{"id":"https://openalex.org/W2963801922","doi":"https://doi.org/10.1016/j.resmer.2019.07.003","title":"Subglottic tracheal stenosis associated with Ehlers-Danlos Syndrome, Hypermobilty Type","display_name":"Subglottic tracheal stenosis associated with Ehlers-Danlos Syndrome, Hypermobilty Type","publication_year":2019,"publication_date":"2019-07-18","ids":{"openalex":"https://openalex.org/W2963801922","doi":"https://doi.org/10.1016/j.resmer.2019.07.003","mag":"2963801922","pmid":"https://pubmed.ncbi.nlm.nih.gov/31476586"},"language":"en","primary_location":{"id":"doi:10.1016/j.resmer.2019.07.003","doi":"https://doi.org/10.1016/j.resmer.2019.07.003","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.resmer.2019.07.003","pdf_url":"https://www.sciencedirect.com/science/article/am/pii/S2590041219300194?via%3Dihub","source":{"id":"https://openalex.org/S4210196504","display_name":"Respiratory Medicine and Research","issn_l":"2590-0412","issn":["2590-0412"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-c","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-20","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"other-oa","license_id":"https://openalex.org/licenses/other-oa","version":"acceptedVersion","is_accepted":true,"is_published":false,"raw_source_name":"Respiratory Medicine and Research","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"hybrid","oa_url":"https://www.sciencedirect.com/science/article/am/pii/S2590041219300194?via%3Dihub","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5072573847","display_name":"Patrice Guiraudet","orcid":"https://orcid.org/0000-0001-7506-9713","observed_orcids":["https://orcid.org/0000-0001-7506-9713"]},"institutions":[{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]},{"id":"https://openalex.org/I4210091279","display_name":"Universit\u00e9 Sorbonne Paris Nord","ror":"https://ror.org/0199hds37","country_code":"FR","type":"education","lineage":["https://openalex.org/I4210091279"]},{"id":"https://openalex.org/I4210091437","display_name":"Sorbonne Paris Cit\u00e9","ror":"https://ror.org/001z21q04","country_code":"FR","type":"other","lineage":["https://openalex.org/I204730241","https://openalex.org/I4210091437"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4210129146","display_name":"H\u00f4pital Avicenne","ror":"https://ror.org/03n6vs369","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159","https://openalex.org/I4210129146"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"P. Guiraudet","raw_affiliation_strings":["Assistance publique - h\u00f4pitaux de Paris (AP-HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France; Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France","Assistance publique - h\u00f4pitaux de Paris (AP\u2013HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France","Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Assistance publique - h\u00f4pitaux de Paris (AP-HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France; Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210091279","https://openalex.org/I4210091437","https://openalex.org/I4210097159","https://openalex.org/I4210129146"]},{"raw_affiliation_string":"Assistance publique - h\u00f4pitaux de Paris (AP\u2013HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France","institution_ids":["https://openalex.org/I4210091279","https://openalex.org/I4210091437","https://openalex.org/I4210097159","https://openalex.org/I4210129146"]},{"raw_affiliation_string":"Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210091279"]}]},{"author_position":"middle","author":{"id":null,"display_name":"S. Morel","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"S. Morel","raw_affiliation_strings":["Centre de pneumologie (SM), La Varenne Saint-Hilaire, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Centre de pneumologie (SM), La Varenne Saint-Hilaire, France","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5030373135","display_name":"Fatma