{"id":"https://openalex.org/W3040593189","doi":"https://doi.org/10.34119/bjhrv3n3-127","title":"Relato de caso de Esclerose Lateral Amiotr\u00f3fica (ELA) de in\u00edcio bulbar","display_name":"Relato de caso de Esclerose Lateral Amiotr\u00f3fica (ELA) de in\u00edcio bulbar","publication_year":2020,"publication_date":"2020-01-01","ids":{"openalex":"https://openalex.org/W3040593189","doi":"https://doi.org/10.34119/bjhrv3n3-127","mag":"3040593189"},"language":"es","primary_location":{"id":"doi:10.34119/bjhrv3n3-127","doi":"https://doi.org/10.34119/bjhrv3n3-127","is_oa":true,"landing_page_url":"http://doi.org/10.34119/bjhrv3n3-127","pdf_url":null,"source":{"id":"https://openalex.org/S4210177346","display_name":"Brazilian Journal of Health Review","issn_l":"2595-6825","issn":["2595-6825"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":["erih-plus"],"host_organization":"https://openalex.org/P4310312106","host_organization_name":"Brazilian Journal of Development","host_organization_lineage":["https://openalex.org/P4310312106"],"host_organization_lineage_names":["Brazilian Journal of Development"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Brazilian Journal of Health Review","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"http://doi.org/10.34119/bjhrv3n3-127","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5083852247","display_name":"Luana Marques Ribeiro","orcid":"https://orcid.org/0000-0003-2589-9465","observed_orcids":["https://orcid.org/0000-0003-2589-9465"]},"institutions":[{"id":"https://openalex.org/I4210144357","display_name":"Universidade Vila Velha","ror":"https://ror.org/04r8gaf17","country_code":"BR","type":"education","lineage":["https://openalex.org/I4210144357"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Luana Marques Ribeiro","raw_affiliation_strings":["Universidade Vila Velha (UVV)"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Universidade Vila Velha (UVV)","institution_ids":["https://openalex.org/I4210144357"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5016867504","display_name":"Vinicius Marques Falc\u00e3o","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Vinicius Marques Falc\u00e3o","raw_affiliation_strings":["Empresa Brasileira de Ensino Pesquisa e Extens\u00e3o (MULTIVIX)"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Empresa Brasileira de Ensino Pesquisa e Extens\u00e3o (MULTIVIX)","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5012574146","display_name":"Nayna Carvalho Oliveira","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Nayna Carvalho Oliveira","raw_affiliation_strings":["Empresa Brasileira de Ensino Pesquisa e Extens\u00e3o (MULTIVIX)"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Empresa Brasileira de Ensino Pesquisa e Extens\u00e3o (MULTIVIX)","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5077605243","display_name":"Amanda Cavalcante Lozer","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Amanda Cavalcante Lozer","raw_affiliation_strings":["Empresa Brasileira de Ensino Pesquisa e Extens\u00e3o (MULTIVIX)"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Empresa Brasileira de Ensino Pesquisa e Extens\u00e3o (MULTIVIX)","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5047009431","display_name":"Nath\u00e1lia Espindola Le\u00e7a Pereira","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210144357","display_name":"Universidade Vila Velha","ror":"https://ror.org/04r8gaf17","country_code":"BR","type":"education","lineage":["https://openalex.org/I4210144357"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Nath\u00e1lia Espindola Le\u00e7a Pereira","raw_affiliation_strings":["Universidade Vila Velha (UVV)"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Universidade Vila Velha (UVV)","institution_ids":["https://openalex.org/I4210144357"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5048104269","display_name":"Victor Nahas Rosa Campos","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Victor Nahas Rosa