{"id":"https://openalex.org/W3122814802","doi":"https://doi.org/10.2310/fm.1122","title":"Pemphigus and Bullous Pemphigoid","display_name":"Pemphigus and Bullous Pemphigoid","publication_year":2020,"publication_date":"2020-05-14","ids":{"openalex":"https://openalex.org/W3122814802","doi":"https://doi.org/10.2310/fm.1122","mag":"3122814802"},"language":"en","primary_location":{"id":"doi:10.2310/fm.1122","doi":"https://doi.org/10.2310/fm.1122","is_oa":false,"landing_page_url":"https://doi.org/10.2310/fm.1122","pdf_url":null,"source":{"id":"https://openalex.org/S4363605459","display_name":"DeckerMed Family Medicine","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"DeckerMed Family Medicine","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5112545997","display_name":"Aakaash Varma","orcid":"https://orcid.org/0009-0001-0016-7965","observed_orcids":["https://orcid.org/0009-0001-0016-7965"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Aakaash Varma","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5001452732","display_name":"Annette Czernik","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Annette Czernik","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5027151083","display_name":"Jacob Oren Levitt","orcid":"https://orcid.org/0000-0001-7250-285X","observed_orcids":["https://orcid.org/0000-0001-7250-285X"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Jacob Levitt","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":0,"institutions_distinct_count":0,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":13,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11730","display_name":"Autoimmune Bullous Skin Diseases","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11730","display_name":"Autoimmune Bullous Skin Diseases","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11650","display_name":"Skin and Cellular Biology Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/1307","display_name":"Cell Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T12355","display_name":"Genetic and rare skin diseases.","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/pemphigus","display_name":"pemphigus","score":0.9990000128746033},{"id":"https://openalex.org/keywords/bullous-pemphigoid","display_name":"bullous pemphigoid","score":0.9990000128746033},{"id":"https://openalex.org/keywords/paraneoplastic-pemphigus","display_name":"paraneoplastic pemphigus","score":0.9210000038146973},{"id":"https://openalex.org/keywords/hailey-hailey-disease","display_name":"Hailey-Hailey disease","score":0.9769999980926514},{"id":"https://openalex.org/keywords/acantholysis","display_name":"acantholysis","score":0.843999981880188},{"id":"https://openalex.org/keywords/desmoglein-antibodies","display_name":"desmoglein antibodies","score":0.7770000100135803},{"id":"https://openalex.org/keywords/direct-immunofluorescence","display_name":"direct immunofluorescence","score":0.8970000147819519},{"id":"https://openalex.org/keywords/immunosuppressive-therapy","display_name":"immunosuppressive therapy","score":0.7919999957084656},{"id":"https://openalex.org/keywords/rituximab","display_name":"rituximab","score":0.9980000257492065},{"id":"https://openalex.org/keywords/prednisone","display_name":"prednisone","score":0.9480000138282776},{"id":"https://openalex.org/keywords/intravenous-immunoglobulin","display_name":"intravenous immunoglobulin","score":0.9929999709129333},{"id":"https://openalex.org/keywords/botulinum-toxin","display_name":"botulinum toxin","score":0.847000002861023},{"id":"https://openalex.org/keywords/blistering-skin-disease","display_name":"blistering skin disease","score":0.5109999775886536}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9242174625396729},{"id":"https://openalex.org/C2781327288","wikidata":"https://www.wikidata.org/wiki/Q1483214","display_name":"Pemphigus","level":2,"score":0.8845769166946411},{"id":"https://openalex.org/C2780684067","wikidata":"https://www.wikidata.org/wiki/Q415794","display_name":"Acantholysis","level":4,"score":0.841153621673584},{"id":"https://openalex.org/C2779252107","wikidata":"https://www.wikidata.org/wiki/Q1004647","display_name":"Bullous pemphigoid","level":3,"score":0.7678338885307312},{"id":"https://openalex.org/C2781313415","wikidata":"https://www.wikidata.org/wiki/Q3899001","display_name":"Pemphigus