{"id":"https://openalex.org/W4307774262","doi":"https://doi.org/10.1093/rheumatology/keac623","title":"Diagnosing and treating ANCA-associated vasculitis: an updated review for clinical practice","display_name":"Diagnosing and treating ANCA-associated vasculitis: an updated review for clinical practice","publication_year":2022,"publication_date":"2022-10-29","ids":{"openalex":"https://openalex.org/W4307774262","doi":"https://doi.org/10.1093/rheumatology/keac623","pmid":"https://pubmed.ncbi.nlm.nih.gov/36315063"},"language":"en","primary_location":{"id":"doi:10.1093/rheumatology/keac623","doi":"https://doi.org/10.1093/rheumatology/keac623","is_oa":false,"landing_page_url":"https://doi.org/10.1093/rheumatology/keac623","pdf_url":null,"source":{"id":"https://openalex.org/S183989336","display_name":"Rheumatology","issn_l":"1462-0324","issn":["1462-0324","1462-0332"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-1","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Rheumatology","raw_type":"journal-article"},"volume":null,"type":"review","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"green","oa_url":"https://academic.oup.com/rheumatology/article-pdf/62/5/1787/50120907/keac623.pdf","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5017750912","display_name":"Baptiste Chevet","orcid":"https://orcid.org/0000-0002-9646-7603","observed_orcids":["https://orcid.org/0000-0002-9646-7603"]},"institutions":[{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Baptiste Chevet","raw_affiliation_strings":["LBAI, UMR1227, Univ Brest, Inserm, Labex IGO, CHU de Brest , Brest, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"LBAI, UMR1227, Univ Brest, Inserm, Labex IGO, CHU de Brest , Brest, France","institution_ids":["https://openalex.org/I154526488"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5007242477","display_name":"Divi Cornec","orcid":"https://orcid.org/0000-0002-9159-702X","observed_orcids":["https://orcid.org/0000-0002-9159-702X"]},"institutions":[{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]}],"countries":["FR"],"is_corresponding":true,"raw_author_name":"Divi Cornec","raw_affiliation_strings":["LBAI, UMR1227, Univ Brest, Inserm, Labex IGO, CHU de Brest , Brest, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"LBAI, UMR1227, Univ Brest, Inserm, Labex IGO, CHU de Brest , Brest, France","institution_ids":["https://openalex.org/I154526488"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5007539867","display_name":"Marta Casal Moura","orcid":"https://orcid.org/0000-0001-7439-6501","observed_orcids":["https://orcid.org/0000-0001-7439-6501"]},"institutions":[{"id":"https://openalex.org/I1330342723","display_name":"Mayo Clinic","ror":"https://ror.org/02qp3tb03","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Marta Casal Moura","raw_affiliation_strings":["Department Division of Pulmonary and Critical Care Medicine, Department of Medicine, and Thoracic Research Disease Unit, Mayo Clinic College of Medicine and Science , Rochester, MN, USA"],"raw_orcid":"https://orcid.org/0000-0001-7439-6501","affiliations":[{"raw_affiliation_string":"Department Division of Pulmonary and Critical Care Medicine, Department of Medicine, and Thoracic Research Disease Unit, Mayo Clinic College of Medicine and Science , Rochester, MN, USA","institution_ids":["https://openalex.org/I1330342723"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5091002248","display_name":"\u00c9milie Cornec-Le Gall","orcid":"https://orcid.org/0000-0003-1958-4459","observed_orcids":["https://orcid.org/0000-0003-1958-4459"]},"institutions":[{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]},{"id":"https://openalex.org/I161929037","display_name":"Universit\u00e9 de Bretagne Occidentale","ror":"https://ror.org/01b8h3982","country_code":"FR","type":"education","lineage":["https://openalex.org/I161929037","https://openalex.org/I4405260085"]},{"id":"https://openalex.org/I4210165461","display_name":"G\u00e9n\u00e9tique, G\u00e9nomique Fonctionnelle et Biotechnologies","ror":"https://ror.org/05xxb2f26","country_code":"FR","type":"facility","lineage":["https://openalex.org/I154526488","https://openalex.org/I4210105774","https://openalex.org/I4210128919","https://openalex.org/I4210132604","https://openalex.org/I4210161065","https://openalex.org/I4210165461","https://openalex.org/I4405260085"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Emilie