{"id":"https://openalex.org/W2933204792","doi":"https://doi.org/10.1177/0961203319840430","title":"A case with good response to belimumab for lupus nephritis complicated by IgG4-related disease","display_name":"A case with good response to belimumab for lupus nephritis complicated by IgG4-related disease","publication_year":2019,"publication_date":"2019-03-27","ids":{"openalex":"https://openalex.org/W2933204792","doi":"https://doi.org/10.1177/0961203319840430","mag":"2933204792","pmid":"https://pubmed.ncbi.nlm.nih.gov/30917769"},"language":"en","primary_location":{"id":"doi:10.1177/0961203319840430","doi":"https://doi.org/10.1177/0961203319840430","is_oa":false,"landing_page_url":"https://doi.org/10.1177/0961203319840430","pdf_url":null,"source":{"id":"https://openalex.org/S115920904","display_name":"Lupus","issn_l":"0961-2033","issn":["0961-2033","1477-0962"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-d","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-100","russia-white-list-2"],"host_organization":"https://openalex.org/P4310320017","host_organization_name":"SAGE Publishing","host_organization_lineage":["https://openalex.org/P4310320017"],"host_organization_lineage_names":["SAGE Publishing"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Lupus","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5055846400","display_name":"Motohisa Yamamoto","orcid":"https://orcid.org/0000-0003-2742-2484","observed_orcids":["https://orcid.org/0000-0003-2742-2484"]},"institutions":[{"id":"https://openalex.org/I141882310","display_name":"Sapporo Medical University","ror":"https://ror.org/01h7cca57","country_code":"JP","type":"education","lineage":["https://openalex.org/I141882310"]}],"countries":["JP"],"is_corresponding":true,"raw_author_name":"M Yamamoto","raw_affiliation_strings":["Department of Rheumatology and Clinical Immunology, Sapporo Medical University School of Medicine, Sapporo, Japan"],"raw_orcid":"https://orcid.org/0000-0003-2742-2484","affiliations":[{"raw_affiliation_string":"Department of Rheumatology and Clinical Immunology, Sapporo Medical University School of Medicine, Sapporo, Japan","institution_ids":["https://openalex.org/I141882310"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5055911022","display_name":"Satsuki Aochi","orcid":"https://orcid.org/0000-0002-3032-9558","observed_orcids":["https://orcid.org/0000-0002-3032-9558"]},"institutions":[{"id":"https://openalex.org/I4405283292","display_name":"Self-Defense Forces Sapporo Hospital","ror":"https://ror.org/01cyyvw83","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4405273344","https://openalex.org/I4405283292"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"S Aochi","raw_affiliation_strings":["Department of Internal Medicine, Japan Self Defense Forces Sapporo Hospital, Sapporo, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Internal Medicine, Japan Self Defense Forces Sapporo Hospital, Sapporo, Japan","institution_ids":["https://openalex.org/I4405283292"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5077042715","display_name":"Chisako Suzuki","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I141882310","display_name":"Sapporo Medical University","ror":"https://ror.org/01h7cca57","country_code":"JP","type":"education","lineage":["https://openalex.org/I141882310"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"C Suzuki","raw_affiliation_strings":["Department of Rheumatology and Clinical Immunology, Sapporo Medical University School of Medicine, Sapporo, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Rheumatology and Clinical Immunology, Sapporo Medical University School of Medicine, Sapporo, Japan","institution_ids":["https://openalex.org/I141882310"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5085142320","display_name":"Seiji Nakamura","orcid":"https://orcid.org/0000-0002-6373-8817","observed_orcids":["https://orcid.org/0000-0002-6373-8817"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"S Nakamura","raw_affiliation_strings":["Department of Rheumatology, Hokkaido Orthopedic Memorial Hospital, Sapporo, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Rheumatology, Hokkaido Orthopedic Memorial Hospital, Sapporo, Japan","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5110441857","display_name":"R Murakami","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4405256101","display_name":"JR