{"id":"https://openalex.org/W2591840668","doi":"https://doi.org/10.1002/ajh.24718","title":"Beyond the transition of adolescents and young adults with sickle cell disease to adult care: Role of geography","display_name":"Beyond the transition of adolescents and young adults with sickle cell disease to adult care: Role of geography","publication_year":2017,"publication_date":"2017-03-10","ids":{"openalex":"https://openalex.org/W2591840668","doi":"https://doi.org/10.1002/ajh.24718","mag":"2591840668","pmid":"https://pubmed.ncbi.nlm.nih.gov/28295532"},"language":"en","primary_location":{"id":"doi:10.1002/ajh.24718","doi":"https://doi.org/10.1002/ajh.24718","is_oa":true,"landing_page_url":"https://doi.org/10.1002/ajh.24718","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ajh.24718","source":{"id":"https://openalex.org/S199810014","display_name":"American Journal of Hematology","issn_l":"0361-8609","issn":["0361-8609","1096-8652"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-1","poland-140","russia-white-list-1"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Hematology","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"bronze","oa_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ajh.24718","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":null,"display_name":"Nina Anderson","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210160682","display_name":"St. Christopher's Hospital for Children","ror":"https://ror.org/05t3ett24","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I4210160682"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Nina Anderson","raw_affiliation_strings":["St. Christopher Hospital, Philadelphia, Pennsylvania, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"St. Christopher Hospital, Philadelphia, Pennsylvania, USA","institution_ids":["https://openalex.org/I4210160682"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5037909608","display_name":"James R. Eckman","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I150468666","display_name":"Emory University","ror":"https://ror.org/03czfpz43","country_code":"US","type":"education","lineage":["https://openalex.org/I150468666"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"James R. Eckman","raw_affiliation_strings":["Emory University School of Medicine, Atlanta, Georgia, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Emory University School of Medicine, Atlanta, Georgia, USA","institution_ids":["https://openalex.org/I150468666"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5090681994","display_name":"Samir K. Ballas","orcid":"https://orcid.org/0000-0002-7566-1466","observed_orcids":["https://orcid.org/0000-0002-7566-1466"]},"institutions":[{"id":"https://openalex.org/I149251103","display_name":"Thomas Jefferson University","ror":"https://ror.org/00ysqcn41","country_code":"US","type":"education","lineage":["https://openalex.org/I149251103"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"Samir K. Ballas","raw_affiliation_strings":["Cardeza Foundation for Hematologic Research, Department of Medicine, Sidney Kimmel Medical College, Thomas Jefferson University, Philadelphia, Pennsylvania, USA"],"raw_orcid":"https://orcid.org/0000-0002-7566-1466","affiliations":[{"raw_affiliation_string":"Cardeza Foundation for Hematologic Research, Department of Medicine, Sidney Kimmel Medical College, Thomas Jefferson University, Philadelphia, Pennsylvania, USA","institution_ids":["https://openalex.org/I149251103"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":3,"corresponding_author_ids":["https://openalex.org/A5090681994"],"corresponding_institution_ids":["https://openalex.org/I149251103"],"apc_list":{"value":5450,"currency":"USD","value_usd":5450},"apc_paid":null,"fwci":0.5083,"has_fulltext":true,"cited_by_count":4,"citation_normalized_percentile":{"value":0.7034615,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":96},"biblio":{"volume":"92","issue":"6","first_page":"E110","last_page":"E112"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12823","display_name":"Adolescent