{"id":"https://openalex.org/W3020985697","doi":null,"title":"Hidradenitis Suppurativa and Concomitant Down Syndrome: Literature Review of Other Associated Mucocutaneous Manifestations in Adults.","display_name":"Hidradenitis Suppurativa and Concomitant Down Syndrome: Literature Review of Other Associated Mucocutaneous Manifestations in Adults.","publication_year":2017,"publication_date":"2017-01-01","ids":{"openalex":"https://openalex.org/W3020985697","mag":"3020985697","pmid":"https://pubmed.ncbi.nlm.nih.gov/28859733"},"language":"en","primary_location":{"id":"pmid:28859733","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/28859733","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Skinmed","raw_type":"Case Reports"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5016613633","display_name":"Virendra Nath Sehgal","orcid":"https://orcid.org/0000-0001-7091-9539","observed_orcids":["https://orcid.org/0000-0001-7091-9539"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Virendra N Sehgal","raw_affiliation_strings":["DermatoVenereology (Skin/VD) Centre, Sehgal Nursing Home, Panchwati, Delhi, India; drsehgal@ndf.vsnl.net.in","DermatoVenereology (Skin/VD) Centre, Sehgal Nursing Home, Panchwati, Delhi, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"DermatoVenereology (Skin/VD) Centre, Sehgal Nursing Home, Panchwati, Delhi, India; drsehgal@ndf.vsnl.net.in","institution_ids":[]},{"raw_affiliation_string":"DermatoVenereology (Skin/VD) Centre, Sehgal Nursing Home, Panchwati, Delhi, India","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5037805211","display_name":"Naresh Sehgal","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Naresh Sehgal","raw_affiliation_strings":["DermatoVenereology (Skin/VD) Centre, Sehgal Nursing Home, Panchwati, Delhi, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"DermatoVenereology (Skin/VD) Centre, Sehgal Nursing Home, Panchwati, Delhi, India","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5042070619","display_name":"Ruchi Sehgal","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Ruchi Sehgal","raw_affiliation_strings":["DermatoVenereology (Skin/VD) Centre, Sehgal Nursing Home, Panchwati, Delhi, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"DermatoVenereology (Skin/VD) Centre, Sehgal Nursing Home, Panchwati, Delhi, India","institution_ids":[]}]}],"institutions":[],"countries_distinct_count":0,"institutions_distinct_count":0,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.6053,"has_fulltext":false,"cited_by_count":3,"citation_normalized_percentile":{"value":0.73055904,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":93},"biblio":{"volume":"15","issue":"4","first_page":"253","last_page":"258"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12731","display_name":"Hidradenitis Suppurativa and Treatments","score":0.9990000128746033,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12731","display_name":"Hidradenitis Suppurativa and Treatments","score":0.9990000128746033,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12355","display_name":"Genetic and rare skin diseases.","score":0.00019999999494757503,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12328","display_name":"Autoimmune and Inflammatory Disorders","score":0.00019999999494757503,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/hidradenitis-suppurativa","display_name":"hidradenitis suppurativa","score":1.0},{"id":"https://openalex.org/keywords/down-syndrome","display_name":"Down syndrome","score":0.9990000128746033},{"id":"https://openalex.org/keywords/mucocutaneous-manifestations","display_name":"mucocutaneous manifestations","score":0.8980000019073486},{"id":"https://openalex.org/keywords/hurley-staging","display_name":"Hurley staging","score":0.875},{"id":"https://openalex.org/keywords/apocrine-sweat-glands","display_name":"apocrine sweat glands","score":0.7940000295639038},{"id":"https://openalex.org/keywords/elastosis-perforans-serpiginosa","display_name":"elastosis perforans serpiginosa","score":0.9279999732971191},{"id":"https://openalex.org/keywords/fissured-tongue","display_name":"fissured tongue","score":0.9520000219345093},{"id":"https://openalex.org/keywords/macroglossia","display_name":"macroglossia","score":0.972000002861023},{"id":"https://openalex.org/keywords/syringoma","display_name":"syringoma","score":0.968999981880188},{"id":"https://openalex.org/keywords/palmoplantar-keratoderma","display_name":"palmoplantar keratoderma","score":0.9340000152587891},{"id":"https://openalex.org/keywords/cheilitis","display_name":"cheilitis","score":0.9860000014305115},{"id":"https://openalex.org/keywords/dry-skin","display_name":"dry skin","score":0.828000009059906},{"id":"https://openalex.org/keywords/atopic-dermatitis","display_name":"atopic dermatitis","score":0.9900000095367432},{"id":"https://openalex.org/keywords/seborrheic-dermatitis","display_name":"seborrheic dermatitis","score":0.9990000128746033},{"id":"https://openalex.org/keywords/vitiligo","display_name":"vitiligo","score":1.0},{"id":"https://openalex.org/keywords/cutis-marmorata","display_name":"cutis marmorata","score":0.9990000128746033},{"id":"https://openalex.org/keywords/alopecia-areata","display_name":"alopecia