Cornec-Le Gall","raw_affiliation_strings":["Department of Rheumatology, Univ Brest, Inserm, UMR 1078, GGB , Brest, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Rheumatology, Univ Brest, Inserm, UMR 1078, GGB , Brest, France","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I161929037","https://openalex.org/I4210165461"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5073207965","display_name":"Fernando Custodio Fervenza","orcid":"https://orcid.org/0000-0002-9952-209X","observed_orcids":["https://orcid.org/0000-0002-9952-209X"]},"institutions":[{"id":"https://openalex.org/I1330342723","display_name":"Mayo Clinic","ror":"https://ror.org/02qp3tb03","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Fernando C Fervenza","raw_affiliation_strings":["Division of Nephrology and Hypertension, Mayo Clinic , Rochester, MN, USA"],"raw_orcid":"https://orcid.org/0000-0002-9952-209X","affiliations":[{"raw_affiliation_string":"Division of Nephrology and Hypertension, Mayo Clinic , Rochester, MN, USA","institution_ids":["https://openalex.org/I1330342723"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5047878379","display_name":"Kenneth J. Warrington","orcid":"https://orcid.org/0000-0001-7708-2487","observed_orcids":["https://orcid.org/0000-0001-7708-2487"]},"institutions":[{"id":"https://openalex.org/I1330342723","display_name":"Mayo Clinic","ror":"https://ror.org/02qp3tb03","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Kenneth J Warrington","raw_affiliation_strings":["Division of Rheumatology, Mayo Clinic , Rochester, MN, USA"],"raw_orcid":"https://orcid.org/0000-0001-7708-2487","affiliations":[{"raw_affiliation_string":"Division of Rheumatology, Mayo Clinic , Rochester, MN, USA","institution_ids":["https://openalex.org/I1330342723"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5012967877","display_name":"Ulrich Specks","orcid":"https://orcid.org/0000-0002-6559-1206","observed_orcids":["https://orcid.org/0000-0002-6559-1206"]},"institutions":[{"id":"https://openalex.org/I1330342723","display_name":"Mayo Clinic","ror":"https://ror.org/02qp3tb03","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1330342723"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Ulrich Specks","raw_affiliation_strings":["Department Division of Pulmonary and Critical Care Medicine, Department of Medicine, and Thoracic Research Disease Unit, Mayo Clinic College of Medicine and Science , Rochester, MN, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department Division of Pulmonary and Critical Care Medicine, Department of Medicine, and Thoracic Research Disease Unit, Mayo Clinic College of Medicine and Science , Rochester, MN, USA","institution_ids":["https://openalex.org/I1330342723"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5022570560","display_name":"Alvise Berti","orcid":"https://orcid.org/0000-0002-7831-921X","observed_orcids":["https://orcid.org/0000-0002-7831-921X"]},"institutions":[{"id":"https://openalex.org/I193223587","display_name":"University of Trento","ror":"https://ror.org/05trd4x28","country_code":"IT","type":"education","lineage":["https://openalex.org/I193223587"]},{"id":"https://openalex.org/I4210088115","display_name":"Ospedale Santa Chiara","ror":"https://ror.org/007x5wz81","country_code":"IT","type":"healthcare","lineage":["https://openalex.org/I4210088115"]}],"countries":["IT"],"is_corresponding":false,"raw_author_name":"Alvise Berti","raw_affiliation_strings":["Rheumatology, Santa Chiara Regional Hospital, APSS Trento, and Department of Cellular, Computational and Integrative Biology (CIBIO), University of Trento , Italy"],"raw_orcid":"https://orcid.org/0000-0002-7831-921X","affiliations":[{"raw_affiliation_string":"Rheumatology, Santa Chiara Regional Hospital, APSS Trento, and Department of Cellular, Computational and Integrative Biology (CIBIO), University of Trento , Italy","institution_ids":["https://openalex.org/I193223587","https://openalex.org/I4210088115"]}]}],"institutions":[],"countries_distinct_count":3,"institutions_distinct_count":6,"corresponding_author_ids":["https://openalex.org/A5007242477"],"corresponding_institution_ids":["https://openalex.org/I154526488"],"apc_list":{"value":3192,"currency":"GBP","value_usd":3949},"apc_paid":null,"fwci":2.2274,"has_fulltext":true,"cited_by_count":82,"citation_normalized_percentile":{"value":0.91397849,"is_in_top_1_percent":false,"is_in_top_10_percent":true},"cited_by_percentile_year":{"min":98,"max":100},"biblio":{"volume":"62","issue":"5","first_page":"1787","last_page":"1803"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10697","display_name":"Vasculitis and related conditions","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10697","display_name":"Vasculitis and related conditions","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11029","display_name":"Renal Diseases and Glomerulopathies","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2727","display_name":"Nephrology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T14015","display_name":"Otitis Media and Relapsing Polychondritis","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/anca-associated-vasculitis","display_name":"ANCA-associated vasculitis","score":0.996999979019165},{"id":"https://openalex.org/keywords/granulomatosis-with-polyangiitis","display_name":"granulomatosis with polyangiitis","score":0.9980000257492065},{"id":"https://openalex.org/keywords/microscopic-polyangiitis","display_name":"microscopic polyangiitis","score":1.0},{"id":"https://openalex.org/keywords/small-vessel-vasculitis","display_name":"small vessel vasculitis","score":0.8870000243186951},{"id":"https://openalex.org/keywords/anca-testing","display_name":"ANCA testing","score":0.8519999980926514},{"id":"https://openalex.org/keywords/rituximab","display_name":"rituximab","score":0.7509999871253967},{"id":"https://openalex.org/keywords/steroid-sparing-therapy","display_name":"steroid-sparing therapy","score":0.9070000052452087},{"id":"https://openalex.org/keywords/avacopan","display_name":"avacopan","score":0.9929999709129333},{"id":"https://openalex.org/keywords/therapeutic-plasma-exchange","display_name":"plasma exchange","score":0.9430000185966492},{"id":"https://openalex.org/keywords/recurrence","display_name":"recurrence","score":0.6660000085830688},{"id":"https://openalex.org/keywords/damage-accrual","display_name":"damage accrual","score":0.8389999866485596},{"id":"https://openalex.org/keywords/biomarkers","display_name":"biomarkers","score":0.6060000061988831},{"id":"https://openalex.org/keywords/risk-factors","display_name":"risk factors","score":0.5139999985694885},{"id":"https://openalex.org/keywords/diagnosis","display_name":"diagnosis","score":0.3569999933242798},{"id":"https://openalex.org/keywords/treatment-algorithm","display_name":"treatment algorithm","score":0.6570000052452087}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9779069423675537},{"id":"https://openalex.org/C2778910314","wikidata":"https://www.wikidata.org/wiki/Q1934069","display_name":"Microscopic polyangiitis","level":4,"score":0.664269208908081},{"id":"https://openalex.org/C2780653079","wikidata":"https://www.wikidata.org/wiki/Q412323","display_name":"Rituximab","level":3,"score":0.657535195350647},{"id":"https://openalex.org/C2776015282","wikidata":"https://www.wikidata.org/wiki/Q644318","display_name":"Vasculitis","level":3,"score":0.5196624994277954},{"id":"https://openalex.org/C2781229154","wikidata":"https://www.wikidata.org/wiki/Q1161568","display_name":"Granulomatosis with polyangiitis","level":4,"score":0.4954608678817749},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.4952906668186188},{"id":"https://openalex.org/C177713679","wikidata":"https://www.wikidata.org/wiki/Q679690","display_name":"Intensive care medicine","level":1,"score":0.450992614030838},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.3895898461341858},{"id":"https://openalex.org/C2779338263","wikidata":"https://www.wikidata.org/wiki/Q208414","display_name":"Lymphoma","level":2,"score":0.0}],"mesh":[{"descriptor_ui":"D000069283","descriptor_name":"Rituximab","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D005938","descriptor_name":"Glucocorticoids","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009364","descriptor_name":"Neoplasm Recurrence, Local","qualifier_ui":"Q000139","qualifier_name":"chemically induced","is_major_topic":false},{"descriptor_ui":"D012074","descriptor_name":"Remission