{"id":"https://openalex.org/W4285587116","doi":"https://doi.org/10.1002/acr2.11485","title":"Investigation of Inactive Disease States Among Patients With Juvenile Idiopathic Arthritis in the Childhood Arthritis and Rheumatology Research Alliance Registry","display_name":"Investigation of Inactive Disease States Among Patients With Juvenile Idiopathic Arthritis in the Childhood Arthritis and Rheumatology Research Alliance Registry","publication_year":2022,"publication_date":"2022-07-16","ids":{"openalex":"https://openalex.org/W4285587116","doi":"https://doi.org/10.1002/acr2.11485","pmid":"https://pubmed.ncbi.nlm.nih.gov/35841332","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/9469475"},"language":"en","primary_location":{"id":"doi:10.1002/acr2.11485","doi":"https://doi.org/10.1002/acr2.11485","is_oa":true,"landing_page_url":"https://doi.org/10.1002/acr2.11485","pdf_url":null,"source":{"id":"https://openalex.org/S4210182786","display_name":"ACR Open Rheumatology","issn_l":"2578-5745","issn":["2578-5745"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","doyens","jufo-1","ki-jl-1","norway-1","oarl","poland-20","russia-white-list-4"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"ACR Open Rheumatology","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","doaj","pubmed"],"open_access":{"is_oa":true,"oa_status":"gold","oa_url":"https://doi.org/10.1002/acr2.11485","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5003818704","display_name":"Melissa L. Mannion","orcid":"https://orcid.org/0000-0002-2216-970X","observed_orcids":["https://orcid.org/0000-0002-2216-970X"]},"institutions":[{"id":"https://openalex.org/I32389192","display_name":"University of Alabama at Birmingham","ror":"https://ror.org/008s83205","country_code":"US","type":"education","lineage":["https://openalex.org/I32389192"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"Melissa L. Mannion","raw_affiliation_strings":["University of Alabama at Birmingham, Birmingham, AL, USA"],"raw_orcid":"https://orcid.org/0000-0002-2216-970X","affiliations":[{"raw_affiliation_string":"University of Alabama at Birmingham, Birmingham, AL, USA","institution_ids":["https://openalex.org/I32389192"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5043053903","display_name":"Fenglong Xie","orcid":"https://orcid.org/0000-0002-7365-4801","observed_orcids":["https://orcid.org/0000-0002-7365-4801"]},"institutions":[{"id":"https://openalex.org/I32389192","display_name":"University of Alabama at Birmingham","ror":"https://ror.org/008s83205","country_code":"US","type":"education","lineage":["https://openalex.org/I32389192"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Fenglong Xie","raw_affiliation_strings":["University of Alabama at Birmingham, Birmingham, AL, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Alabama at Birmingham, Birmingham, AL, USA","institution_ids":["https://openalex.org/I32389192"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5057456571","display_name":"Timothy Beukelman","orcid":"https://orcid.org/0000-0001-9463-6306","observed_orcids":["https://orcid.org/0000-0001-9463-6306"]},"institutions":[{"id":"https://openalex.org/I32389192","display_name":"University of Alabama at Birmingham","ror":"https://ror.org/008s83205","country_code":"US","type":"education","lineage":["https://openalex.org/I32389192"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Timothy Beukelman","raw_affiliation_strings":["University of Alabama at Birmingham, Birmingham, AL, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Alabama at Birmingham, Birmingham, AL, USA","institution_ids":["https://openalex.org/I32389192"]}]},{"author_position":"last","author":{"id":null,"display_name":"for the CARRA Registry Investigators","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I32389192","display_name":"University of Alabama at Birmingham","ror":"https://ror.org/008s83205","country_code":"US","type":"education","lineage":["https://openalex.org/I32389192"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"for the CARRA Registry Investigators","raw_affiliation_strings":["University of Alabama at Birmingham, Birmingham, AL, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Alabama at