{"id":"https://openalex.org/W2614745940","doi":"https://doi.org/10.3201/eid2306.161884","title":"Sporadic Creutzfeldt-Jakob Disease in 2 Plasma Product Recipients, United Kingdom","display_name":"Sporadic Creutzfeldt-Jakob Disease in 2 Plasma Product Recipients, United Kingdom","publication_year":2017,"publication_date":"2017-06-01","ids":{"openalex":"https://openalex.org/W2614745940","doi":"https://doi.org/10.3201/eid2306.161884","mag":"2614745940","pmid":"https://pubmed.ncbi.nlm.nih.gov/28516863","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/5443442"},"language":"en","primary_location":{"id":"doi:10.3201/eid2306.161884","doi":"https://doi.org/10.3201/eid2306.161884","is_oa":true,"landing_page_url":"https://doi.org/10.3201/eid2306.161884","pdf_url":"https://wwwnc.cdc.gov/eid/article/23/6/pdfs/16-1884.pdf","source":{"id":"https://openalex.org/S189281586","display_name":"Emerging infectious diseases","issn_l":"1080-6040","issn":["1080-6040","1080-6059"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","oarl","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315581","host_organization_name":"Centers for Disease Control and Prevention","host_organization_lineage":["https://openalex.org/P4310315581"],"host_organization_lineage_names":["Centers for Disease Control and Prevention"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Emerging Infectious Diseases","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj","pubmed"],"open_access":{"is_oa":true,"oa_status":"diamond","oa_url":"https://wwwnc.cdc.gov/eid/article/23/6/pdfs/16-1884.pdf","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5017619339","display_name":"Patrick JM Urwin","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I125671874","display_name":"National Health Service","ror":"https://ror.org/02wnqcb97","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I125671874","https://openalex.org/I1311074006"]},{"id":"https://openalex.org/I2800150677","display_name":"Western General Hospital","ror":"https://ror.org/009kr6r15","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1324252669","https://openalex.org/I2800150677"]},{"id":"https://openalex.org/I4210157707","display_name":"University Hospital Lewisham","ror":"https://ror.org/04vgz8j88","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I4210157707","https://openalex.org/I4210164769"]},{"id":"https://openalex.org/I98677209","display_name":"University of Edinburgh","ror":"https://ror.org/01nrxwf90","country_code":"GB","type":"education","lineage":["https://openalex.org/I98677209"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Patrick Urwin","raw_affiliation_strings":["University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","National Health Service Blood and Transplant, London (P.E. Hewitt);","University Hospital Lewisham, London, UK (K. Thanigaikumar);"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","institution_ids":["https://openalex.org/I2800150677","https://openalex.org/I98677209"]},{"raw_affiliation_string":"National Health Service Blood and Transplant, London (P.E. Hewitt);","institution_ids":["https://openalex.org/I125671874"]},{"raw_affiliation_string":"University Hospital Lewisham, London, UK (K. Thanigaikumar);","institution_ids":["https://openalex.org/I4210157707"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5075236216","display_name":"Kumar Thanigaikumar","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2800150677","display_name":"Western General Hospital","ror":"https://ror.org/009kr6r15","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1324252669","https://openalex.org/I2800150677"]},{"id":"https://openalex.org/I4210157707","display_name":"University Hospital Lewisham","ror":"https://ror.org/04vgz8j88","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I4210157707","https://openalex.org/I4210164769"]},{"id":"https://openalex.org/I98677209","display_name":"University of Edinburgh","ror":"https://ror.org/01nrxwf90","country_code":"GB","type":"education","lineage":["https://openalex.org/I98677209"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Kumar Thanigaikumar","raw_affiliation_strings":["University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","University