{"id":"https://openalex.org/W2892313124","doi":"https://doi.org/10.1093/ageing/afy140.190","title":"259Cerebral Amyloid Angiopathy - Related Inflammation: A Case Report","display_name":"259Cerebral Amyloid Angiopathy - Related Inflammation: A Case Report","publication_year":2018,"publication_date":"2018-09-01","ids":{"openalex":"https://openalex.org/W2892313124","doi":"https://doi.org/10.1093/ageing/afy140.190","mag":"2892313124"},"language":"en","primary_location":{"id":"doi:10.1093/ageing/afy140.190","doi":"https://doi.org/10.1093/ageing/afy140.190","is_oa":false,"landing_page_url":"https://doi.org/10.1093/ageing/afy140.190","pdf_url":null,"source":{"id":"https://openalex.org/S31768639","display_name":"Age and Ageing","issn_l":"0002-0729","issn":["0002-0729","1468-2834"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-a","doyens","jufo-3","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Age and Ageing","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5069863497","display_name":"Kowshika Thavarajah","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2802992464","display_name":"University Hospital Limerick","ror":"https://ror.org/04y3ze847","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I2800263200","https://openalex.org/I2802992464","https://openalex.org/I37076085","https://openalex.org/I4210136517"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Kowshika Thavarajah","raw_affiliation_strings":["University Hospital Limerick, Limerick, Ireland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University Hospital Limerick, Limerick, Ireland","institution_ids":["https://openalex.org/I2802992464"]}]},{"author_position":"middle","author":{"id":null,"display_name":"Colin Quinn","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2802992464","display_name":"University Hospital Limerick","ror":"https://ror.org/04y3ze847","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I2800263200","https://openalex.org/I2802992464","https://openalex.org/I37076085","https://openalex.org/I4210136517"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Colin Quinn","raw_affiliation_strings":["University Hospital Limerick, Limerick, Ireland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University Hospital Limerick, Limerick, Ireland","institution_ids":["https://openalex.org/I2802992464"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5061053285","display_name":"Sean Patrick Murphy","orcid":"https://orcid.org/0000-0002-6582-4065","observed_orcids":["https://orcid.org/0000-0002-6582-4065"]},"institutions":[{"id":"https://openalex.org/I2803071314","display_name":"Mater Misericordiae University Hospital","ror":"https://ror.org/040hqpc16","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I2803071314"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Sean Murphy","raw_affiliation_strings":["Mater Misericordiae Hospital, Dublin, Ireland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Mater Misericordiae Hospital, Dublin, Ireland","institution_ids":["https://openalex.org/I2803071314"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5101472249","display_name":"Ahmed Gabr","orcid":"https://orcid.org/0000-0002-8577-3541","observed_orcids":["https://orcid.org/0000-0002-8577-3541"]},"institutions":[{"id":"https://openalex.org/I2802992464","display_name":"University Hospital Limerick","ror":"https://ror.org/04y3ze847","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I2800263200","https://openalex.org/I2802992464","https://openalex.org/I37076085","https://openalex.org/I4210136517"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Ahmed Gabr","raw_affiliation_strings":["University Hospital Limerick, Limerick, Ireland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University Hospital Limerick, Limerick, Ireland","institution_ids":["https://openalex.org/I2802992464"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5103448109","display_name":"Declan Lyons","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2802992464","display_name":"University Hospital Limerick","ror":"https://ror.org/04y3ze847","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I2800263200","https://openalex.org/I2802992464","https://openalex.org/I37076085","https://openalex.org/I4210136517"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Declan