Induction","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D014890","descriptor_name":"Granulomatosis with Polyangiitis","qualifier_ui":"Q000188","qualifier_name":"drug therapy","is_major_topic":true},{"descriptor_ui":"D016896","descriptor_name":"Treatment Outcome","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D019268","descriptor_name":"Antibodies, Antineutrophil Cytoplasmic","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D056648","descriptor_name":"Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis","qualifier_ui":"Q000188","qualifier_name":"drug therapy","is_major_topic":true}],"locations_count":4,"locations":[{"id":"doi:10.1093/rheumatology/keac623","doi":"https://doi.org/10.1093/rheumatology/keac623","is_oa":false,"landing_page_url":"https://doi.org/10.1093/rheumatology/keac623","pdf_url":null,"source":{"id":"https://openalex.org/S183989336","display_name":"Rheumatology","issn_l":"1462-0324","issn":["1462-0324","1462-0332"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-1","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Rheumatology","raw_type":"journal-article"},{"id":"pmid:36315063","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/36315063","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Rheumatology (Oxford, England)","raw_type":"Review"},{"id":"pmh:oai:iris.unitn.it:11572/415957","doi":null,"is_oa":true,"landing_page_url":"https://academic.oup.com/rheumatology/article/62/5/1787/6782952?login=true#403707599","pdf_url":"https://academic.oup.com/rheumatology/article-pdf/62/5/1787/50120907/keac623.pdf","source":{"id":"https://openalex.org/S4377196320","display_name":"Iris (University of Trento)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I193223587","host_organization_name":"University of Trento","host_organization_lineage":["https://openalex.org/I193223587"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":"info:eu-repo/semantics/article"},{"id":"pmh:oai:HAL:hal-04188157v1","doi":null,"is_oa":false,"landing_page_url":"https://hal.science/hal-04188157","pdf_url":null,"source":{"id":"https://openalex.org/S4306402512","display_name":"HAL","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I4405252976","host_organization_name":"Centre pour la Communication Scientifique Directe","host_organization_lineage":["https://openalex.org/I4405252976"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Rheumatology, 2023, 62 (5), pp.1787-1803. &#x27E8;10.1093/rheumatology/keac623&#x27E9;","raw_type":"info:eu-repo/semantics/article"}],"best_oa_location":{"id":"pmh:oai:iris.unitn.it:11572/415957","doi":null,"is_oa":true,"landing_page_url":"https://academic.oup.com/rheumatology/article/62/5/1787/6782952?login=true#403707599","pdf_url":"https://academic.oup.com/rheumatology/article-pdf/62/5/1787/50120907/keac623.pdf","source":{"id":"https://openalex.org/S4377196320","display_name":"Iris (University of Trento)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I193223587","host_organization_name":"University of Trento","host_organization_lineage":["https://openalex.org/I193223587"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":"info:eu-repo/semantics/article"},"sustainable_development_goals":[{"display_name":"Good health and well-being","score":1.0,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[{"id":"https://openalex.org/G4110203128","display_name":"Immunoth\u00e9rapies Grand Ouest","funder_award_id":"ANR-11-LABX-0016","funder_id":"https://openalex.org/F4320320883","funder_display_name":"Agence Nationale de la Recherche"}],"funders":[{"id":"https://openalex.org/F4320320883","display_name":"Agence Nationale de la Recherche","ror":"https://ror.org/00rbzpz17"}],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W4307774262.pdf","grobid_xml":"https://content.openalex.org/works/W4307774262.grobid-xml"},"referenced_works_count":156,"referenced_works":["https://openalex.org/W63618183","https://openalex.org/W64175382","https://openalex.org/W75985149","https://openalex.org/W90726672","https://openalex.org/W137802152","https://openalex.org/W216005197","https://openalex.org/W1517672737","https://openalex.org/W1683214757","https://openalex.org/W1964243735","https://openalex.org/W1970345179","https://openalex.org/W1972218512","https://openalex.org/W1975466495","https://openalex.org/W1979398789","