Campos","raw_affiliation_strings":["Empresa Brasileira de Ensino Pesquisa e Extens\u00e3o (MULTIVIX)"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Empresa Brasileira de Ensino Pesquisa e Extens\u00e3o (MULTIVIX)","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5029060726","display_name":"Ana Luiza Martins Pinto","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210144357","display_name":"Universidade Vila Velha","ror":"https://ror.org/04r8gaf17","country_code":"BR","type":"education","lineage":["https://openalex.org/I4210144357"]}],"countries":["BR"],"is_corresponding":false,"raw_author_name":"Ana Luiza Martins Pinto","raw_affiliation_strings":["Universidade Vila Velha (UVV)"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Universidade Vila Velha (UVV)","institution_ids":["https://openalex.org/I4210144357"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5009250433","display_name":"Soo Yang Lee","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Soo Yang Lee","raw_affiliation_strings":["MULTIVIX"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"MULTIVIX","institution_ids":[]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.2539,"has_fulltext":false,"cited_by_count":2,"citation_normalized_percentile":{"value":0.50781316,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":87,"max":93},"biblio":{"volume":"3","issue":"3","first_page":"5555","last_page":"5561"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10855","display_name":"Amyotrophic Lateral Sclerosis Research","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10855","display_name":"Amyotrophic Lateral Sclerosis Research","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10863","display_name":"Voice and Speech Disorders","score":9.999999747378752e-05,"subfield":{"id":"https://openalex.org/subfields/3616","display_name":"Speech and Hearing"},"field":{"id":"https://openalex.org/fields/36","display_name":"Health Professions"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12400","display_name":"Neurogenetic and Muscular Disorders Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/amyotrophic-lateral-sclerosis","display_name":"amyotrophic lateral sclerosis","score":0.9039999842643738},{"id":"https://openalex.org/keywords/bulbar-onset","display_name":"bulbar onset","score":0.9110000133514404},{"id":"https://openalex.org/keywords/dysarthria","display_name":"dysarthria","score":0.6639999747276306},{"id":"https://openalex.org/keywords/dysphagia","display_name":"dysphagia","score":0.9599999785423279},{"id":"https://openalex.org/keywords/myotonia","display_name":"myotonia","score":0.6330000162124634},{"id":"https://openalex.org/keywords/riluzole","display_name":"riluzole","score":0.5960000157356262},{"id":"https://openalex.org/keywords/non-invasive-ventilation","display_name":"non-invasive ventilation","score":0.7839999794960022},{"id":"https://openalex.org/keywords/bilevel-positive-airway-pressure","display_name":"bilevel positive airway pressure","score":0.7889999747276306},{"id":"https://openalex.org/keywords/corticobulbar-tract","display_name":"corticobulbar tract","score":0.8019999861717224},{"id":"https://openalex.org/keywords/respiratory-failure","display_name":"respiratory failure","score":0.7720000147819519},{"id":"https://openalex.org/keywords/differential-diagnosis","display_name":"differential diagnosis","score":0.35100001096725464},{"id":"https://openalex.org/keywords/temporal-lobe-atrophy","display_name":"temporal lobe atrophy","score":0.6150000095367432}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.4312078058719635},{"id":"https://openalex.org/C15708023","wikidata":"https://www.wikidata.org/wiki/Q80083","display_name":"Humanities","level":1,"score":0.32855135202407837},{"id":"https://openalex.org/C142362112","wikidata":"https://www.wikidata.org/wiki/Q735","display_name":"Art","level":0,"score":0.25515836477279663}],"mesh":[],"locations_count":5,"locations":[{"id":"doi:10.34119/bjhrv3n3-127","doi":"https://doi.org/10.34119/bjhrv3n3-127","is_oa":true,"landing_page_url":"http://doi.org/10.34119/bjhrv3n3-127","pdf_url":null,"source":{"id":"https://openalex.org/S4210177346","display_name":"Brazilian