Sapporo Hospital","ror":"https://ror.org/03s0kpb69","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4405256101"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"R Murakami","raw_affiliation_strings":["Department of Rheumatology, JR Sapporo Hospital, Sapporo, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Rheumatology, JR Sapporo Hospital, Sapporo, Japan","institution_ids":["https://openalex.org/I4405256101"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5005567534","display_name":"Yusuke Ogawa","orcid":"https://orcid.org/0000-0001-9256-5102","observed_orcids":["https://orcid.org/0000-0001-9256-5102"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Y Ogawa","raw_affiliation_strings":["Hokkaido Renal Pathology Center, Sapporo, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Hokkaido Renal Pathology Center, Sapporo, Japan","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5102850765","display_name":"Hiroki Takahashi","orcid":"https://orcid.org/0000-0001-6791-936X","observed_orcids":["https://orcid.org/0000-0001-6791-936X"]},"institutions":[{"id":"https://openalex.org/I141882310","display_name":"Sapporo Medical University","ror":"https://ror.org/01h7cca57","country_code":"JP","type":"education","lineage":["https://openalex.org/I141882310"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"H Takahashi","raw_affiliation_strings":["Department of Rheumatology and Clinical Immunology, Sapporo Medical University School of Medicine, Sapporo, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Rheumatology and Clinical Immunology, Sapporo Medical University School of Medicine, Sapporo, Japan","institution_ids":["https://openalex.org/I141882310"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":3,"corresponding_author_ids":["https://openalex.org/A5055846400"],"corresponding_institution_ids":["https://openalex.org/I141882310"],"apc_list":{"value":4150,"currency":"USD","value_usd":4150},"apc_paid":null,"fwci":1.6932,"has_fulltext":false,"cited_by_count":31,"citation_normalized_percentile":{"value":0.82776254,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":93,"max":99},"biblio":{"volume":"28","issue":"6","first_page":"786","last_page":"789"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10308","display_name":"Systemic Lupus Erythematosus Research","score":0.8407999873161316,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10308","display_name":"Systemic Lupus Erythematosus Research","score":0.8407999873161316,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11576","display_name":"IgG4-Related and Inflammatory Diseases","score":0.08749999850988388,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11029","display_name":"Renal Diseases and Glomerulopathies","score":0.03739999979734421,"subfield":{"id":"https://openalex.org/subfields/2727","display_name":"Nephrology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/belimumab","display_name":"belimumab","score":0.972000002861023},{"id":"https://openalex.org/keywords/igg4-related-disease","display_name":"IgG4-related disease","score":0.9139999747276306},{"id":"https://openalex.org/keywords/lupus-nephritis","display_name":"lupus nephritis","score":0.9700000286102295},{"id":"https://openalex.org/keywords/systemic-lupus-erythematosus","display_name":"systemic lupus erythematosus","score":0.9990000128746033},{"id":"https://openalex.org/keywords/proteinuria","display_name":"proteinuria","score":0.5220000147819519},{"id":"https://openalex.org/keywords/corticosteroid-tapering","display_name":"corticosteroid tapering","score":0.8119999766349792},{"id":"https://openalex.org/keywords/mycophenolate-mofetil","display_name":"mycophenolate mofetil","score":0.9020000100135803},{"id":"https://openalex.org/keywords/hypergammaglobulinemia","display_name":"hypergammaglobulinemia","score":0.8629999756813049},{"id":"https://openalex.org/keywords/kidney-biopsy","display_name":"renal biopsy","score":0.5049999952316284},{"id":"https://openalex.org/keywords/anti-cd20-therapy","display_name":"anti-CD20 therapy","score":0.5590000152587891}],"concepts":[{"id":"https://openalex.org/C2781205201","wikidata":"https://www.wikidata.org/wiki/Q1996249","display_name":"Belimumab","level":5,"score":0.9557455778121948},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9458914399147034},{"id":"https://openalex.org/C2779912601","wikidata":"https://www.wikidata.org/wiki/Q1621830","display_name":"Lupus