{"id":"https://openalex.org/W3008399355","doi":"https://doi.org/10.1182/blood.2019004216","title":"The TEMPI syndrome","display_name":"The TEMPI syndrome","publication_year":2020,"publication_date":"2020-02-27","ids":{"openalex":"https://openalex.org/W3008399355","doi":"https://doi.org/10.1182/blood.2019004216","mag":"3008399355","pmid":"https://pubmed.ncbi.nlm.nih.gov/32108223"},"language":"en","primary_location":{"id":"doi:10.1182/blood.2019004216","doi":"https://doi.org/10.1182/blood.2019004216","is_oa":false,"landing_page_url":"https://doi.org/10.1182/blood.2019004216","pdf_url":null,"source":{"id":"https://openalex.org/S200071133","display_name":"Blood","issn_l":"0006-4971","issn":["0006-4971","1528-0020"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Blood","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5088797237","display_name":"David B. Sykes","orcid":"https://orcid.org/0000-0002-9788-0221","observed_orcids":["https://orcid.org/0000-0002-9788-0221"]},"institutions":[{"id":"https://openalex.org/I4210087915","display_name":"Massachusetts General Hospital","ror":"https://ror.org/002pd6e78","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I4210087915","https://openalex.org/I48633490"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"David B. Sykes","raw_affiliation_strings":["Massachusetts General Hospital, Boston, MA;"],"raw_orcid":"https://orcid.org/0000-0002-9788-0221","affiliations":[{"raw_affiliation_string":"Massachusetts General Hospital, Boston, MA;","institution_ids":["https://openalex.org/I4210087915"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5052288829","display_name":"Casey Lee O'Connell","orcid":"https://orcid.org/0000-0001-7665-3911","observed_orcids":["https://orcid.org/0000-0001-7665-3911"]},"institutions":[{"id":"https://openalex.org/I1174212","display_name":"University of Southern California","ror":"https://ror.org/03taz7m60","country_code":"US","type":"education","lineage":["https://openalex.org/I1174212"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Casey O\u2019Connell","raw_affiliation_strings":["Keck School of Medicine, University of Southern California, Los Angeles, CA; and"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Keck School of Medicine, University of Southern California, Los Angeles, CA; and","institution_ids":["https://openalex.org/I1174212"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5063714660","display_name":"Wilfried Schroyens","orcid":"https://orcid.org/0000-0003-4244-3523","observed_orcids":["https://orcid.org/0000-0003-4244-3523"]},"institutions":[{"id":"https://openalex.org/I4210102047","display_name":"Antwerp University Hospital","ror":"https://ror.org/01hwamj44","country_code":"BE","type":"funder","lineage":["https://openalex.org/I4210102047"]}],"countries":["BE"],"is_corresponding":false,"raw_author_name":"Wilfried Schroyens","raw_affiliation_strings":["Department of Hematology, Antwerp University Hospital, Antwerp, Belgium"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Hematology, Antwerp University Hospital, Antwerp, Belgium","institution_ids":["https://openalex.org/I4210102047"]}]}],"institutions":[],"countries_distinct_count":2,"institutions_distinct_count":3,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":{"value":5500,"currency":"USD","value_usd":5500},"apc_paid":null,"fwci":5.3667,"has_fulltext":false,"cited_by_count":53,"citation_normalized_percentile":{"value":0.96721311,"is_in_top_1_percent":false,"is_in_top_10_percent":true},"cited_by_percentile_year":{"min":95,"max":100},"biblio":{"volume":"135","issue":"15","first_page":"1199","last_page":"1203"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10649","display_name":"Multiple Myeloma Research and Treatments","score":0.9926999807357788,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10649","display_name":"Multiple Myeloma Research and Treatments","score":0.9926999807357788,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11628","display_name":"Myeloproliferative Neoplasms: Diagnosis and Treatment","score":0.0007999999797903001,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11534","display_name":"Erythropoietin and Anemia Treatment","score":0.0005000000237487257,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/telangiectasia","display_name":"telangiectasia","score":0.8199999928474426},{"id":"https://openalex.org/keywords/erythrocytosis","display_name":"erythrocytosis","score":0.9120000004768372},{"id":"https://openalex.org/keywords/monoclonal-gammopathy","display_name":"monoclonal gammopathy","score":0.9929999709129333},{"id":"https://openalex.org/keywords/perinephric-fluid-collection","display_name":"perinephric fluid collection","score":0.9079999923706055},{"id":"https://openalex.org/keywords/intrapulmonary-shunting","display_name":"intrapulmonary shunting","score":0.9850000143051147},{"id":"https://openalex.org/keywords/monoclonal-antibodies","display_name":"monoclonal antibodies","score":0.8569999933242798},{"id":"https://openalex.org/keywords/acquired-disorders","display_name":"acquired disorders","score":0.38100001215934753}],"concepts":[{"id":"https://openalex.org/C2778112473","wikidata":"https://www.wikidata.org/wiki/Q4301818","display_name":"Monoclonal gammopathy","level":5,"score":0.7248938679695129},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.5855902433395386},{"id":"https://openalex.org/C163864487","wikidata":"https://www.wikidata.org/wiki/Q6901461","display_name":"Monoclonal","level":4,"score":0.42773517966270447},{"id":"https://openalex.org/C2778534260","wikidata":"https://www.wikidata.org/wiki/Q218706","display_name":"Erythropoietin","level":2,"score":0.41071152687072754},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.3645508885383606},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.35624563694000244},{"id":"https://openalex.org/C542903549","wikidata":"https://www.wikidata.org/wiki/Q422248","display_name":"Monoclonal