Journal of Health Review","issn_l":"2595-6825","issn":["2595-6825"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":["erih-plus"],"host_organization":"https://openalex.org/P4310312106","host_organization_name":"Brazilian Journal of Development","host_organization_lineage":["https://openalex.org/P4310312106"],"host_organization_lineage_names":["Brazilian Journal of Development"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Brazilian Journal of Health Review","raw_type":"journal-article"},{"id":"pmh:oai:ojs.brazilianjournals.com:article/10962","doi":null,"is_oa":false,"landing_page_url":"https://www.brazilianjournals.com/index.php/BJHR/article/view/10962","pdf_url":null,"source":{"id":"https://openalex.org/S4306402641","display_name":"LA Referencia (Red Federada de Repositorios Institucionales de Publicaciones Cient\u00edficas)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I4383465926","host_organization_name":"LA Referencia","host_organization_lineage":["https://openalex.org/I4383465926"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Brazilian Journal of Health Review; Vol 3, No 3 (2020); 5555-5561","raw_type":"<dc:type>info:eu-repo/semantics/article"},{"id":"pmh:oai:ojs.www.brazilianjournals.com:article/10962","doi":null,"is_oa":false,"landing_page_url":"http://www.brazilianjournals.com/index.php/BJHR/article/view/10962","pdf_url":null,"source":{"id":"https://openalex.org/S4306402641","display_name":"LA Referencia (Red Federada de Repositorios Institucionales de Publicaciones Cient\u00edficas)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I4383465926","host_organization_name":"LA Referencia","host_organization_lineage":["https://openalex.org/I4383465926"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Brazilian Journal of Health Review; Vol 3, No 3 (2020); 5555-5561","raw_type":"<dc:type>info:eu-repo/semantics/article"},{"id":"pmh:oai:americanae.aecid.es:2647548","doi":null,"is_oa":false,"landing_page_url":"http://americanae.aecid.es/americanae/es/registros/registro.do?tipoRegistro=MTD&idBib=2647548","pdf_url":null,"source":{"id":"https://openalex.org/S4306400786","display_name":"Americanae (AECID Library)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Brazilian Journal of Health Review; Vol 3, No 3 (2020); 5555-5561","raw_type":"<dc:type>info:eu-repo/semantics/article"},{"id":"pmh:oai:ojs2.ojs.brazilianjournals.com.br:article/10962","doi":null,"is_oa":false,"landing_page_url":"https://ojs.brazilianjournals.com.br/ojs/index.php/BJHR/article/view/10962","pdf_url":null,"source":{"id":"https://openalex.org/S4306402641","display_name":"LA Referencia (Red Federada de Repositorios Institucionales de Publicaciones Cient\u00edficas)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I4383465926","host_organization_name":"LA Referencia","host_organization_lineage":["https://openalex.org/I4383465926"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"instacron:BJRH","raw_type":"info:eu-repo/semantics/article"}],"best_oa_location":{"id":"doi:10.34119/bjhrv3n3-127","doi":"https://doi.org/10.34119/bjhrv3n3-127","is_oa":true,"landing_page_url":"http://doi.org/10.34119/bjhrv3n3-127","pdf_url":null,"source":{"id":"https://openalex.org/S4210177346","display_name":"Brazilian Journal of Health Review","issn_l":"2595-6825","issn":["2595-6825"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":["erih-plus"],"host_organization":"https://openalex.org/P4310312106","host_organization_name":"Brazilian Journal of Development","host_organization_lineage":["https://openalex.org/P4310312106"],"host_organization_lineage_names":["Brazilian Journal of Development"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Brazilian Journal of Health