Dhouib","orcid":"https://orcid.org/0000-0001-6819-6466","observed_orcids":["https://orcid.org/0000-0001-6819-6466"]},"institutions":[{"id":"https://openalex.org/I4210091279","display_name":"Universit\u00e9 Sorbonne Paris Nord","ror":"https://ror.org/0199hds37","country_code":"FR","type":"education","lineage":["https://openalex.org/I4210091279"]},{"id":"https://openalex.org/I4210091437","display_name":"Sorbonne Paris Cit\u00e9","ror":"https://ror.org/001z21q04","country_code":"FR","type":"other","lineage":["https://openalex.org/I204730241","https://openalex.org/I4210091437"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4210129146","display_name":"H\u00f4pital Avicenne","ror":"https://ror.org/03n6vs369","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159","https://openalex.org/I4210129146"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"F. Dhouib","raw_affiliation_strings":["Assistance publique - h\u00f4pitaux de Paris (AP-HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Assistance publique - h\u00f4pitaux de Paris (AP-HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France","institution_ids":["https://openalex.org/I4210091279","https://openalex.org/I4210091437","https://openalex.org/I4210097159","https://openalex.org/I4210129146"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5027068255","display_name":"Y. Uzunhan","orcid":"https://orcid.org/0000-0002-1607-1407","observed_orcids":["https://orcid.org/0000-0002-1607-1407"]},"institutions":[{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]},{"id":"https://openalex.org/I4210091279","display_name":"Universit\u00e9 Sorbonne Paris Nord","ror":"https://ror.org/0199hds37","country_code":"FR","type":"education","lineage":["https://openalex.org/I4210091279"]},{"id":"https://openalex.org/I4210091437","display_name":"Sorbonne Paris Cit\u00e9","ror":"https://ror.org/001z21q04","country_code":"FR","type":"other","lineage":["https://openalex.org/I204730241","https://openalex.org/I4210091437"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4210129146","display_name":"H\u00f4pital Avicenne","ror":"https://ror.org/03n6vs369","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159","https://openalex.org/I4210129146"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Y. Uzunhan","raw_affiliation_strings":["Assistance publique - h\u00f4pitaux de Paris (AP-HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France; Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France","Assistance publique - h\u00f4pitaux de Paris (AP\u2013HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France","Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Assistance publique - h\u00f4pitaux de Paris (AP-HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France; Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210091279","https://openalex.org/I4210091437","https://openalex.org/I4210097159","https://openalex.org/I4210129146"]},{"raw_affiliation_string":"Assistance publique - h\u00f4pitaux de Paris (AP\u2013HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France","institution_ids":["https://openalex.org/I4210091279","https://openalex.org/I4210091437","https://openalex.org/I4210097159","https://openalex.org/I4210129146"]},{"raw_affiliation_string":"Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210091279"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5114033627","display_name":"Robin Dh\u00f4te","orcid":"https://orcid.org/0000-0001-9969-9947","observed_orcids":["https://orcid.org/0000-0001-9969-9947"]},"institutions":[{"id":"https://openalex.org/I4210091279","display_name":"Universit\u00e9 Sorbonne Paris Nord","ror":"https://ror.org/0199hds37","country_code":"FR","type":"education","lineage":["https://openalex.org/I4210091279"]},{"id":"https://openalex.org/I4210091437","display_name":"Sorbonne Paris Cit\u00e9","ror":"https://ror.org/001z21q04","country_code":"FR","type":"other","lineage":["https://openalex.org/I204730241","https://openalex.org/I4210091437"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4210129146","display_name":"H\u00f4pital