and Pediatric Healthcare","score":0.9672999978065491,"subfield":{"id":"https://openalex.org/subfields/3616","display_name":"Speech and Hearing"},"field":{"id":"https://openalex.org/fields/36","display_name":"Health Professions"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12823","display_name":"Adolescent and Pediatric Healthcare","score":0.9672999978065491,"subfield":{"id":"https://openalex.org/subfields/3616","display_name":"Speech and Hearing"},"field":{"id":"https://openalex.org/fields/36","display_name":"Health Professions"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10554","display_name":"Hemoglobinopathies and Related Disorders","score":0.030400000512599945,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12174","display_name":"Hospital Admissions and Outcomes","score":0.00019999999494757503,"subfield":{"id":"https://openalex.org/subfields/2711","display_name":"Emergency Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/sickle-cell-disease","display_name":"sickle cell disease","score":1.0},{"id":"https://openalex.org/keywords/transition-to-adult-care","display_name":"transition to adult care","score":0.8669999837875366},{"id":"https://openalex.org/keywords/adolescents-and-young-adults","display_name":"adolescents and young adults","score":0.9620000123977661},{"id":"https://openalex.org/keywords/regional-variation","display_name":"regional variation","score":0.6209999918937683},{"id":"https://openalex.org/keywords/hydroxyurea-therapy","display_name":"hydroxyurea therapy","score":0.421999990940094},{"id":"https://openalex.org/keywords/health-care-access","display_name":"health care access","score":0.40799999237060547},{"id":"https://openalex.org/keywords/healthcare-access-disparities","display_name":"health care access disparities","score":0.36399999260902405},{"id":"https://openalex.org/keywords/patient-provider-communication","display_name":"patient-provider communication","score":0.414000004529953},{"id":"https://openalex.org/keywords/emergency-department-care","display_name":"emergency department care","score":0.4090000092983246},{"id":"https://openalex.org/keywords/patient-self-management","display_name":"patient self-management","score":0.33899998664855957},{"id":"https://openalex.org/keywords/patient-decision-making","display_name":"patient decision-making","score":0.32199999690055847},{"id":"https://openalex.org/keywords/health-insurance-coverage","display_name":"health insurance coverage","score":0.3199999928474426},{"id":"https://openalex.org/keywords/health-care-costs","display_name":"health care costs","score":0.328000009059906}],"concepts":[{"id":"https://openalex.org/C205545832","wikidata":"https://www.wikidata.org/wiki/Q17156455","display_name":"Young adult","level":2,"score":0.622516930103302},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.6111165881156921},{"id":"https://openalex.org/C194232998","wikidata":"https://www.wikidata.org/wiki/Q1606712","display_name":"Transition (genetics)","level":3,"score":0.49986767768859863},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.46009984612464905},{"id":"https://openalex.org/C2909537177","wikidata":"https://www.wikidata.org/wiki/Q4685925","display_name":"Adult