{"id":"https://openalex.org/W2425390775","doi":null,"title":"Characteristics of a benign subtype of dense deposit disease: comparison with the progressive form of this disease.","display_name":"Characteristics of a benign subtype of dense deposit disease: comparison with the progressive form of this disease.","publication_year":1983,"publication_date":"1983-10-01","ids":{"openalex":"https://openalex.org/W2425390775","mag":"2425390775","pmid":"https://pubmed.ncbi.nlm.nih.gov/6556977"},"language":"en","primary_location":{"id":"pmid:6556977","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/6556977","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clinical nephrology","raw_type":"Journal Article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":null,"display_name":"M Klein","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"M Klein","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5063620991","display_name":"S Poucell","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"S Poucell","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5084762320","display_name":"Gerald S. Arbus","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"G S Arbus","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5113543021","display_name":"Mary E. McGraw","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"M McGraw","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5113504154","display_name":"C. Phillips Rance","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"C P Rance","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":null,"display_name":"S J Yoon","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"S J Yoon","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5042022278","display_name":"Reuben Baumal","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"R Baumal","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":0,"institutions_distinct_count":0,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.9181,"has_fulltext":false,"cited_by_count":33,"citation_normalized_percentile":{"value":0.75241875,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":97},"biblio":{"volume":"20","issue":"4","first_page":"163","last_page":"71"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10993","display_name":"Complement system in diseases","score":0.9556000232696533,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T10993","display_name":"Complement system in diseases","score":0.9556000232696533,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T11029","display_name":"Renal Diseases and Glomerulopathies","score":0.04349999874830246,"subfield":{"id":"https://openalex.org/subfields/2727","display_name":"Nephrology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10697","display_name":"Vasculitis and related conditions","score":0.00019999999494757503,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/dense-deposit-disease","display_name":"dense deposit disease","score":0.9990000128746033},{"id":"https://openalex.org/keywords/end-stage-renal-disease","display_name":"end-stage renal disease","score":0.8059999942779541},{"id":"https://openalex.org/keywords/glomerular-basement-membrane","display_name":"glomerular basement membrane","score":0.7559999823570251},{"id":"https://openalex.org/keywords/electron-dense-deposits","display_name":"electron-dense deposits","score":0.824999988079071},{"id":"https://openalex.org/keywords/nephritic-syndrome","display_name":"nephritic syndrome","score":0.7979999780654907},{"id":"https://openalex.org/keywords/nephrotic-syndrome","display_name":"nephrotic syndrome","score":1.0},{"id":"https://openalex.org/keywords/proteinuria","display_name":"proteinuria","score":0.8500000238418579},{"id":"https://openalex.org/keywords/hematuria","display_name":"hematuria","score":0.8429999947547913},{"id":"https://openalex.org/keywords/complement-c3","display_name":"complement C3","score":0.7799999713897705},{"id":"https://openalex.org/keywords/factor-b","display_name":"factor B","score":0.8730000257492065},{"id":"https://openalex.org/keywords/c3-nephritic-factor","display_name":"C3 nephritic factor","score":0.9829999804496765},{"id":"https://openalex.org/keywords/complement-system","display_name":"complement system","score":0.5120000243186951},{"id":"https://openalex.org/keywords/kidney-biopsy","display_name":"renal biopsy","score":0.5730000138282776}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.923029899597168},{"id":"https://openalex.org/C2778930706","wikidata":"https://www.wikidata.org/wiki/Q504790","display_name":"Nephrotic syndrome","level":2,"score":0.7334941625595093},{"id":"https://openalex.org/C2777910003","wikidata":"https://www.wikidata.org/wiki/Q1707292","display_name":"Asymptomatic","level":2,"score":0.6732067465782166},{"id":"https://openalex.org/C2779147130","wikidata":"https://www.wikidata.org/wiki/Q2074424","display_name":"Nephritic syndrome","level":4,"score":0.6223291158676147},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.6149566769599915},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.6080105304718018},{"id":"https://openalex.org/C2777785397","wikidata":"https://www.wikidata.org/wiki/Q492194","display_name":"Group B","level":2,"score":0.5908174514770508},{"id":"https://openalex.org/C2779561371","wikidata":"https://www.wikidata.org/wiki/Q570197","display_name":"Proteinuria","level":3,"score":0.5597986578941345},{"id":"https://openalex.org/C2780678043","wikidata":"https://www.wikidata.org/wiki/Q743241","display_name":"Group