Avicenne","ror":"https://ror.org/03n6vs369","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159","https://openalex.org/I4210129146"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"R. Dhote","raw_affiliation_strings":["Assistance publique - h\u00f4pitaux de Paris (AP-HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Assistance publique - h\u00f4pitaux de Paris (AP-HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France","institution_ids":["https://openalex.org/I4210091279","https://openalex.org/I4210091437","https://openalex.org/I4210097159","https://openalex.org/I4210129146"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5058540104","display_name":"Emmanuel Martinod","orcid":"https://orcid.org/0000-0001-8465-4498","observed_orcids":["https://orcid.org/0000-0001-8465-4498"]},"institutions":[{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]},{"id":"https://openalex.org/I4210091279","display_name":"Universit\u00e9 Sorbonne Paris Nord","ror":"https://ror.org/0199hds37","country_code":"FR","type":"education","lineage":["https://openalex.org/I4210091279"]},{"id":"https://openalex.org/I4210091437","display_name":"Sorbonne Paris Cit\u00e9","ror":"https://ror.org/001z21q04","country_code":"FR","type":"other","lineage":["https://openalex.org/I204730241","https://openalex.org/I4210091437"]},{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4210129146","display_name":"H\u00f4pital Avicenne","ror":"https://ror.org/03n6vs369","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159","https://openalex.org/I4210129146"]}],"countries":["FR"],"is_corresponding":true,"raw_author_name":"E. Martinod","raw_affiliation_strings":["Assistance publique - h\u00f4pitaux de Paris (AP-HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France; Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France. Electronic address: emmanuel.martinod@aphp.fr","Assistance publique - h\u00f4pitaux de Paris (AP\u2013HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France","Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Assistance publique - h\u00f4pitaux de Paris (AP-HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France; Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France. Electronic address: emmanuel.martinod@aphp.fr","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210091279","https://openalex.org/I4210091437","https://openalex.org/I4210097159","https://openalex.org/I4210129146"]},{"raw_affiliation_string":"Assistance publique - h\u00f4pitaux de Paris (AP\u2013HP), h\u00f4pitaux universitaires Paris Seine-Saint-Denis, h\u00f4pital Avicenne, chirurgie thoracique et vasculaire (PG, EM), Anesth\u00e9sie-r\u00e9animation (FD), pneumologie (YU), m\u00e9decine interne (RD), universit\u00e9 Paris 13, Sorbonne Paris Cit\u00e9, facult\u00e9 de m\u00e9decine SMBH, Bobigny, France","institution_ids":["https://openalex.org/I4210091279","https://openalex.org/I4210091437","https://openalex.org/I4210097159","https://openalex.org/I4210129146"]},{"raw_affiliation_string":"Hypoxia and the Lung laboratory (Inserm U1272), universit\u00e9 Paris 13, Paris, France","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210091279"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":5,"corresponding_author_ids":["https://openalex.org/A5058540104"],"corresponding_institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210091279","https://openalex.org/I4210091437","https://openalex.org/I4210097159","https://openalex.org/I4210129146"],"apc_list":{"value":1670,"currency":"USD","value_usd":1670},"apc_paid":{"value":1670,"currency":"USD","value_usd":1670},"fwci":0.1759,"has_fulltext":true,"cited_by_count":3,"citation_normalized_percentile":{"value":0.51758228,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":87,"max":95},"biblio":{"volume":"76","issue":null,"first_page":"19","last_page":"21"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11260","display_name":"Tracheal and airway disorders","score":0.7056000232696533,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11260","display_name":"Tracheal