Lyons","raw_affiliation_strings":["University Hospital Limerick, Limerick, Ireland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University Hospital Limerick, Limerick, Ireland","institution_ids":["https://openalex.org/I2802992464"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5037714575","display_name":"Margaret O\u2019Connor","orcid":"https://orcid.org/0000-0001-9984-9204","observed_orcids":["https://orcid.org/0000-0001-9984-9204"]},"institutions":[{"id":"https://openalex.org/I2802992464","display_name":"University Hospital Limerick","ror":"https://ror.org/04y3ze847","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I2800263200","https://openalex.org/I2802992464","https://openalex.org/I37076085","https://openalex.org/I4210136517"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Margaret O\u2019Connor","raw_affiliation_strings":["University Hospital Limerick, Limerick, Ireland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University Hospital Limerick, Limerick, Ireland","institution_ids":["https://openalex.org/I2802992464"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5102906487","display_name":"Catherine Peters","orcid":"https://orcid.org/0000-0003-4406-4535","observed_orcids":["https://orcid.org/0000-0003-4406-4535"]},"institutions":[{"id":"https://openalex.org/I2802992464","display_name":"University Hospital Limerick","ror":"https://ror.org/04y3ze847","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I2800263200","https://openalex.org/I2802992464","https://openalex.org/I37076085","https://openalex.org/I4210136517"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Catherine Peters","raw_affiliation_strings":["University Hospital Limerick, Limerick, Ireland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University Hospital Limerick, Limerick, Ireland","institution_ids":["https://openalex.org/I2802992464"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5057691233","display_name":"Monzar Musa","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2802992464","display_name":"University Hospital Limerick","ror":"https://ror.org/04y3ze847","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I2800263200","https://openalex.org/I2802992464","https://openalex.org/I37076085","https://openalex.org/I4210136517"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Monzar Musa","raw_affiliation_strings":["University Hospital Limerick, Limerick, Ireland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University Hospital Limerick, Limerick, Ireland","institution_ids":["https://openalex.org/I2802992464"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5014882222","display_name":"Carol McKiernan","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2802992464","display_name":"University Hospital Limerick","ror":"https://ror.org/04y3ze847","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I2800263200","https://openalex.org/I2802992464","https://openalex.org/I37076085","https://openalex.org/I4210136517"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Carol McKiernan","raw_affiliation_strings":["University Hospital Limerick, Limerick, Ireland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University Hospital Limerick, Limerick, Ireland","institution_ids":["https://openalex.org/I2802992464"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5057391522","display_name":"Nallasegarampillai Muthalvan","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2802992464","display_name":"University Hospital Limerick","ror":"https://ror.org/04y3ze847","country_code":"IE","type":"healthcare","lineage":["https://openalex.org/I2800263200","https://openalex.org/I2802992464","https://openalex.org/I37076085","https://openalex.org/I4210136517"]}],"countries":["IE"],"is_corresponding":false,"raw_author_name":"Nallasegarampillai Muthalvan","raw_affiliation_strings":["University Hospital Limerick, Limerick, Ireland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University Hospital