{"id":"https://openalex.org/W3000458198","doi":"https://doi.org/10.3949/ccjm.87a.18051","title":"Sickle cell disease: A primary care update","display_name":"Sickle cell disease: A primary care update","publication_year":2020,"publication_date":"2020-01-01","ids":{"openalex":"https://openalex.org/W3000458198","doi":"https://doi.org/10.3949/ccjm.87a.18051","mag":"3000458198","pmid":"https://pubmed.ncbi.nlm.nih.gov/31990651"},"language":"en","primary_location":{"id":"doi:10.3949/ccjm.87a.18051","doi":"https://doi.org/10.3949/ccjm.87a.18051","is_oa":true,"landing_page_url":"https://doi.org/10.3949/ccjm.87a.18051","pdf_url":null,"source":{"id":"https://openalex.org/S20761018","display_name":"Cleveland Clinic Journal of Medicine","issn_l":"0891-1150","issn":["0891-1150","1939-2869"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-1","medline","norway-1","poland-40","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315641","host_organization_name":"Cleveland Clinic","host_organization_lineage":["https://openalex.org/P4310315641"],"host_organization_lineage_names":["Cleveland Clinic"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Cleveland Clinic Journal of Medicine","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://doi.org/10.3949/ccjm.87a.18051","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5000970882","display_name":"Grace Onimoe","orcid":"https://orcid.org/0000-0002-1673-4151","observed_orcids":["https://orcid.org/0000-0002-1673-4151"]},"institutions":[{"id":"https://openalex.org/I1299218025","display_name":"MetroHealth","ror":"https://ror.org/0377srw41","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1299218025"]},{"id":"https://openalex.org/I4210157264","display_name":"MetroHealth Medical Center","ror":"https://ror.org/05j4p5w63","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1299218025","https://openalex.org/I4210157264"]},{"id":"https://openalex.org/I58956616","display_name":"Case Western Reserve University","ror":"https://ror.org/051fd9666","country_code":"US","type":"education","lineage":["https://openalex.org/I58956616"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Grace Onimoe","raw_affiliation_strings":["Department of Pediatrics, The Metrohealth Hospital, and Assistant Professor, Case Western Reserve University, Cleveland, OH"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatrics, The Metrohealth Hospital, and Assistant Professor, Case Western Reserve University, Cleveland, OH","institution_ids":["https://openalex.org/I1299218025","https://openalex.org/I4210157264","https://openalex.org/I58956616"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5012627913","display_name":"Seth Joshua Rotz","orcid":"https://orcid.org/0000-0003-2896-1113","observed_orcids":["https://orcid.org/0000-0003-2896-1113"]},"institutions":[{"id":"https://openalex.org/I1316902750","display_name":"Cleveland Clinic","ror":"https://ror.org/03xjacd83","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1316902750"]},{"id":"https://openalex.org/I36373038","display_name":"Cleveland Clinic Lerner College of Medicine","ror":"https://ror.org/02x4b0932","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1316902750","https://openalex.org/I36373038"]},{"id":"https://openalex.org/I58956616","display_name":"Case Western Reserve University","ror":"https://ror.org/051fd9666","country_code":"US","type":"education","lineage":["https://openalex.org/I58956616"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Seth Rotz","raw_affiliation_strings":["Department of Pediatric Hematology and Oncology and Blood and Marrow Transplant Program, Cleveland Clinic; Assistant Professor, Cleveland Clinic Lerner College of Medicine of Case Western Reserve University, Cleveland, OH rotzs@ccf.org","Assistant Professor, Cleveland Clinic Lerner College of Medicine of Case Western Reserve University, Cleveland, OH","Department of Pediatric Hematology and Oncology and Blood and Marrow Transplant Program, Cleveland Clinic"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Hematology and Oncology and Blood and Marrow Transplant Program, Cleveland Clinic; Assistant Professor, Cleveland Clinic Lerner College of Medicine of Case Western Reserve University, Cleveland, OH rotzs@ccf.org","institution_ids":["https://openalex.org/I1316902750","https://openalex.org/I36373038","https://openalex.org/I58956616"]},{"raw_affiliation_string":"Assistant Professor, Cleveland Clinic Lerner College of Medicine of Case Western Reserve University, Cleveland, OH","institution_ids":["https://openalex.org/I36373038","https://openalex.org/I58956616"]},{"raw_affiliation_string":"Department of Pediatric Hematology and Oncology and Blood and Marrow Transplant Program, Cleveland