https://openalex.org/W1988601867","https://openalex.org/W1989239104","https://openalex.org/W1999520120","https://openalex.org/W2001824449","https://openalex.org/W2007778318","https://openalex.org/W2011309580","https://openalex.org/W2013572128","https://openalex.org/W2028155613","https://openalex.org/W2029562600","https://openalex.org/W2031517139","https://openalex.org/W2036292718","https://openalex.org/W2040613743","https://openalex.org/W2041565487","https://openalex.org/W2042539877","https://openalex.org/W2052605495","https://openalex.org/W2058357963","https://openalex.org/W2060695647","https://openalex.org/W2063340779","https://openalex.org/W2074402338","https://openalex.org/W2076527880","https://openalex.org/W2078261620","https://openalex.org/W2084056567","https://openalex.org/W2090832683","https://openalex.org/W2093539807","https://openalex.org/W2097453206","https://openalex.org/W2100809783","https://openalex.org/W2108616041","https://openalex.org/W2109360480","https://openalex.org/W2113281485","https://openalex.org/W2115164659","https://openalex.org/W2119641571","https://openalex.org/W2119900188","https://openalex.org/W2121602116","https://openalex.org/W2122790621","https://openalex.org/W2123092609","https://openalex.org/W2126583107","https://openalex.org/W2126910882","https://openalex.org/W2127547339","https://openalex.org/W2127762664","https://openalex.org/W2129925171","https://openalex.org/W2131235777","https://openalex.org/W2132820210","https://openalex.org/W2134743399","https://openalex.org/W2138612272","https://openalex.org/W2139510501","https://openalex.org/W2142122741","https://openalex.org/W2145161120","https://openalex.org/W2151319492","https://openalex.org/W2151534030","https://openalex.org/W2153415140","https://openalex.org/W2157356913","https://openalex.org/W2162416852","https://openalex.org/W2162637360","https://openalex.org/W2167110581","https://openalex.org/W2167945026","https://openalex.org/W2171643265","https://openalex.org/W2171950933","https://openalex.org/W2178294708","https://openalex.org/W2227274114","https://openalex.org/W2266467924","https://openalex.org/W2274841233","https://openalex.org/W2283152765","https://openalex.org/W2333082923","https://openalex.org/W2473041787","https://openalex.org/W2474029657","https://openalex.org/W2496249381","https://openalex.org/W2571866645","https://openalex.org/W2574946413","https://openalex.org/W2590549497","https://openalex.org/W2613744835","https://openalex.org/W2619991145","https://openalex.org/W2620110075","https://openalex.org/W2620589618","https://openalex.org/W2739805807","https://openalex.org/W2754110304","https://openalex.org/W2769949274","https://openalex.org/W2779456451","https://openalex.org/W2787654282","https://openalex.org/W2790210974","https://openalex.org/W2796161886","https://openalex.org/W2800927321","https://openalex.org/W2811004238","https://openalex.org/W2884768618","https://openalex.org/W2888674564","https://openalex.org/W2890408829","https://openalex.org/W2899304926","https://openalex.org/W2900996857","https://openalex.org/W2908342189","https://openalex.org/W2909154432","https://openalex.org/W2921462029","https://openalex.org/W2921856986","https://openalex.org/W2928941816","https://openalex.org/W2936396720","https://openalex.org/W2948163967","https://openalex.org/W2967124351","https://openalex.org/W2972602773","https://openalex.org/W2974445467","https://openalex.org/W2980242378","https://openalex.org/W2998595296","https://openalex.org/W3004897282","https://openalex.org/W3006137031","https://openalex.org/W3008507861","https://openalex.org/W3011038678","https://openalex.org/W3015505099","https://openalex.org/W3018616991","https://openalex.org/W3031234495","https://openalex.org/W3033755273","https://openalex.org/W3037338668","https://openalex.org/W3040421122","https://openalex.org/W3041655488","https://openalex.org/W3047249778","https://openalex.org/W3049256694","https://openalex.org/W3080098141","https://openalex.org/W3080818324","https://openalex.org/W3087336541","https://openalex.org/W3094679971","https://openalex.org/W3105999081","https://openalex.org/W3108594910","https://openalex.org/W3116551151","https://openalex.org/W3128389767","https://openalex.org/W3131777419","https://openalex.org/W3153280438","https://openalex.org/W3164741966","https://