nephritis","level":3,"score":0.7629204988479614},{"id":"https://openalex.org/C2779561371","wikidata":"https://www.wikidata.org/wiki/Q570197","display_name":"Proteinuria","level":3,"score":0.6832351684570312},{"id":"https://openalex.org/C2781087799","wikidata":"https://www.wikidata.org/wiki/Q7312483","display_name":"Renal biopsy","level":3,"score":0.5432980060577393},{"id":"https://openalex.org/C2780514984","wikidata":"https://www.wikidata.org/wiki/Q17146775","display_name":"Hypergammaglobulinemia","level":3,"score":0.5116329789161682},{"id":"https://openalex.org/C2776715498","wikidata":"https://www.wikidata.org/wiki/Q11426176","display_name":"Prednisolone","level":2,"score":0.4882946014404297},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.4838796854019165},{"id":"https://openalex.org/C2776912625","wikidata":"https://www.wikidata.org/wiki/Q1485","display_name":"Systemic lupus erythematosus","level":3,"score":0.4707879424095154},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.4671138525009155},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.44675445556640625},{"id":"https://openalex.org/C2777178219","wikidata":"https://www.wikidata.org/wiki/Q425154","display_name":"Tocilizumab","level":3,"score":0.4457481801509857},{"id":"https://openalex.org/C2780841215","wikidata":"https://www.wikidata.org/wiki/Q422549","display_name":"Glucocorticoid","level":2,"score":0.4432932734489441},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.44081079959869385},{"id":"https://openalex.org/C45189115","wikidata":"https://www.wikidata.org/wiki/Q502159","display_name":"Serology","level":3,"score":0.4394933879375458},{"id":"https://openalex.org/C159654299","wikidata":"https://www.wikidata.org/wiki/Q79460","display_name":"Antibody","level":2,"score":0.35380882024765015},{"id":"https://openalex.org/C2775934546","wikidata":"https://www.wikidata.org/wiki/Q179991","display_name":"Biopsy","level":2,"score":0.27013298869132996},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.20153871178627014},{"id":"https://openalex.org/C2780091579","wikidata":"https://www.wikidata.org/wiki/Q9377","display_name":"Kidney","level":2,"score":0.12228664755821228},{"id":"https://openalex.org/C170286685","wikidata":"https://www.wikidata.org/wiki/Q409346","display_name":"B-cell activating factor","level":4,"score":0.0719161331653595},{"id":"https://openalex.org/C2778453870","wikidata":"https://www.wikidata.org/wiki/Q188930","display_name":"B cell","level":3,"score":0.0}],"mesh":[{"descriptor_ui":"D000077733","descriptor_name":"Immunoglobulin G4-Related Disease","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D000077733","descriptor_name":"Immunoglobulin G4-Related Disease","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":true},{"descriptor_ui":"D000077733","descriptor_name":"Immunoglobulin G4-Related Disease","qualifier_ui":"Q000188","qualifier_name":"drug therapy","is_major_topic":true},{"descriptor_ui":"D000974","descriptor_name":"Antibodies, Antinuclear","qualifier_ui":"Q000097","qualifier_name":"blood","is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005334","descriptor_name":"Fever","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007166","descriptor_name":"Immunosuppressive Agents","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D007668","descriptor_name":"Kidney","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D008181","descriptor_name":"Lupus Nephritis","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D008181","descriptor_name":"Lupus Nephritis","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":true},{"descriptor_ui":"D008181","descriptor_name":"Lupus Nephritis","qualifier_ui":"Q000188","qualifier_name":"drug therapy","is_major_topic":true},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009173","descriptor_name":"Mycophenolic Acid","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D011507","descriptor_name":"Proteinuria","qualifier_ui":"Q000188","qualifier_name":"drug therapy","is_major_topic":false},{"descriptor_ui":"D011507","descriptor_name":"Proteinuria","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D014057","descriptor_name":"Tomography, X-Ray