areata","score":0.9319999814033508}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9649651050567627},{"id":"https://openalex.org/C2776002364","wikidata":"https://www.wikidata.org/wiki/Q341999","display_name":"Hidradenitis suppurativa","level":3,"score":0.875402569770813},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.8514298796653748},{"id":"https://openalex.org/C2779075128","wikidata":"https://www.wikidata.org/wiki/Q42165","display_name":"Buttocks","level":2,"score":0.6678148508071899},{"id":"https://openalex.org/C2779203496","wikidata":"https://www.wikidata.org/wiki/Q545408","display_name":"Anhidrosis","level":2,"score":0.6274861097335815},{"id":"https://openalex.org/C150875184","wikidata":"https://www.wikidata.org/wiki/Q6151549","display_name":"Apocrine","level":2,"score":0.6182110905647278},{"id":"https://openalex.org/C156662089","wikidata":"https://www.wikidata.org/wiki/Q6931223","display_name":"Mucocutaneous zone","level":3,"score":0.5176151990890503},{"id":"https://openalex.org/C2779384505","wikidata":"https://www.wikidata.org/wiki/Q17007513","display_name":"Concomitant","level":2,"score":0.497419148683548},{"id":"https://openalex.org/C2777645581","wikidata":"https://www.wikidata.org/wiki/Q1671433","display_name":"Intertriginous","level":3,"score":0.48539599776268005},{"id":"https://openalex.org/C2776728111","wikidata":"https://www.wikidata.org/wiki/Q1641068","display_name":"Hyperpigmentation","level":2,"score":0.44668352603912354},{"id":"https://openalex.org/C2777484424","wikidata":"https://www.wikidata.org/wiki/Q448310","display_name":"Seborrheic dermatitis","level":2,"score":0.42709147930145264},{"id":"https://openalex.org/C2778487983","wikidata":"https://www.wikidata.org/wiki/Q524095","display_name":"Macroglossia","level":3,"score":0.4249756336212158},{"id":"https://openalex.org/C2779744641","wikidata":"https://www.wikidata.org/wiki/Q9614","display_name":"Tongue","level":2,"score":0.27614158391952515},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.26912450790405273},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.24958422780036926},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.1569005250930786}],"mesh":[{"descriptor_ui":"D004314","descriptor_name":"Down Syndrome","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D014063","descriptor_name":"Tongue, Fissured","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D017497","descriptor_name":"Hidradenitis Suppurativa","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D055815","descriptor_name":"Young Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"pmid:28859733","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/28859733","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Skinmed","raw_type":"Case Reports"},{"id":"mag:3020985697","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/28859733","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":"PubMed","raw_type":null}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":0.9907000064849854,"display_name":"Good health and well-being"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W7169546964","https://openalex.org/W2688006449","https://openalex.org/W2509519671","https://openalex.org/W2974023208","https://openalex.org/W3107992259","https://openalex.org/W7163351916","https://openalex.org/W4245744276","https://openalex.org/W132999463","https://openalex.org/W2802757240","https://openalex.org/W3083703573"],"abstract_inverted_index":{"This":[0],"contribution":[1],"describes":[2],"hidradenitis":[3],"suppurativa":[4],"(HS)":[5],"occurring":[6],"in":[7],"Down":[8],"disease":[9],"that":[10],"presented":[11],"with":[12,51],"morphology":[13],"conforming":[14],"to":[15],"an":[16],"overlap":[17],"of":[18,23,31,72,82],"stages":[19],"1":[20],"and":[21,44,64,70,79,89,110],"2":[22],"the":[24,29,60,77],"Hurley":[25],"staging":[26],"system,":[27],"namely":[28],"formation":[30],"solitary":[32],"or":[33,39,46],"multiple":[34,47],"isolated":[35],"abscesses":[36],"without":[37],"scarring":[38],"sinus":[40,52],"tracts,":[41],"recurrent":[42],"abscesses,":[43],"single":[45],"widely":[48],"separated":[49],"lesions":[50,67],"tract":[53],"formation,":[54],"occupying":[55],"apocrine":[56],"sweat":[57],"gland-bearing":[58],"areas:":[59],"inner":[61],"thighs,":[62],"groin,":[63],"buttocks.":[65],"The":[66],"were":[68],"bilateral":[69],"symmetrical,":[71],"rare":[73],"occurrence.":[74],"In":[75],"addition,":[76],"clinical":[78],"pathognomonic":[80],"features":[81],"several":[83],"other":[84],"concomitant":[85],"diseases":[86],"are":[87],"defined":[88],"reviewed;":[90],"these":[91],"include":[92],"elastosis":[93],"perforans":[94],"serpiginosa,":[95],"fissured":[96],"tongue/macroglossia,":[97],"syringomas,":[98],"palmoplantar":[99],"keratodermas,":[100],"cheilitis,":[101],"xerosis,":[102],"atopic":[103],"dermatitis,":[104,106],"seborrheic":[105],"vitiligo,":[107],"cutis":[108],"marmorata,":[109],"alopecia":[111],"areata.":[112]},"counts_by_year":[{"year":2022,"cited_by_count":1},{"year":2019,"cited_by_count":1},{"year":2018,"cited_by_count":1}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2020-05-13T00:00:00"}
