{"id":"https://openalex.org/W2890475699","doi":"https://doi.org/10.1161/circ.132.suppl_3.18417","title":"Abstract 18417: Clinical Presentation, Cardiac Phenotype and Long Term Prognosis of Patients With Late Onset Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy","display_name":"Abstract 18417: Clinical Presentation, Cardiac Phenotype and Long Term Prognosis of Patients With Late Onset Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy","publication_year":2015,"publication_date":"2015-11-10","ids":{"openalex":"https://openalex.org/W2890475699","doi":"https://doi.org/10.1161/circ.132.suppl_3.18417","mag":"2890475699"},"language":"en","primary_location":{"id":"doi:10.1161/circ.132.suppl_3.18417","doi":"https://doi.org/10.1161/circ.132.suppl_3.18417","is_oa":false,"landing_page_url":"https://doi.org/10.1161/circ.132.suppl_3.18417","pdf_url":null,"source":{"id":"https://openalex.org/S116251202","display_name":"Circulation","issn_l":"0009-7322","issn":["0009-7322","1524-4539"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315671","host_organization_name":"Lippincott Williams & Wilkins","host_organization_lineage":["https://openalex.org/P4310315671","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Lippincott Williams & Wilkins","Wolters Kluwer"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Circulation","raw_type":"journal-article"},"volume":null,"type":"conference-abstract","indexed_in":["crossref"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5060643136","display_name":"Aditya Bhonsale","orcid":"https://orcid.org/0000-0001-7827-5977","observed_orcids":["https://orcid.org/0000-0001-7827-5977"]},"institutions":[{"id":"https://openalex.org/I145311948","display_name":"Johns Hopkins University","ror":"https://ror.org/00za53h95","country_code":"US","type":"education","lineage":["https://openalex.org/I145311948"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Aditya Bhonsale","raw_affiliation_strings":["Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","Aditya Bhonsale"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","institution_ids":["https://openalex.org/I145311948"]},{"raw_affiliation_string":"Aditya Bhonsale","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5090978835","display_name":"Anneline S.J.M. te Riele","orcid":"https://orcid.org/0000-0002-4694-4790","observed_orcids":["https://orcid.org/0000-0002-4694-4790","https://orcid.org/0000-0003-1115-6193"]},"institutions":[{"id":"https://openalex.org/I3018483916","display_name":"University Medical Center Utrecht","ror":"https://ror.org/0575yy874","country_code":"NL","type":"healthcare","lineage":["https://openalex.org/I3018483916"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"Anneline S te Riele","raw_affiliation_strings":["Cardiology, Univ Med Cntr Utrecht, Utrecht, Netherlands","Anneline S te Riele"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, Univ Med Cntr Utrecht, Utrecht, Netherlands","institution_ids":["https://openalex.org/I3018483916"]},{"raw_affiliation_string":"Anneline S te Riele","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5076611405","display_name":"Abhishek Chandrakant Sawant","orcid":"https://orcid.org/0000-0001-9276-4443","observed_orcids":["https://orcid.org/0000-0001-9276-4443"]},"institutions":[{"id":"https://openalex.org/I145311948","display_name":"Johns Hopkins University","ror":"https://ror.org/00za53h95","country_code":"US","type":"education","lineage":["https://openalex.org/I145311948"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Abhishek Sawant","raw_affiliation_strings":["Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","Abhishek Sawant"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","institution_ids":["https://openalex.org/I145311948"]},{"raw_affiliation_string":"Abhishek Sawant","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5070742769","display_name":"Judith A. Groeneweg","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I3018483916","display_name":"University Medical Center Utrecht","ror":"https://ror.org/0575yy874","country_code":"NL","type":"healthcare","lineage":["https://openalex.org/I3018483916"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"Judith Groeneweg","raw_affiliation_strings":["Cardiology, Univ Med Cntr Utrecht, Utrecht, Netherlands","Judith Groeneweg"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, Univ Med Cntr