Hospital Lewisham, London, UK (K. Thanigaikumar);"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","institution_ids":["https://openalex.org/I2800150677","https://openalex.org/I98677209"]},{"raw_affiliation_string":"University Hospital Lewisham, London, UK (K. Thanigaikumar);","institution_ids":["https://openalex.org/I4210157707"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5002436634","display_name":"James W. Ironside","orcid":"https://orcid.org/0000-0001-5869-2108","observed_orcids":["https://orcid.org/0000-0001-5869-2108"]},"institutions":[{"id":"https://openalex.org/I125671874","display_name":"National Health Service","ror":"https://ror.org/02wnqcb97","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I125671874","https://openalex.org/I1311074006"]},{"id":"https://openalex.org/I2800150677","display_name":"Western General Hospital","ror":"https://ror.org/009kr6r15","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1324252669","https://openalex.org/I2800150677"]},{"id":"https://openalex.org/I348769827","display_name":"Public Health England","ror":"https://ror.org/00vbvha87","country_code":"GB","type":"government","lineage":["https://openalex.org/I1311074006","https://openalex.org/I348769827"]},{"id":"https://openalex.org/I4210157707","display_name":"University Hospital Lewisham","ror":"https://ror.org/04vgz8j88","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I4210157707","https://openalex.org/I4210164769"]},{"id":"https://openalex.org/I98677209","display_name":"University of Edinburgh","ror":"https://ror.org/01nrxwf90","country_code":"GB","type":"education","lineage":["https://openalex.org/I98677209"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"James W. Ironside","raw_affiliation_strings":["University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","National Health Service Blood and Transplant/Public Health England Epidemiology Unit, Cambridge, UK (C. Llewelyn","University Hospital Lewisham, London, UK (K. Thanigaikumar);"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","institution_ids":["https://openalex.org/I2800150677","https://openalex.org/I98677209"]},{"raw_affiliation_string":"National Health Service Blood and Transplant/Public Health England Epidemiology Unit, Cambridge, UK (C. Llewelyn","institution_ids":["https://openalex.org/I125671874","https://openalex.org/I348769827"]},{"raw_affiliation_string":"University Hospital Lewisham, London, UK (K. Thanigaikumar);","institution_ids":["https://openalex.org/I4210157707"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5111963732","display_name":"Anna M. Molesworth","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I125671874","display_name":"National Health Service","ror":"https://ror.org/02wnqcb97","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I125671874","https://openalex.org/I1311074006"]},{"id":"https://openalex.org/I2800150677","display_name":"Western General Hospital","ror":"https://ror.org/009kr6r15","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1324252669","https://openalex.org/I2800150677"]},{"id":"https://openalex.org/I348769827","display_name":"Public Health England","ror":"https://ror.org/00vbvha87","country_code":"GB","type":"government","lineage":["https://openalex.org/I1311074006","https://openalex.org/I348769827"]},{"id":"https://openalex.org/I4210157707","display_name":"University Hospital Lewisham","ror":"https://ror.org/04vgz8j88","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I4210157707","https://openalex.org/I4210164769"]},{"id":"https://openalex.org/I98677209","display_name":"University of Edinburgh","ror":"https://ror.org/01nrxwf90","country_code":"GB","type":"education","lineage":["https://openalex.org/I98677209"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Anna Molesworth","raw_affiliation_strings":["University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","National Health Service Blood and Transplant/Public Health England Epidemiology Unit, Cambridge, UK (C. Llewelyn","University Hospital Lewisham, London, UK (K. Thanigaikumar);"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","institution_ids":["https://openalex.org/I2800150677","https://openalex.org/I98677209"]},{"raw_affiliation_string":"National