{"id":"https://openalex.org/W2419089890","doi":null,"title":"[Undiagnosed hereditary angioedema in a patient undergoing emergency caesarean section].","display_name":"[Undiagnosed hereditary angioedema in a patient undergoing emergency caesarean section].","publication_year":2012,"publication_date":"2012-12-01","ids":{"openalex":"https://openalex.org/W2419089890","mag":"2419089890","pmid":"https://pubmed.ncbi.nlm.nih.gov/23362781"},"language":"ja","primary_location":{"id":"pmid:23362781","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/23362781","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Masui. The Japanese journal of anesthesiology","raw_type":"Case Reports"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5062377313","display_name":"Yukihiko Tomita","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210111404","display_name":"National Cerebral and Cardiovascular Center","ror":"https://ror.org/01v55qb38","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210111404"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"Yukihiko Tomita","raw_affiliation_strings":["Department of Anesthesiology, National Cerebral and Cardiovascular Center, Suita 565-0873"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Anesthesiology, National Cerebral and Cardiovascular Center, Suita 565-0873","institution_ids":["https://openalex.org/I4210111404"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5110716072","display_name":"Masataka Kamei","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Masataka Kamei","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5084702213","display_name":"Satoshi Jyujou","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Satoshi Jyujou","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5013002234","display_name":"Chinami Horiuchi","orcid":"https://orcid.org/0000-0002-3175-9015","observed_orcids":["https://orcid.org/0000-0002-3175-9015"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Chinami Horiuchi","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5063804607","display_name":"Shinji Katsuragi","orcid":"https://orcid.org/0000-0003-1651-1561","observed_orcids":["https://orcid.org/0000-0003-1651-1561","https://orcid.org/0009-0004-1609-1995"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Shinji Katsuragi","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5110405428","display_name":"Yoshihiko Onishi","orcid":"https://orcid.org/0000-0003-0510-3829","observed_orcids":["https://orcid.org/0000-0003-0510-3829"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Yoshihiko Onishi","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":0,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"61","issue":"12","first_page":"1376","last_page":"9"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11917","display_name":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11917","display_name":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10993","display_name":"Complement system in diseases","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T11280","display_name":"Hemophilia Treatment and Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/hereditary-angioedema","display_name":"hereditary angioedema","score":0.9990000128746033},{"id":"https://openalex.org/keywords/emergency-cesarean-section","display_name":"emergency cesarean section","score":0.9670000076293945},{"id":"https://openalex.org/keywords/lip-swelling","display_name":"lip swelling","score":0.6990000009536743},{"id":"https://openalex.org/keywords/upper-airway-obstruction","display_name":"upper airway obstruction","score":0.8180000185966492},{"id":"https://openalex.org/keywords/c1-inhibitor","display_name":"C1 inhibitor","score":0.7870000004768372},{"id":"https://openalex.org/keywords/complement-c4","display_name":"complement C4","score":0.8420000076293945},{"id":"https://openalex.org/keywords/c1-inhibitor-replacement-therapy","display_name":"C1 inhibitor replacement therapy","score":0.953000009059906},{"id":"https://openalex.org/keywords/neuraxial-block","display_name":"neuraxial blockade","score":0.9279999732971191},{"id":"https://openalex.org/keywords/surgical-complications","display_name":"surgical complications","score":0.4300000071525574}],"concepts":[{"id":"https://openalex.org/C2777788586","wikidata":"https://www.wikidata.org/wiki/Q2096745","display_name":"Hereditary angioedema","level":2,"score":0.9612617492675781},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8943732976913452},{"id":"https://openalex.org/C2780886150","wikidata":"https://www.wikidata.org/wiki/Q152234","display_name":"Edema","level":2,"score":0.5938130617141724},{"id":"https://openalex.org/C2910317908","wikidata":"https://www.wikidata.org/wiki/Q152234","display_name":"Laryngeal Edema","level":3,"score":0.579267680644989},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.5272026658058167},{"id":"https://openalex.org/C2779121184","wikidata":"https://www.wikidata.org/wiki/Q1166142","display_name":"Erythema","level":2,"score":0.5130749940872192},{"id":"https://openalex.org/C2778333281","wikidata":"https://www.wikidata.org/wiki/Q4330029","display_name":"Airway obstruction","level":3,"score":0.49989867210388184},{"id":"https://openalex.org/C2778445469","wikidata":"https://www.wikidata.org/wiki/Q10658237","display_name":"Neuraxial