":2,"score":0.7376095056533813},{"id":"https://openalex.org/C2779051857","wikidata":"https://www.wikidata.org/wiki/Q911386","display_name":"Stomatitis","level":2,"score":0.7355756163597107},{"id":"https://openalex.org/C2780801072","wikidata":"https://www.wikidata.org/wiki/Q837512","display_name":"Differential diagnosis","level":2,"score":0.6352367997169495},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.5836849808692932},{"id":"https://openalex.org/C107130276","wikidata":"https://www.wikidata.org/wiki/Q133805","display_name":"Epidemiology","level":2,"score":0.5588845014572144},{"id":"https://openalex.org/C163276114","wikidata":"https://www.wikidata.org/wiki/Q484591","display_name":"Natural history","level":2,"score":0.5062295794487},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.4921411871910095},{"id":"https://openalex.org/C177713679","wikidata":"https://www.wikidata.org/wiki/Q679690","display_name":"Intensive care medicine","level":1,"score":0.37080439925193787},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.282207190990448},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.15878471732139587}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.15406/joentr.2022.14.00506","doi":"https://doi.org/10.15406/joentr.2022.14.00506","is_oa":true,"landing_page_url":"https://doi.org/10.15406/joentr.2022.14.00506","pdf_url":"https://medcraveonline.com/JOENTR/JOENTR-14-00506.pdf","source":{"id":"https://openalex.org/S2764820234","display_name":"Journal of Otolaryngology-ENT Research","issn_l":"2379-6359","issn":["2379-6359"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310320093","host_organization_name":"MedCrave Group","host_organization_lineage":["https://openalex.org/P4310320093"],"host_organization_lineage_names":["MedCrave Group"],"type":"journal"},"license":"cc-by-nc","license_id":"https://openalex.org/licenses/cc-by-nc","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Otolaryngology-ENT Research","raw_type":"journal-article"}],"best_oa_location":{"id":"doi:10.15406/joentr.2022.14.00506","doi":"https://doi.org/10.15406/joentr.2022.14.00506","is_oa":true,"landing_page_url":"https://doi.org/10.15406/joentr.2022.14.00506","pdf_url":"https://medcraveonline.com/JOENTR/JOENTR-14-00506.pdf","source":{"id":"https://openalex.org/S2764820234","display_name":"Journal of Otolaryngology-ENT Research","issn_l":"2379-6359","issn":["2379-6359"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310320093","host_organization_name":"MedCrave Group","host_organization_lineage":["https://openalex.org/P4310320093"],"host_organization_lineage_names":["MedCrave Group"],"type":"journal"},"license":"cc-by-nc","license_id":"https://openalex.org/licenses/cc-by-nc","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Otolaryngology-ENT Research","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":0.9940000176429749}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W4320073399.pdf","grobid_xml":"https://content.openalex.org/works/W4320073399.grobid-xml"},"referenced_works_count":44,"referenced_works":["https://openalex.org/W1516577284","https://openalex.org/W1780500931","https://openalex.org/W1963503118","https://openalex.org/W1970338512","https://openalex.org/W1978695980","https://openalex.org/W1989565542","https://openalex.org/W1991039396","https://openalex.org/W2002056653","https://openalex.org/W2003015756","https://openalex.org/W2003505641","https://openalex.org/W2009878301","https://openalex.org/W2044331399","https://openalex.org/W2048791692","https://openalex.org/W2048819076","https://openalex.org/W2053239273","https://openalex.org/W2059365540","https://openalex.org/W2065239649","https://openalex.org/W2090576960","https://openalex.org/W2098392594","https://openalex.org/W2102211749","https://openalex.org/W2102767914","https://openalex.org/W2113016607","https://openalex.org/W2125156936","https://openalex.org/W2158249293","https://openalex.org/W2161427172","https://openalex.org/W2162822903","https://openalex.org/W2170757962","https://openalex.org/W2171343487","https://openalex.org/W2195523158","https://openalex.org/W2294803425","https://openalex.org/W2298807173","https://openalex.org/W2330320015","https://openalex.org/W2466248711","https://openalex.org/W2480597338","https://openalex.org/W2510025416","https://openalex.org/W2619751619","https://openalex.org/W2738234244","https://openalex.org/W2801631069","https://openalex.org/W2891605216","https://openalex.org/W2908224725","https://openalex.org/W2917223556","https://openalex.org/W2920328336","https://openalex.org/W4236114071","https://openalex.org/W4323966255"],"related_works":["https://openalex.org/W2627032450","https://openalex.org/W4285208151","https://openalex.org/W2530453810","https://openalex.org/W2042201207","https://openalex.org/W7025038374","https://openalex.org/W4309038939","https://openalex.org/W2912015960","https://openalex.org/W2939934523","https://openalex.org/W3177196196","https://openalex.org/W2917223556"],"abstract_inverted_index":{"Periodic":[0],"fever,":[1],"aphthous":[2],"stomatitis,":[3],"pharyngitis,":[4],"and":[5,62,65],"cervical":[6],"adenitis":[7],"(PFAPA)":[8],"syndrome":[9,15,50],"is":[10,30],"rare,":[11],"benign":[12],"recurrent/periodic":[13],"fever":[14],"of":[16,26,48],"unknown":[17],"etiology":[18],"that":[19],"normally":[20],"affects":[21],"children":[22],"under":[23],"the":[24],"age":[25],"5.":[27],"The":[28],"diagnosis":[29,58],"made":[31],"based":[32],"on":[33],"clinical":[34,56],"assumption,":[35],"after":[36],"excluding":[37],"other":[38],"pathology.":[39],"In":[40],"this":[41],"report":[42],"to":[43],"provide":[44],"a":[45],"practical":[46],"assessment":[47],"PFAPA":[49],"regarding":[51],"epidemiology,":[52],"pathogenesis,":[53],"natural":[54],"history,":[55],"manifestations,":[57],"criteria,":[59],"differential":[60],"diagnosis,":[61],"available":[63],"medical":[64],"surgical":[66],"treatments.":[67]},"counts_by_year":[{"year":2024,"cited_by_count":1}],"updated_date":"2026-11-06T12:05:46.655746","created_date":"2023-02-12T00:00:00"}