Health Service Blood and Transplant/Public Health England Epidemiology Unit, Cambridge, UK (C. Llewelyn","institution_ids":["https://openalex.org/I125671874","https://openalex.org/I348769827"]},{"raw_affiliation_string":"University Hospital Lewisham, London, UK (K. Thanigaikumar);","institution_ids":["https://openalex.org/I4210157707"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5047229762","display_name":"Richard Knight","orcid":"https://orcid.org/0000-0002-7429-4190","observed_orcids":["https://orcid.org/0000-0002-7429-4190"]},"institutions":[{"id":"https://openalex.org/I125671874","display_name":"National Health Service","ror":"https://ror.org/02wnqcb97","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I125671874","https://openalex.org/I1311074006"]},{"id":"https://openalex.org/I2800150677","display_name":"Western General Hospital","ror":"https://ror.org/009kr6r15","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1324252669","https://openalex.org/I2800150677"]},{"id":"https://openalex.org/I348769827","display_name":"Public Health England","ror":"https://ror.org/00vbvha87","country_code":"GB","type":"government","lineage":["https://openalex.org/I1311074006","https://openalex.org/I348769827"]},{"id":"https://openalex.org/I4210157707","display_name":"University Hospital Lewisham","ror":"https://ror.org/04vgz8j88","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I4210157707","https://openalex.org/I4210164769"]},{"id":"https://openalex.org/I98677209","display_name":"University of Edinburgh","ror":"https://ror.org/01nrxwf90","country_code":"GB","type":"education","lineage":["https://openalex.org/I98677209"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Richard S. Knight","raw_affiliation_strings":["University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","National Health Service Blood and Transplant/Public Health England Epidemiology Unit, Cambridge, UK (C. Llewelyn","University Hospital Lewisham, London, UK (K. Thanigaikumar);"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","institution_ids":["https://openalex.org/I2800150677","https://openalex.org/I98677209"]},{"raw_affiliation_string":"National Health Service Blood and Transplant/Public Health England Epidemiology Unit, Cambridge, UK (C. Llewelyn","institution_ids":["https://openalex.org/I125671874","https://openalex.org/I348769827"]},{"raw_affiliation_string":"University Hospital Lewisham, London, UK (K. Thanigaikumar);","institution_ids":["https://openalex.org/I4210157707"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5089663819","display_name":"Patricia E. Hewitt","orcid":"https://orcid.org/0000-0002-4181-3206","observed_orcids":["https://orcid.org/0000-0002-4181-3206"]},"institutions":[{"id":"https://openalex.org/I2800150677","display_name":"Western General Hospital","ror":"https://ror.org/009kr6r15","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1324252669","https://openalex.org/I2800150677"]},{"id":"https://openalex.org/I4210157707","display_name":"University Hospital Lewisham","ror":"https://ror.org/04vgz8j88","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I4210157707","https://openalex.org/I4210164769"]},{"id":"https://openalex.org/I98677209","display_name":"University of Edinburgh","ror":"https://ror.org/01nrxwf90","country_code":"GB","type":"education","lineage":["https://openalex.org/I98677209"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Patricia E. Hewitt","raw_affiliation_strings":["University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","University Hospital Lewisham, London, UK (K. Thanigaikumar);"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","institution_ids":["https://openalex.org/I2800150677","https://openalex.org/I98677209"]},{"raw_affiliation_string":"University Hospital Lewisham, London, UK (K. Thanigaikumar);","institution_ids":["https://openalex.org/I4210157707"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5113672004","display_name":"CHARLOTTE A. LLEWELYN","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2800150677","display_name":"Western General