{"id":"https://openalex.org/W2786355704","doi":null,"title":"Comparison of sensitivity and specificity of MAS and HLH diagnostic guidelines in 362 children with MAS complicating systemic JIA","display_name":"Comparison of sensitivity and specificity of MAS and HLH diagnostic guidelines in 362 children with MAS complicating systemic JIA","publication_year":2013,"publication_date":"2013-01-01","ids":{"openalex":"https://openalex.org/W2786355704","mag":"2786355704"},"language":"en","primary_location":{"id":"mag:2786355704","doi":null,"is_oa":false,"landing_page_url":"https://www.bib.irb.hr/673223","pdf_url":null,"source":null,"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":null},"volume":null,"type":"article","indexed_in":[],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5064869878","display_name":"Sergio Dav\u00ec","orcid":"https://orcid.org/0000-0002-8707-8040","observed_orcids":["https://orcid.org/0000-0002-8707-8040"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Sergio Dav\u00ec","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0002-8707-8040","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5022336463","display_name":"Francesca Minoia","orcid":"https://orcid.org/0000-0002-5093-8422","observed_orcids":["https://orcid.org/0000-0002-5093-8422"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Francesca Minoia","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0002-5093-8422","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5036371598","display_name":"AnnaCarin Horne","orcid":"https://orcid.org/0000-0002-2878-4463","observed_orcids":["https://orcid.org/0000-0002-2878-4463"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"AnnaCarin Horne","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0002-2878-4463","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5000636712","display_name":"Erkan Demirkaya","orcid":"https://orcid.org/0000-0003-4525-1789","observed_orcids":["https://orcid.org/0000-0003-4525-1789"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Erkan Demirkaya","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0003-4525-1789","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5028020433","display_name":"Norman T. Ilowite","orcid":"https://orcid.org/0000-0002-8298-8563","observed_orcids":["https://orcid.org/0000-0002-8298-8563"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Norman T. Ilowite","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0002-8298-8563","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5076793208","display_name":"Antonella Insalaco","orcid":"https://orcid.org/0000-0003-1443-1840","observed_orcids":["https://orcid.org/0000-0003-1443-1840"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Antonella Insalaco","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0003-1443-1840","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5050502063","display_name":"Maka Ioseliani","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Maka Ioseliani","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5019966799","display_name":"Marija Jelu\u0161i\u0107","orcid":"https://orcid.org/0000-0002-1728-4260","observed_orcids":["https://orcid.org/0000-0002-1728-4260"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Marija Jelu\u0161i\u0107","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0002-1728-4260","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5011499909","display_name":"Agneza Marija Kapovi\u0107","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Agneza Marija Kapovi\u0107","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5085125040","display_name":"\u00d6zg\u00fcr Kasap\u00e7opur","orcid":"https://orcid.org/0000-0002-1125-7720","observed_orcids":["https://orcid.org/0000-0002-1125-7720"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"\u00d6zg\u00fcr Kasap\u00e7opur","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0002-1125-7720","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5036816060","display_name":"Isabelle Kon\u00e9\u2010Paut","orcid":"https://orcid.org/0000-0001-8939-5763","observed_orcids":["https://orcid.org/0000-0001-8939-5763"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Isabelle Kon\u00e9\u2010Paut","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0001-8939-5763","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5035626824","display_name":"Loredana Lepore","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Loredana Lepore","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5101501322","display_name":"Caifeng Li","orcid":"https://orcid.org/0000-0002-8248-7347","observed_orcids":["https://orcid.org/0000-0002-8248-7347"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Caifeng Li","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0002-8248-7347","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5012181133","display_name":"Silvia Magni\u2010Manzoni","orcid":"https://orcid.org/0000-0002-5714-1141","observed_orcids":["https://orcid.org/0000-0002-5714-1141"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Silvia Magni\u2010Manzoni","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0002-5714-1141","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5034483400","display_name":"Despoina