antibody","level":3,"score":0.33793479204177856},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.333578884601593},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.3025094270706177},{"id":"https://openalex.org/C159654299","wikidata":"https://www.wikidata.org/wiki/Q79460","display_name":"Antibody","level":2,"score":0.18432188034057617}],"mesh":[{"descriptor_ui":"D004921","descriptor_name":"Erythropoietin","qualifier_ui":"Q000097","qualifier_name":"blood","is_major_topic":true},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008171","descriptor_name":"Lung Diseases","qualifier_ui":"Q000097","qualifier_name":"blood","is_major_topic":false},{"descriptor_ui":"D008171","descriptor_name":"Lung Diseases","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":true},{"descriptor_ui":"D008171","descriptor_name":"Lung Diseases","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":false},{"descriptor_ui":"D010265","descriptor_name":"Paraproteinemias","qualifier_ui":"Q000097","qualifier_name":"blood","is_major_topic":false},{"descriptor_ui":"D010265","descriptor_name":"Paraproteinemias","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":true},{"descriptor_ui":"D010265","descriptor_name":"Paraproteinemias","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":false},{"descriptor_ui":"D011086","descriptor_name":"Polycythemia","qualifier_ui":"Q000097","qualifier_name":"blood","is_major_topic":false},{"descriptor_ui":"D011086","descriptor_name":"Polycythemia","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":true},{"descriptor_ui":"D011086","descriptor_name":"Polycythemia","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":false},{"descriptor_ui":"D013577","descriptor_name":"Syndrome","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D013684","descriptor_name":"Telangiectasis","qualifier_ui":"Q000097","qualifier_name":"blood","is_major_topic":false},{"descriptor_ui":"D013684","descriptor_name":"Telangiectasis","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":true},{"descriptor_ui":"D013684","descriptor_name":"Telangiectasis","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.1182/blood.2019004216","doi":"https://doi.org/10.1182/blood.2019004216","is_oa":false,"landing_page_url":"https://doi.org/10.1182/blood.2019004216","pdf_url":null,"source":{"id":"https://openalex.org/S200071133","display_name":"Blood","issn_l":"0006-4971","issn":["0006-4971","1528-0020"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Blood","raw_type":"journal-article"},{"id":"pmid:32108223","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/32108223","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Blood","raw_type":"Journal Article"}],"best_oa_location":null,"sustainable_development_goals":[{"score":0.979200005531311,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":33,"referenced_works":["https://openalex.org/W1568958266","https://openalex.org/W1747880793","https://openalex.org/W1874986605","https://openalex.org/W1975136159","https://openalex.org/W1991852898","https://openalex.org/W1994740295","https://openalex.org/W2008261411","https://openalex.org/W2009528829","https://openalex.org/W2010059437","https://openalex.org/W2063772107","https://openalex.org/W2071120659","https://openalex.org/W2082875455","https://openalex.org/W2087849907","https://openalex.org/W2095890345","https://openalex.org/W2096999034","https://openalex.org/W2111823703","https://openalex.org/W2150108187","https://openalex.org/W2152013192","https://openalex.org/W2172137753","https://openalex.org/W2243219483","https://openalex.org/W2321709204","https://openalex.org/W2339268403","https://openalex.org/W2513163117","https://openalex.org/W2522959591","https://openalex.org/W2806475228","https://openalex.org/W2884732785","https://openalex.org/W2889953488","https://openalex.org/W2910080696","https://openalex.org/W2937502263","https://openalex.org/W2946259664","https://openalex.org/W2953728338","https://openalex.org/W2963455874","https://openalex.org/W4241634465"],"related_works":["https://openalex.org/W4405038683","https://openalex.org/W4280640742","https://openalex.org/W7108757944","https://openalex.org/W2082875455","https://openalex.org/W4252358254","https://openalex.org/W4289517801","https://openalex.org/W2559156138","https://openalex.org/W2172137753","https://openalex.org/W3203394732","https://openalex.org/W2885591951"],"abstract_inverted_index":{"The":[0],"TEMPI":[1,62],"syndrome":[2,63],"is":[3,53],"a":[4,73],"rare":[5],"and":[6,23,32,55,72],"acquired":[7],"disorder":[8],"characterized":[9],"by":[10],"5":[11],"salient":[12],"features,":[13],"which":[14],"compose":[15],"its":[16],"name:":[17],"(1)":[18],"telangiectasias;":[19],"(2)":[20],"elevated":[21],"erythropoietin":[22],"erythrocytosis;":[24],"(3)":[25],"monoclonal":[26,51],"gammopathy;":[27],"(4)":[28],"perinephric":[29],"fluid":[30],"collections;":[31],"(5)":[33],"intrapulmonary":[34],"shunting.":[35],"Complete":[36],"resolution":[37],"of":[38,60,69],"symptoms":[39],"following":[40],"treatment":[41],"with":[42],"plasma":[43],"cell-directed":[44],"therapy":[45],"supports":[46],"the":[47,50,58,61,67],"hypothesis":[48],"that":[49],"antibody":[52],"causal":[54],"pathogenic.":[56],"Understanding":[57],"basis":[59],"will":[64],"depend":[65],"on":[66],"identification":[68],"additional":[70],"patients":[71],"coordinated":[74],"international":[75],"effort.":[76]},"counts_by_year":[{"year":2026,"cited_by_count":7},{"year":2025,"cited_by_count":4},{"year":2024,"cited_by_count":8},{"year":2023,"cited_by_count":8},{"year":2022,"cited_by_count":17},{"year":2021,"cited_by_count":6},{"year":2020,"cited_by_count":3}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2020-03-06T00:00:00"}