care","level":3,"score":0.42179417610168457},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.32362139225006104},{"id":"https://openalex.org/C74909509","wikidata":"https://www.wikidata.org/wiki/Q10387","display_name":"Gerontology","level":1,"score":0.2715926766395569},{"id":"https://openalex.org/C54355233","wikidata":"https://www.wikidata.org/wiki/Q7162","display_name":"Genetics","level":1,"score":0.15307071805000305},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.13296818733215332},{"id":"https://openalex.org/C86803240","wikidata":"https://www.wikidata.org/wiki/Q420","display_name":"Biology","level":0,"score":0.13200145959854126},{"id":"https://openalex.org/C104317684","wikidata":"https://www.wikidata.org/wiki/Q7187","display_name":"Gene","level":2,"score":0.0}],"mesh":[{"descriptor_ui":"D000293","descriptor_name":"Adolescent","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000755","descriptor_name":"Anemia, Sickle Cell","qualifier_ui":"Q000208","qualifier_name":"ethnology","is_major_topic":false},{"descriptor_ui":"D000755","descriptor_name":"Anemia, Sickle Cell","qualifier_ui":"Q000401","qualifier_name":"mortality","is_major_topic":true},{"descriptor_ui":"D000755","descriptor_name":"Anemia, Sickle Cell","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":false},{"descriptor_ui":"D001541","descriptor_name":"Benin","qualifier_ui":"Q000208","qualifier_name":"ethnology","is_major_topic":false},{"descriptor_ui":"D001803","descriptor_name":"Blood Transfusion","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002423","descriptor_name":"Cause of Death","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005500","descriptor_name":"Follow-Up Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005845","descriptor_name":"Georgia","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":false},{"descriptor_ui":"D006297","descriptor_name":"Health Services Accessibility","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008685","descriptor_name":"Meteorological Concepts","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009026","descriptor_name":"Mortality","qualifier_ui":"Q000639","qualifier_name":"trends","is_major_topic":false},{"descriptor_ui":"D011446","descriptor_name":"Prospective Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D012675","descriptor_name":"Senegal","qualifier_ui":"Q000208","qualifier_name":"ethnology","is_major_topic":false},{"descriptor_ui":"D014505","descriptor_name":"Urban Population","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D015143","descriptor_name":"Philadelphia","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":false},{"descriptor_ui":"D019190","descriptor_name":"Iron Overload","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D019190","descriptor_name":"Iron Overload","qualifier_ui":"Q000401","qualifier_name":"mortality","is_major_topic":false},{"descriptor_ui":"D019468","descriptor_name":"Disease Management","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D055815","descriptor_name":"Young Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D060305","descriptor_name":"Transition to Adult Care","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true},{"descriptor_ui":"D062306","descriptor_name":"Geography, Medical","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":3,"locations":[{"id":"doi:10.1002/ajh.24718","doi":"https://doi.org/10.1002/ajh.24718","is_oa":true,"landing_page_url":"https://doi.org/10.1002/ajh.24718","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ajh.24718","source":{"id":"https://openalex.org/S199810014","display_name":"American Journal of Hematology","issn_l":"0361-8609","issn":["0361-8609","1096-8652"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-1","poland-140","russia-white-list-1"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Hematology","raw_type":"journal-article"},{"id":"pmid:28295532","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/28295532","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American journal of hematology","raw_type":"Comparative Study"},{"id":"pmh:oai:jdc.jefferson.edu:cardeza_foundation-1041","doi":null,"is_oa":true,"landing_page_url":"https://jdc.jefferson.edu/cardeza_foundation/41","pdf_url":null,"source":{"id":"https://openalex.org/S4210178181","display_name":"The