Maritsi","orcid":"https://orcid.org/0000-0002-5858-6484","observed_orcids":["https://orcid.org/0000-0002-5858-6484"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Despoina Maritsi","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0002-5858-6484","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5112214492","display_name":"Deborah McCurdy","orcid":"https://orcid.org/0000-0001-8914-3523","observed_orcids":["https://orcid.org/0000-0001-8914-3523"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Deborah McCurdy","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5100520496","display_name":"Rosa Merino","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Rosa Merino","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5020941004","display_name":"Paivi Miettunen","orcid":"https://orcid.org/0000-0002-8769-269X","observed_orcids":["https://orcid.org/0000-0002-8769-269X"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Paivi Miettunen","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5080140512","display_name":"Nicolino Ruperto","orcid":"https://orcid.org/0000-0001-8407-7782","observed_orcids":["https://orcid.org/0000-0001-8407-7782"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Nicolino Ruperto","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0001-8407-7782","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5027612338","display_name":"Alberto Martini","orcid":"https://orcid.org/0000-0001-7642-1459","observed_orcids":["https://orcid.org/0000-0001-7642-1459"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Alberto Martini","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0001-7642-1459","affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5034036024","display_name":"Randy Quentin Cron","orcid":"https://orcid.org/0000-0003-2661-3086","observed_orcids":["https://orcid.org/0000-0003-2661-3086"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Randy Q. Cron","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0003-2661-3086","affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5029874460","display_name":"Angelo Ravelli","orcid":"https://orcid.org/0000-0001-9658-0385","observed_orcids":["https://orcid.org/0000-0001-9658-0385"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Angelo Ravelli","raw_affiliation_strings":[],"raw_orcid":"https://orcid.org/0000-0001-9658-0385","affiliations":[]}],"institutions":[],"countries_distinct_count":0,"institutions_distinct_count":0,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":{"value":0.35231581,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":null,"issue":null,"first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11892","display_name":"Kawasaki Disease and Coronary Complications","score":9.999999747378752e-05,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11153","display_name":"Streptococcal Infections and Treatments","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2739","display_name":"Public Health, Environmental and Occupational Health"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/macrophage-activation-syndrome","display_name":"macrophage activation syndrome","score":0.9829999804496765},{"id":"https://openalex.org/keywords/hemophagocytic-lymphohistiocytosis","display_name":"hemophagocytic lymphohistiocytosis","score":0.9380000233650208},{"id":"https://openalex.org/keywords/systemic-juvenile-idiopathic-arthritis","display_name":"systemic juvenile idiopathic arthritis","score":0.8930000066757202},{"id":"https://openalex.org/keywords/diagnostic-criteria","display_name":"diagnostic criteria","score":0.7910000085830688},{"id":"https://openalex.org/keywords/sensitivity-and-specificity","display_name":"sensitivity and specificity","score":0.8840000033378601},{"id":"https://openalex.org/keywords/pediatric-rheumatology","display_name":"pediatric rheumatology","score":0.628000020980835}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.5737770795822144},{"id":"https://openalex.org/C21200559","wikidata":"https://www.wikidata.org/wiki/Q7451068","display_name":"Sensitivity (control systems)","level":2,"score":0.4821145534515381},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.36181628704071045},{"id":"https://openalex.org/C127413603","wikidata":"https://www.wikidata.org/wiki/Q11023","display_name":"Engineering","level":0,"score":0.0},{"id":"https://openalex.org/C24326235","wikidata":"https://www.wikidata.org/wiki/Q126095","display_name":"Electronic engineering","level":1,"score":0.0}],"mesh":[],"locations_count":1,"locations":[{"id":"mag:2786355704","doi":null,"is_oa":false,"landing_page_url":"https://www.bib.irb.hr/673223","pdf_url":null,"source":null,"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":null,"raw_type":null}],"best_oa_location":null,"sustainable_development_goals":[{"score":0.9907000064849854,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"sustainable_development_goals_aurora":[],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W2739767001"],"abstract_inverted_index":null,"counts_by_year":[],"updated_date":"2026-09-22T06:50:58.402377","created_date":"2025-10-10T00:00:00"}