Utrecht, Utrecht, Netherlands","institution_ids":["https://openalex.org/I3018483916"]},{"raw_affiliation_string":"Judith Groeneweg","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5087814371","display_name":"Cynthia A. James","orcid":"https://orcid.org/0000-0001-8040-4600","observed_orcids":["https://orcid.org/0000-0001-8040-4600","https://orcid.org/0000-0003-0854-0418"]},"institutions":[{"id":"https://openalex.org/I145311948","display_name":"Johns Hopkins University","ror":"https://ror.org/00za53h95","country_code":"US","type":"education","lineage":["https://openalex.org/I145311948"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Cynthia A James","raw_affiliation_strings":["Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","Cynthia A James"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","institution_ids":["https://openalex.org/I145311948"]},{"raw_affiliation_string":"Cynthia A James","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5044491062","display_name":"Brittney A. Murray","orcid":"https://orcid.org/0000-0001-7870-8584","observed_orcids":["https://orcid.org/0000-0001-7870-8584"]},"institutions":[{"id":"https://openalex.org/I145311948","display_name":"Johns Hopkins University","ror":"https://ror.org/00za53h95","country_code":"US","type":"education","lineage":["https://openalex.org/I145311948"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Brittney Murray","raw_affiliation_strings":["Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","Brittney Murray"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","institution_ids":["https://openalex.org/I145311948"]},{"raw_affiliation_string":"Brittney Murray","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5079407938","display_name":"Crystal Tichnel","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I145311948","display_name":"Johns Hopkins University","ror":"https://ror.org/00za53h95","country_code":"US","type":"education","lineage":["https://openalex.org/I145311948"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Crystal Tichnel","raw_affiliation_strings":["Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","Crystal Tichnel"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","institution_ids":["https://openalex.org/I145311948"]},{"raw_affiliation_string":"Crystal Tichnel","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5038816338","display_name":"Dennis Dooijes","orcid":"https://orcid.org/0000-0003-0312-5354","observed_orcids":["https://orcid.org/0000-0003-0312-5354"]},"institutions":[{"id":"https://openalex.org/I193662353","display_name":"Utrecht University","ror":"https://ror.org/04pp8hn57","country_code":"NL","type":"education","lineage":["https://openalex.org/I193662353"]},{"id":"https://openalex.org/I3018483916","display_name":"University Medical Center Utrecht","ror":"https://ror.org/0575yy874","country_code":"NL","type":"healthcare","lineage":["https://openalex.org/I3018483916"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"Dennis Dooijes","raw_affiliation_strings":["Dept of Genetics, Univ Med Cntr Utrecht, Utrecht, Netherlands","Dennis Dooijes"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Dept of Genetics, Univ Med Cntr Utrecht, Utrecht, Netherlands","institution_ids":["https://openalex.org/I193662353","https://openalex.org/I3018483916"]},{"raw_affiliation_string":"Dennis Dooijes","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5072654220","display_name":"Jeroen F. van der Heijden","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I3018483916","display_name":"University Medical Center Utrecht","ror":"https://ror.org/0575yy874","country_code":"NL","type":"healthcare","lineage":["https://openalex.org/I3018483916"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"Jeroen v Heijden","raw_affiliation_strings":["Cardiology, Univ Med Cntr Utrecht, Utrecht, Netherlands","Jeroen v Heijden"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, Univ Med Cntr Utrecht, Utrecht, Netherlands","institution_ids":["https://openalex.org/I3018483916"]},{"raw_affiliation_string":"Jeroen v Heijden","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5063475669","display_name":"Harikrishna S. Tandri","orcid":"https://orcid.org/0000-0003-2651-4352","observed_orcids":["https://orcid.org/0000-0003-2651-4352"]},"institutions":[{"id":"https://openalex.org/I145311948","display_name":"Johns Hopkins