Medicine Forum","issn_l":"2325-2863","issn":["2325-2863"],"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"journal"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Cardeza Foundation for Hematologic Research","raw_type":"article"}],"best_oa_location":{"id":"doi:10.1002/ajh.24718","doi":"https://doi.org/10.1002/ajh.24718","is_oa":true,"landing_page_url":"https://doi.org/10.1002/ajh.24718","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ajh.24718","source":{"id":"https://openalex.org/S199810014","display_name":"American Journal of Hematology","issn_l":"0361-8609","issn":["0361-8609","1096-8652"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-1","poland-140","russia-white-list-1"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Hematology","raw_type":"journal-article"},"sustainable_development_goals":[{"score":1.0,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W2591840668.pdf","grobid_xml":"https://content.openalex.org/works/W2591840668.grobid-xml"},"referenced_works_count":13,"referenced_works":["https://openalex.org/W1891741475","https://openalex.org/W1912736220","https://openalex.org/W2032423016","https://openalex.org/W2092573310","https://openalex.org/W2098388627","https://openalex.org/W2128068389","https://openalex.org/W2138719823","https://openalex.org/W2152076865","https://openalex.org/W2177708260","https://openalex.org/W2473332645","https://openalex.org/W2519717139","https://openalex.org/W2560833249","https://openalex.org/W2576799710"],"related_works":["https://openalex.org/W2519717139","https://openalex.org/W4404459591","https://openalex.org/W1979700466","https://openalex.org/W3197644973","https://openalex.org/W2969838010","https://openalex.org/W2156782953","https://openalex.org/W7993411","https://openalex.org/W6987673155","https://openalex.org/W2587895986","https://openalex.org/W2405661608"],"abstract_inverted_index":{"The":[0,67,260,321,405,517,580,624,659,674,793,836,890],"transition":[1,31,144,170,269,325,445,489,504,545,663,710,871],"of":[2,5,41,45,69,89,96,145,158,198,217,313,355,379,392,403,468,519,530,542,563,582,600,627,745,796,805,821,838,872,893,901,929,932,941,943,962,964,991],"medical":[3,42,146,152,173],"care":[4,147,356,675,696,911,969],"patients":[6,295,470,498,524,532,565,573,584,642,1009],"with":[7,58,91,98,136,162,324,435,525,739,758,785,864,877,938],"sickle":[8,286,449,459,472,903],"cell":[9,287,450,460,473,904],"disease":[10],"(SCD)":[11],"from":[12,133,148,222,240,357,446,491,1010],"pediatric":[13,359,448],"to":[14,51,101,139,150,171,188,229,278,281,292,336,361,374,388,456,493,648,656,678,735,755,782,879,918,1017],"adult":[15,151,172,285,290,365,458,880],"providers":[16,288],"represents":[17],"a":[18,137,155,699,703,822],"milestone":[19],"in":[20,104,116,125,182,185,194,202,209,224,232,266,283,296,310,369,395,523,585,589,602,609,612,616,666,669,681,721,729,747,771,799,809,814,828,833,840,850,853,859,896,909,914,951,956,967,973,978,988,1000],"their":[21,297],"lives.":[22],"Major":[23],"concerns":[24],"among":[25,56,127,348,594],"adolescents":[26,431,873],"and":[27,49,79,109,112,118,129,166,176,206,242,254,302,333,351,415,432,481,505,558,705,725,741,812,817,842,867,874,913,922,954,959,976],"young":[28,433,875],"adults":[29,103,434,876],"about":[30],"include":[32,412,717,750,763,1003],"taking":[33],"responsibility":[34],"for":[35,299,440],"self,":[36],"making":[37],"own":[38],"decisions,":[39],"cost":[40],"care,":[43,881],"fear":[44],"suboptimal":[46],"pain":[47,568],"management,":[48],"reluctance":[50],"leave":[52],"known":[53,754,781],"providers.":[54],"Survival":[55],"children":[57,90,97,128,203,210],"SCD":[59,99,180,436,543,649,740,746,878],"increased":[60,140,221,865],"progressively":[61],"over":[62,94],"the":[63,82,87,105,143,163,169,183,225,233,247,311,318,358,362,370,377,390,396,401,421,425,447,457,536