Clinic","institution_ids":["https://openalex.org/I1316902750"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":5,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":4.63,"has_fulltext":false,"cited_by_count":59,"citation_normalized_percentile":{"value":0.95322141,"is_in_top_1_percent":false,"is_in_top_10_percent":true},"cited_by_percentile_year":{"min":98,"max":100},"biblio":{"volume":"87","issue":"1","first_page":"19","last_page":"27"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10554","display_name":"Hemoglobinopathies and Related Disorders","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10554","display_name":"Hemoglobinopathies and Related Disorders","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11280","display_name":"Hemophilia Treatment and Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12094","display_name":"Hemoglobin structure and function","score":0.0,"subfield":{"id":"https://openalex.org/subfields/1303","display_name":"Biochemistry"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/sickle-cell-disease","display_name":"sickle cell disease","score":1.0},{"id":"https://openalex.org/keywords/hemoglobinopathies","display_name":"hemoglobinopathies","score":0.7519999742507935},{"id":"https://openalex.org/keywords/primary-care","display_name":"primary care","score":0.8199999928474426},{"id":"https://openalex.org/keywords/patient-centered-medical-home","display_name":"patient-centered medical home","score":0.7200000286102295},{"id":"https://openalex.org/keywords/health-maintenance","display_name":"health maintenance","score":0.8259999752044678},{"id":"https://openalex.org/keywords/chronic-anemia","display_name":"chronic anemia","score":0.8830000162124634},{"id":"https://openalex.org/keywords/vaso-occlusive-crisis","display_name":"vaso-occlusive crisis","score":0.9200000166893005},{"id":"https://openalex.org/keywords/multiple-organ-injury","display_name":"multiple organ injury","score":0.8429999947547913},{"id":"https://openalex.org/keywords/disease-complications","display_name":"disease complications","score":0.7590000033378601},{"id":"https://openalex.org/keywords/clinical-guidelines","display_name":"clinical guidelines","score":0.5479999780654907}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.952688455581665},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.7664872407913208},{"id":"https://openalex.org/C177713679","wikidata":"https://www.wikidata.org/wiki/Q679690","display_name":"Intensive care medicine","level":1,"score":0.6474262475967407},{"id":"https://openalex.org/C2779668550","wikidata":"https://www.wikidata.org/wiki/Q1642147","display_name":"Hemoglobinopathy","level":3,"score":0.6439824104309082},{"id":"https://openalex.org/C2984752397","wikidata":"https://www.wikidata.org/wiki/Q3259956","display_name":"Primary care","level":2,"score":0.6029539108276367},{"id":"https://openalex.org/C2778248108","wikidata":"https://www.wikidata.org/wiki/Q5445","display_name":"Anemia","level":2,"score":0.5623828172683716},{"id":"https://openalex.org/C2778620579","wikidata":"https://www.wikidata.org/wiki/Q185034","display_name":"Sickle cell anemia","level":3,"score":0.4901605546474457},{"id":"https://openalex.org/C2779473830","wikidata":"https://www.wikidata.org/wiki/Q1540899","display_name":"MEDLINE","level":2,"score":0.43405526876449585},{"id":"https://openalex.org/C160735492","wikidata":"https://www.wikidata.org/wiki/Q31207","display_name":"Health care","level":2,"score":0.42468947172164917},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.4036986231803894},{"id":"https://openalex.org/C512399662","wikidata":"https://www.wikidata.org/wiki/Q3505712","display_name":"Family medicine","level":1,"score":0.2565499544143677},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.16160959005355835},{"id":"https://openalex.org/C50522688","wikidata":"https://www.wikidata.org/wiki/Q189833","display_name":"Economic growth","level":1,"score":0.0},{"id":"https://openalex.org/C162324750","wikidata":"https://www.wikidata.org/wiki/Q8134","display_name":"Economics","level":0,"score":0.0},{"id":"https://openalex.org/C17744445","wikidata":"https://www.wikidata.org/wiki/Q36442","display_name":"Political science","level":0,"score":0.0},{"id":"https://openalex.org/C199539241","wikidata":"https://www.wikidata.org/wiki/Q7748","display_name":"Law","level":1,"score":0.0}],"mesh":[{"descriptor_ui":"D000293","descriptor_name":"Adolescent","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000755","descriptor_name":"Anemia, Sickle Cell","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D000755","descriptor_name":"Anemia, Sickle Cell","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":false},{"descriptor_ui":"D000755","descriptor_name":"Anemia, Sickle Cell","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":true},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D011320","descriptor_name":"Primary Health Care","qualifier_ui":"Q000379","qualifier_name":"methods","is_major_topic":true},{"descriptor_ui":"D014481","descriptor_name":"United States","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":false},{"descriptor_ui":"D018802","descriptor_name":"Patient-Centered