Hospital","ror":"https://ror.org/009kr6r15","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1324252669","https://openalex.org/I2800150677"]},{"id":"https://openalex.org/I4210157707","display_name":"University Hospital Lewisham","ror":"https://ror.org/04vgz8j88","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I4210157707","https://openalex.org/I4210164769"]},{"id":"https://openalex.org/I98677209","display_name":"University of Edinburgh","ror":"https://ror.org/01nrxwf90","country_code":"GB","type":"education","lineage":["https://openalex.org/I98677209"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Charlotte Llewelyn","raw_affiliation_strings":["University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","University Hospital Lewisham, London, UK (K. Thanigaikumar);"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","institution_ids":["https://openalex.org/I2800150677","https://openalex.org/I98677209"]},{"raw_affiliation_string":"University Hospital Lewisham, London, UK (K. Thanigaikumar);","institution_ids":["https://openalex.org/I4210157707"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5112784442","display_name":"Jan M. MacKenzie","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I125671874","display_name":"National Health Service","ror":"https://ror.org/02wnqcb97","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I125671874","https://openalex.org/I1311074006"]},{"id":"https://openalex.org/I2800150677","display_name":"Western General Hospital","ror":"https://ror.org/009kr6r15","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1324252669","https://openalex.org/I2800150677"]},{"id":"https://openalex.org/I348769827","display_name":"Public Health England","ror":"https://ror.org/00vbvha87","country_code":"GB","type":"government","lineage":["https://openalex.org/I1311074006","https://openalex.org/I348769827"]},{"id":"https://openalex.org/I4210157707","display_name":"University Hospital Lewisham","ror":"https://ror.org/04vgz8j88","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I4210157707","https://openalex.org/I4210164769"]},{"id":"https://openalex.org/I98677209","display_name":"University of Edinburgh","ror":"https://ror.org/01nrxwf90","country_code":"GB","type":"education","lineage":["https://openalex.org/I98677209"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Jan Mackenzie","raw_affiliation_strings":["University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","National Health Service Blood and Transplant/Public Health England Epidemiology Unit, Cambridge, UK (C. Llewelyn","University Hospital Lewisham, London, UK (K. Thanigaikumar);"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","institution_ids":["https://openalex.org/I2800150677","https://openalex.org/I98677209"]},{"raw_affiliation_string":"National Health Service Blood and Transplant/Public Health England Epidemiology Unit, Cambridge, UK (C. Llewelyn","institution_ids":["https://openalex.org/I125671874","https://openalex.org/I348769827"]},{"raw_affiliation_string":"University Hospital Lewisham, London, UK (K. Thanigaikumar);","institution_ids":["https://openalex.org/I4210157707"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5050265113","display_name":"Robert G Will","orcid":"https://orcid.org/0009-0003-0897-2832","observed_orcids":["https://orcid.org/0009-0003-0897-2832"]},"institutions":[{"id":"https://openalex.org/I125671874","display_name":"National Health Service","ror":"https://ror.org/02wnqcb97","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I125671874","https://openalex.org/I1311074006"]},{"id":"https://openalex.org/I2800150677","display_name":"Western General Hospital","ror":"https://ror.org/009kr6r15","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1324252669","https://openalex.org/I2800150677"]},{"id":"https://openalex.org/I348769827","display_name":"Public Health England","ror":"https://ror.org/00vbvha87","country_code":"GB","type":"government","lineage":["https://openalex.org/I1311074006","https://openalex.org/I348769827"]},{"id":"https://openalex.org/I98677209","display_name":"University of Edinburgh","ror":"https://ror.org/01nrxwf90","country_code":"GB","type":"education","lineage":["https://openalex.org/I98677209"]}],"countries":["GB"],"is_corresponding":true,"raw_author_name":"Robert