{"id":"https://openalex.org/W2612377989","doi":"https://doi.org/10.1002/ccr3.941","title":"Hemoglobin Titusville: a rare low oxygen affinity hemoglobinopathy","display_name":"Hemoglobin Titusville: a rare low oxygen affinity hemoglobinopathy","publication_year":2017,"publication_date":"2017-05-11","ids":{"openalex":"https://openalex.org/W2612377989","doi":"https://doi.org/10.1002/ccr3.941","mag":"2612377989","pmid":"https://pubmed.ncbi.nlm.nih.gov/28588857","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/5457981"},"language":"en","primary_location":{"id":"doi:10.1002/ccr3.941","doi":"https://doi.org/10.1002/ccr3.941","is_oa":true,"landing_page_url":"https://doi.org/10.1002/ccr3.941","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ccr3.941","source":{"id":"https://openalex.org/S2737168579","display_name":"Clinical Case Reports","issn_l":"2050-0904","issn":["2050-0904"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","norway-1","poland-20","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clinical Case Reports","raw_type":"journal-article"},"parent_works":[],"lineage":["https://openalex.org/W2612377989"],"child_works_count":0,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj","pubmed"],"open_access":{"is_oa":true,"oa_status":"gold","oa_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ccr3.941","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5072670262","display_name":"Senan John Yasar","orcid":"https://orcid.org/0000-0002-1167-3900","observed_orcids":["https://orcid.org/0000-0002-1167-3900"]},"institutions":[{"id":"https://openalex.org/I76835614","display_name":"University of Missouri","ror":"https://ror.org/02ymw8z06","country_code":"US","type":"education","lineage":["https://openalex.org/I76835614"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"Senan John Yasar","raw_affiliation_strings":["University of Missouri, One Hospital Drive 29, Columbia, 65212 Missouri, USA"],"raw_orcid":"https://orcid.org/0000-0002-1167-3900","affiliations":[{"raw_affiliation_string":"University of Missouri, One Hospital Drive 29, Columbia, 65212 Missouri, USA","institution_ids":["https://openalex.org/I76835614"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5010608997","display_name":"Vivian Irene Ravn Berg","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I120230055","display_name":"Poznan University of Medical Sciences","ror":"https://ror.org/02zbb2597","country_code":"PL","type":"education","lineage":["https://openalex.org/I120230055"]}],"countries":["PL"],"is_corresponding":false,"raw_author_name":"Vivian Irene Ravn Berg","raw_affiliation_strings":["Poznan University of Medical Sciences, 41 Jackowskiego St, Poznan, 60-512 Poland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Poznan University of Medical Sciences, 41 Jackowskiego St, Poznan, 60-512 Poland","institution_ids":["https://openalex.org/I120230055"]}]},{"author_position":"middle","author":{"id":null,"display_name":"Asim Ahmad","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I76835614","display_name":"University of Missouri","ror":"https://ror.org/02ymw8z06","country_code":"US","type":"education","lineage":["https://openalex.org/I76835614"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Asim Ahmad","raw_affiliation_strings":["University of Missouri, One Hospital Drive 29, Columbia, 65212 Missouri, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Missouri, One Hospital Drive 29, Columbia, 65212 Missouri, USA","institution_ids":["https://openalex.org/I76835614"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5111671808","display_name":"Donald C. Doll","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I76835614","display_name":"University of Missouri","ror":"https://ror.org/02ymw8z06","country_code":"US","type":"education","lineage":["https://openalex.org/I76835614"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Donald Doll","raw_affiliation_strings":["University of Missouri, One Hospital Drive 29, Columbia, 65212 Missouri, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"University of Missouri, One Hospital Drive 29, Columbia, 65212 Missouri, USA","institution_ids":["https://openalex.org/I76835614"]}]}],"institutions":[],"countries_distinct_count":2,"institutions_distinct_count":2,"corresponding_author_ids":["https://openalex.org/A5072670262"],"corresponding_institution_ids":["https://openalex.org/I76835614"],"apc_list":{"value":1820,"currency":"USD","value_usd":1820},"apc_paid":{"value":1820,"currency":"USD","value_usd":1820},"fwci":1.1601,"has_fulltext":true,"cited_by_count":7,"citation_normalized_percentile":{"value":0.76798825,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":87,"max":97},"biblio":{"volume":"5","issue":"6","first_page":"1011","last_page":"1012"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10554","display_name":"Hemoglobinopathies and Related Disorders","score":0.9375,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10554","display_name":"Hemoglobinopathies and Related Disorders","score":0.9375,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12094","display_name":"Hemoglobin structure and