and airway disorders","score":0.7056000232696533,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11310","display_name":"Connective tissue disorders research","score":0.27709999680519104,"subfield":{"id":"https://openalex.org/subfields/1311","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T12818","display_name":"Pneumothorax, Barotrauma, Emphysema","score":0.00139999995008111,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/ehlers-danlos-syndrome","display_name":"Ehlers-Danlos syndrome","score":0.9279999732971191},{"id":"https://openalex.org/keywords/hypermobility-type","display_name":"hypermobility type","score":0.8360000252723694},{"id":"https://openalex.org/keywords/subglottic-tracheal-stenosis","display_name":"subglottic tracheal stenosis","score":0.9649999737739563},{"id":"https://openalex.org/keywords/airway-collapse","display_name":"airway collapse","score":0.5889999866485596},{"id":"https://openalex.org/keywords/obstructive-sleep-apnea","display_name":"obstructive sleep apnea","score":0.7870000004768372},{"id":"https://openalex.org/keywords/respiratory-manifestations","display_name":"respiratory manifestations","score":0.5080000162124634},{"id":"https://openalex.org/keywords/connective-tissue-diseases","display_name":"connective tissue diseases","score":0.8240000009536743},{"id":"https://openalex.org/keywords/dyspnea","display_name":"dyspnea","score":0.6660000085830688},{"id":"https://openalex.org/keywords/pneumothorax","display_name":"pneumothorax","score":0.7670000195503235},{"id":"https://openalex.org/keywords/hemoptysis","display_name":"hemoptysis","score":0.7200000286102295},{"id":"https://openalex.org/keywords/chest-wall-deformity","display_name":"chest wall deformity","score":0.5569999814033508},{"id":"https://openalex.org/keywords/respiratory-muscle-weakness","display_name":"respiratory muscle weakness","score":0.7760000228881836},{"id":"https://openalex.org/keywords/asthma","display_name":"asthma","score":0.628000020980835},{"id":"https://openalex.org/keywords/chest-x-ray-findings","display_name":"chest X-ray findings","score":0.375},{"id":"https://openalex.org/keywords/emphysema","display_name":"emphysema","score":0.8389999866485596},{"id":"https://openalex.org/keywords/calcified-nodules","display_name":"calcified nodules","score":0.5989999771118164}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9095585942268372},{"id":"https://openalex.org/C29456083","wikidata":"https://www.wikidata.org/wiki/Q1221899","display_name":"Gynecology","level":1,"score":0.49560463428497314}],"mesh":[{"descriptor_ui":"D001999","descriptor_name":"Bronchoscopy","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D004535","descriptor_name":"Ehlers-Danlos Syndrome","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D014135","descriptor_name":"Tracheal Stenosis","qualifier_ui":"Q000000981","qualifier_name":"diagnostic imaging","is_major_topic":false},{"descriptor_ui":"D014135","descriptor_name":"Tracheal Stenosis","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":true}],"locations_count":3,"locations":[{"id":"doi:10.1016/j.resmer.2019.07.003","doi":"https://doi.org/10.1016/j.resmer.2019.07.003","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.resmer.2019.07.003","pdf_url":"https://www.sciencedirect.com/science/article/am/pii/S2590041219300194?via%3Dihub","source":{"id":"https://openalex.org/S4210196504","display_name":"Respiratory Medicine and Research","issn_l":"2590-0412","issn":["2590-0412"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-c","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-20","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"other-oa","license_id":"https://openalex.org/licenses/other-oa","version":"acceptedVersion","is_accepted":true,"is_published":false,"raw_source_name":"Respiratory Medicine and Research","raw_type":"journal-article"},{"id":"pmid:31476586","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/31476586","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Respiratory