Review","raw_type":"journal-article"},"sustainable_development_goals":[{"score":1.0,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W7153718145","https://openalex.org/W2758751657","https://openalex.org/W2031514989","https://openalex.org/W3007105721","https://openalex.org/W1948698278","https://openalex.org/W2968241422","https://openalex.org/W6990841795","https://openalex.org/W7220604426","https://openalex.org/W4405444348","https://openalex.org/W7215516340"],"abstract_inverted_index":{"ELA":[0,34,222],"\u00e9":[1,174,204],"uma":[2],"doen\u00e7a":[3,120],"neurodegenerativa":[4],"mais":[5],"prevalente":[6],"em":[7,148,223],"homens,":[8],"podendo":[9],"ser":[10],"cervical,":[11],"lombar":[12],"ou":[13],"bulbar":[14,35],"(25%":[15],"dos":[16,72],"casos),":[17],"essa":[18],"\u00faltima":[19],"definida":[20],"pela":[21],"degenera\u00e7\u00e3o":[22,82],"do":[23,172,180,197,247],"neur\u00f4nio":[24],"motor":[25],"superior":[26],"e/ou":[27],"inferior.":[28],"Esse":[29],"relato":[30],"exp\u00f5e":[31],"caso":[32],"de":[33,43,60,64,135,153,158,228],"e":[36,52,62,87,92,104,109,127,132,138,161,210,215,243],"seu":[37],"quadro":[38],"t\u00edpico":[39],"atrav\u00e9s":[40],"da":[41,100,124,178,184,213],"an\u00e1lise":[42],"prontu\u00e1rio.":[44],"Homem,":[45],"60,":[46],"hipertenso,":[47],"sofria":[48],"disartria,":[49],"engasgos,":[50],"c\u00e2imbras":[51,160],"esquecimento":[53],"h\u00e1":[54],"2":[55],"meses.":[56],"Observou-se":[57],"fascicula\u00e7\u00f5es,":[58],"atrofia":[59,134],"l\u00edngua":[61],"miotonia":[63,157],"MMSS.":[65],"A":[66,75,190],"Resson\u00e2ncia":[67],"Magn\u00e9tica":[68],"revelou":[69],"redu\u00e7\u00e3o":[70],"volum\u00e9trica":[71],"lobos":[73],"temporais.":[74],"eletroneuromiografia":[76],"indicou":[77,114],"\u201cAcometimento":[78],"pr\u00e9-ganglionar":[79],"bilateral":[80],"com":[81,98,156],"motora\u201d.":[83],"Receitou-se":[84],"Dexa-citoneurin,":[85],"Riluzol":[86],"Vitaminas":[88],"B6,":[89],"E,":[90],"C":[91],"D.":[93],"Ap\u00f3s":[94],"4":[95],"meses,":[96],"retornou":[97],"melhora":[99],"mem\u00f3ria,":[101],"estridores":[102],"lar\u00edngeos":[103,137],"ins\u00f4nia.":[105],"Prescrito":[106],"Donaren":[107],"Retard":[108],"encaminhado":[110],"ao":[111],"pneumologista,":[112],"que":[113,219],"BIPAP,":[115],"cessando":[116],"o":[117,175,202,232],"estridor.":[118],"Essa":[119],"caracteriza-se":[121],"por":[122,195],"disfun\u00e7\u00f5es":[123],"degluti\u00e7\u00e3o,":[125],"voz":[126],"articula\u00e7\u00e3o,":[128],"acomete":[129],"nervos":[130],"faciais":[131],"gera":[133],"m\u00fasculos":[136],"linguais,":[139],"explicando":[140],"os":[141,206],"sintomas.":[142],"Tem":[143],"in\u00edcio":[144],"tardio":[145],"(60-69":[146],"anos)":[147],"rela\u00e7\u00e3o":[149],"\u00e0s":[150],"outras":[151],"formas":[152],"ELA.":[154],"Evoluiu":[155],"MMSS,":[159],"paresia":[162],"espa?stica.":[163],"Uma":[164],"boa":[165],"terap\u00eautica":[166],"neuroprotetora":[167],"contra":[168],"a":[169,188,240,245],"a\u00e7\u00e3o":[170],"apopt\u00f3tica":[171],"glutamato":[173,181],"Riluzol,":[176],"antagonista":[177],"libera\u00e7\u00e3o":[179],"e,":[182],"junto":[183],"ventila\u00e7\u00e3o":[185],"n\u00e3o-invasiva,":[186],"aumenta":[187],"sobrevida.":[189],"insufici\u00eancia":[191],"respirat\u00f3ria":[192],"(IR)":[193],"ocorre":[194],"acometimento":[196],"trato":[198],"corticobulbar.":[199],"Nesse":[200],"\u00ednterim,":[201],"foco":[203],"amenizar":[205],"sintomas":[207],"orofar\u00edngeos,":[208],"musculoesquel\u00e9ticos":[209],"depressivos,":[211],"al\u00e9m":[212],"ansiedade":[214],"dispneia.":[216],"\u00c9":[217],"importante":[218],"m\u00e9dicos":[220],"incluam":[221],"seus":[224],"diagn\u00f3sticos":[225],"diferenciais.":[226],"Apesar":[227],"n\u00e3o":[229],"ter":[230],"cura,":[231],"tratamento":[233],"efetivo":[234],"pode":[235],"retardar":[236],"sua":[237],"evolu\u00e7\u00e3o,":[238],"reduzir":[239],"deteriora\u00e7\u00e3o":[241],"motora":[242],"prolongar":[244],"sobrevida":[246],"paciente.":[248]},"counts_by_year":[{"year":2022,"cited_by_count":1},{"year":2021,"cited_by_count":1}],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2020-07-10T00:00:00"}