blockade","level":3,"score":0.4973502457141876},{"id":"https://openalex.org/C105922876","wikidata":"https://www.wikidata.org/wiki/Q1423981","display_name":"Airway","level":2,"score":0.4798980951309204},{"id":"https://openalex.org/C81182388","wikidata":"https://www.wikidata.org/wiki/Q353963","display_name":"Complication","level":2,"score":0.44220951199531555},{"id":"https://openalex.org/C2777995640","wikidata":"https://www.wikidata.org/wiki/Q1129007","display_name":"Angioedema","level":2,"score":0.42454782128334045},{"id":"https://openalex.org/C42219234","wikidata":"https://www.wikidata.org/wiki/Q131130","display_name":"Anesthesia","level":1,"score":0.4031158983707428},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.20342105627059937},{"id":"https://openalex.org/C2992886682","wikidata":"https://www.wikidata.org/wiki/Q282736","display_name":"Spinal anesthesia","level":2,"score":0.0}],"mesh":[{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002585","descriptor_name":"Cesarean Section","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true},{"descriptor_ui":"D004630","descriptor_name":"Emergencies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D050718","descriptor_name":"Complement C1 Inhibitor Protein","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D054179","descriptor_name":"Angioedemas, Hereditary","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D054179","descriptor_name":"Angioedemas, Hereditary","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false}],"locations_count":2,"locations":[{"id":"pmid:23362781","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/23362781","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Masui. The Japanese journal of anesthesiology","raw_type":"Case Reports"},{"id":"mag:2419089890","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/23362781","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":"PubMed","raw_type":null}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":1.0,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W2468605174","https://openalex.org/W4288063922","https://openalex.org/W2076257077","https://openalex.org/W2058726165","https://openalex.org/W2062934486","https://openalex.org/W2182483767","https://openalex.org/W2939842697","https://openalex.org/W2324625631","https://openalex.org/W1979037729","https://openalex.org/W2396331101"],"abstract_inverted_index":{"Hereditary":[0],"angioedema":[1],"(HAE)":[2],"is":[3,27,52],"characterized":[4],"by":[5],"acute,":[6],"recurrent":[7],"attacks":[8],"of":[9,23,34,45,72,80,94,152,161,167,185],"localized":[10],"edema.":[11],"Surgical":[12],"procedures,":[13],"trauma,":[14],"and":[15,117,135,158,192],"infections":[16],"have":[17],"been":[18],"considered":[19],"as":[20,70],"potential":[21],"triggers":[22],"HAE.":[24],"Although":[25],"HAE":[26,36,58,96,144,181],"a":[28,92,165],"rare":[29],"genetic":[30],"disorder,":[31],"approximately":[32],"50-60%":[33],"all":[35],"patients":[37,59],"are":[38,83],"involved":[39],"with":[40,180],"at":[41,111],"least":[42],"one":[43],"occurrence":[44],"upper":[46],"airway":[47,50],"obstruction.":[48],"The":[49,200],"trouble":[51],"the":[53,125,168],"most":[54],"life-threating":[55],"complication":[56],"in":[57,139],"because":[60],"HAE-related":[61],"edema":[62],"does":[63],"not":[64],"respond":[65],"to":[66,87,124,141],"typical":[67],"treatment,":[68],"such":[69],"administration":[71],"epinephrine,":[73],"antihistamines,":[74],"or":[75],"glucocorticoids.":[76],"Indeed,":[77],"mortality":[78],"rates":[79],"laryngeal":[81],"attack":[82],"estimated":[84],"around":[85],"25%":[86],"40%.":[88],"Here":[89],"we":[90,149],"describe":[91],"case":[93],"undiagnosed":[95],"patient":[97,201],"undergoing":[98],"emergency":[99],"caesarean":[100],"section":[101],"under":[102],"neuraxial":[103],"blockade.":[104],"A":[105],"31-year-old":[106],"woman":[107],"showed":[108,174],"multiple":[109],"regions":[110],"her":[112,189],"lip":[113,120,190],"margin":[114],"during":[115,134],"surgery":[116],"rapidly":[118],"developed":[119],"swelling":[121,191],"after":[122,136,210],"admission":[123],"ward.":[126],"Neither":[127],"respiratory":[128],"nor":[129],"hemodynamic":[130],"instability":[131],"was":[132,202],"found":[133],"surgery.":[137,211],"Immediately,":[138],"order":[140],"assess":[142],"whether":[143],"caused":[145],"these":[146],"dermatological":[147],"manifestations,":[148],"measured":[150],"values":[151],"both":[153],"complement":[154,169],"component":[155],"4":[156],"(C4)":[157],"functional":[159],"activity":[160],"C1-esterase":[162],"inhibitor":[163],"(C1-inh),":[164],"protein":[166],"system.":[170],"These":[171],"laboratory":[172],"data":[173],"low":[175],"levels,":[176],"which":[177],"were":[178],"compatible":[179],"definition.":[182],"After":[183],"commencement":[184],"C1-inhibitor":[186],"replacement":[187],"therapy,":[188],"erythema":[193],"gradually":[194],"disappeared":[195],"without":[196],"adverse":[197],"drug":[198],"reactions.":[199],"finally":[203],"discharged":[204],"from":[205],"our":[206],"institution":[207],"10":[208],"days":[209]},"counts_by_year":[],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2016-06-24T00:00:00"}