G. Will","raw_affiliation_strings":["University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","National Health Service Blood and Transplant/Public Health England Epidemiology Unit, Cambridge, UK (C. Llewelyn"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Edinburgh Western General Hospital, Edinburgh, Scotland, UK","institution_ids":["https://openalex.org/I2800150677","https://openalex.org/I98677209"]},{"raw_affiliation_string":"National Health Service Blood and Transplant/Public Health England Epidemiology Unit, Cambridge, UK (C. Llewelyn","institution_ids":["https://openalex.org/I125671874","https://openalex.org/I348769827"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":5,"corresponding_author_ids":["https://openalex.org/A5050265113"],"corresponding_institution_ids":["https://openalex.org/I125671874","https://openalex.org/I2800150677","https://openalex.org/I348769827","https://openalex.org/I98677209"],"apc_list":null,"apc_paid":null,"fwci":0.8768,"has_fulltext":true,"cited_by_count":17,"citation_normalized_percentile":{"value":0.69689449,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":97},"biblio":{"volume":"23","issue":"6","first_page":null,"last_page":null},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11335","display_name":"Prion Diseases and Protein Misfolding","score":1.0,"subfield":{"id":"https://openalex.org/subfields/1312","display_name":"Molecular Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T11335","display_name":"Prion Diseases and Protein Misfolding","score":1.0,"subfield":{"id":"https://openalex.org/subfields/1312","display_name":"Molecular Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T11305","display_name":"Amyloidosis: Diagnosis, Treatment, Outcomes","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2724","display_name":"Internal Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10993","display_name":"Complement system in diseases","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/sporadic-creutzfeldt-jakob-disease","display_name":"sporadic Creutzfeldt-Jakob disease","score":1.0},{"id":"https://openalex.org/keywords/hemophilia-b","display_name":"hemophilia B","score":0.7649999856948853},{"id":"https://openalex.org/keywords/von-willebrand-disease","display_name":"von Willebrand disease","score":1.0},{"id":"https://openalex.org/keywords/clotting-disorders","display_name":"clotting disorders","score":0.9330000281333923},{"id":"https://openalex.org/keywords/variant-creutzfeldt-jakob-disease","display_name":"variant Creutzfeldt-Jakob disease","score":0.9340000152587891},{"id":"https://openalex.org/keywords/neuropathology","display_name":"neuropathology","score":0.7329999804496765},{"id":"https://openalex.org/keywords/prion-disease-surveillance","display_name":"prion disease surveillance","score":0.5139999985694885}],"concepts":[{"id":"https://openalex.org/C2779343474","wikidata":"https://www.wikidata.org/wiki/Q3109175","display_name":"Context (archaeology)","level":2,"score":0.6983272433280945},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.6313865780830383},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.602776050567627},{"id":"https://openalex.org/C2910731194","wikidata":"https://www.wikidata.org/wiki/Q49989","display_name":"Creutzfeldt-Jakob Syndrome","level":4,"score":0.51424640417099},{"id":"https://openalex.org/C2778780528","wikidata":"https://www.wikidata.org/wiki/Q709360","display_name":"Von Willebrand disease","level":4,"score":0.4322417378425598},{"id":"https://openalex.org/C2992139802","wikidata":"https://www.wikidata.org/wiki/Q179217","display_name":"Clotting factor","level":2,"score":0.42046990990638733},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.3738461434841156},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.36256182193756104},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.3078373670578003},{"id":"https://openalex.org/C2779394231","wikidata":"https://www.wikidata.org/wiki/Q412310","display_name":"Von Willebrand