Limerick, Limerick, Ireland","institution_ids":["https://openalex.org/I2802992464"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":{"value":2805,"currency":"GBP","value_usd":3699},"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":{"value":0.13862621,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"47","issue":"suppl_5","first_page":"v13","last_page":"v60"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11763","display_name":"Intracerebral and Subarachnoid Hemorrhage Research","score":0.9970999956130981,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11763","display_name":"Intracerebral and Subarachnoid Hemorrhage Research","score":0.9970999956130981,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T13648","display_name":"Cerebrovascular and genetic disorders","score":0.0008999999845400453,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T13201","display_name":"Infectious Encephalopathies and Encephalitis","score":0.00039999998989515007,"subfield":{"id":"https://openalex.org/subfields/2725","display_name":"Infectious Diseases"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/cerebral-amyloid-angiopathy-related-inflammation","display_name":"cerebral amyloid angiopathy-related inflammation","score":0.8949999809265137},{"id":"https://openalex.org/keywords/encephalopathy","display_name":"encephalopathy","score":0.7549999952316284},{"id":"https://openalex.org/keywords/vasogenic-cerebral-oedema","display_name":"vasogenic cerebral oedema","score":0.7770000100135803},{"id":"https://openalex.org/keywords/white-matter-hyperintensities","display_name":"white matter hyperintensities","score":0.9620000123977661},{"id":"https://openalex.org/keywords/microhemorrhages","display_name":"microhemorrhages","score":0.8790000081062317},{"id":"https://openalex.org/keywords/prednisone","display_name":"prednisone","score":0.5479999780654907},{"id":"https://openalex.org/keywords/immunosuppressive-therapy","display_name":"immunosuppressive therapy","score":0.8640000224113464},{"id":"https://openalex.org/keywords/differential-diagnosis","display_name":"differential diagnosis","score":0.6200000047683716},{"id":"https://openalex.org/keywords/elderly-patients","display_name":"elderly patients","score":0.3700000047683716}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.91640305519104},{"id":"https://openalex.org/C2777790613","wikidata":"https://www.wikidata.org/wiki/Q191562","display_name":"Cerebral amyloid angiopathy","level":4,"score":0.8207155466079712},{"id":"https://openalex.org/C2776914184","wikidata":"https://www.wikidata.org/wiki/Q101991","display_name":"Inflammation","level":2,"score":0.6027534604072571},{"id":"https://openalex.org/C2777633098","wikidata":"https://www.wikidata.org/wiki/Q2736051","display_name":"Amyloid (mycology)","level":2,"score":0.5593116879463196},{"id":"https://openalex.org/C2779703115","wikidata":"https://www.wikidata.org/wiki/Q539702","display_name":"Angiopathy","level":3,"score":0.4977128803730011},{"id":"https://openalex.org/C2779951007","wikidata":"https://www.wikidata.org/wiki/Q816798","display_name":"Amyloidosis","level":2,"score":0.4439904987812042},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.40125173330307007},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.2353031039237976},{"id":"https://openalex.org/C2779483572","wikidata":"https://www.wikidata.org/wiki/Q83030","display_name":"Dementia","level":3,"score":0.16213995218276978},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.12385356426239014},{"id":"https://openalex.org/C134018914","wikidata":"https://www.wikidata.org/wiki/Q162606","display_name":"Endocrinology","level":1,"score":0.11868888139724731},{"id":"https://openalex.org/C555293320","wikidata":"https://www.wikidata.org/wiki/Q12206","display_name":"Diabetes mellitus","level":2,"score":0.07785746455192566}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.1093/ageing/afy140.190","doi":"https://doi.org/10.1093/ageing/afy140.190","is_oa":false,"landing_page_url":"https://doi.org/10.1093/ageing/afy140.190","pdf_url":null,"source":{"id":"https://openalex.org/S31768639","display_name":"Age and Ageing","issn_l":"0002-0729","issn":["0002-0729","1468-2834"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-a","doyens","jufo-3","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Age and