,564,583,598,619,679,682,687,718,723,736,742,764,775,778,803,810,815,818,829,834,854,861,870,915,927,930,939,952,957,960,974,979,1014],"last":[64],"40":[65],"years.":[66,213,495],"advent":[68],"newborn":[70],"screening,":[71],"antibiotic":[72],"prophylaxis,":[73],"newer":[74],"vaccines,":[75],"safer":[76],"blood":[77,653],"transfusion,":[78],"hydroxyurea":[80,375],"are":[81,270,326,334,587,671,753,983,997],"major":[83,422,625],"factors":[84,338,862,987],"that":[85,179,246,262,399,597,608,640,650,752,767,802,899,1002,1006],"prolonged":[86],"survival":[88,126],"SCD.":[92],"Consequently,":[93],"95%":[95],"live":[100],"be":[102,279,732,756,783,886,919],"Western":[106],"world":[107],"(Europe":[108],"North":[110],"America)":[111],"other":[113],"countries":[114,1012],"especially":[115],"Jamaica":[117],"Brazil.1-3":[119],"Unfortunately,":[120],"despite":[121],"this":[122,255,264,305,384],"impressive":[123],"improvement":[124],"adolescents,":[130],"it":[131,315],"suffers":[132],"an":[134,307,708],"eclipse":[135],"setback":[138],"mortality":[141,181,219,248,267,661,868],"after":[142,168,251,268,444,503,539,544,622,662,869],"pediatrics":[149],"care.4":[153],"Thus,":[154],"high":[156],"risk":[157],"death":[159,508,520,601,628,851],"is":[160,306,316,596,637,664,768,789],"associated":[161,323,738,757,784,863],"time":[164],"during":[165,618],"shortly":[167],"programs.5":[174],"Hamideh":[175],"Alvarez6":[177],"reported":[178],"US":[184],"1999-2009":[186],"compared":[187],"1979-1998,":[189],"significantly":[190,949],"decreased":[191],"by":[192,200,207],"61%":[193],"infants":[195],"<1":[196],"year":[197,227,235],"age,":[199,218,921],"67%":[201],"aged":[204,211],"1-4years,":[205],"22-35%":[208],"5-19":[212],"After":[214],"19":[215],"years":[216,442,502,513,538,621],"rates":[220],"0.6":[223],"15-19":[226],"group":[228],"1.4/100":[230],"000":[231],"20-24":[234],"group.":[236],"A":[237],"recent":[238],"study":[239,837],"California":[241,841],"Georgia":[243,688,843],"also":[244,826],"documented":[245],"rate":[249,518,599,852],"increases":[250],"age":[252,487,506],"15":[253],"difference":[256],"persists":[257],"through":[258],"adulthood.7":[259],"reasons":[261],"cause":[263,626],"surge":[265],"not":[271,317,341,672,845],"well":[272],"known.":[273,673],"Initially":[274],"they":[275],"were":[276,437,578],"thought":[277,331],"due":[280,335,632,647],"difficulties":[282],"identifying":[284],"or":[289,345],"hematologists":[291],"enroll":[293],"transitioned":[294],"programs":[298],"regular":[300],"follow-up":[301],"management.":[303],"Although":[304],"important":[308,593,986,999],"issue":[309],"saga":[312],"transition,":[314],"only":[319],"reason.":[320],"problems":[322,737],"much":[327,605],"more":[328,733,769,786],"complex":[329],"than":[330,607,668],"before":[332],"multiple":[337],"including,":[339],"but":[340,831],"limited":[342],"to,":[343],"poor":[344],"inadequate":[346,353],"communication":[347],"patients,":[349],"parents":[350],"providers,":[352],"transfer":[354],"team":[360],"accepting":[363],"future":[364],"programs,":[366],"negative":[367],"experiences":[368],"emergency":[371,695],"rooms,":[372],"access":[373],"therapy,":[376],"country":[378,398],"residence,":[380],"etc.8,":[381],"9":[382,482,576],"In":[383,428,774,857],"correspondence,":[385],"we":[386,408],"wish":[387],"emphasize":[389],"role":[391],"geographical":[393,406],"variations":[394,982,996],"same":[397],"affect":[400],"outcome":[402],"transition.":[404,540,623],"regions":[407],"will":[409],"focus":[410],"on":[411],"Philadelphia,":[413,429],"PA10":[414],"Atlanta,":[416,722],"GA.11":[417],"Table":[418,590],"1":[419],"lists":[420],"differences":[423,849],"between":[424,569],"two":[426,683,855],"cities.":[427],"90":[430],"followed":[438],"prospectively":[439],"10":[441,501,537,620],"(1994-2004)":[443],"program":[451,711],"at":[452,462,488,507,692,907