A","level":2,"score":0.5373574495315552},{"id":"https://openalex.org/C182629451","wikidata":"https://www.wikidata.org/wiki/Q18251054","display_name":"Complement factor B","level":4,"score":0.4314672350883484},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.33476996421813965},{"id":"https://openalex.org/C2780091579","wikidata":"https://www.wikidata.org/wiki/Q9377","display_name":"Kidney","level":2,"score":0.3055676221847534},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.2098684012889862},{"id":"https://openalex.org/C111684460","wikidata":"https://www.wikidata.org/wiki/Q334848","display_name":"Complement system","level":3,"score":0.1909348964691162},{"id":"https://openalex.org/C159654299","wikidata":"https://www.wikidata.org/wiki/Q79460","display_name":"Antibody","level":2,"score":0.0}],"mesh":[{"descriptor_ui":"D002648","descriptor_name":"Child","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002675","descriptor_name":"Child, Preschool","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D003176","descriptor_name":"Complement C3","qualifier_ui":"Q000032","qualifier_name":"analysis","is_major_topic":false},{"descriptor_ui":"D003178","descriptor_name":"Complement C3 Nephritic Factor","qualifier_ui":"Q000032","qualifier_name":"analysis","is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005921","descriptor_name":"Glomerulonephritis","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D005921","descriptor_name":"Glomerulonephritis","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D005921","descriptor_name":"Glomerulonephritis","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":true},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007678","descriptor_name":"Kidney Glomerulus","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D007678","descriptor_name":"Kidney Glomerulus","qualifier_ui":"Q000648","qualifier_name":"ultrastructure","is_major_topic":true},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008854","descriptor_name":"Microscopy, Electron","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009404","descriptor_name":"Nephrotic Syndrome","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D009404","descriptor_name":"Nephrotic Syndrome","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":true},{"descriptor_ui":"D011415","descriptor_name":"Complement Factor B","qualifier_ui":"Q000032","qualifier_name":"analysis","is_major_topic":false}],"locations_count":2,"locations":[{"id":"pmid:6556977","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/6556977","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clinical nephrology","raw_type":"Journal Article"},{"id":"mag:2425390775","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/6556977","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":"PubMed","raw_type":null}],"best_oa_location":null,"sustainable_development_goals":[{"score":0.98580002784729,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Observational Study","id":"https://openalex.org/study-designs/observational-study"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W2381989923","https://openalex.org/W2115104000","https://openalex.org/W2094340679","https://openalex.org/W2105335062","https://openalex.org/W2108448935","https://openalex.org/W2385229322","https://openalex.org/W4248683811","https://openalex.org/W2369277813","https://openalex.org/W2079527864","https://openalex.org/W4206864283"],"abstract_inverted_index":{"Pathologic,":[0],"clinical":[1,104],"and":[2,55,90,100,122,131,139,142,163,166,187,200],"serum":[3,46,153,194],"complement":[4],"studies":[5,174],"were":[6,18],"performed":[7],"on":[8],"18":[9],"patients":[10,17,26,42,59,77,92,110,133,157,178],"with":[11,60,94,112,179],"dense":[12],"deposit":[13],"disease":[14],"(DDD).":[15],"The":[16],"divided":[19],"into":[20],"3":[21],"groups:":[22],"group":[23,39,56,88,108,129,155],"A":[24,89,130],"(10":[25],"who":[27,43],"developed":[28,44],"end-stage":[29],"renal":[30,64],"failure":[31],"within":[32,48],"2.9":[33],"+/-":[34,50,68,120],"1.0":[35],"years":[36,52,70],"of":[37,53,63,71,137,145,154,161,169,196],"onset)":[38,54],"B":[40,91,132,141,165,199],"(3":[41],"elevated":[45],"creatinines":[47],"6.8":[49],"4.8":[51],"C":[57,109,156],"(5":[58],"no":[61],"evidence":[62],"insufficiency":[65],"after":[66],"11.0":[67],"1.4":[69],"follow-up).":[72],"Renal":[73],"biopsies":[74],"from":[75,128],"all":[76],"showed":[78],"intramembranous,":[79],"electron-dense":[80],"deposits":[81],"in":[82],"glomerular":[83],"capillary":[84],"basement":[85],"membranes.":[86],"Most":[87],"presented":[93,111],"a":[95,114,124,184],"nephritic":[96,147],"and/or":[97],"nephrotic":[98,115],"syndrome":[99,116],"followed":[101,123],"an":[102],"active":[103],"course.":[105,126],"In":[106,151],"contrast,":[107,152],"either":[113],"or":[117],"asymptomatic":[118],"proteinuria":[119],"hematuria":[121],"benign":[125,185],"Sera":[127],"contained":[134,158],"reduced":[135],"concentrations":[136],"C3":[138,146,162,170,201],"factor":[140,148,164,198],"large":[143],"amounts":[144,160],"(NeF)":[149],"activity.":[150,172,203],"normal":[159],"low":[167],"levels":[168,195],"NeF":[171,202],"These":[173],"show":[175],"that":[176,188],"some":[177],"DDD":[180],"(group":[181],"C)":[182],"have":[183],"illness":[186],"they":[189],"can":[190],"be":[191],"identified":[192],"by":[193],"C3,":[197]},"counts_by_year":[{"year":2018,"cited_by_count":1},{"year":2013,"cited_by_count":2},{"year":2012,"cited_by_count":3}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