openalex.org/W3167754380","https://openalex.org/W3194020033","https://openalex.org/W3199908752","https://openalex.org/W3200479416","https://openalex.org/W3201135618","https://openalex.org/W3214568069","https://openalex.org/W3215402239","https://openalex.org/W4200407971","https://openalex.org/W4200421136","https://openalex.org/W4206696907","https://openalex.org/W4210607322","https://openalex.org/W4210817412","https://openalex.org/W4214501619","https://openalex.org/W4214559267","https://openalex.org/W4224317346","https://openalex.org/W4237487483","https://openalex.org/W4241675591","https://openalex.org/W4255010602","https://openalex.org/W6603148072","https://openalex.org/W6680509875"],"related_works":["https://openalex.org/W4404668525","https://openalex.org/W4389674132","https://openalex.org/W2940479799","https://openalex.org/W2079295501","https://openalex.org/W7135056228","https://openalex.org/W59450537","https://openalex.org/W4285212118","https://openalex.org/W2525182362","https://openalex.org/W4289524260","https://openalex.org/W4400573902"],"abstract_inverted_index":{"ANCA-associated":[0],"vasculitides":[1],"(AAV)":[2],"are":[3,36,80,154],"a":[4,45,88,138],"group":[5],"of":[6,22,41,47,109,119,146,185],"rare,":[7],"primary,":[8],"systemic":[9],"necrotizing":[10],"small-vessel":[11],"vasculitides.":[12],"Granulomatosis":[13],"with":[14,38,54,60,151,163,205],"polyangiitis":[15,18],"and":[16,30,101,125,131,144,157,166,197,211,228,235],"microscopic":[17],"account":[19],"for":[20,107,141,221,229],"\u223c80-90%":[21],"all":[23,96],"AAV.":[24,43,195],"Exposure":[25],"to":[26,180,190,208],"silica":[27],"dust,":[28],"farming":[29],"chronic":[31,64],"nasal":[32],"Staphylococcus":[33],"aureus":[34],"carriage":[35],"associated":[37],"increased":[39],"risk":[40],"developing":[42],"When":[44],"diagnosis":[46,210],"AAV":[48],"is":[49,168,176],"suspected,":[50],"as":[51,63,137],"in":[52,159,188,194,203],"patients":[53],"multisystem":[55],"organ":[56],"dysfunction":[57],"or":[58,72,225],"those":[59],"features":[61],"such":[62],"recurrent":[65],"rhinosinusitis,":[66],"cavitated":[67],"lung":[68],"nodules,":[69],"palpable":[70],"purpura":[71],"acute":[73],"kidney":[74],"injury,":[75],"then":[76],"appropriate":[77],"further":[78],"investigations":[79],"needed,":[81],"including":[82],"ANCA":[83,196],"testing.":[84],"In":[85,148,173],"this":[86],"scenario,":[87],"structured":[89],"clinical":[90,122,206],"assessment":[91,207],"should":[92,215],"be":[93,105,201,216],"conducted,":[94],"evaluating":[95],"the":[97,110,117,121,126,182],"organs":[98],"possibly":[99],"involved,":[100],"tissue":[102],"biopsy":[103],"may":[104],"necessary":[106],"confirmation":[108],"diagnosis.":[111],"Therapeutic":[112],"algorithms":[113],"vary":[114],"based":[115],"on":[116],"severity":[118],"AAV,":[120],"diagnosis/ANCA":[123],"specificity,":[124],"patient's":[127],"age,":[128],"weight,":[129],"comorbidities":[130],"prognosis.":[132],"Recent":[133],"data":[134],"favour":[135],"rituximab":[136],"preferable":[139],"option":[140],"both":[142],"induction":[143],"maintenance":[145],"remission.":[147],"addition,":[149],"regimens":[150],"less":[152],"glucocorticoids":[153],"equally":[155],"effective":[156,170],"safer":[158],"inducing":[160],"remission":[161],"compared":[162],"conventional":[164],"regimens,":[165],"avacopan":[167],"an":[169],"glucocorticoid-sparing":[171],"option.":[172],"contrast,":[174],"there":[175],"not":[177],"compelling":[178],"evidence":[179],"support":[181],"routine":[183],"use":[184],"plasma":[186],"exchange":[187],"addition":[189],"standard":[191],"remission-induction":[192],"therapy":[193],"other":[198],"biomarkers":[199],"can":[200],"helpful":[202],"association":[204],"guide":[209],"treatment":[212],"decisions.":[213],"Patients":[214],"frequently":[217],"evaluated":[218],"during":[219],"follow-up":[220],"possible":[222],"disease":[223],"relapses":[224],"treatment-related":[226],"morbidity,":[227],"monitoring":[230],"damage":[231],"accrual,":[232],"especially":[233],"metabolic":[234],"cardiovascular":[236],"damage.":[237]},"counts_by_year":[{"year":2026,"cited_by_count":24},{"year":2025,"cited_by_count":34},{"year":2024,"cited_by_count":18},{"year":2023,"cited_by_count":6}],"updated_date":"2026-11-06T12:05:46.655746","created_date":"2022-11-05T00:00:00"}