medicine and research","raw_type":"Case Reports"},{"id":"pmh:oai:HAL:hal-03488120v1","doi":null,"is_oa":true,"landing_page_url":"https://hal.science/hal-03488120","pdf_url":null,"source":{"id":"https://openalex.org/S4306402512","display_name":"HAL","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I4405252976","host_organization_name":"Centre pour la Communication Scientifique Directe","host_organization_lineage":["https://openalex.org/I4405252976"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-nc","license_id":"https://openalex.org/licenses/cc-by-nc","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Respiratory Medicine and Research, 2019, 76, pp.19 - 21. &#x27E8;10.1016/j.resmer.2019.07.003&#x27E9;","raw_type":"info:eu-repo/semantics/article"}],"best_oa_location":{"id":"doi:10.1016/j.resmer.2019.07.003","doi":"https://doi.org/10.1016/j.resmer.2019.07.003","is_oa":true,"landing_page_url":"https://doi.org/10.1016/j.resmer.2019.07.003","pdf_url":"https://www.sciencedirect.com/science/article/am/pii/S2590041219300194?via%3Dihub","source":{"id":"https://openalex.org/S4210196504","display_name":"Respiratory Medicine and Research","issn_l":"2590-0412","issn":["2590-0412"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-c","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-20","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"other-oa","license_id":"https://openalex.org/licenses/other-oa","version":"acceptedVersion","is_accepted":true,"is_published":false,"raw_source_name":"Respiratory Medicine and Research","raw_type":"journal-article"},"sustainable_development_goals":[{"display_name":"Good health and well-being","score":0.9994999766349792,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W2963801922.pdf","grobid_xml":"https://content.openalex.org/works/W2963801922.grobid-xml"},"referenced_works_count":9,"referenced_works":["https://openalex.org/W1976289297","https://openalex.org/W2037214002","https://openalex.org/W2079483440","https://openalex.org/W2141184049","https://openalex.org/W2153707891","https://openalex.org/W2536752374","https://openalex.org/W2593591555","https://openalex.org/W2779731567","https://openalex.org/W2804359827"],"related_works":["https://openalex.org/W4386286732","https://openalex.org/W2767264256","https://openalex.org/W1660398196","https://openalex.org/W16803282","https://openalex.org/W7071611695","https://openalex.org/W4367601075","https://openalex.org/W2905016574","https://openalex.org/W2438775154","https://openalex.org/W2060876938","https://openalex.org/W2067025613"],"abstract_inverted_index":{"Les":[0,27],"syndromes":[1,199],"d'Ehlers-Danlos":[2],"(SED)":[3],"sont":[4,33,61,110],"un":[5,56,68,148],"groupe":[6],"h\u00e9t\u00e9rog\u00e8ne":[7],"de":[8,42,78,124,126,133,159,197],"maladies":[9],"h\u00e9r\u00e9ditaires":[10],"rares":[11],"du":[12,40,91,95],"tissu":[13],"conjonctif":[14],"caract\u00e9ris\u00e9es":[15],"par":[16,112,178],"la":[17,53,79,179,184,192],"triade":[18],"clinique":[19],"hyperlaxit\u00e9":[20],"articulaire,":[21],"hyper\u00e9lasticit\u00e9":[22],"cutan\u00e9e":[23],"et":[24,35,51,63,87,116,190],"fragilit\u00e9":[25],"tissulaire.":[26],"manifestations":[28,225,394],"respiratoires":[29],"associ\u00e9es":[30,66],"aux":[31],"SED":[32,46,104,177],"fr\u00e9quentes":[34],"vari\u00e9es.":[36],"Elles":[37,119],"d\u00e9pendent":[38],"principalement":[39],"type":[41,239],"SED.":[43],"Dans":[44,102],"les":[45,100,107,117],"non":[47],"vasculaires":[48],"(SEDnv),":[49],"hypermobile":[50,243],"classique,":[52],"dyspn\u00e9e":[54],"est":[55,97,130],"sympt\u00f4me":[57],"fr\u00e9quent.":[58],"Ses":[59],"\u00e9tiologies":[60],"larges":[62],"peuvent":[64],"\u00eatre":[65,165],"chez":[67,147],"m\u00eame":[69],"patient":[70,340,403],":":[71],"asthme,":[72],"faiblesse":[73],"des":[74,83,135,173,176,188,195],"muscles":[75],"respiratoires,":[76],"d\u00e9formation":[77],"cage":[80],"thoracique,":[81],"collapsus":[82],"voies":[84],"a\u00e9riennes":[85],"sup\u00e9rieures":[86],"inf\u00e9rieures.":[88],"La":