Care","qualifier_ui":"Q000379","qualifier_name":"methods","is_major_topic":true},{"descriptor_ui":"D055815","descriptor_name":"Young Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.3949/ccjm.87a.18051","doi":"https://doi.org/10.3949/ccjm.87a.18051","is_oa":true,"landing_page_url":"https://doi.org/10.3949/ccjm.87a.18051","pdf_url":null,"source":{"id":"https://openalex.org/S20761018","display_name":"Cleveland Clinic Journal of Medicine","issn_l":"0891-1150","issn":["0891-1150","1939-2869"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-1","medline","norway-1","poland-40","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315641","host_organization_name":"Cleveland Clinic","host_organization_lineage":["https://openalex.org/P4310315641"],"host_organization_lineage_names":["Cleveland Clinic"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Cleveland Clinic Journal of Medicine","raw_type":"journal-article"},{"id":"pmid:31990651","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/31990651","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Cleveland Clinic journal of medicine","raw_type":"Journal Article"}],"best_oa_location":{"id":"doi:10.3949/ccjm.87a.18051","doi":"https://doi.org/10.3949/ccjm.87a.18051","is_oa":true,"landing_page_url":"https://doi.org/10.3949/ccjm.87a.18051","pdf_url":null,"source":{"id":"https://openalex.org/S20761018","display_name":"Cleveland Clinic Journal of Medicine","issn_l":"0891-1150","issn":["0891-1150","1939-2869"],"is_oa":true,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-1","medline","norway-1","poland-40","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315641","host_organization_name":"Cleveland Clinic","host_organization_lineage":["https://openalex.org/P4310315641"],"host_organization_lineage_names":["Cleveland Clinic"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Cleveland Clinic Journal of Medicine","raw_type":"journal-article"},"sustainable_development_goals":[{"score":0.9940000176429749,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":43,"referenced_works":["https://openalex.org/W1528211603","https://openalex.org/W1590229730","https://openalex.org/W1981445782","https://openalex.org/W2001175629","https://openalex.org/W2008192490","https://openalex.org/W2020493440","https://openalex.org/W2029806252","https://openalex.org/W2032740782","https://openalex.org/W2042416746","https://openalex.org/W2045552353","https://openalex.org/W2054511463","https://openalex.org/W2058291116","https://openalex.org/W2068600140","https://openalex.org/W2071771677","https://openalex.org/W2077174747","https://openalex.org/W2083687462","https://openalex.org/W2104724413","https://openalex.org/W2107820422","https://openalex.org/W2119580559","https://openalex.org/W2132032699","https://openalex.org/W2134543755","https://openalex.org/W2143487777","https://openalex.org/W2150519485","https://openalex.org/W2189707660","https://openalex.org/W2326476344","https://openalex.org/W2339933044","https://openalex.org/W2407981502","https://openalex.org/W2490064445","https://openalex.org/W2511966007","https://openalex.org/W2552002719","https://openalex.org/W2555810804","https://openalex.org/W2559643145","https://openalex.org/W2562103559","https://openalex.org/W2593923181","https://openalex.org/W2732579641","https://openalex.org/W2751678853","https://openalex.org/W2776982164","https://openalex.org/W2782382390","https://openalex.org/W2789879801","https://openalex.org/W2794039702","https://openalex.org/W2883955692","https://openalex.org/W2889666963","https://openalex.org/W4285719527"],"related_works":["https://openalex.org/W3087349852","https://openalex.org/W2043535763","https://openalex.org/W2005941663","https://openalex.org/W2795162300","https://openalex.org/W7165685106","https://openalex.org/W2138777194","https://openalex.org/W2965562857","https://openalex.org/W2474629055","https://openalex.org/W2520767525","https://openalex.org/W4285077240"],"abstract_inverted_index":{"Sickle":[0],"cell":[1],"disease":[2,60],"(SCD)":[3],"is":[4],"the":[5,10,35],"most":[6],"common":[7],"hemoglobinopathy":[8],"in":[9,34],"United":[11],"States":[12],"and":[13,23,54,62],"causes":[14],"significant":[15],"disease-related":[16],"morbidity":[17],"including":[18],"multiorgan":[19],"damage,":[20],"chronic":[21],"anemia,":[22],"debilitating":[24],"pain":[25],"crises.":[26],"Primary":[27],"care":[28,40],"physicians":[29],"play":[30],"a":[31,56],"key":[32],"role":[33],"medical":[36],"home":[37],"model":[38],"of":[39,59],"for":[41,51],"adults":[42],"with":[43],"SCD.":[44],"This":[45],"review":[46],"focuses":[47],"on":[48],"current":[49,63],"recommendations":[50],"health":[52],"maintenance":[53],"provides":[55],"brief":[57],"summary":[58],"complications":[61],"updates.":[64]},"counts_by_year":[{"year":2026,"cited_by_count":5},{"year":2025,"cited_by_count":10},{"year":2024,"cited_by_count":21},{"year":2023,"cited_by_count":15},{"year":2022,"cited_by_count":8}],"updated_date":"2026-11-07T11:25:07.637180","created_date":"2020-01-23T00:00:00"}