University","ror":"https://ror.org/00za53h95","country_code":"US","type":"education","lineage":["https://openalex.org/I145311948"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Harikrishna Tandri","raw_affiliation_strings":["Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","Harikrishna Tandri"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","institution_ids":["https://openalex.org/I145311948"]},{"raw_affiliation_string":"Harikrishna Tandri","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5087108967","display_name":"J. Peter van Tintelen","orcid":"https://orcid.org/0000-0003-3854-6749","observed_orcids":["https://orcid.org/0000-0003-3854-6749"]},"institutions":[{"id":"https://openalex.org/I887064364","display_name":"University of Amsterdam","ror":"https://ror.org/04dkp9463","country_code":"NL","type":"education","lineage":["https://openalex.org/I887064364"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"Peter v Tintelen","raw_affiliation_strings":["Dept of Clinical Genetics, Academic Med Cntr, Univ of Amsterdam, Amsterdam, Netherlands","Peter v Tintelen"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Dept of Clinical Genetics, Academic Med Cntr, Univ of Amsterdam, Amsterdam, Netherlands","institution_ids":["https://openalex.org/I887064364"]},{"raw_affiliation_string":"Peter v Tintelen","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5076454382","display_name":"Daniel Philip Judge","orcid":"https://orcid.org/0000-0002-3407-0248","observed_orcids":["https://orcid.org/0000-0002-3407-0248"]},"institutions":[{"id":"https://openalex.org/I145311948","display_name":"Johns Hopkins University","ror":"https://ror.org/00za53h95","country_code":"US","type":"education","lineage":["https://openalex.org/I145311948"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Daniel P Judge","raw_affiliation_strings":["Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","Daniel P Judge"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","institution_ids":["https://openalex.org/I145311948"]},{"raw_affiliation_string":"Daniel P Judge","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5061063096","display_name":"Richard N.W. Hauer","orcid":"https://orcid.org/0000-0003-1467-7234","observed_orcids":["https://orcid.org/0000-0003-1467-7234"]},"institutions":[{"id":"https://openalex.org/I4210105827","display_name":"Netherlands Heart Institute","ror":"https://ror.org/01mh6b283","country_code":"NL","type":"facility","lineage":["https://openalex.org/I4210105827"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"Richard Hauer","raw_affiliation_strings":["Cardiology, ICIN-Netherlands Heart Institute, Utrecht, Netherlands","Richard Hauer"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, ICIN-Netherlands Heart Institute, Utrecht, Netherlands","institution_ids":["https://openalex.org/I4210105827"]},{"raw_affiliation_string":"Richard Hauer","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5025889874","display_name":"Hugh G Calkins","orcid":"https://orcid.org/0000-0002-9262-9433","observed_orcids":["https://orcid.org/0000-0002-9262-9433"]},"institutions":[{"id":"https://openalex.org/I145311948","display_name":"Johns Hopkins University","ror":"https://ror.org/00za53h95","country_code":"US","type":"education","lineage":["https://openalex.org/I145311948"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Hugh Calkins","raw_affiliation_strings":["Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","Hugh Calkins"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Cardiology, Johns Hopkins Univ Sch of Medicine, Baltimore, MD","institution_ids":["https://openalex.org/I145311948"]},{"raw_affiliation_string":"Hugh Calkins","institution_ids":[]}]}],"institutions":[],"countries_distinct_count":2,"institutions_distinct_count":5,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":null,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":null,"cited_by_percentile_year":null,"biblio":{"volume":"132","issue":"suppl_3","first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11922","display_name":"Cardiovascular Effects of Exercise","score":0.9955999851226807,"subfield":{"id":"https://openalex.org/subfields/2705","display_name":"Cardiology and Cardiovascular Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11922","display_name":"Cardiovascular Effects of Exercise","score":0.9955999851226807,"subfield":{"id":"https://openalex.org/subfields/2705","display_name":"Cardiology