Birmingham, Birmingham, AL, USA","institution_ids":["https://openalex.org/I32389192"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":["https://openalex.org/A5003818704"],"corresponding_institution_ids":["https://openalex.org/I32389192"],"apc_list":{"value":2800,"currency":"USD","value_usd":2800},"apc_paid":{"value":2800,"currency":"USD","value_usd":2800},"fwci":1.2723,"has_fulltext":false,"cited_by_count":7,"citation_normalized_percentile":{"value":0.80685441,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":89,"max":97},"biblio":{"volume":"4","issue":"9","first_page":"825","last_page":"831"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10200","display_name":"Rheumatoid Arthritis Research and Therapies","score":0.00019999999494757503,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11892","display_name":"Kawasaki Disease and Coronary Complications","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/juvenile-idiopathic-arthritis","display_name":"juvenile idiopathic arthritis","score":1.0},{"id":"https://openalex.org/keywords/inactive-disease","display_name":"inactive disease","score":0.9789999723434448},{"id":"https://openalex.org/keywords/disease-activity-index","display_name":"disease activity index","score":0.8859999775886536},{"id":"https://openalex.org/keywords/physician-s-global-assessment","display_name":"physician global assessment","score":0.7710000276565552}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8695073127746582},{"id":"https://openalex.org/C198451711","wikidata":"https://www.wikidata.org/wiki/Q327657","display_name":"Rheumatology","level":2,"score":0.7690866589546204},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.70147705078125},{"id":"https://openalex.org/C2777077863","wikidata":"https://www.wikidata.org/wiki/Q170990","display_name":"Arthritis","level":2,"score":0.6708363890647888},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.5761223435401917},{"id":"https://openalex.org/C72563966","wikidata":"https://www.wikidata.org/wiki/Q1303415","display_name":"Cohort","level":2,"score":0.5218678712844849},{"id":"https://openalex.org/C1862650","wikidata":"https://www.wikidata.org/wiki/Q186005","display_name":"Physical therapy","level":1,"score":0.4987154006958008},{"id":"https://openalex.org/C115961737","wikidata":"https://www.wikidata.org/wiki/Q1516282","display_name":"Juvenile","level":2,"score":0.4941728413105011},{"id":"https://openalex.org/C86803240","wikidata":"https://www.wikidata.org/wiki/Q420","display_name":"Biology","level":0,"score":0.0},{"id":"https://openalex.org/C54355233","wikidata":"https://www.wikidata.org/wiki/Q7162","display_name":"Genetics","level":1,"score":0.0}],"mesh":[],"locations_count":4,"locations":[{"id":"doi:10.1002/acr2.11485","doi":"https://doi.org/10.1002/acr2.11485","is_oa":true,"landing_page_url":"https://doi.org/10.1002/acr2.11485","pdf_url":null,"source":{"id":"https://openalex.org/S4210182786","display_name":"ACR Open Rheumatology","issn_l":"2578-5745","issn":["2578-5745"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","doyens","jufo-1","ki-jl-1","norway-1","oarl","poland-20","russia-white-list-4"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"ACR Open Rheumatology","raw_type":"journal-article"},{"id":"pmh:oai:pubmedcentral.nih.gov:9469475","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/9469475","pdf_url":null,"source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"ACR Open Rheumatol","raw_type":"Text"},{"id":"pmid:35841332","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/35841332","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"ACR open rheumatology","raw_type":"Journal Article"},{"id":"pmh:oai:doaj.org/article:74e13b749b7a4bfdb946e63e636e3a41","doi":null,"is_oa":true,"landing_page_url":"https://doaj.org/article/74e13b749b7a4bfdb946e63e636e3a41","pdf_url":null,"source":{"id":"https://openalex.org/S4306401280","display_name":"DOAJ (DOAJ: Directory of Open Access Journals)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-sa","license_id":"https://openalex.org/licenses/cc-by-sa","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"ACR Open Rheumatology, Vol 4, Iss 9, Pp 825-831 (2022)","raw_type":"article"}],"best_oa_location":{"id":"doi:10.1002/acr2.11485","doi":"https://doi.org/10.1002/acr2.11485","is_oa":true,"landing_page_url":"https://doi.org/10.1002/acr2.11485","pdf_url":null,"source":{"id":"https://openalex.org/S4210182786","display_name":"ACR Open