,946],"St.":[453],"Christopher":[454],"Hospital":[455],"center":[461],"Thomas":[463],"Jefferson":[464],"University":[465],"Hospital.":[466],"Sixty-five":[467],"these":[469,595,641],"had":[471,477,483,643,707],"anemia":[474],"(SS),":[475],"16":[476],"Hb":[478],"SC":[479],"disease,":[480,788],"sickle-\u03b2+-Thalassemia":[484],"(S-\u03b2+-thal).":[485],"Their":[486],"varied":[490],"18":[492],"25":[494],"Twenty":[496],"(22.2%)":[497],"died":[499,534],"within":[500,535],"was":[509,521,604,629,807,825,935,948,971],"24.9":[510],"\u00b1":[511],"2.95":[512],"(range":[514],"23-26":[515],"years).":[516],"highest":[522,808,827,950,972],"SS":[526],"where":[527],"17":[528],"out":[529],"65":[531],"(26%)":[533],"Complications":[541],"included":[546],"stroke,":[547],"acute":[548,902,910,968],"chest":[549],"syndrome,":[550],"avascular":[551],"necrosis,":[552],"leg":[553],"ulcers,":[554],"anxiety,":[555],"depression,":[556],"priapism":[557],"multi-organ":[559],"failure.":[560],"About":[561],"one-third":[562],"developed":[566],"persistent":[567],"vaso-occlusive":[570],"crises.":[571],"Nineteen":[572],"(10":[574],"males,":[575],"females)":[577],"employed.":[579],"demographic":[581],"Atlanta":[586,603,613,667,730,748],"shown":[588],"1.":[591],"Most":[592],"lower":[606,665],"Philadelphia:":[610],"5.8%":[611],"versus":[614],"22.2%":[615],"Philadelphia":[617,670,776],"iron":[630,657],"overload":[631],"chronic":[633,644],"organ":[634,645],"damage.":[635],"It":[636],"most":[638,790],"likely":[639],"damage":[646],"required":[651],"frequent":[652],"transfusions":[654],"leading":[655],"overload.":[658],"reason":[660],"systems":[676],"available":[677],"youth":[680],"cities":[684],"differ":[685],"because":[686],"Comprehensive":[689],"Sickle":[690],"Center":[691],"Grady":[693],"provides":[694],"24":[697],"h":[698],"day":[700],"7":[701],"days":[702],"week":[704],"has":[706],"active":[709],"since":[712],"1985.":[713],"Other":[714],"possible":[715],"causes":[716],"warmer":[719],"weather":[720],"cultural":[724],"psychosocial":[726],"community":[727],"fabric":[728],"may":[731,749],"attentive":[734],"genetic":[743],"types":[744,762],"those":[751],"milder":[759],"disease.":[760],"These":[761,995],"Senegalese":[765],"haplotype":[766],"common":[770],"Southern":[772],"USA.":[773],"area":[777],"Benin":[779],"haplotype,":[780],"severe":[787],"common.":[791],"Notably,":[792],"Multicenter":[794,891],"Study":[795,892],"Hydroxyurea":[797,894],"(MSH)":[798,895],"SS12":[800,897],"showed":[801,898],"number":[804],"crises":[806],"Northeast":[811,830,953],"lowest":[813,832,955,977],"South":[816],"average":[819],"duration":[820],"painful":[823,905],"crisis":[824],"West.":[835],"deaths":[839],"did":[844],"show":[846],"any":[847],"significant":[848],"states.7":[856],"summary,":[858],"analyzing":[860,989],"morbidity":[866],"specific":[882],"geographic":[883,923],"issues":[884],"should":[885],"taken":[887],"into":[888],"consideration.":[889],"management":[900],"episodes":[906],"home,":[908],"facilities,":[912],"hospital,":[916],"seems":[917],"sex,":[920],"region":[924,936],"dependent.":[925],"Specifically,":[926],"choice":[928],"route":[931],"opioid":[933],"administration":[934],"dependent":[937],"frequency":[940,961],"utilization":[942,963],"oral":[944],"opioids":[945,966],"home":[947],"West":[958,975],"parenteral":[965],"facilities":[970],"Midwest.":[980],"Geographic":[981],"emerging":[984],"as":[985],"results":[990],"randomized":[992],"controlled":[993],"trials.13":[994],"specifically":[998],"trials":[1001],"rare":[1004],"diseases":[1005],"require":[1007],"enrolling":[1008],"many":[1011],"across":[1013],"globe.":[1015],"Nothing":[1016],"report.":[1018]},"counts_by_year":[{"year":2025,"cited_by_count":2},{"year":2021,"cited_by_count":1},{"year":2018,"cited_by_count":1}],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2017-03-16T00:00:00"}