[89,151],"pr\u00e9valence":[90],"syndrome":[92,286],"d'apn\u00e9es":[93],"obstructives":[94],"sommeil":[96],"\u00e9lev\u00e9e":[98],"dans":[99],"SEDnv.":[101],"le":[103,113,122],"vasculaire":[105],"(SEDv),":[106],"complications":[108,311],"pulmonaires":[109,175],"domin\u00e9es":[111],"pneumothorax,":[114,313],"l'h\u00e9mothorax":[115],"h\u00e9moptysies.":[118],"pr\u00e9c\u00e8dent":[120],"souvent":[121],"diagnostic":[123],"SEDv":[125,140],"plusieurs":[127],"ann\u00e9es.":[128],"Il":[129],"donc":[131],"imp\u00e9ratif":[132],"rechercher":[134],"arguments":[136],"en":[137,186],"faveur":[138],"d'un":[139],"devant":[141],"tout":[142],"pneumothorax":[143,343],"ou":[144],"h\u00e9mothorax":[145],"spontan\u00e9":[146],"jeune":[149],"patient.":[150],"pr\u00e9sence":[152],"d'anomalies":[153],"scanographiques":[154],"parenchymateuses":[155],"\u00e9vocatrices":[156],"(emphys\u00e8me,":[157],"clusters":[158,355],"nodules":[160],"calcifi\u00e9s,":[161],"nodule":[162],"excav\u00e9)":[163],"peut":[164],"une":[166],"aide":[167],"au":[168],"diagnostic.":[169],"Une":[170],"meilleure":[171],"connaissance":[172],"atteintes":[174],"communaut\u00e9":[180],"pneumologique":[181],"permettrait":[182],"d'am\u00e9liorer":[183],"prise":[185],"charge":[187],"malades":[189],"d'ouvrir":[191],"voie":[193],"\u00e0":[194],"travaux":[196],"recherche.Ehlers-Danlos":[198],"(EDS)":[200],"represent":[201],"a":[202,254,338],"heterogeneous":[203],"group":[204],"of":[205,240,282,292,323,335,348,356,387,392,395],"heritable":[206],"connective":[207],"tissue":[208,222],"disorders":[209],"characterized":[210],"by":[211,325,381,397],"the":[212,238,247,265,293,308,321,333,371,388,398,407],"clinical":[213],"\"triad\"":[214],"consisting":[215],"in":[216,264,287,337],"joint":[217],"hypermobility,":[218],"skin":[219],"hyperextensibility":[220],"and":[221,231,244,261,276,315,405],"fragility.":[223],"Respiratory":[224],"associated":[226],"with":[227,341,379],"EDS":[228,306,396],"are":[229,259,312],"frequent":[230,249],"variable.":[232],"They":[233],"vary":[234],"mainly":[235],"according":[236],"to":[237,299,331,365],"EDS.":[241],"In":[242,304],"classical":[245],"EDS,":[246],"most":[248],"non-vascular":[250],"types,":[251],"dyspnea":[252,295],"is":[253,289,297,329,368],"common":[255],"symptom.":[256],"Its":[257],"etiologies":[258],"wide-ranging":[260],"can":[262,361],"coexist":[263],"same":[266],"patient:":[267],"asthma,":[268],"respiratory":[269,393],"muscle":[270],"weakness,":[271],"chest":[272],"wall":[273],"abnormalities,":[274],"upper":[275],"lower":[277],"airway":[278],"collapse.":[279],"The":[280,346],"prevalence":[281],"obstructive":[283],"sleep":[284],"apnea":[285],"nvEDS":[288],"high.":[290],"Identification":[291],"relevant":[294],"mechanism":[296],"essential":[298],"providing":[300],"appropriate":[301],"therapeutic":[302],"measures.":[303],"vascular":[305],"(vEDS),":[307],"main":[309],"pulmonary":[310],"hemothorax":[314],"hemoptysis.":[316],"As":[317],"they":[318],"frequently":[319],"precede":[320],"diagnosis":[322],"vEDS":[324,336],"several":[326],"years,":[327],"it":[328],"imperative":[330],"raise":[332],"possibility":[334],"young":[339],"spontaneous":[342],"or":[344],"hemothorax.":[345],"presence":[347],"suggestive":[349],"computed":[350],"tomography":[351],"parenchymal":[352],"abnormalities":[353],"(emphysema,":[354],"calcified":[357],"nodules,":[358],"cavitated":[359],"nodule)":[360],"be":[362,376],"an":[363,382],"aid":[364],"diagnosis.":[366,389],"Treatment":[367],"based":[369],"on":[370],"usual":[372],"approaches,":[373],"which":[374],"must":[375],"carried":[377],"out":[378],"caution":[380],"experienced":[383],"operator":[384],"fully":[385],"informed":[386],"Better":[390],"knowledge":[391],"pneumological":[399],"community":[400],"would":[401],"improve":[402],"care":[404],"pave":[406],"way":[408],"for":[409],"further":[410],"research.":[411]},"counts_by_year":[{"year":2025,"cited_by_count":2},{"year":2021,"cited_by_count":1}],"updated_date":"2026-11-08T12:12:28.789561","created_date":"2019-07-30T00:00:00"}