Ageing","raw_type":"journal-article"}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":1.0,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W3013800676","https://openalex.org/W7164191898","https://openalex.org/W4367399910","https://openalex.org/W4407234807","https://openalex.org/W4303192927","https://openalex.org/W3186472286","https://openalex.org/W2793722333","https://openalex.org/W4319734225","https://openalex.org/W2337319560","https://openalex.org/W1529532582"],"abstract_inverted_index":{"Background:":[0],"Cerebral":[1],"amyloid":[2],"angiopathy":[3],"related":[4],"inflammation":[5],"(CAA-ri)":[6],"can":[7,24],"lead":[8],"to":[9,56],"a":[10,62,179,204,215,255],"potentially":[11],"rapidly":[12],"progressive":[13],"encephalopathy":[14],"and":[15,74,85,116,131,173,190,192,201,242,248,261,266],"usually":[16],"occurs":[17],"in":[18,40,50,275],"older":[19],"adults.":[20],"A":[21],"definitive":[22],"diagnosis":[23,206],"only":[25],"be":[26,273],"made":[27],"histologically":[28],"although":[29,285],"typical":[30],"clinical":[31,41,180],"symptoms":[32],"along":[33],"with":[34,79,87,98,149,257,280],"characteristic":[35],"MRI":[36,121,227],"findings":[37],"may":[38,282],"aid":[39],"diagnosis1.":[42],"Methods:":[43],"An":[44],"82-year-old":[45],"man":[46],"was":[47,70,77,83,161,178,209,212,240],"found":[48],"obtunded":[49],"his":[51,59,199],"house":[52],"having":[53],"been":[54],"unresponsive":[55],"messages":[57],"from":[58],"son":[60],"for":[61,170],"period":[63],"of":[64,101,126,182,198,207,220,234,288],"several":[65],"days.":[66],"At":[67],"presentation":[68,200],"he":[69],"alert":[71],"but":[72],"disorientated":[73],"restless.":[75],"GCS":[76],"13/15":[78],"normal":[80],"BP.":[81],"Speech":[82],"slow":[84],"hesitant":[86],"neurological":[88],"examination":[89],"otherwise":[90,162],"unremarkable.":[91],"Haematological":[92],"investigations":[93],"revealed":[94,142,231],"raised":[95],"inflammatory":[96],"markers":[97],"biochemical":[99],"evidence":[100],"mild":[102],"rhabdomyolysis.":[103],"Non":[104],"contrast":[105],"CT":[106],"brain":[107,122],"showed":[108,246],"asymmetrical":[109,262],"vasogenic":[110],"oedema":[111,127],"involving":[112],"bilateral":[113,143],"temporal,":[114],"parietal":[115],"occipital":[117],"lobes.":[118],"Contrast":[119],"enhanced":[120],"demonstrated":[123],"multifocal":[124],"areas":[125],"affecting":[128],"corresponding":[129],"cortical":[130,145],"subcortical":[132],"white":[133,236,263],"matter":[134,237,264],"regions":[135],"without":[136],"enhancement.":[137],"Blood":[138],"sensitive":[139],"SWI":[140],"sequences":[141],"multiple":[144],"punctuate":[146],"hypointensities":[147],"consistent":[148],"microhemorrhages":[150],"sparing":[151],"the":[152,235,276],"basal":[153],"ganglia":[154],"bilaterally.":[155],"Work":[156],"up":[157,226],"including":[158],"CSF":[159],"analysis":[160],"unrevealing.":[163],"Results:":[164],"Initial":[165],"treatment":[166],"included":[167],"empirical":[168],"cover":[169],"viral":[171],"encephalitis":[172],"anticonvulsant":[174],"therapy":[175],"as":[176],"there":[177],"suspicion":[181],"unwitnessed":[183],"seizure":[184],"activity.":[185],"His":[186],"blood":[187],"picture":[188],"normalized":[189],"disorientation":[191],"speech":[193],"disturbance":[194],"resolved.":[195],"In":[196,254],"view":[197],"radiological":[202],"features,":[203],"presumptive":[205],"CAA-ri":[208,271],"made.":[210],"He":[211,239],"commenced":[213],"on":[214,269],"6":[216,228],"week":[217],"tapering":[218],"course":[219],"oral":[221],"prednisone":[222],"30":[223],"mg.":[224],"Follow":[225],"weeks":[229],"later":[230],"complete":[232],"resolution":[233],"hyperintensities.":[238],"asymptomatic":[241],"remained":[243],"independent.":[244],"MMSE":[245],"attention":[247],"recall":[249],"deficits":[250],"at":[251],"24/30.":[252],"Conclusion:":[253],"patient":[256],"acute":[258],"cognitive":[259],"decline":[260],"hyperintensities":[265],"associated":[267],"microhaemorhages":[268],"MRI,":[270],"should":[272],"considered":[274],"differential":[277],"diagnosis.":[278],"Treatment":[279],"immunosuppression":[281],"improve":[283],"prognosis":[284],"further":[286],"study":[287],"this":[289],"rare":[290],"condition":[291],"is":[292],"needed.":[293]},"counts_by_year":[],"updated_date":"2026-11-06T12:05:46.655746","created_date":"2018-09-27T00:00:00"}