and Cardiovascular Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10882","display_name":"Cardiomyopathy and Myosin Studies","score":0.002199999988079071,"subfield":{"id":"https://openalex.org/subfields/2705","display_name":"Cardiology and Cardiovascular Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10217","display_name":"Cardiac electrophysiology and arrhythmias","score":0.001500000013038516,"subfield":{"id":"https://openalex.org/subfields/2705","display_name":"Cardiology and Cardiovascular Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/arrhythmogenic-right-ventricular-cardiomyopathy","display_name":"arrhythmogenic right ventricular cardiomyopathy","score":0.9769999980926514},{"id":"https://openalex.org/keywords/late-onset","display_name":"late onset","score":0.6140000224113464},{"id":"https://openalex.org/keywords/elderly-patients","display_name":"elderly patients","score":0.9319999814033508},{"id":"https://openalex.org/keywords/sustained-ventricular-tachycardia","display_name":"sustained ventricular tachycardia","score":0.9229999780654907},{"id":"https://openalex.org/keywords/cardiac-syncope","display_name":"cardiac syncope","score":0.8299999833106995},{"id":"https://openalex.org/keywords/pkp2-mutation","display_name":"PKP2 mutation","score":0.7549999952316284},{"id":"https://openalex.org/keywords/pathogenic-variants","display_name":"pathogenic variants","score":0.5040000081062317},{"id":"https://openalex.org/keywords/ventricular-ectopy","display_name":"ventricular ectopy","score":0.7609999775886536},{"id":"https://openalex.org/keywords/arrhythmia-free-survival","display_name":"arrhythmia-free survival","score":0.656000018119812},{"id":"https://openalex.org/keywords/risk-factors","display_name":"risk factors","score":0.4729999899864197},{"id":"https://openalex.org/keywords/family-history-medicine","display_name":"family history (medicine)","score":0.48500001430511475},{"id":"https://openalex.org/keywords/ventricular-arrhythmia-recurrence","display_name":"ventricular arrhythmia recurrence","score":0.5239999890327454},{"id":"https://openalex.org/keywords/heart-failure","display_name":"heart failure","score":0.43299999833106995},{"id":"https://openalex.org/keywords/left-ventricular-dysfunction","display_name":"left ventricular dysfunction","score":0.7749999761581421}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9570276141166687},{"id":"https://openalex.org/C2777892804","wikidata":"https://www.wikidata.org/wiki/Q2555727","display_name":"Arrhythmogenic right ventricular dysplasia","level":4,"score":0.8586593866348267},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.7562005519866943},{"id":"https://openalex.org/C164705383","wikidata":"https://www.wikidata.org/wiki/Q10379","display_name":"Cardiology","level":1,"score":0.6900071501731873},{"id":"https://openalex.org/C2778797674","wikidata":"https://www.wikidata.org/wiki/Q847583","display_name":"Cardiomyopathy","level":3,"score":0.6770064234733582},{"id":"https://openalex.org/C2778198053","wikidata":"https://www.wikidata.org/wiki/Q181754","display_name":"Heart failure","level":2,"score":0.49082812666893005},{"id":"https://openalex.org/C2776331378","wikidata":"https://www.wikidata.org/wiki/Q56002","display_name":"Ventricular tachycardia","level":2,"score":0.46631819009780884},{"id":"https://openalex.org/C2777601897","wikidata":"https://www.wikidata.org/wiki/Q3409113","display_name":"Presentation (obstetrics)","level":2,"score":0.4416774809360504},{"id":"https://openalex.org/C2777093960","wikidata":"https://www.wikidata.org/wiki/Q594446","display_name":"Implantable cardioverter-defibrillator","level":2,"score":0.43100735545158386},{"id":"https://openalex.org/C2775935837","wikidata":"https://www.wikidata.org/wiki/Q202837","display_name":"Sudden cardiac death","level":2,"score":0.42490154504776},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.2009863257408142}],"mesh":[],"locations_count":1,"locations":[{"id":"doi:10.1161/circ.132.suppl_3.18417","doi":"https://doi.org/10.1161/circ.132.suppl_3.18417","is_oa":false,"landing_page_url":"https://doi.org/10.1161/circ.132.suppl_3.18417","pdf_url":null,"source":{"id":"https://openalex.org/S116251202","display_name":"Circulation","issn_l":"0009-7322","issn":["0009-7322","1524-4539"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315671","host_organization_name":"Lippincott Williams & Wilkins","host_organization_lineage":["https://openalex.org/P4310315671","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Lippincott Williams & Wilkins","Wolters Kluwer"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Circulation","raw_type":"journal-article"}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":1.0}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W1994835229","https://openalex.org/W2588110527","https://openalex.org/W2510429599","https://openalex.org/W1517069328","https://openalex.org/W2158700691","https://openalex.org/W2158221215","https://openalex.org/W2340024721","https://openalex.org/W2921050660","https://openalex.org/W37912716","https://openalex.org/W4413012644"],"abstract_inverted_index":{"Introduction:":[0],"The":[1,101],"phenotypic":[2,24],"features":[3],"and":[4,25,41,48,121,170,177,204,239,254,277,299,308,318],"clinical":[5,51],"course":[6],"of":[7,28,90,143,161,194,248,263,271],"elderly":[8,94,102,317],"Arrhythmogenic":[9],"Right":[10],"Ventricular":[11],"Dysplasia/Cardiomyopathy":[12],"(ARVD/C)":[13],"patients":[14,30,62,147,179,266],"(age>":[15],"50":[16,269],"years":[17,78,142,160,270],"at":[18,79,158],"diagnosis)":[19],"is":[20,85,98,300],"unknown.":[21],"Methods:":[22],"Demographic,":[23],"genotypic":[26],"data":[27],"502":[29],"with":[31,64,73,152,217,245,274,302,322],"ARVC":[32],"diagnosis":[33],"(2010":[34],"Task":[35],"Force":[36],"Criteria)":[37],"from":[38],"Johns":[39],"Hopkins":[40],"Utrecht":[42],"(NL)":[43],"ARVD/C":[44,265],"registries":[45],"was":[46,57,173],"obtained":[47],"long":[49],"term":[50],"outcomes":[52],"ascertained.":[53],"Results:":[54],"Late":[55],"presentation":[56,91,292],"seen":[58,174],"in":[59,92,166,175,315],"104":[60],"(21%)":[61],"(38%":[63],"PKP2":[65],"mutation;":[66],"no":[67],"DSP":[68],"or":[69,285],"DSG2":[70],"mutation":[71,111,197,241],"carrier)":[72],"3%":[74],"being":[75],"\u2265":[76],"65":[77],"diagnosis.":[80],"Sustained":[81],"ventricular":[82,124,150,249,255,309],"tachycardia":[83],"(VT)":[84],"the":[86,93,138,221,316],"major":[87,227],"(43%)":[88],"mode":[89],"while":[95,251],"cardiac":[96,184],"syncope":[97,284],"infrequent":[99],"(p<0.001).":[100],"are":[103,278,311,319],"significantly":[104,312],"less":[105,279,313],"likely":[106,280],"to":[107,134,281],"harbor":[108],"a":[109,195,296],"pathogenic":[110,196,240,287],"(53%;":[112],"p=0.005),":[113],"have":[114,122,282],"precordial":[115],"T":[116],"wave":[117],"repolarization":[118],"changes":[119,307],"(p<0.001)":[120],"lower":[123],"ectopy":[125,256,310],"burden":[126],"(median":[127],"count":[128],"1503":[129],"vs":[130],"2497;":[131],"p=0.026)":[132],"compared":[133],"younger":[135],"patients.":[136],"In":[137,220,289],"elderly,":[139,222],"over":[140],"7\u00b15":[141],"follow":[144,162],"up,":[145],"68(65%)":[146],"experienced":[148],"sustained":[149,275],"arrhythmias":[151,250],"similar":[153],"(p=0.08)":[154],"arrhythmia":[155],"free":[156],"survival":[157],"5":[159],"up":[163],"(73%":[164],"vs.60%":[165],"younger).":[167],"LV":[168],"dysfunction":[169],"heart":[171],"failure":[172],"24(32%)":[176],"15(14%)":[178],"respectively":[180],"without":[181],"need":[182],"for":[183],"transplantation.":[185],"Male":[186],"gender":[187,237],"(OR":[188,198,208],"2.12,":[189],"95%CI":[190,200,210],"(1.3-3.45);":[191],"p=0.002),":[192],"absence":[193],"1.94,":[199],"(1.20,":[201],"3.12);":[202],"p=0.006)":[203],"family":[205,233],"member":[206],"status":[207],"2.09,":[209],"(1.24,":[211],"3.51);":[212],"P=0.006)":[213],"were":[214,243,258],"independently":[215],"associated":[216,244,301,321],"late":[218,291],"presentation.":[219],"EP":[223],"study":[224],"inducibility":[225],"(<0.001),":[226],"RV":[228],"structural":[229],"disease":[230],"(p=0.022),":[231],"absent":[232],"history":[234],"(p<0.001),":[235],"male":[236],"(p=0.002)":[238],"(p=0.001)":[242],"increased":[246],"risk":[247],"ECG":[252],"abnormalities":[253],"(p=0.489)":[257],"not.":[259],"Conclusion:":[260],"One":[261],"fifth":[262],"all":[264],"present":[267],"after":[268],"age,":[272],"often":[273],"VT":[276],"prior":[283],"identifiable":[286],"mutation.":[288],"ARVD/C,":[290],"does":[293],"not":[294,320],"confer":[295],"benign":[297],"prognosis":[298],"high":[303],"arrhythmic":[304,323],"risk.":[305],"Electrocardiographic":[306],"common":[314],"events.":[324]},"counts_by_year":[],"updated_date":"2026-10-11T09:32:39.932853","created_date":"2018-09-27T00:00:00"}