vulgaris","level":2,"score":0.6920467615127563},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.6822812557220459},{"id":"https://openalex.org/C2780063514","wikidata":"https://www.wikidata.org/wiki/Q1394580","display_name":"Paraneoplastic pemphigus","level":4,"score":0.6525962948799133},{"id":"https://openalex.org/C2780653079","wikidata":"https://www.wikidata.org/wiki/Q412323","display_name":"Rituximab","level":3,"score":0.6191936135292053},{"id":"https://openalex.org/C2778720950","wikidata":"https://www.wikidata.org/wiki/Q424972","display_name":"Prednisone","level":2,"score":0.5938277840614319},{"id":"https://openalex.org/C2778075117","wikidata":"https://www.wikidata.org/wiki/Q881811","display_name":"Pemphigoid","level":4,"score":0.5853201150894165},{"id":"https://openalex.org/C2778862538","wikidata":"https://www.wikidata.org/wiki/Q263609","display_name":"Pemphigus foliaceus","level":4,"score":0.4825800955295563},{"id":"https://openalex.org/C2776536667","wikidata":"https://www.wikidata.org/wiki/Q627291","display_name":"Cicatricial pemphigoid","level":5,"score":0.4339594542980194},{"id":"https://openalex.org/C98246554","wikidata":"https://www.wikidata.org/wiki/Q5280334","display_name":"Direct fluorescent antibody","level":3,"score":0.4229419231414795},{"id":"https://openalex.org/C163764329","wikidata":"https://www.wikidata.org/wiki/Q785022","display_name":"Autoantibody","level":3,"score":0.39982035756111145},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.331609308719635},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.2551589608192444},{"id":"https://openalex.org/C159654299","wikidata":"https://www.wikidata.org/wiki/Q79460","display_name":"Antibody","level":2,"score":0.15450254082679749},{"id":"https://openalex.org/C2779338263","wikidata":"https://www.wikidata.org/wiki/Q208414","display_name":"Lymphoma","level":2,"score":0.08092653751373291},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.0799451470375061}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.2310/fm.1122","doi":"https://doi.org/10.2310/fm.1122","is_oa":false,"landing_page_url":"https://doi.org/10.2310/fm.1122","pdf_url":null,"source":{"id":"https://openalex.org/S4363605459","display_name":"DeckerMed Family Medicine","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"DeckerMed Family Medicine","raw_type":"journal-article"}],"best_oa_location":null,"sustainable_development_goals":[{"display_name":"Good health and well-being","score":0.9391000270843506,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W1997384320","https://openalex.org/W2418347364","https://openalex.org/W3041326334","https://openalex.org/W7060802858","https://openalex.org/W1972919010","https://openalex.org/W101894745","https://openalex.org/W3192827373","https://openalex.org/W4253895043","https://openalex.org/W2030206529","https://openalex.org/W2013536072"],"abstract_inverted_index":{"Pemphigus":[0],"disorders":[1,8],"are":[2,9],"characterized":[3,10,57],"by":[4,11,58],"acantholysis,":[5],"whereas":[6],"pemphigoid":[7,19],"a":[12,22,75,82,95],"dermal-epidermal":[13],"split.":[14],"Diagnosis":[15],"of":[16,24,49,61,97],"pemphigus":[17,55,85],"or":[18,27],"relies":[20],"on":[21,68],"combination":[23,48],"positive":[25,65],"anti-desmoglein":[26],"anti-collagen":[28],"XVII":[29],"serology,":[30],"confirmatory":[31],"direct":[32],"immunofluorescence,":[33],"and":[34,52,92,104,115],"clinical":[35],"features.":[36],"Treatment":[37],"for":[38,77],"immunobullous":[39],"disease":[40,80],"revolves":[41],"around":[42],"various":[43],"immunosuppressants,":[44],"most":[45],"often":[46],"some":[47],"rituximab,":[50,122],"prednisone,":[51],"IVIg.":[53],"Paraneoplastic":[54],"is":[56,81],"hemorrhagic":[59],"crusting":[60],"the":[62],"lips":[63],"with":[64],"indirect":[66],"immunofluorescence":[67],"rat":[69],"bladder":[70],"epithelium,":[71],"which":[72],"should":[73],"prompt":[74],"search":[76],"malignancy.":[78],"Hailey-Hailey":[79],"genetically":[83],"mediated":[84],"that":[86],"typically":[87],"occurs":[88],"in":[89],"skin":[90],"folds":[91],"responds":[93],"to":[94],"number":[96],"agents":[98],"including":[99],"botulinum":[100],"toxin,":[101],"topical":[102],"steroids,":[103],"other":[105],"anecdotal":[106],"therapies.":[107],"This":[108],"review":[109],"contains":[110],"17":[111],"figures,":[112],"2":[113],"tables,":[114],"109":[116],"references.":[117],"Keywords:":[118],"blister,":[119],"pemphigus,":[120],"bullous,":[121],"bullae,":[123],"prednisone":[124]},"counts_by_year":[],"updated_date":"2026-09-22T06:50:58.402377","created_date":"2021-02-01T00:00:00"}