function","score":0.05480000004172325,"subfield":{"id":"https://openalex.org/subfields/1303","display_name":"Biochemistry"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T12845","display_name":"Methemoglobinemia and Tumor Lysis Syndrome","score":0.00039999998989515007,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/hemoglobinopathies","display_name":"hemoglobinopathies","score":0.7910000085830688},{"id":"https://openalex.org/keywords/diagnostic-workup","display_name":"diagnostic workup","score":0.6019999980926514},{"id":"https://openalex.org/keywords/laboratory-evaluation","display_name":"laboratory evaluation","score":0.5419999957084656},{"id":"https://openalex.org/keywords/hemoglobin-variants","display_name":"hemoglobin variants","score":0.42899999022483826}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8284461498260498},{"id":"https://openalex.org/C2779668550","wikidata":"https://www.wikidata.org/wiki/Q1642147","display_name":"Hemoglobinopathy","level":3,"score":0.705990731716156},{"id":"https://openalex.org/C2778917026","wikidata":"https://www.wikidata.org/wiki/Q43041","display_name":"Hemoglobin","level":2,"score":0.5324811339378357},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.2683659791946411},{"id":"https://openalex.org/C2776175824","wikidata":"https://www.wikidata.org/wiki/Q1145668","display_name":"Hemolytic anemia","level":2,"score":0.17124027013778687}],"mesh":[],"locations_count":5,"locations":[{"id":"doi:10.1002/ccr3.941","doi":"https://doi.org/10.1002/ccr3.941","is_oa":true,"landing_page_url":"https://doi.org/10.1002/ccr3.941","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ccr3.941","source":{"id":"https://openalex.org/S2737168579","display_name":"Clinical Case Reports","issn_l":"2050-0904","issn":["2050-0904"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","norway-1","poland-20","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clinical Case Reports","raw_type":"journal-article"},{"id":"pmh:oai:europepmc.org:4310795","doi":null,"is_oa":true,"landing_page_url":"http://europepmc.org/articles/PMC5457981","pdf_url":null,"source":{"id":"https://openalex.org/S4306400806","display_name":"Europe PMC (PubMed Central)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1303153112","host_organization_name":"European Bioinformatics Institute","host_organization_lineage":["https://openalex.org/I1303153112"],"host_organization_lineage_names":[],"type":"repository"},"license":"other-oa","license_id":"https://openalex.org/licenses/other-oa","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"","raw_type":"Text"},{"id":"pmid:28588857","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/28588857","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clinical case reports","raw_type":"Case Reports"},{"id":"pmh:oai:pubmedcentral.nih.gov:5457981","doi":null,"is_oa":true,"landing_page_url":"https://pmc.ncbi.nlm.nih.gov/articles/PMC5457981/","pdf_url":null,"source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clin Case Rep","raw_type":"Text"},{"id":"pmh:oai:doaj.org/article:28c36646c3a2435e8ba0f904f7ac828a","doi":null,"is_oa":false,"landing_page_url":"https://doaj.org/article/28c36646c3a2435e8ba0f904f7ac828a","pdf_url":null,"source":{"id":"https://openalex.org/S4306401280","display_name":"DOAJ (DOAJ: Directory of Open Access Journals)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Clinical Case Reports, Vol 5, Iss 6, Pp 1011-1012 (2017)","raw_type":"article"}],"best_oa_location":{"id":"doi:10.1002/ccr3.941","doi":"https://doi.org/10.1002/ccr3.941","is_oa":true,"landing_page_url":"https://doi.org/10.1002/ccr3.941","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ccr3.941","source":{"id":"https://openalex.org/S2737168579","display_name":"Clinical Case Reports","issn_l":"2050-0904","issn":["2050-0904"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","norway-1","poland-20","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clinical Case Reports","raw_type":"journal-article"},"sustainable_development_goals":[{"score":0.9391000270843506,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W2612377989.pdf","grobid_xml":"https://content.openalex.org/works/W2612377989.grobid-xml"},"referenced_works_count":5,"referenced_works":["https://openalex.org/W51941104","https://openalex.org/W1984560477","https://openalex.org/W2022156607","https://openalex.org/W2110922812","https://openalex.org/W4322700914"],"related_works":["https://openalex.org/W4417073970","https://openalex.org/W2022156607","https://openalex.org/W4392708494","https://openalex.org/W2030698353","https://openalex.org/W4394768161","https://openalex.org/W1508188147","https://openalex.org/W7005453690","https://openalex.org/W4287221825","https://openalex.org/W2912816678","https://openalex.org/W4411389066"],"abstract_inverted_index":{"The":[0],"relevance":[1],"of":[2,19],"this":[3],"case":[4],"lies":[5],"in":[6],"the":[7],"extensive":[8],"diagnostic":[9],"workup":[10],"that":[11],"can":[12],"be":[13],"avoided":[14],"with":[15],"proper":[16],"laboratory":[17],"evaluation":[18],"relatively":[20],"unsophisticated":[21],"tests.":[22]},"counts_by_year":[{"year":2025,"cited_by_count":1},{"year":2023,"cited_by_count":1},{"year":2019,"cited_by_count":2},{"year":2018,"cited_by_count":3}],"updated_date":"2026-11-10T11:39:43.021295","created_date":"2017-05-19T00:00:00"}