Computed","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D061067","descriptor_name":"Antibodies, Monoclonal, Humanized","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":true}],"locations_count":2,"locations":[{"id":"doi:10.1177/0961203319840430","doi":"https://doi.org/10.1177/0961203319840430","is_oa":false,"landing_page_url":"https://doi.org/10.1177/0961203319840430","pdf_url":null,"source":{"id":"https://openalex.org/S115920904","display_name":"Lupus","issn_l":"0961-2033","issn":["0961-2033","1477-0962"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-d","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-100","russia-white-list-2"],"host_organization":"https://openalex.org/P4310320017","host_organization_name":"SAGE Publishing","host_organization_lineage":["https://openalex.org/P4310320017"],"host_organization_lineage_names":["SAGE Publishing"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Lupus","raw_type":"journal-article"},{"id":"pmid:30917769","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/30917769","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Lupus","raw_type":"Case Reports"}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":0.98580002784729}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":12,"referenced_works":["https://openalex.org/W2035995635","https://openalex.org/W2052231078","https://openalex.org/W2058688878","https://openalex.org/W2070527591","https://openalex.org/W2131366312","https://openalex.org/W2156770685","https://openalex.org/W2159860161","https://openalex.org/W2166822765","https://openalex.org/W2343617423","https://openalex.org/W2399507807","https://openalex.org/W2775607224","https://openalex.org/W2791812865"],"related_works":["https://openalex.org/W4390538866","https://openalex.org/W4281264529","https://openalex.org/W2278053047","https://openalex.org/W2524018888","https://openalex.org/W3165115595","https://openalex.org/W4285087110","https://openalex.org/W3013558407","https://openalex.org/W4294415042","https://openalex.org/W4410288388","https://openalex.org/W4210386064"],"abstract_inverted_index":{"Immunoglobulin":[0],"(Ig)G4-related":[1],"disease":[2],"(IgG4-RD)":[3],"is":[4],"an":[5],"unusual":[6],"complication":[7],"of":[8,72,83,122,140,148,159],"systemic":[9],"lupus":[10,94],"erythematosus":[11],"(SLE).":[12],"We":[13],"report":[14,158],"a":[15,160],"case":[16,161],"in":[17,47,86,162],"which":[18,163],"belimumab":[19],"proved":[20,124],"efficacious":[21],"for":[22,42,62],"not":[23],"only":[24],"SLE,":[25],"but":[26,118],"also":[27],"IgG4-RD.":[28],"A":[29],"58-year-old":[30],"Japanese":[31],"woman":[32],"had":[33],"suffered":[34],"from":[35,98],"photodermatosis":[36],"and":[37,50,59,65,96,109,113,134,145,166],"erythema":[38],"on":[39],"the":[40,87,120,156],"limbs":[41],"20":[43],"years.":[44],"She":[45],"presented":[46],"slight":[48],"fever":[49],"fatigue":[51],"since":[52],"2016.":[53],"Laboratory":[54],"data":[55],"showed":[56],"hypergammaglobulinemia,":[57],"proteinuria":[58,135],"positive":[60],"results":[61],"anti-nuclear":[63],"antibody":[64],"anti-double-stranded":[66],"DNA":[67],"antibody.":[68],"Furthermore,":[69],"elevated":[70],"levels":[71],"serum":[73,146],"IgG4":[74,149],"were":[75,168],"detected.":[76],"Contrast-enhanced":[77],"computed":[78],"tomography":[79],"disclosed":[80],"multiple":[81],"areas":[82],"poor":[84],"enhancement":[85],"kidneys.":[88],"The":[89,138],"patient":[90],"was":[91,102,128,142],"diagnosed":[92],"with":[93,104,130],"nephritis":[95],"IgG4-RD":[97,167],"renal":[99],"biopsy.":[100],"Treatment":[101],"started":[103,129],"prednisolone":[105],"at":[106],"40":[107],"mg/day":[108],"mycophenolate":[110],"mofetil.":[111],"Proteinuria":[112],"serological":[114],"findings":[115],"improved":[116],"initially,":[117],"tapering":[119],"dose":[121,139],"glucocorticoid":[123,141],"difficult.":[125],"After":[126],"treatment":[127],"belimumab,":[131],"clinical":[132],"symptoms":[133],"resolved":[136],"completely.":[137],"successfully":[143],"tapered":[144],"concentration":[147],"fell":[150],"further.":[151],"This":[152],"appears":[153],"to":[154],"represent":[155],"first":[157],"both":[164],"SLE":[165],"effectively":[169],"treated":[170],"using":[171],"belimumab.":[172]},"counts_by_year":[{"year":2026,"cited_by_count":5},{"year":2025,"cited_by_count":10},{"year":2024,"cited_by_count":3},{"year":2023,"cited_by_count":3},{"year":2022,"cited_by_count":5},{"year":2021,"cited_by_count":3},{"year":2020,"cited_by_count":2}],"updated_date":"2026-11-05T12:25:35.769452","created_date":"2019-04-11T00:00:00"}