factor","level":3,"score":0.2973511815071106},{"id":"https://openalex.org/C89560881","wikidata":"https://www.wikidata.org/wiki/Q101026","display_name":"Platelet","level":2,"score":0.12296414375305176},{"id":"https://openalex.org/C86803240","wikidata":"https://www.wikidata.org/wiki/Q420","display_name":"Biology","level":0,"score":0.0974409282207489},{"id":"https://openalex.org/C151730666","wikidata":"https://www.wikidata.org/wiki/Q7205","display_name":"Paleontology","level":1,"score":0.0},{"id":"https://openalex.org/C3019804061","wikidata":"https://www.wikidata.org/wiki/Q14881255","display_name":"Prion protein","level":3,"score":0.0}],"mesh":[{"descriptor_ui":"D001921","descriptor_name":"Brain","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006113","descriptor_name":"United Kingdom","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007562","descriptor_name":"Creutzfeldt-Jakob Syndrome","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":true},{"descriptor_ui":"D007562","descriptor_name":"Creutzfeldt-Jakob Syndrome","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":true},{"descriptor_ui":"D007562","descriptor_name":"Creutzfeldt-Jakob Syndrome","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":6,"locations":[{"id":"doi:10.3201/eid2306.161884","doi":"https://doi.org/10.3201/eid2306.161884","is_oa":true,"landing_page_url":"https://doi.org/10.3201/eid2306.161884","pdf_url":"https://wwwnc.cdc.gov/eid/article/23/6/pdfs/16-1884.pdf","source":{"id":"https://openalex.org/S189281586","display_name":"Emerging infectious diseases","issn_l":"1080-6040","issn":["1080-6040","1080-6059"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","oarl","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315581","host_organization_name":"Centers for Disease Control and Prevention","host_organization_lineage":["https://openalex.org/P4310315581"],"host_organization_lineage_names":["Centers for Disease Control and Prevention"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Emerging Infectious Diseases","raw_type":"journal-article"},{"id":"pmh:oai:europepmc.org:4305634","doi":null,"is_oa":true,"landing_page_url":"http://europepmc.org/articles/PMC5443442","pdf_url":null,"source":{"id":"https://openalex.org/S4306400806","display_name":"Europe PMC (PubMed Central)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1303153112","host_organization_name":"European Bioinformatics Institute","host_organization_lineage":["https://openalex.org/I1303153112"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"","raw_type":"Text"},{"id":"pmh:oai:pubmedcentral.nih.gov:5443442","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/5443442","pdf_url":null,"source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Emerg Infect Dis","raw_type":"Text"},{"id":"pmid:28516863","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/28516863","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Emerging infectious diseases","raw_type":"Case Reports"},{"id":"pmh:oai:pure.ed.ac.uk:openaire/64f2958e-5867-46d4-bfdd-b4fcc9c97cdd","doi":null,"is_oa":true,"landing_page_url":"https://www.research.ed.ac.uk/files/36268761/16_1884.pdf","pdf_url":"https://www.research.ed.ac.uk/files/36268761/16_1884.pdf","source":{"id":"https://openalex.org/S4306400321","display_name":"Edinburgh Research Explorer (University of Edinburgh)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I98677209","host_organization_name":"University of Edinburgh","host_organization_lineage":["https://openalex.org/I98677209"],"host_organization_lineage_names":[],"type":"repository"},"license":"other-oa","license_id":"https://openalex.org/licenses/other-oa","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Urwin, P, Thanigaikumar, K, Ironside, J, Molesworth, A, Knight, R, Hewitt, P E, Llewelyn, C, Mackenzie, J & Will, R 2017, 'Sporadic Creutzfeldt-Jakob Disease in 2 Plasma Product Recipients, United Kingdom', Emerging Infectious Diseases. https://doi.org/10.3201/eid2306.161884","raw_type":"info:eu-repo/semantics/article"},{"id":"pmh:oai:doaj.org/article:0e97587ad6964c22a5fefacf26295e39","doi":null,"is_oa":true,"landing_page_url":"https://doaj.org/article/0e97587ad6964c22a5fefacf26295e39","pdf_url":null,"source":{"id":"https://openalex.org/S4306401280","display_name":"DOAJ (DOAJ: Directory of Open Access