{"id":"https://openalex.org/W3030108557","doi":"https://doi.org/10.1016/b978-0-12-816768-7.00026-0","title":"IPEX and IPEX-like disorders","display_name":"IPEX and IPEX-like disorders","publication_year":2020,"publication_date":"2020-01-01","ids":{"openalex":"https://openalex.org/W3030108557","doi":"https://doi.org/10.1016/b978-0-12-816768-7.00026-0","mag":"3030108557"},"language":"en","primary_location":{"id":"doi:10.1016/b978-0-12-816768-7.00026-0","doi":"https://doi.org/10.1016/b978-0-12-816768-7.00026-0","is_oa":false,"landing_page_url":"https://doi.org/10.1016/b978-0-12-816768-7.00026-0","pdf_url":null,"source":{"id":"https://openalex.org/S4306463230","display_name":"Elsevier eBooks","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"ebook platform"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Stiehm's Immune Deficiencies","raw_type":"book-chapter"},"volume":{"id":"https://openalex.org/W1711601237","display_name":"Stiehm's Immune Deficiencies"},"type":"book-chapter","indexed_in":["crossref"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5071168848","display_name":"Troy R. Torgerson","orcid":"https://orcid.org/0000-0003-3489-5036","observed_orcids":["https://orcid.org/0000-0003-3489-5036"]},"institutions":[{"id":"https://openalex.org/I1295499534","display_name":"Seattle Children's Hospital","ror":"https://ror.org/01njes783","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1295499534"]},{"id":"https://openalex.org/I201448701","display_name":"University of Washington","ror":"https://ror.org/00cvxb145","country_code":"US","type":"education","lineage":["https://openalex.org/I201448701"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"Troy R. Torgerson","raw_affiliation_strings":["Associate Professor of Pediatrics, Immunology/Rheumatology, University of Washington and Seattle Children's Hospital, Seattle, WA, United States"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Associate Professor of Pediatrics, Immunology/Rheumatology, University of Washington and Seattle Children's Hospital, Seattle, WA, United States","institution_ids":["https://openalex.org/I1295499534","https://openalex.org/I201448701"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":["https://openalex.org/A5071168848"],"corresponding_institution_ids":["https://openalex.org/I1295499534","https://openalex.org/I201448701"],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":1,"citation_normalized_percentile":{"value":0.16509776,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":89,"max":94},"biblio":{"volume":null,"issue":null,"first_page":"617","last_page":"631"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11725","display_name":"Immunodeficiency and Autoimmune Disorders","score":0.9970999956130981,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T11725","display_name":"Immunodeficiency and Autoimmune Disorders","score":0.9970999956130981,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T10031","display_name":"T-cell and B-cell Immunology","score":0.003000000026077032,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/ipex-syndrome","display_name":"IPEX syndrome","score":0.9769999980926514},{"id":"https://openalex.org/keywords/primary-immunodeficiency","display_name":"primary immunodeficiency","score":0.8109999895095825},{"id":"https://openalex.org/keywords/autoimmunity","display_name":"autoimmunity","score":0.9350000023841858},{"id":"https://openalex.org/keywords/autoinflammation","display_name":"autoinflammation","score":0.902999997138977},{"id":"https://openalex.org/keywords/atopy","display_name":"atopy","score":0.9860000014305115},{"id":"https://openalex.org/keywords/regulatory-t-cells","display_name":"regulatory T cells","score":0.734000027179718},{"id":"https://openalex.org/keywords/immunodeficiency","display_name":"immunodeficiency","score":0.8259999752044678},{"id":"https://openalex.org/keywords/infection-susceptibility","display_name":"infection susceptibility","score":0.7179999947547913}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.31605255603790283}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.1016/b978-0-12-816768-7.00026-0","doi":"https://doi.org/10.1016/b978-0-12-816768-7.00026-0","is_oa":false,"landing_page_url":"https://doi.org/10.1016/b978-0-12-816768-7.00026-0","pdf_url":null,"source":{"id":"https://openalex.org/S4306463230","display_name":"Elsevier eBooks","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"ebook platform"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Stiehm's Immune Deficiencies","raw_type":"book-chapter"}],"best_oa_location":null,"sustainable_development_goals":[{"score":0.9476000070571899,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":38,"referenced_works":["https://openalex.org/W1486722793","https://openalex.org/W1499151513","https://openalex.org/W1966289025","https://openalex.org/W1972187865","https://openalex.org/W1984828633","https://openalex.org/W2012597366","https://openalex.org/W2016098094","https://openalex.org/W2023910502","https://openalex.org/W2031719425","https://openalex.org/W2046573218","https://openalex.org/W2053356256","https://openalex.org/W2077940776","https://openalex.org/W2098267826","https://openalex.org/W2099667165","https://openalex.org/W2108270409","https://openalex.org/W2113499607","https://openalex.org/W2144280353","https://openalex.org/W2156131655","https://openalex.org/W2169248706","https://openalex.org/W2178197433","https://openalex.org/W2199311095","https://openalex.org/W2211932244","https://openalex.org/W2317480157","https://openalex.org/W2326288135","https://openalex.org/W2467020097","https://openalex.org/W2595944899","https://openalex.org/W2622876879","https://openalex.org/W2758845410","https://openalex.org/W2774825032","https://openalex.org/W2790239219","https://openalex.org/W2795242253","https://openalex.org/W2806826340","https://openalex.org/W2883457299","https://openalex.org/W2886181943","https://openalex.org/W2890748154","https://openalex.org/W2898668831","https://openalex.org/W2941331726","https://openalex.org/W2964065645"],"related_works":["https://openalex.org/W3171631773","https://openalex.org/W2086437343","https://openalex.org/W3212666477","https://openalex.org/W1998157143","https://openalex.org/W4281838462","https://openalex.org/W4313514507","https://openalex.org/W2275768091","https://openalex.org/W2108270409","https://openalex.org/W7155167088","https://openalex.org/W3133347613"],"abstract_inverted_index":null,"counts_by_year":[{"year":2024,"cited_by_count":1}],"updated_date":"2026-10-10T09:11:00.788812","created_date":"2020-06-05T00:00:00"}