Rheumatology","issn_l":"2578-5745","issn":["2578-5745"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","doyens","jufo-1","ki-jl-1","norway-1","oarl","poland-20","russia-white-list-4"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":"cc-by-nc-nd","license_id":"https://openalex.org/licenses/cc-by-nc-nd","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"ACR Open Rheumatology","raw_type":"journal-article"},"sustainable_development_goals":[{"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3","score":0.98580002784729}],"study_designs":[{"display_name":"Observational Study","id":"https://openalex.org/study-designs/observational-study"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":15,"referenced_works":["https://openalex.org/W2024714476","https://openalex.org/W2078545407","https://openalex.org/W2114155762","https://openalex.org/W2135974703","https://openalex.org/W2140194654","https://openalex.org/W2151572354","https://openalex.org/W2340414165","https://openalex.org/W2596326082","https://openalex.org/W2607459568","https://openalex.org/W2616808971","https://openalex.org/W2794680134","https://openalex.org/W2797862713","https://openalex.org/W2941230658","https://openalex.org/W2959439664","https://openalex.org/W3042508094"],"related_works":["https://openalex.org/W2596326082","https://openalex.org/W2167277273","https://openalex.org/W2549133424","https://openalex.org/W2321247185","https://openalex.org/W2190268485","https://openalex.org/W2166909692","https://openalex.org/W2121544391","https://openalex.org/W4290974102","https://openalex.org/W2752260934","https://openalex.org/W3049112601"],"abstract_inverted_index":{"Objective":[0],"Inactive":[1],"disease":[2,18,73,85,108,163,225,272],"is":[3],"the":[4,42,62,119,153,237,266],"treatment":[5],"goal":[6],"for":[7,17,32,46,90,97,106,160,268],"juvenile":[8],"idiopathic":[9],"arthritis":[10],"(JIA),":[11],"but":[12],"there":[13],"are":[14,262],"multiple":[15],"measures":[16,38,230],"activity.":[19],"The":[20,100],"objective":[21],"was":[22,104,240],"to":[23,60,264],"compare":[24],"individuals":[25],"with":[26,49,115,122,213],"JIA":[27,50,116,214],"who":[28,77,245,252],"meet":[29,187],"different":[30],"definitions":[31],"inactive":[33,84,162,192,224,271],"disease.":[34],"Methods":[35],"Disease":[36,174],"activity":[37],"were":[39,86],"determined":[40],"at":[41],"1\u2010year":[43,123],"follow\u2010up":[44],"visit":[45,124],"all":[47,112],"patients":[48,114,212,222,244],"enrolled":[51,117],"in":[52,118,215,236,270],"a":[53,135,144,170,208,218,254],"North":[54,216],"American":[55,154],"multicenter":[56,209],"registry":[57],"from":[58],"2015":[59],"2019,":[61],"Childhood":[63],"Arthritis":[64,173],"and":[65,72,93,166,194,200,250],"Rheumatology":[66,157],"Research":[67],"Alliance":[68],"(CARRA)":[69],"Registry.":[70,238],"Patient":[71],"characteristics":[74],"between":[75,243],"those":[76,251],"met":[78,152,196,246],"only":[79],"one":[80],"composite":[81,189,229],"definition":[82,190],"of":[83,139,148,156,178,191,202,211,221,234,256],"compared":[87],"by":[88,226],"\u03c72":[89],"categorical":[91],"variables":[92],"Wilcoxon":[94],"rank":[95],"sum":[96],"continuous":[98],"variables.":[99],"Spearman":[101],"correlation":[102],"coefficient":[103],"calculated":[105],"simple":[107],"measures.":[109,273],"Results":[110],"Among":[111],"2904":[113],"CARRA":[120],"Registry":[121],"data,":[125],"1984":[126],"(68%)":[127],"had":[128,134,143,169,223,253],"no":[129],"active":[130],"joints,":[131],"1485":[132],"(51%)":[133],"physician":[136],"global":[137,146],"score":[138,147],"0,":[140,149],"1366":[141],"(47%)":[142,184],"patient/parent":[145],"1293":[150],"(45%)":[151],"College":[155],"provisional":[158],"criteria":[159,249],"clinical":[161,171],"(ACR":[164],"CID),":[165],"1325":[167],"(46%)":[168],"Juvenile":[172],"Activity":[175],"Score":[176],"(cJADAS10)":[177],"1":[179,203,232,257],"or":[180,204,228,258],"less.":[181,205,259],"Almost":[182],"half":[183],"did":[185],"not":[186],"either":[188],"disease,":[193],"38%":[195],"both":[197],"ACR":[198,247],"CID":[199,248],"cJADAS10":[201,255],"Conclusion":[206],"In":[207],"cohort":[210],"America,":[217],"large":[219],"proportion":[220],"single":[227],"after":[231],"year":[233],"observation":[235],"There":[239],"significant":[241],"overlap":[242],"Additional":[260],"studies":[261],"needed":[263],"evaluate":[265],"reasons":[267],"discordance":[269]},"counts_by_year":[{"year":2025,"cited_by_count":3},{"year":2024,"cited_by_count":3},{"year":2023,"cited_by_count":1}],"updated_date":"2026-10-30T12:39:25.321706","created_date":"2022-07-16T00:00:00"}