Journals)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by-sa","license_id":"https://openalex.org/licenses/cc-by-sa","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Emerging Infectious Diseases, Vol 23, Iss 6, Pp 893-897 (2017)","raw_type":"article"}],"best_oa_location":{"id":"doi:10.3201/eid2306.161884","doi":"https://doi.org/10.3201/eid2306.161884","is_oa":true,"landing_page_url":"https://doi.org/10.3201/eid2306.161884","pdf_url":"https://wwwnc.cdc.gov/eid/article/23/6/pdfs/16-1884.pdf","source":{"id":"https://openalex.org/S189281586","display_name":"Emerging infectious diseases","issn_l":"1080-6040","issn":["1080-6040","1080-6059"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","oarl","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315581","host_organization_name":"Centers for Disease Control and Prevention","host_organization_lineage":["https://openalex.org/P4310315581"],"host_organization_lineage_names":["Centers for Disease Control and Prevention"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Emerging Infectious Diseases","raw_type":"journal-article"},"sustainable_development_goals":[{"display_name":"Good health and well-being","score":1.0,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W2614745940.pdf","grobid_xml":"https://content.openalex.org/works/W2614745940.grobid-xml"},"referenced_works_count":14,"referenced_works":["https://openalex.org/W1493654567","https://openalex.org/W1503999029","https://openalex.org/W1979678617","https://openalex.org/W1995678929","https://openalex.org/W2038142248","https://openalex.org/W2040984993","https://openalex.org/W2058148369","https://openalex.org/W2072244190","https://openalex.org/W2120331054","https://openalex.org/W2126000688","https://openalex.org/W2134727684","https://openalex.org/W2168669094","https://openalex.org/W2252255302","https://openalex.org/W4252808594"],"related_works":["https://openalex.org/W2107836315","https://openalex.org/W1836242379","https://openalex.org/W2145587739","https://openalex.org/W2087081185","https://openalex.org/W2084643380","https://openalex.org/W2134727684","https://openalex.org/W2053487236","https://openalex.org/W3118992939","https://openalex.org/W2101433794","https://openalex.org/W2917417518"],"abstract_inverted_index":{"Sporadic":[0],"Creutzfeldt-Jakob":[1],"disease":[2],"(sCJD)":[3],"has":[4,120],"not":[5,121],"been":[6,55,122],"previously":[7,57],"reported":[8],"in":[9,26,30,76,95,136,144],"patients":[10,31,53],"with":[11,15,32,71,112],"clotting":[12,39],"disorders":[13],"treated":[14],"fractionated":[16,72],"plasma":[17,73,113],"products.":[18],"We":[19],"report":[20],"2":[21],"cases":[22,82,97,129],"of":[23,35,68,89,103,118,127,139],"sCJD":[24,119],"identified":[25],"the":[27,47,77,104,110,116,125,137],"United":[28,78],"Kingdom":[29],"a":[33,133],"history":[34],"extended":[36],"treatment":[37,70,111],"for":[38,64,142],"disorders;":[40],"1":[41],"patient":[42],"had":[43,54,83],"hemophilia":[44],"B":[45],"and":[46,85,100,115,124],"other":[48],"von":[49],"Willebrand":[50],"disease.":[51],"Both":[52],"informed":[56],"that":[58],"they":[59],"were":[60],"at":[61],"increased":[62],"risk":[63],"variant":[65],"CJD":[66,143],"because":[67],"past":[69],"products":[74,114],"sourced":[75],"Kingdom.":[79],"However,":[80],"both":[81,96],"clinical":[84],"investigative":[86],"features":[87],"suggestive":[88],"sCJD.":[90],"This":[91],"diagnosis":[92],"was":[93],"confirmed":[94],"on":[98],"neuropathologic":[99],"biochemical":[101],"analysis":[102],"brain.":[105],"A":[106],"causal":[107],"link":[108],"between":[109],"development":[117],"established,":[123],"occurrence":[126],"these":[128],"may":[130],"simply":[131],"reflect":[132],"chance":[134],"event":[135],"context":[138],"systematic":[140],"surveillance":[141],"large":[145],"populations.":[146]},"counts_by_year":[{"year":2026,"cited_by_count":1},{"year":2025,"cited_by_count":1},{"year":2024,"cited_by_count":2},{"year":2023,"cited_by_count":1},{"year":2022,"cited_by_count":1},{"year":2021,"cited_by_count":2},{"year":2020,"cited_by_count":3},{"year":2019,"cited_by_count":1},{"year":2018,"cited_by_count":4},{"year":2017,"cited_by_count":1}],"updated_date":"2026-11-07T11:25:07.637180","created_date":"2017-05-26T00:00:00"}
